scholarly journals Ventral tethering in split cord malformation

2001 ◽  
Vol 10 (1) ◽  
pp. 1-11 ◽  
Author(s):  
Dachling Pang

Object The author studied the specific issue of ventral tethering in cases of type II split cord malformation (SCM). He also discussed the issue of ventral tethering in patients with type I SCM in whom a bony septum and dural sleeve have been resected. Methods Eleven (21%) of 52 patients with type II SCM were found to have a ventral fibrous septum tethering the hemicords to the ventral dura. Four categories of ventral septa were noted: 1) pure ventral intradural septa (three patients); 2) complete dorsoventral intradural septa (three patients); 3) dorsoventral septa continuous with a dermal sinus tract (two patients); and 4) ventral or complete septa continuous with ventral intestinal bands causing intestinal malrotation or diverticulum (three patients). Excluding one autopsy case, all 10 patients had symptoms or progressive neurological syndromes at diagnosis. Magnetic resonance imaging was completely ineffective, and computerized tomography (CT) myelography was only partially effective in detecting ventral tethering in 50% of cases. The only other positive predictor of ventral tethering is the association of dermal sinus tract and intestinal malformations. Combining this predictor with CT myelography, only 60% of the cases of ventral tethering could be suspected before surgery. Conclusions The author recommends examining all patients with type II SCM, and at surgery the ventral surface of the split length and reunion site should be thoroughly inspected to reveal a ventral band.

2020 ◽  
Vol 15 (1) ◽  
pp. 172
Author(s):  
JuanEsteban Muñoz Montoya ◽  
MarcialAnaya Jara ◽  
MaríaPaula Vargas Osorio ◽  
FernandoRueda Franco

2013 ◽  
Vol 2013 ◽  
pp. 1-3 ◽  
Author(s):  
Michael G. Fazio ◽  
Alyson M. Kil ◽  
Veronica J. Rooks ◽  
Timothy J. Biega

We report the use of diffusion-weighted magnetic resonance imaging to diagnose and manage a rare case of a symptomatic thoracic intramedullary congenital epidermoid cyst with associated dermal sinus in a girl. Congenital intramedullary epidermoid cysts with associated dermal sinuses are very rare occurrences and seldom present symptomatically in very young children. We present a case of a 32-month old with a draining dimpled skin lesion. Magnetic resonance images demonstrated an intramedullary epidermoid with a dorsal dermal sinus tract opening to the skin surface which was confirmed surgically. The patient was treated with debulking to prevent recurrent infection and progression of neurological symptoms. This case demonstrates the use of diffuse-weighted MRI to assist in the diagnosis and surgical management of an atypical presentation of a rare developmental abnormality, which is not well documented in the pediatric radiological literature. Failure to diagnosis may have significant neurological permanent debilitating consequences.


2003 ◽  
Vol 15 (1) ◽  
pp. 1-3 ◽  
Author(s):  
Niyazi Nefi Kara

The congenital dermal sinus is an abnormal epithelium-lined sinus tract between the skin surface and deeper tissues. It occurs during neurulation when the neural groove closes to form the neural tube on Day 26 of gestation and results from a failure of neuroectoderm to separate from the cutaneous ectoderm. The most frequent location is the lumbosacral area; an upper thoracic location is quite rare. This 37-year-old man presented with headache and numbness in both arms. No specific neurological findings were observed. Physical examination revealed a dimple at T-2. Radiography and magnetic resonance imaging of the thoracic spine revealed spina bifida at T1–3, a meningocele, and a dermal sinus tract complex. The treatment approach and outcome in this unusual case are presented.


2018 ◽  
Vol 15 (03) ◽  
pp. 152-154
Author(s):  
Megan B. Garcia ◽  
Anjali N. Kunz

Abstract Prevotella species are gram-negative anaerobic commensal bacteria of the oropharynx, which frequently cause periodontal disease but are otherwise rarely implicated in serious bacterial infections. Cranial dermoid cysts are benign neoplasms that grow along the planes of the embryonic neural tube closure. In infants, they most commonly present in frontal locations, including periorbital, nasal, and within the anterior fontanelle. Although dermoid cysts are slow growing, usually uncomplicated, and easily treated definitively with surgical excision, cranial cysts located on the midline are associated with a higher risk for persistent dermal sinus tract with intracranial extension of the tumor. We describe a case of a 10-month-old male patient with an occipital midline dermoid cyst with intracranial extension, infected with Prevotella melaninogenica, and complicated by intracranial abscess formation and meningitis.This case highlights two unusual disease entities: the uncommon occipital location of a dermoid cyst, and complications of that cyst caused by a serious bacterial infection with a normal oral flora. We discuss the recommendation for neuroimaging prior to surgical excision of a midline dermoid cyst, given the risk for dermal sinus tract with intracranial communication. We also discuss potential mechanisms for bacterial inoculation of this cyst with Prevotella melaninogenica. This pathogen has not previously been reported as a complication of dermoid cysts.


2006 ◽  
Vol 23 (5) ◽  
pp. 569-571 ◽  
Author(s):  
R. Shane Tubbs ◽  
Philip K. Frykman ◽  
Carroll M. Harmon ◽  
W. Jerry Oakes ◽  
John C. Wellons

Neurosurgery ◽  
2007 ◽  
Vol 61 (3) ◽  
pp. E661-E661 ◽  
Author(s):  
William J. Mack ◽  
Saadi Ghatan

Abstract OBJECTIVE Congenital dermal sinus tracts most frequently occur in the midline and are often associated with dermoid or epidermoid inclusion cysts. A lateral cranial origin is extremely rare and anatomically inconsistent with an etiology involving closure of the rostral neural tube during embryogenesis. CLINICAL PRESENTATION We describe the first case of a pterional cranial dermal sinus tract associated with a small epidermoid, with extension to the dura of the anterior cranial fossa. INTERVENTION The extra- and intracranial portions of the tract were visualized and resected with the use of an operating microscope. Pathological diagnosis confirmed dermal sinus tract. CONCLUSION We review the existing literature and address the developmental and clinical features pertinent to the management of cranial dermal sinus tracts, emphasizing the need for exploration of these potentially harmful lesions.


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