Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.

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Persistent Oxygen Requirement beyond Prematurity: A Case of Acquired Pulmonary Vein Stenosis

Case Reports in Pediatrics ◽

10.1155/2017/3106871 ◽

2017 ◽

Vol 2017 ◽

pp. 1-4

Author(s):

Tyler A. Fick ◽

Bernadette Richards ◽

Carl H. Backes ◽

Molly K. Ball

Keyword(s):

Pulmonary Vein ◽

Treatment Options ◽

Pulmonary Vein Stenosis ◽

Comorbid Conditions ◽

Oxygen Requirement ◽

Cardiac Defect ◽

Collaborative Studies ◽

Vein Stenosis

Acquired pulmonary vein stenosis is a rare cardiac defect and diagnosis can often be challenging, as many cases present with refractory or prolonged oxygen requirement over the expected course. Comorbid conditions can cloud this diagnosis further. Prognosis is poor for most patients. We present a case of idiopathic acquired pulmonary vein stenosis and discuss diagnostics, treatment options, and the need for further collaborative studies.

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Commentary: Management outcomes of primary pulmonary vein stenosis: What we know now and what we can expect in the future

Journal of Thoracic and Cardiovascular Surgery ◽

10.1016/j.jtcvs.2019.10.201 ◽

2020 ◽

Vol 159 (3) ◽

pp. 1039 ◽

Cited By ~ 1

Author(s):

Haifa Hong

Keyword(s):

Pulmonary Vein ◽

Pulmonary Vein Stenosis ◽

The Future ◽

Vein Stenosis

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Surveillance of a Patient Born With Tetralogy of Fallot and Total Anomalous Pulmonary Venous Return With Recurrent Pulmonary Vein Stenosis: The Role of Echocardiography to Aid in Treatment Options

Journal of Diagnostic Medical Sonography ◽

10.1177/8756479320952070 ◽

2020 ◽

Vol 36 (6) ◽

pp. 580-584

Author(s):

Dana Jones

Keyword(s):

Tetralogy Of Fallot ◽

Pulmonary Vein ◽

Venous Return ◽

Treatment Options ◽

Pulmonary Veins ◽

Pulmonary Vein Stenosis ◽

Interventional Treatment ◽

Anomalous Pulmonary Venous Return ◽

Vein Stenosis

Surveillance of patients with congenital heart disease is difficult in some clinical settings. This case study follows the progress of a patient, born with prenatally missed diagnoses of tetralogy of Fallot (TOF) and total anomalous pulmonary venous return (TAPVR), for over two years. The patient acquired pulmonary vein stenosis following initial TOF/TAPVR repair, which made the case an interesting longitudinal study. Multiple cardiac catheterizations for stents and balloon angioplasties of the pulmonary veins were necessary. This case study illustrates this patient’s success with treatment options such as chemotherapy medications, as well as the failure of each treatment. It was also important to note that the interval of time between each interventional treatment weighed heavily upon results of frequent echocardiograms.

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