scholarly journals Sarcoma de Ewing extraesquelético de rápido crecimiento en paciente de 2 años: Reporte de caso. / Fast growing extraskeletal Ewing sarcoma in a 2 year old patient: Case report.

2019 ◽  
Vol 46 (4) ◽  
pp. 302-307
Author(s):  
Juan Pablo Luengas Monroy ◽  
Daniella Chacón Valenzuela ◽  
Nichole Marcela Rojas Chaverra ◽  
Erika Yamile Torrijos Castañeda

El sarcoma de Ewing forma parte de una familia de tumores que se  caracterizan por presentar translocaciones que involucran al gen EWS y algún miembro de la familia ETS que posee un dominio de unión al ADN. Se presenta el caso de un paciente de dos años de edad con una masa cervical de crecimiento rápido que por compresión local comprometió estructuras nerviosas manifestándose inicialmente con un retardo en el neurodesarrollo. Se diagnosticó Sarcoma de Ewing/Tumor neuroectodérmico primitivo por biopsia. Este es un tipo de tumor raro con una presentación inusual a nivel cervical; el cual debe tenerse en cuenta al momento de evaluar pacientes con masas cervicales en especial las de crecimiento rápido con el fin de dar un tratamiento preciso y oportuno.

2021 ◽  
Vol 80 ◽  
pp. 105676
Author(s):  
Tomohiko Sakuda ◽  
Taisuke Furuta ◽  
Muhammad Phetrus Johan ◽  
Koji Arihiro ◽  
Nobuo Adachi

2021 ◽  
pp. 55-56
Author(s):  
K Pratyusha ◽  
Satish Arakeri ◽  
Surekha Arakeri

Introduction: Extraskeletal Ewing sarcoma/PNET is a small round cell sarcoma showing gene fusions of EWSR1-FLI1. A 28-year-old male patient presented with right ank pain and low gr Case Report: ade fever since 15 days. On examination: a mass was palpable in the right hypochondrium. Provisional diagnosis of Liver abscess has been made. USG abdomen shows features cystic lesion in the liver with internal septation ?Liver abscess /Hydatid cyst. Intraoperatively, tumor was seen attached to upper pole of kidney. Since tumor was large, it was ruptured intraoperatively and debulking surgery has been done. Under microscopy, tumor was arranged in sheets with intervening stroma showing desmoplastic reaction. Perivascular pseudorosettes are seen. The diagnosis of malignant small round cell tumor has been given. On immunohistochemistry, tumor cells are positive for Vimentin, CD99, NKX2.2 , FLI1, Neurolaments, Synaptophysin with focal immunoreactivity for EMA, Pancytokeratin. Final diagnosis was EXTRASKELETAL EWING SARCOMA/PNET. Discussion: Extra-skeletal Ewing sarcoma/PNET is malignant soft tissue tumor seen in chest wall, thigh, paravertebal region etc. Retroperitoneum is a least common site. Most common presentation is swelling in the soft tissue with compressive symptoms. Histologically, it is composed of undifferentiated small round cells. Conclusion: Clinical examination and radiological ndings leads to ambiguous diagnosis in Ewing sarcoma/PNET. Hence proper histopathological study is essential for nal diagnosis.


2012 ◽  
Vol 8 (4) ◽  
pp. 652
Author(s):  
Priyanka Thakur ◽  
Swaroop Revannasiddaiah ◽  
Madhup Rastogi ◽  
Sudesh Kumar

2021 ◽  
Vol 13 (2) ◽  
pp. 26-35
Author(s):  
M. A. Kutin ◽  
V. V. Ivanov ◽  
P. L. Kalinin

We performed retrospective analysis of publications describing cases of Ewing sarcoma of the skull base with exceedingly rare locations (including the area of the sphenoid bone, its wings, sinus, and adjacent structures). Ewing sarcoma is usually diagnosed in children. The peak incidence is registered in patients aged 10–15 years, whereas adults and children under 5 years of age are very unlikely to develop this disease. In this article, we also report a case of Ewing sarcoma of the skull bones affecting the sphenoid bone and sphenoid sinus. The patient has undergone surgery followed by chemoradiotherapy. High invasion potential (tumor spread in several directions), high malignancy, and compression of the adjacent structures of the brain make the analysis of Ewing sarcoma located in areas that cannot be easily approached particularly interesting for neurosurgeons, since surgery is the main treatment option for such patients.


2019 ◽  
Vol 26 (1) ◽  
pp. 57-61
Author(s):  
Haddadin , William ◽  
Ashokhaibi , Omar ◽  
Shannaq , Ruba

2021 ◽  
pp. 014556132110534
Author(s):  
Michela Borrelli ◽  
Arash Shamsian ◽  
Martin L. Hopp ◽  
Nicholas L. Schenck

Extraskeletal Ewing sarcoma (EES) is a relatively rare primary tumor of the soft tissues predominantly affecting men in the second and third decades of life. They are a less common form of the cancerous growth known as an Ewing sarcoma, which occurs in bones or soft tissue such as cartilage. Head and neck ESS can require intervention including endoscopic sinus surgery, septoplasty, inferior turbinectomy, and left internal nasal valve repairs with septal cartilage This is a case report on an unusual presentation of ESS in the sinonasal region.


2012 ◽  
Vol 94 (4) ◽  
pp. e141-e143 ◽  
Author(s):  
R Kallala ◽  
D Nikkhah ◽  
P Nix ◽  
C Woodhead

Extraskeletal Ewing sarcoma (EES) is a rare soft tissue neoplasm of primitive mesenchymal cells. There is a scarcity of data on EES involving the head and neck, with studies being over years or even decades. We are the first to report a case of EES involving the carotid artery and its subsequent surgical excision and reconstruction.


2018 ◽  
Vol 53 (4) ◽  
pp. 222-228 ◽  
Author(s):  
Joshua T. Scantland ◽  
Mercia J. Gondim ◽  
Andrew S. Koivuniemi ◽  
Daniel H. Fulkerson ◽  
Chie-Schin Shih

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