Camurati-Engelmann disease (progressive hereditary craniodiaphyseal dysplasia)

1978 ◽  
Vol 48 (1) ◽  
pp. 138-142 ◽  
Author(s):  
John K. Yen ◽  
Robert S. Bourke ◽  
A. John Popp ◽  
Carl R. Wirth
Keyword(s):  
Optic Nerve ◽  
Definitive Treatment ◽  
Content Type ◽  
X Ray ◽  
Metabolic Bone Disorder ◽  
Metabolic Bone ◽  
Bone Disorder ◽  
Craniodiaphyseal Dysplasia ◽  
Engelmann Disease ◽  
Fine Print

✓ In a patient with Camurati-Engelmann disease, orbital and optic nerve decompression resulted in improvement of papilledema. Subsequent x-ray films of the optic canals, however, revealed reconstitution of osseous optic canals bilaterally, and papilledema has returned in one eye. Definitive treatment of this dysplastic metabolic bone disorder rests in the control of rapid abnormal bone formation.

Pituitary apoplexy: a review and reappraisal

1972 ◽  
Vol 37 (3) ◽  
pp. 280-288 ◽  
Author(s):  
Richard L. Rovit ◽  
Jack M. Fein
Keyword(s):  
Myocardial Infarction ◽  
Acute Myocardial Infarction ◽  
Optic Nerve ◽  
Pituitary Tumor ◽  
Pituitary Apoplexy ◽  
Content Type ◽  
X Ray ◽  
Chromophobe Adenoma ◽  
Sudden Headache ◽  
Fine Print

✓ The authors report their experience with nine cases of acute pituitary apoplexy; eight had proven chromophobe adenomas, and two of these patients had the clinical stigmata of Cushing's syndrome. One patient who displayed acromegalic features was treated with x-ray, and no pathological specimen was obtained. The outstanding clinical features of acute pituitary apoplexy were sudden headache, depressed consciousness, ophthalmoplegia, meningismus, and signs of compression of the optic nerve or chiasma. Clinical or laboratory evidence of severe hypopituitarism was rare. The apoplectic syndrome was the first indication of the presence of a pituitary tumor in all nine cases. In one case anticoagulant therapy (for an acute myocardial infarction) appeared to have precipitated hemorrhage in an unrecognized chromophobe adenoma. The authors suggest that acute pituitary apoplexy is a surgical emergency resulting from sudden ischemia, necrosis, and hemorrhage when an expanding pituitary neoplasm has become impacted at the diaphragmatic notch.

Primary optic nerve sheath meningiomas

1989 ◽  
Vol 70 (1) ◽  
pp. 37-40 ◽  
Author(s):  
W. Craig Clark ◽  
Charles S. Theofilos ◽  
James C. Fleming
Keyword(s):  
Optic Nerve ◽  
Management Strategy ◽  
Optic Nerve Sheath ◽  
Definitive Treatment ◽  
Optimal Management ◽  
Tumor Removal ◽  
Content Type ◽  
Nerve Sheath ◽  
Optic Nerve Sheath Meningioma ◽  
Fine Print

✓ Between 1979 and 1987 the authors treated nine cases of primary optic nerve sheath meningioma. The definitive treatment for these lesions is surgical resection, although no single best plan for optimal management has been determined. The data indicate that only small anterior tumors may be removed with preservation of useful vision. With posterior circumferential tumors, there have been no cases of tumor removal with preservation of vision. A management strategy directed toward preservation of vision is discussed.

Visual changes after gamma knife surgery for optic nerve tumors

2005 ◽  
Vol 102 (Special_Supplement) ◽  
pp. 143-146 ◽  
Author(s):  
Yang Kwon ◽  
Jun Seok Bae ◽  
Jae Myung Kim ◽  
Do Hee Lee ◽  
Soon Young Kim ◽  
...  
Keyword(s):  
Optic Nerve ◽  
Gamma Knife ◽  
Gamma Knife Surgery ◽  
Optic Glioma ◽  
Content Type ◽  
Nerve Sheath ◽  
Optic Nerve Sheath Meningioma ◽  
Optic Nerve Tumors ◽  
Visual Changes ◽  
Fine Print

✓ Tumors involving the optic nerve (optic glioma, optic nerve sheath meningioma) are benign but difficult to treat. Gamma knife surgery (GKS) may be a useful treatment. The authors present data obtained in three such cases and record the effects of GKS.

Anterior sacral meningocele contiguous with a pelvic hamartoma

1984 ◽  
Vol 61 (1) ◽  
pp. 188-190 ◽  
Author(s):  
Eugene Leibowitz ◽  
William Barton ◽  
Parvis Sadighi ◽  
Jeffrey S. Ross
Keyword(s):  
Computerized Tomography ◽  
Content Type ◽  
Transabdominal Approach ◽  
X Ray ◽  
Anterior Sacral Meningocele ◽  
Fine Print

✓ A patient with an anterior sacral meningocele combined with a hamartoma was diagnosed with x-ray films, myelography, and computerized tomography. She was successfully operated on by a transabdominal approach.

Neuroepithelial cyst in the optic nerve

1987 ◽  
Vol 67 (1) ◽  
pp. 137-139 ◽  
Author(s):  
Alberto Isla ◽  
José Palacios ◽  
José M. Roda ◽  
Manuel Gutierrez ◽  
Cesáreo González ◽  
...  
Keyword(s):  
Optic Nerve ◽  
Computerized Tomography ◽  
Cystic Lesion ◽  
Histological Study ◽  
Content Type ◽  
Neuroepithelial Cyst ◽  
Loss Of Vision ◽  
Progressive Loss ◽  
Suprasellar Region ◽  
Fine Print

✓ A 34-year-old woman presented with progressive loss of vision in her left eye of 2 months' evolution. Computerized tomography showed a hypodense lesion in the suprasellar region. At surgery a cystic lesion was found inside the optic nerve. Histological study proved it to be a neuroepithelial cyst. The pathogenesis of a neuroepithelial cyst in such an exceptional site is discussed.

X-ray-translucent retractors in spine surgery

1986 ◽  
Vol 64 (3) ◽  
pp. 520-521 ◽  
Author(s):  
Peter Knöringer
Keyword(s):  
Spine Surgery ◽  
Vertebral Column ◽  
Operating Time ◽  
Surgical Instruments ◽  
X Rays ◽  
Content Type ◽  
X Ray ◽  
Image Intensification ◽  
Fine Print

✓ With surgery of the vertebral column under image intensification, surgical instruments and conventional metal retractors often obscure important x-ray landmarks. Surgery is more difficult, operating time is longer, and exposure to x-rays is increased. The author has developed x-ray-translucent retractors for ventral and dorsal operations. Although for reasons of strength these retractors have somewhat more bulk than equivalent metal retractors, they are sufficiently stable and are compatible with spacial requirements. They can be sterilized and reused.

Intraorbital optic nerve hemangioblastoma with von Hippel-Lindau disease

1982 ◽  
Vol 56 (3) ◽  
pp. 426-429 ◽  
Author(s):  
Seiich In ◽  
Jun Miyagi ◽  
Nobuto Kojho ◽  
Shinken Kuramoto ◽  
Masaki Uehara
Keyword(s):  
Optic Nerve ◽  
Content Type ◽  
Von Hippel Lindau ◽  
Von Hippel Lindau Disease ◽  
Dural Attachment ◽  
Microscopic Findings ◽  
Fine Print

✓ An intraorbital hemangioblastoma of the optic nerve is reported in a 23-year-old woman with von Hippel-Lindau disease. The absence of dural attachment and the microscopic findings were characteristic of hemangioblastoma. Four years later the patient developed a cystic hemangioblastoma in the left cerebellum which was successfully treated.

Tethered cord syndrome in children with anorectal malformations

2000 ◽  
Vol 92 (4) ◽  
pp. 626-630 ◽  
Author(s):  
Natarajan Muthukumar ◽  
Bhuvaneswari Subramaniam ◽  
Thangaraj Gnanaseelan ◽  
Ramesh Rathinam ◽  
Appaswamy Thiruthavadoss
Keyword(s):  
Tethered Cord ◽  
Anorectal Malformations ◽  
Neurological Deficits ◽  
Radiographic Evidence ◽  
Content Type ◽  
X Ray ◽  
Neurological Improvement ◽  
Intraspinal Anomalies ◽  
Bone Abnormalities ◽  
Fine Print

Object. Anorectal malformations are known to be associated with neurological deficits, which may contribute to the disability suffered by patients with these malformations. This study was undertaken to determine the incidence and pattern of sacral abnormalities in children with anorectal malformations, the incidence and nature of the neurological deficits, and the incidence and nature of operable intraspinal abnormalities in patients with this condition.Methods. Neurological evaluation was performed in 81 children with anorectal malformations. Plain x-ray films were obtained to identify the presence of sacral abnormalities. The patients with neurological deficits were evaluated for the presence of operable intraspinal anomalies, and when such anomalies were identified, correction of the same was undertaken. In 21% of these children radiographic evidence of sacral abnormalities was shown. Fifteen percent of patients harbored neurological deficits, and 10% harbored operable intraspinal anomalies. In addition, one patient had split notochord syndrome. Patients with operable intraspinal anomalies underwent surgical correction, with resultant neurological improvement.Conclusions. Bone abnormalities of the sacrum, neurological deficits, and operable intraspinal lesions are not uncommon in children with anorectal malformations. Because the neurological deficits can contribute to the disability suffered by these individuals, we recommend routine screening of patients with anorectal malformations and neurological deficits and/or sacral abnormalities for the early identification and treatment of potentially correctable intraspinal lesions.

Total removal of large global meningiomas at the medial aspect of the sphenoid ridge

1971 ◽  
Vol 34 (1) ◽  
pp. 107-113 ◽  
Author(s):  
Albert W. Cook
Keyword(s):  
Optic Nerve ◽  
Middle Cerebral Artery ◽  
Operative Technique ◽  
Middle Meningeal Artery ◽  
Medial Aspect ◽  
Total Removal ◽  
Content Type ◽  
Meningeal Artery ◽  
Sphenoid Ridge ◽  
Fine Print

✓ An operative technique for total removal of large global meningiomas at the medial aspect of the sphenoid ridge is described, and experience with 11 patients reported. The technique involves extradural liberation of the dural and tumor attachments to the underlying bone, and extradural occlusion of the blood supply through bone and middle meningeal artery. Subsequent procedures are carried out sequentially in the parasellar area to free the optic nerve and carotid, in the subtemporal tentorial region to release tumor from neighboring structures, and in the Sylvian fissure to isolate the middle cerebral artery.

Impaction fracture of the lumbar vertebrae with dural tear

1980 ◽  
Vol 53 (6) ◽  
pp. 765-771 ◽  
Author(s):  
Carole A. Miller ◽  
Richard C. Dewey ◽  
William E. Hunt
Keyword(s):  
Lumbar Spine ◽  
Cauda Equina ◽  
Lumbar Vertebrae ◽  
Dural Tear ◽  
Mechanism Of Injury ◽  
Content Type ◽  
X Ray ◽  
Jefferson Fracture ◽  
Vertical Impaction ◽  
Fine Print

✓ The authors describe a lumbar spine fracture that is characterized on anteroposterior x-ray views by separation of the pedicular shadows. It is almost invariably associated with posterior interlaminar herniation of the cauda equina through a dorsal dural split, and anterolateral entrapment or amputation of the nerve root. The fracture is unstable and requires internal fixation and fusion at the time of neurolysis. Fractures meeting these criteria should be explored as soon as the patient's condition permits. Myelography is usually unnecessary and may be contraindicated in some cases. The postulated mechanism of injury is hyperextension with vertical impaction and rupture of the ring made up of the lamina, pedicle, and vertebral body. The ring is fractured in several places in a manner similar to that seen in “Jefferson fracture” of C-1. The special anatomical relationships of the thoracolumbar junction and the plane of the lumbar facets are also discussed.

Sign in / Sign up

Export Citation Format

Share Document