scholarly journals Retroperitoneal teratoma with obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome in infant

2021 ◽  
pp. 102104
Author(s):  
Tamaki Iwade ◽  
Koichi Ohno
Keyword(s):  
Renal Agenesis ◽  
Retroperitoneal Teratoma ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina

Abdominopelvic Pain in Patient with Uterus Didelphys and Unilateral Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA Syndrome)

2021 ◽  
Author(s):  
Zahra Tavoli ◽  
Ali Montazeri
Keyword(s):  
Renal Agenesis ◽  
Primary Diagnosis ◽  
Case Presentation ◽  
Uterus Didelphys ◽  
Future Fertility ◽  
History Of ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina ◽  
Magnetic Resonance Imaging Mri

Introduction: Uterus didelphys with obstructed hemivagina associated with ipsilateral renal agenesis (OHVIRA syndrome) is a rare female urogenital malformation and delay in its diagnosis could lead to several complications. Case presentation: A 21-year-old virgin woman was admitted to the emergency department (ED) with severe abdominal pain, without fever and vaginal discharge. She reported a history of cyclic abdominopelvic pain and dysmenorrhea for 5 years. The primary diagnosis (OHVIRA syndrome) was made using ultrasonography, spiral computed tomography (CT) and magnetic resonance imaging (MRI). In addition, laparoscopy was performed to confirm diagnosis and drain hematosalpinx. Then, hysteroscopy was carried out for septum resection and catheter insertion. At one-month follow-up the ultrasonography showed normal left hemicavity of uterus associated with significant decrease in dysmenorrhea. Conclusion: Being aware of OHVIRA syndrome and clinical suspicion of this rare anomaly are essential for making a timely diagnosis, preventing complications, relieving symptoms, and preserving future fertility.

HERLYN–WERNER–WUNDERLICH SYNDROME: CLINICAL CASE OF A 17 YEAR OLD PATIENT

2021 ◽  
Vol 100 (4) ◽  
pp. 185-189
Author(s):  
S.S. Nikitin ◽  
◽  
N.B. Guseva ◽  
M.E. Ukvalberg ◽  
N.A. Ivanova ◽  
...  
Keyword(s):  
Clinical Practice ◽  
Reproductive Health ◽  
Early Diagnosis ◽  
Clinical Case ◽  
Renal Agenesis ◽  
Uterus Didelphys ◽  
Mullerian Ducts ◽  
Level 3 ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina

Herlyn–Werner–Wunderlich syndrome (HWWS) is a rare syndrome in clinical practice in which there is a combination of complete uterus didelphys and OHVIRA syndrome (obstructed hemivagina and ipsilateral renal agenesis). HWWS refers to associative defects of the reproductive and urinary systems and occurs due to anomalies in the development of the Müllerian ducts. The review part of the article presents questions of its epidemiology, and provides historical information. The clinical picture, methods of examination and treatment are considered. Particular attention is paid to the difficulty of diagnosing HWWS and the need for its early diagnosis in order to preserve the reproductive health of girls. A clinical case of a 17-year-old patient with HWWS diagnosed during urgent laparoscopy, the complication of which was hematopiocolpos, is presented. The patient was referred to a level 3 hospital for specialized medical care, where she was operated on.

scholarly journals OHVIRA Syndrome: A Case Report

2020 ◽  
Vol 14 (1) ◽  
pp. 54-56
Author(s):  
Dilruba Zeba ◽  
Fahmida Zesmin ◽  
Rajib Roy
Keyword(s):  
Renal Agenesis ◽  
Lower Abdominal Pain ◽  
Vaginal Septum ◽  
Regular Cycle ◽  
Mullerian Ducts ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina ◽  
Lateral Fusion ◽  
Acute Retention

OHVIRA syndrome or Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly of female urogenital tract which is represented by the triad of uterine didelphys, obstructed hemivagina and ipsilateral renal agenesis. This rare variant of Müllerian duct anomalies represent failure of vertical and the lateral fusion of Müllerian ducts around 9 weeks of gestation. OHVIRA syndrome comprises about 2-3% of Müllerian abnormalities. A 13 years old girl got admission in FMCH on 15.3.2018 with lower abdominal pain and acute retention of urine. Her menarche was established 6 months back with regular cycle and associated with dysmenorrhoea. Imaging studies revealed uterine didelphys, highly dilated cervix with hematocolpos and absence of right kidney. The vaginal septum was excised. The patient recovered fully and was under follow up for 6 months. There was no evidence of further outflow tract obstruction. Faridpur Med. Coll. J. Jan 2019;14(1): 54-56

scholarly journals Uterus Didelphys with Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA Syndrome)

2015 ◽  
Vol 19 (4) ◽  
Author(s):  
Mauri José Piazza ◽  
Newton Sergio De Carvalho ◽  
Ana Paula Lisboa Peixoto ◽  
Almir Antonio Urbanetz
Keyword(s):  
Renal Agenesis ◽  
Uterus Didelphys ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina

Female counterpart of the Zinner syndrome in men: decoding the ‘OHVIRA’ syndrome

2021 ◽  
Vol 14 (2) ◽  
pp. e239625
Author(s):  
Vikas Kumar Panwar ◽  
Tushar Aditya Narain ◽  
Ankur Mittal ◽  
Harkirat Singh Talwar
Keyword(s):  
Pelvic Pain ◽  
Renal Agenesis ◽  
Surgical Intervention ◽  
Developmental Anomaly ◽  
Male Factor ◽  
Vaginal Septum ◽  
Uterine Anomalies ◽  
Ohvira Syndrome ◽  
Obstructed Hemivagina ◽  
Female Counterpart

The obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome, a rare Mullerian duct anomaly, is a triad of uterine anomalies with ipsilateral renal agenesis and obstructed hemivagina. The aetiopathogenesis of this developmental anomaly is debatable, with several theories being postulated to explain its occurrence. We report two cases of this rare syndrome which were detected on imaging done for unrelated reasons. Case 1 is a 24-year-old woman who presented with primary infertility. After an incidental detection of the syndrome and ruling out a male factor, she has been planned for excision of the vaginal septum. Case 2 is a 47-year-old woman with OHVIRA detected during the evaluation of urolithiasis and is asymptomatic for the syndrome. The OHVIRA syndrome can be asymptomatic or may present as haematocolpos, pelvic pain and infertility which requires surgical intervention, after which successful pregnancies have been reported.

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