RARE-09. POORLY DIFFERENTIATED CLIVAL CHORDOMA IN EXTREME YOUNG AGE; CASE ILLUSTRATION AND REVIEW OF LITERATURE

Chordomas are rare tumors believed to be originated from notochordal remnants. Of all intracranial neoplasms, the incidence of cranial chordomas is less than 1%1. The youngest patient with an intracranial chordoma reported in the literature was a newborn in the first few days after birth9. Intracranial chondroma are more predominant in males compared to females1. The clinical features of intracranial chondroma in the pediatric age group commonly include increased Intracranial pressure, lower cranial nerves palsy, and torticollis2. There is no optimum treatment, however, surgical resection of the tumor followed by radiation therapy reported successful outcome3. This is a case of a poorly differentiated clival chordoma of a 23-month old boy. The clinical features, pathological, radiological findings, and surgical technique are discussed with an elaboration of the current review of the literature of clival chordoma in the extreme young age group. To the best of our knowledge, this is the youngest age of clivus chordoma reported in Saudi Arabia.

Intracranial chondroma of the falx-cerebi: a clinical case

Intracranial chondroma is a rare pathology with the occurrence of 0.1 % to 0.5 % of all primary intracranial tumours. The mechanism of tumour formation outside cartilaginous tissue is controversial. The majority of data point at a very diverse cellular composition of the Dura mater and the tumour may emerge as a result of fi broblast activation. Frequently, the tumour is a manifestation of multiple enchodromatosis (Ollier’s disease) or Maff ucci syndrome. Clinical manifestations of the disease are unspecifi c and generalised. Diff erential diagnosis of the tumour is complicated due to the absence of pathognomonic neurovisualisation characteristics. Th erefore, it is only possible to verify the diagnosis via pathomorphological examination. Chondroma is a benign neoplasm and its complete resection is essential for the positive outcome and longer life duration of the patients. Th e article presents a clinical case of successful surgical treatment of a patient with intracranial chondroma of falxcerebri.

Falx chondroma with hyperostosis of the scull: A case report

Introducion. Intracranial chondroma is a very rare, slow growing, benign cartilaginous tumor that arises usually from the base of the scull. Chondroma located at the falx is extremely rare. According to our best knowledge 15 cases of falx chondromas have been reported in the literature. Case Outline. This is the first case report of falx chondroma located in the parietal area associated with hyperostosis. Magnetic resonance imaging of the brain revealed a 3?4?4 cm solid, calcified, ring-shaped, well-defined tumor at the posterior falx. The patient underwent surgery and complete resection was performed. Histological examination confirmed chondroma of the falx. Postoperative CT scan showed no residual of tumor and the patient was discharged. Conclusion. The long-term prognosis is good after a total excision of the tumor. Awareness of this rare pathology in the differential diagnosis of falx mass could facilitate the diagnosis.