scholarly journals Congenital segmental dilatation of intestine with different morphology: A case report

2021 ◽  
Vol 10 ◽  
pp. 41
Author(s):  
Muhammad Bilal Mirza ◽  
Sumaira Noor Maham ◽  
Nabila Talat
Keyword(s):  
Rare Entity ◽  
Repeat Surgery ◽  
Case Presentation ◽  
Postoperative Course ◽  
Initial Surgery ◽  
Neonatal Intestinal Obstruction ◽  
Complete Surgical Resection ◽  
Segmental Dilatation ◽  
Male Neonate ◽  
Segmental Dilatation Of Intestine

Background: Congenital segmental dilatation of intestine is a rare entity characterized by a localized dilated segment of the intestine. It manifests as neonatal intestinal obstruction. Occurrence with another surgical anomaly may masquerade it and complicate the treatment course. Case Presentation: A 1-day-old male neonate with anorectal malformation underwent colostomy as first stage of the treatment. The stoma did not function postoperatively. At repeat surgery, congenital segmental dilatation of the ileum, with slightly different morphology, was found. Resection of the lesion and ileostomy were formed. Postoperative course remained uneventful. Conclusion: Congenital segmental dilatation of intestine may be missed at initial surgery. Complete surgical resection is curative.

Early Recurrence of an Infantile Endodermal Oculomotor Nerve Cyst following Surgical Fenestration: A Case Report

2021 ◽  
Vol 56 (2) ◽  
pp. 157-162
Author(s):  
Victor M. Lu ◽  
Aditya Raghunathan ◽  
Michael J. Link ◽  
David J. Daniels
Keyword(s):  
Case Report ◽  
Surgical Intervention ◽  
Early Recurrence ◽  
Oculomotor Nerve ◽  
Rare Entity ◽  
Oculomotor Palsy ◽  
Case Presentation ◽  
Postoperative Course

Introduction: Infantile endodermal oculomotor nerve cyst (EONC) is an extremely rare entity. There are very few pediatric cases reported in the literature, and as expected, oculomotor palsy is the most common presenting symptom. To date however, the risk of recurrence of these lesions following surgical intervention is unclear due to a lack of long-term radiological follow-up. Case Presentation: We present a case of a 13-month-old male patient with an EONC and detail his surgical fenestration and postoperative course. Somewhat surprisingly, re-expansion occurred within 6 months and remained stable 2 years later. Discussion: A surgical approach to fenestration of an EONC in an infant is possible and should be performed by an expert neurosurgeon. Early recurrence is underreported in the current literature, and we encourage longer term radiological surveillance of these lesions after surgery to optimize primary and recurrent management in the future.

Congenital Segmental Intestinal Dilatation: A Clinical Dilemma

2021 ◽  
pp. 097321792110406
Author(s):  
Bhavya Kukreja ◽  
Ajay Prakash Mehta ◽  
Harsh Wardhan ◽  
Bhawna Sachdeva Narula ◽  
Poonam Sidana
Keyword(s):  
Differential Diagnosis ◽  
Neonatal Period ◽  
Case Reports ◽  
Rare Condition ◽  
Rare Clinical Entity ◽  
Preterm Baby ◽  
Neonatal Intestinal Obstruction ◽  
Segmental Dilatation ◽  
Clinical Dilemma ◽  
Segmental Dilatation Of Intestine

Congenital segmental dilatation of intestine is a rare clinical entity encountered in neonates with very few case reports from world over. It usually presents with symptoms of partial or total obstruction in neonatal period or infancy. We report a case of a preterm baby with segmental dilatation of intestine which was managed surgically. Diagnosis was confirmed intraoperatively as well as histologically. Consideration of this entity in differential diagnosis of neonatal intestinal obstruction may enable for better understanding and more reporting of this rare condition.

scholarly journals Diagnostic dilemma of congenital segmental jejunal pseudo-dilatation associated with immature ganglion cells in the colon: A case report

2020 ◽  
Vol 9 ◽  
pp. 13
Author(s):  
Suman Bikram Adhikari ◽  
Shovita Rana ◽  
Sanat Chalise
Keyword(s):  
Intestinal Obstruction ◽  
Ganglion Cells ◽  
Abdominal Distension ◽  
Diagnostic Dilemma ◽  
Case Presentation ◽  
Male Baby ◽  
Radiological Features ◽  
Neonatal Intestinal Obstruction ◽  
Segmental Dilatation ◽  
Prompt Diagnosis

Background: Neonatal intestinal obstruction is one of the emergency conditions with many etiologies, amongst which congenital segmental dilatation of small intestine is one, which is characterized by three to four folds increase in diameter of the bowel. Immaturity of ganglion cells of large intestine is also one of the congenital intestinal neuronal malformations which may cause neonatal intestinal obstruction. Prompt diagnosis of these conditions is very difficult as clinical and radiological features are non-specific to them. Case Presentation: A 3-day-old male baby presented with failure to pass meconium, abdominal distension, and bilious vomiting. At surgery, the baby had congenital segmental pseudo-dilatation of jejunum with immature ganglion cells in colon. Since it was not typical of a congenital segmental dilatation, it was left as such. The baby needed another laparotomy for resection of segmental pseudo-dilatation along with ileostomy. Conclusion: Because of rarity and diagnostic dilemma, re-laparotomy with ileostomy, which could have been avoided, were performed in the baby. Lack of typical features of congenital segmental dilatation along with presence of immature ganglion cells in the colon were unusual findings in this case

scholarly journals Cystic papillary adenoma of the seminal vesicle

BMC Urology ◽  
2021 ◽  
Vol 21 (1) ◽  
Author(s):  
B. Heijkoop ◽  
D. Bolton ◽  
D. Katz ◽  
Andrew Ryan ◽  
J. Epstein ◽  
...  
Keyword(s):  
Seminal Vesicle ◽  
Rare Case ◽  
Groin Pain ◽  
Iliac Fossa ◽  
Papillary Adenoma ◽  
Rare Entity ◽  
Macroscopic Haematuria ◽  
Case Presentation ◽  
Adjacent Organ ◽  
Epithelial Tumours

Abstract Background Primary Seminal Vesicle (SV) tumours are a rare entity, with most SV masses representing invasion of the SV by malignancy originating in an adjacent organ, most often the prostate. Previously reported primary SV epithelial tumours have included adenocarcinoma and cystadenoma, with limited prior reports of inracystic papillary structures. Case presentation A 35-year-old male presented with azoospermia, intermittent macroscopic haematuria, and mild right iliac fossa and groin pain. A papillary appearing seminal vesicle mass was found on imaging and seminal vesicoscopy. The mass was robotically excised with diagnosis of benign cystic papillary adenoma made. Conclusion In this manuscript we describe a rare case of a benign cystic papillary adenoma of the seminal vesicle, a unique histological entity differentiated from cystadenoma of the Seminal Vesicle by its papillary component.

scholarly journals Bilateral scrotoshisis a rare entity: case report

2021 ◽  
Vol 17 (1) ◽  
Author(s):  
Shazia Perveen ◽  
Mishraz Shaikh ◽  
Sajid Ali
Keyword(s):  
Case Report ◽  
Rare Entity ◽  
Case Presentation ◽  
Rare Anomaly ◽  
Normal Term ◽  
Twin Delivery

Abstract Background Scrotoschisis is a rare anomaly in which the testis is lying outside scrotum congenitally. Only few cases have been reported in literature under different names most of which are unilateral. We have found only one case of bilateral scrotoschisis in literature. Case presentation Newborn presented to us after normal term twin delivery as a case of bilateral scrotoschisis in which both testes were lying outside the scrotum congenitally. Baby underwent uneventful bilateral orchiopexy and was discharged home the next day. Conclusion Scrotoschisis is a very rare genital anomaly with only a few cases reported in literature. This report would add to the literature which would help in studying the exact mechanism and embryopathogenesis of this anomaly which is not known yet.

Frontal Sinus Drainage in Acute Pediatric Sinusitis With Intracranial Complications

2021 ◽  
pp. 194589242199131
Author(s):  
Stephen R. Chorney ◽  
Adva Buzi ◽  
Mark D. Rizzi
Keyword(s):  
Surgical Procedures ◽  
Frontal Sinus ◽  
Case Series ◽  
Primary Objective ◽  
Acute Sinusitis ◽  
Intracranial Abscess ◽  
Repeat Surgery ◽  
Initial Surgery ◽  
Intracranial Complications ◽  
Sinus Drainage

Background The indication for frontal sinus drainage is uncertain when managing pediatric acute sinusitis with intracranial complications. Objective The primary objective was to determine if addressing the frontal sinus reduced need for subsequent surgical procedures in children presenting with acute sinusitis complicated by intracranial abscess. Methods A case series with chart review was performed at a tertiary children’s hospital between 2007 and 2019. Children under 18 years of age requiring surgery for complicated acute sinusitis that included the frontal sinus with noncontiguous intracranial abscess were included. Outcomes were compared among children for whom the frontal sinus was drained endoscopically, opened intracranially, or left undrained. Results Thirty-five children with a mean age of 11.1 years (95% CI: 9.9-12.3) met inclusion. Most presented with epidural abscess (37%). Hospitalizations lasted 12.9 days (95% CI: 10.2-15.5), 46% required a second surgery, 11% required three or more surgeries, and 31% were readmitted within 60 days. Initial surgery for 29% included endoscopic frontal sinusotomy, 34% had a frontal sinus cranialization and 37% did not have any initial drainage of the frontal sinus. Groups were similar with respect to demographics, severity of infection, need for repeat surgery, length of stay, and readmissions (p > .05). Further, persistence of cranial neuropathies, seizures, or major neurological sequelae after discharge were no different among groups (p > .05). Conclusion Drainage of the frontal sinus, when technically feasible, was not associated with reduced surgical procedures or increased complications and there is unclear benefit on measured clinical outcomes.

scholarly journals Ileoileal knotting: a rare cause of intestinal obstruction: a case report

2021 ◽  
Vol 15 (1) ◽  
Author(s):  
Yusuf Mohammed ◽  
Kirubel Tesfaye
Keyword(s):  
Abdominal Pain ◽  
Intestinal Obstruction ◽  
Sudden Onset ◽  
Rapid Progression ◽  
Case Presentation ◽  
Postoperative Course ◽  
Child Bearing ◽  
Mechanical Intestinal Obstruction ◽  
Tentative Diagnosis ◽  
Very High

Abstract Background Ileoileal knotting is one of the rarest causes of intestinal obstruction. The pathology involves knotting of the ileum around itself, leading to mechanical intestinal obstruction that can rapidly evolve to gangrene. Case presentation Here we will discuss the case of an 18-year-old Oromo girl who presented with sudden onset of severe abdominal pain and signs of generalized peritonitis.Ultrasound examination showed massive peritoneal and cul-de-sac fluid. Explorative laparotomy was done, with a tentative diagnosis of ruptured ovarian cyst. Intraoperative finding was a gangrenous ileoileal knot. The gangrenous segment was resected and ileotransverse anastomosis done. Postoperative course was uneventful, and the patient was discharged improved on the sixth postoperative day. Conclusion We present this case to highlight the diagnostic difficulty that one can face in females of child-bearing age and to create awareness of this rare cause of intestinal obstruction, as morbidity and mortality are very high because of rapid progression to gangrene.

scholarly journals Closed Gastroschisis

2017 ◽  
Vol 6 (3) ◽  
pp. 61 ◽  
Author(s):  
Mohammed Abdel-Latif ◽  
Mohamed Hisham Soliman ◽  
Khaled Mohaned El-Asmar ◽  
Mohamed Abdel-Sattar ◽  
Ibrahim M Abdelraheem ◽  
...  
Keyword(s):  
Intestinal Obstruction ◽  
Short Bowel Syndrome ◽  
Intestinal Atresia ◽  
Rare Entity ◽  
Short Bowel ◽  
Neonatal Intestinal Obstruction

Closed gastroschisis is a rare entity usually associated with intestinal atresia and short bowel syndrome. We report two cases of closed gastroschisis presenting with neonatal intestinal obstruction and para-umbilical evisceration without an abdominal defect.

scholarly journals A Case of Ectopic Odontogenic Ghost Cell Tumor: Histogenetic Features of a New Entity

2021 ◽  
Author(s):  
Yuri Noda ◽  
Chisato Ohe ◽  
Mitsuaki Ishida ◽  
Kimiaki Okano ◽  
Kaori Sando ◽  
...  
Keyword(s):  
Final Diagnosis ◽  
Cell Tumor ◽  
Clinicopathological Features ◽  
Rare Entity ◽  
Ghost Cell ◽  
Case Presentation ◽  
Floor Of The Mouth ◽  
Odontogenic Origin ◽  
Odontogenic Neoplasm

Abstract Background: Odontogenic tumors arising from extra-alveolar sites are extremerly rare. Dentinogenic ghost cell tumor (DGCT) is an uncommon odontogenic neoplasm characterized by CTNNB1 mutation, ghost cell appearance, and dentinoid-like calcification. We present a case of an ectopic DGCT arising from a calcifying odontogenic cyst in the floor of the mouth. Case presentation: A 72-year-old man presented with a painless sublingual swelling. Imaging revealed a multi-lobulated, solid-cyst mass on the floor of the mouth. Cytology showed folded epithelial clusters composed of basaloid cells, keratinized material, and dentinoid matrix. Histology also revealed a multi-cystic, cribriform to solid nest. Immunohistochemically, CK19, CK5/6, bcl-2, and p63 were diffuse positive. CTNTTB1 mutation was detected, leading to the final diagnosis of an ectopic DGCT. There was no recurrence during a 6-month follow-up. Conclusion: This is the first report to comprehensively describe the clinicopathological features of an ectopic DGCT of odontogenic origin, developing similarly to that of a true odontogenic DGCT. Accurate diagnosis of this rare entity is necessary to avoid overtreatment.

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