scholarly journals Isolated Myocardial Infarction of the Right Ventricle Complicated by Myocardial Rupture with Cardiac Tamponade in a Female Patient with Arrhythmogenic Right Ventricular Dysplasia

Kardiologiia ◽  
2019 ◽  
Vol 59 (6) ◽  
pp. 86-90
Author(s):  
M. N. Baranova ◽  
M. Yu. Ogarkov ◽  
A. E. Skripchenko ◽  
F. N. Chavdar ◽  
A. Yu. Yankin ◽  
...  
Keyword(s):  
Myocardial Infarction ◽  
Right Ventricle ◽  
Right Ventricular ◽  
Cardiac Tamponade ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
Transmural Infarction ◽  
Right Ventricular Dysplasia ◽  
Anterolateral Wall ◽  
Myocardial Rupture ◽  
The Right

Arrhythmogenic dysplasia of the right ventricle is a rare pathology of the myocardium, the diagnosis of which is difficult. Isolated myocardial infarction of the right ventricle occurs and is diagnosed extremely rarely. In this article we describe a case of arrhythmogenic right ventricular dysplasia, complicated by transmural infarction of the anterolateral wall of the right ventricle, myocardial rupture, and cardiac tamponade.

scholarly journals Cardiac Magnetic Resonance Imaging (MRI) Findings in Arrhythmogenic Right Ventricular Dysplasia (ARVD) Compared with Echocardiography

2018 ◽  
Vol 6 (3) ◽  
pp. 80 ◽  
Author(s):  
Marzie Motevali ◽  
Zainab Siahi ◽  
Ali Mohammadzadeh ◽  
Akbar Sangi
Keyword(s):  
Magnetic Resonance Imaging ◽  
Magnetic Resonance ◽  
Right Ventricle ◽  
Right Ventricular ◽  
Cardiac Mri ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
Resonance Imaging ◽  
Mri Findings ◽  
Right Ventricular Dysplasia ◽  
The Right

Arrhythmogenic right ventricular dysplasia (ARVD) is an abnormality in the right side of the heart that may lead to sudden death. The study aims to compare cardiac MRI (magnetic resonance imaging findings) with echocardiography in patients with ARVD. For the cross-sectional study, patients with ARVD that were diagnosed using Task Force criteria were included, and their cardiac MRI findings were evaluated. Additionally, the right ventricle was divided into three levels—basal, middle, and apical—and each of them was also subdivided into three secondary segments. Gadolinium enhancement was evaluated in each segment. Overall, 39 patients were studied. Thirty-one patients (81%) were men. The average age of female and male patients was 37.8 ± 4.6 and 32.48 ± 5.8, respectively. The average ejection fraction found was 43 ± 9.4 and 42.8 ± 8.5% by MRI and echocardiography, respectively. Additionally, 46 and 35.8% of the patients had hypokinesia in the right ventricle, found based on MRI and echocardiography, respectively. The right ventricular aneurysm was found in 20.5 and 5.1% of patients based on MRI and echocardiography, respectively. The cardiac MRI managed to diagnose some cases which echocardiography was not able to detect. Thus, MRI plays an important role in presenting diagnostic data for the management of patients with ARVD and also making the diagnosis in suspicious patients definitive.

Marked Lipomatous Infiltration of the Right Ventricle: MRI Findings in Relation to Arrhythmogenic Right Ventricular Dysplasia

2007 ◽  
Vol 188 (5) ◽  
pp. W423-W427 ◽  
Author(s):  
Robson Macedo ◽  
Kalpana Prakasa ◽  
Crystal Tichnell ◽  
Frank Marcus ◽  
Hugh Calkins ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Right Ventricular ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
Mri Findings ◽  
Right Ventricular Dysplasia ◽  
The Right

scholarly journals A clinical case of arrhythmogenic right ventricular dysplasia

2021 ◽  
Vol 2 (1) ◽  
pp. 109-114
Author(s):  
E. V. Solovyoval ◽  
N. A. Popova ◽  
T. V. Vlasoval ◽  
M. L. Gorbunova ◽  
L. N. Antsygina
Keyword(s):  
Right Ventricular ◽  
Clinical Case ◽  
Ventricular Myocardium ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
Myocardial Diseases ◽  
Conduction Disorders ◽  
Right Ventricular Dysplasia ◽  
Common Causes ◽  
The Right

Arhythmogenic right ventricular dysplasia (ADP) refers to hereditary myocardial diseases, in which there are structural and functional disorders in the right ventricular myocardium, causing rhythm and conduction disorders, including fatal ventricular arrhythmias. ADP is considered one of the most common causes of sudden cardiac death in young people and people who are engaged in sports. However, in practice, there are cases of this disease in people of an older age category. Diagnosis of ADP is still difficult due to the possible long-term asymptomatic course of the disease. The article describes a clinical case of ADP in a 48-year-old man.

scholarly journals Sudden Death in a Middle-Aged Gentleman

2020 ◽  
Vol 5 (1) ◽  
Author(s):  
Selvaraja GR
Keyword(s):  
Right Ventricular ◽  
Cause Of Death ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
Late Presentation ◽  
Prior History ◽  
Medical Illness ◽  
Unexpected Death ◽  
Right Ventricular Dysplasia ◽  
Fatty Replacement ◽  
The Right

A sudden unexpected death in a healthy individual often leads to panic within a community and it’s frequently associated with malicious mischief. Suicide, infections, genetic or congenital abnormalities may well lead to sudden deaths. All these possibilities are vital in determining the cause of death and facilitate investigation, hence must be considered judiciously. Here, we report a case of a 49-year-old gentleman without underlying medical illness or prior history of heart disease found dead in his home by his wife. Postmortem and histopathology findings determined the cause of death. External examination revealed no obvious injuries whereas 50% narrowing was disclosed in the left anterior descending artery at internal examination. Histology finding showed fibro-fatty replacement of the right ventricle myocardium. Toxicological analyses were unrewarding. It was concluded that the cause of death was arrhythmogenic right ventricular dysplasia. In conclusion, the findings of the forensic autopsy and histopathology facilitated the investigation and established the cause of death. The cause of death attributed to arrhythmogenic right ventricular dysplasia (ARVD). This case demonstrates ARVD can have a late presentation and it should always be borne in mind as a potential cause of death, necessitating this case report.

Abstract 1768: Magnetic Resonance Imaging Reveals Novel Phenotypic Expression of Desmosomal Mutation in First-Degree Relatives of Patients with Arrhythmogenic Right Ventricular Dysplasia (ARVD). Prevalence and Clinical Significance in Patients Evaluated For ARVD.

Circulation ◽  
2007 ◽  
Vol 116 (suppl_16) ◽  
Author(s):  
Harikrishna Tandri ◽  
Darshan Dalal ◽  
Aditya Jain ◽  
Daniel P Judge ◽  
Theodore Abraham ◽  
...  
Keyword(s):  
Family History ◽  
Right Ventricular ◽  
Phenotypic Expression ◽  
Clinical History ◽  
Arrhythmogenic Right Ventricular Dysplasia ◽  
First Degree Relatives ◽  
Group 4 ◽  
Right Ventricular Dysplasia ◽  
History Of ◽  
The Right

Background: In this report we present the prevalence and significance of a novel MRI abnormality that we identified in desmosomal mutation positive asymptomatic relatives of arrhythmogenic right ventricular dysplasia (ARVD) patients. Methods: MRI of 38 first-degree relatives was analyzed for abnormalities blinded to the mutation status. Focal crinkling of the right ventricle (accordion sign) was observed in 15/25 mutation positive vs. 0/13 mutation negative patients. The presence of this finding was sought in 207 patients evaluated for ARVD blinded to clinical history and was correlated with electrophysiologic findings. Results: Mean age of the population was 32±16, 61% had a family history of ARVD. Based on non-invasive testing the 207 patients were classified into 4 groups 1) 106 normal, 2) 57 Idiopathic ventricular tachycardia (VT), 3) 33 probable ARVD, 4) 11 definite ARVD. A family history of ARVD was present in 74%, 0%, 67% and 36% respectively. 43 patients had the “accordion sign” and the prevalence in the four groups was 10%, 5%, 70% and 100% respectively. The abnormality was seen in the sub-tricuspid region in 62%, outflow tract in 30% in both regions in 8%. After excluding group 4, 48% of patients with the accordion sign had T wave inversion’s beyond V1 compared with 7% of those without the sign (p<0.001). During electrophysiologic testing, reentrant VT could be induced in 44% (7/16) of patients with accordion sign compared to 2% (1/48) without the sign (p<0.01). Conclusion: Focal crinkling of the RV termed “Accordion sign” may represent an early manifestation of ARVD that correlates with mutation positive status and predicts inducibility of ventricular arrhythmias.

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