Thoracic Ectopia Cordis

Ectopia Cordis is a rare congenital anomaly characterized by partial or complete displacement of the heart outside the thoracic cavity with an estimated incidence of 5 to 8 per million live births We report a case of a 22-year-old primigravida, unbooked and immunized woman, with no relevant family or personal history, in which the prenatal fetal ultrasound, performed at 34 weeks of gestation, revealed a defect of the anterior chest wall with exteriorization of the heart. Baby was Pre-term 34 week by date but term by modified Ballard scoring, male weighing 2.4 kg delivered by lower segment caesarean section. Baby had complete thoracic ectopia cordis with large defect in anterior wall of chest and sternum was absent.

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Ectopia cordis: a case report

Revista Brasileira de Saúde Materno Infantil ◽

10.1590/s1519-38292014000300010 ◽

2014 ◽

Vol 14 (3) ◽

pp. 287-290 ◽

Cited By ~ 2

Author(s):

Gonçalo Filipe Infante Mesquita Dias ◽

Ana Vanessa dos Reis Santos ◽

Cátia Filipa Cabrita Paixão Martins ◽

Ana Paula Duarte Ferreira ◽

Joaquim Marques Dinis da Fonseca

Keyword(s):

Congenital Heart Disease ◽

Heart Disease ◽

Congenital Heart ◽

Fetal Echocardiography ◽

Anterior Chest Wall ◽

Personal History ◽

Pathological Examination ◽

Fetal Ultrasound ◽

Ectopia Cordis ◽

Severe Congenital Heart Disease

Introduction: ectopia cordis is a rare congenital malformation, with an estimated incidence of 5 to 8 per million live births. It is defined as a malformation in which the heart is located in an extra-thoracic position. Ectopia cordis may occur as an isolated malformation or associated with other anomalies such as omphalocele, congenital heart disease or integrating Cantrell syndrome. The size and location of the defect influence the prognosis. Description: we report a case of a 24-year-old nulliparous woman, with no relevant family or personal history, in which the prenatal fetal ultrasound, performed at 21 weeks of gestation, revealed adefect of the anterior chest wall with exteriorization of the heart. Discussion: fetal echocardiography revealed a severe congenital heart disease. The parents decided to continue the pregnancy, after being duly informed by a multidisciplinary team. Delivery occurred at 37 weeks of gestation but the female newborn died one hour afterwards. Pathological examination confirmed the sonographic findings.

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A study of cases of rupture uterus in a tertiary medical college of Jharkhand, India

International Journal of Reproduction Contraception Obstetrics and Gynecology ◽

10.18203/2320-1770.ijrcog20172350 ◽

2017 ◽

Vol 6 (6) ◽

pp. 2553

Author(s):

Samarina Kamal ◽

Shashibala Singh

Keyword(s):

Caesarean Section ◽

Health Care Providers ◽

Uterine Rupture ◽

Anterior Wall ◽

Traumatic Rupture ◽

Care Providers ◽

Lower Segment ◽

Obstructed Labor ◽

Lower Segment Caesarean Section ◽

Gynecology And Obstetrics

Background: Uterine rupture is a grave condition which is almost fatal for fetus. The most common risk factor for the uterine rupture is previous uterine surgery. Other major factors are obstructed labor, multiparity, use of uterotonic drugs, placenta percreta and rarely intrauterine manipulations such as internal podalic version and breech extraction.Methods: This study was conducted over a period from March 2014 to September 2015, in the Department of Gynecology and Obstetrics, RIMS Ranchi, Jharkhand. All cases of rupture uterus, who were either admitted with or who developed this complication in the hospital, were included in the study.Results: There were 80 cases of rupture uterus out of 10474 deliveries. The incidence of rupture uterus was more (97.5%) in cases who had no previous antenatal checkup at all. Most of cases of previous caesarean section scar rupture during labour was lower segment caesarean section scar (94.11%). The most common causes of traumatic rupture were injudicious use of oxytocics (75%). Majority of cases of rupture uterus were of complete type (96.25%). The most frequent site of rupture was in the anterior wall of lower segment in 68.75% of cases. The maternal mortality rate cases of rupture uterus were 3.75%.Conclusions: Proper antenatal care and updated training courses of health care providers should be stressed to prevent this catastrophic but avoidable complication.

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Complete Thoracic Ectopia Cordis, Dilemma of the Outcome: A Case Report

Surgical Case Reports ◽

10.31487/j.scr.2021.04.05 ◽

2021 ◽

pp. 1-4

Author(s):

Mohammed J Aboud ◽

Noor M Abudi ◽

Haidar M Joudi ◽

Zeena M Joudi

Keyword(s):

Heart Diseases ◽

Management Strategies ◽

Anterior Chest Wall ◽

Thoracic Cavity ◽

Poor General Condition ◽

Ectopia Cordis ◽

Rare Congenital Abnormality ◽

Congenital Condition ◽

Optimal Evaluation ◽

Future Management

Background: Ectopia Cordis (EC) is a rare congenital condition where the heart is partially or completely lies outside the thoracic cavity (extrathoracic), uncovered by pericardium and skin. Many works of literature reported EC is a rare congenital abnormality with an incidence of about 5-8 per 1 million live births and includes about 0.1% of congenital heart diseases. Methods: This was a male baby, weighing 2.900 kg, received with cyanosis with a defect in the anterior chest wall and heart protruding out through it. On initial physical examination, split sternum with complete thoracic EC (beating outside the thoracic cavity with a complete absence of the pericardium with the apex pointing upwards) were reported. Results: The baby’s poor general condition did not allow further radiologic studies and echocardiography could not be performed. By the time, an arrangement had been planned for him to undergo cardiothoracic referral; unfortunately, he ran a downhill course and succumbed within 36 hours of life. Conclusion: The important for submitting such findings will assist our team: pediatric surgeons, obstetricians, pediatricians and, neonatal intensivists to develop future management strategies when they are enrolled or confronted with such cases, by improving the outcome through a precise workup design to provide the optimal evaluation, diagnosis, and management roadmaps of potential cases of EC.

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Successful pregnancy and delivery in a woman with achondroplasia

Journal of the Pakistan Medical Association ◽

10.47391/jpma.222 ◽

2020 ◽

pp. 1-9

Author(s):

Nasira Tasnim ◽

Madeeha Ghani ◽

Suresh Kumar ◽

Shumaila Naeem ◽

Sobia Luqman

Keyword(s):

Case Report ◽

Caesarean Section ◽

Regional Anaesthesia ◽

Antenatal Visit ◽

Lower Segment ◽

Successful Pregnancy ◽

Live Births ◽

Lower Segment Caesarean Section ◽

First Child ◽

Pregnancy And Delivery

Abstract Achondroplasia is a common form of dwarfism occurring in one out of 25,000 of live births. These patients present many problems during pregnancy and at the time of the delivery. The anaesthetist may also face several difficulties for both general and regional anaesthesia. The aim of this case report is to discuss various obstetric and anaesthetic considerations in such patients and ways to manage the difficulties. A 29-year-old woman expecting her first child, with achondroplasia —height of just 3’2’’ (98 centimetres) — at 31 weeks of gestation, presented to our OPD for antenatal visit on May 15, 2018. Her successful elective lower segment caesarean section was performed on June 25, 2018 at 37 weeks in view of contracted pelvis under general anaesthesia. Continuous...

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Term pregnancy with large anterior wall intramural fibroid: an intra-operative challenge

International Journal of Reproduction Contraception Obstetrics and Gynecology ◽

10.18203/2320-1770.ijrcog20191246 ◽

2019 ◽

Vol 8 (4) ◽

pp. 1696

Author(s):

Seema Mehrotra ◽

Urmila Singh ◽

Vandana Solanki ◽

Nidhi Shanker

Keyword(s):

Caesarean Section ◽

Anterior Wall ◽

Emergency Caesarean Section ◽

Fetal Mortality ◽

Term Pregnancy ◽

Lower Segment ◽

Mortality And Morbidity ◽

Lower Segment Caesarean Section ◽

Smooth Muscle Tumors ◽

Free Area

Leiomyomas are the most common benign smooth muscle tumors of the uterus. The incidence during pregnancy ranges between 1.6 to 10%. The management of fibroids encountered during caesarean section poses a therapeutic dilemma. We present a case of giant anterior wall lower segment leiomyoma complicating term pregnancy which posed a great surgical challenge. Myomectomy was performed before delivering the baby by lower segment caesarean section by locating the tumor free area using preoperative ultrasound. The tumor mass weighed 3kg. This case highlights the preoperative use of ultrasound in emergency caesarean section to avoid classical caesarean section and to prevent fetal mortality and morbidity by avoiding time consuming caesarean myomectomy before the delivery of the baby.

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Infection of Mycobacterium mageritense at surgical site: A first case report of India

Journal of Drug Delivery and Therapeutics ◽

10.22270/jddt.v9i1-s.2386 ◽

2019 ◽

Vol 9 (1-s) ◽

pp. 369-373 ◽

Cited By ~ 1

Author(s):

MANDAVA V RAO

Keyword(s):

Computed Tomography ◽

Case Report ◽

Soft Tissue ◽

Caesarean Section ◽

Urinary Bladder ◽

Anterior Wall ◽

Lower Segment ◽

Lower Segment Caesarean Section ◽

First Case ◽

Peritoneal Space

A 27 years old non diabetic, normotensive, female had undergone lower segment caesarean section (LSCS) with tubular ligation. She complained discharge at left side of stitch line after about 5 weeks of operation, and was treated with broad spectrum antibiotics. As she did not improve, first and second debridement was done in January and February 2017 and pyogenic cultures sent were sterile. Later she was advised for Multiple detector computed tomography (MDCT) in March 2017, which revealed accumulations in pre-peritoneal space of urinary bladder posteriorly and reached to anterior wall of uterus. This pus was from multiple sinuses and were sent for mycobacterial cultures which showed growth of MOTT- M.mageritense further identified by MALDI-TOF and supported by molecular technologies. After identification of this Non-tuberculosis mycobacteria (NTM). She was treated for the same and recovered completely after seven months of anti-NTM treatment. This is the first reported case of M. mageritense in skin and soft tissue in India. Literature also reports a few cases around the globe.

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