The Development of Connective Tissue Diseases in Patients with Autoimmune Hepatitis: A Case Series

2006 ◽  
Vol 35 (6) ◽  
pp. 344-348 ◽  
Author(s):  
Margaret West ◽  
Hugo E. Jasin ◽  
Swati Medhekar
Keyword(s):  
Connective Tissue ◽  
Autoimmune Hepatitis ◽  
Hepatitis A ◽  
Connective Tissue Diseases ◽  
Case Series

Ulnar artery vasculopathy: a common but nonspecific feature of systemic sclerosis

2017 ◽  
Vol 2 (3) ◽  
pp. 221-224
Author(s):  
Tae-Jong Kim ◽  
Soon-Young Song ◽  
Hee Chang Ahn ◽  
Yoon-Kyoung Sung ◽  
Sang-Cheol Bae ◽  
...  
Keyword(s):  
Systemic Sclerosis ◽  
Connective Tissue ◽  
Lupus Erythematosus ◽  
Connective Tissue Diseases ◽  
Case Series ◽  
Ulnar Artery ◽  
Common Finding ◽  
Clinical Factors ◽  
Vessel Disease ◽  
Large Vessel Disease

Introduction Systemic sclerosis (SSc) is characterized by microvascular abnormalities and fibrosis. Several studies have reported that large vessel disease is also common in SSc. The aim of this case series was to investigate whether ulnar artery involvement in patients with SSc is a disease-specific phenomenon, as compared to other connective tissue diseases (CTD). Methods A total of 28 patients, including 7 with SSc and 12 with systemic lupus erythematosus (SLE), underwent brachial arteriography due to severe Raynaud's phenomenon and/or digital ulcerations and were enrolled in the study. They were divided into two groups: an SSc/SSc-overlap group and a non-SSc group. The collection of the clinical parameters was conducted to investigate the associations between clinical factors and the ulnar artery vasculopathy. Results The SSc/SSc-overlap group (n = 10) consisted of 7 patients with SSc and 3 with features overlapping SSc. In the non-SSc group (n = 18), 12 cases of SLE, 2 of mixed connective tissue disease, 1 of dermatomyositis + SLE, 1 of rheumatoid arthritis, 1 of Sjogren's syndrome, and 1 case of skin vasculitis, were included. The relative frequencies of ulnar artery involvement were not significantly different between the SSc/SSc-overlap and non-SSc groups, respectively (n = 6, 60% vs. n = 9, 50%, p = 0.611). Conclusions Although ulnar artery involvement was frequently detected in patients with SSc/SSc-overlap, it was also a common finding in other CTDs; therefore, it is not specific to SSc or SSc-overlap diseases.

scholarly journals Obinutuzumab in connective tissue diseases after former rituximab-non-response: a case series

2022 ◽  
pp. annrheumdis-2021-221756
Author(s):  
Peter Kvacskay ◽  
Wolfgang Merkt ◽  
Janine Günther ◽  
Norbert Blank ◽  
Hanns-Martin Lorenz
Keyword(s):  
Connective Tissue ◽  
Connective Tissue Diseases ◽  
Case Series

HIV and Autoimmune Hepatitis: A Case Series and Literature Review

2017 ◽  
Vol 112 ◽  
pp. S1222
Author(s):  
Zachary Spiritos ◽  
Paul Reynolds ◽  
Samir Parekh ◽  
Adam Perricone ◽  
Brian Quigley
Keyword(s):  
Literature Review ◽  
Autoimmune Hepatitis ◽  
Hepatitis A ◽  
Case Series

scholarly journals PWE-284 Khat as a possible cause of drug induced autoimmune hepatitis; a case series

Gut ◽  
2012 ◽  
Vol 61 (Suppl 2) ◽  
pp. A413.2-A413
Author(s):  
S Riyaz ◽  
M Imran ◽  
M Karajeh
Keyword(s):  
Autoimmune Hepatitis ◽  
Hepatitis A ◽  
Case Series ◽  
Drug Induced ◽  
Possible Cause

scholarly journals Patients with ANCA-Associated Glomerulonephritis and Connective Tissue Diseases: A Comparative Study from the Maine-Anjou AAV Registry

2019 ◽  
Vol 8 (8) ◽  
pp. 1218
Author(s):  
Fanny Guibert ◽  
Anne-Sophie Garnier ◽  
Samuel Wacrenier ◽  
Giorgina Piccoli ◽  
Assia Djema ◽  
...  
Keyword(s):  
Connective Tissue ◽  
Thrombotic Event ◽  
Connective Tissue Diseases ◽  
Case Series ◽  
Rare Condition ◽  
Antineutrophil Cytoplasmic Antibody ◽  
Control Group ◽  
Renal Relapse ◽  
Patients Experience

Background and objectives: The overlap between antineutrophil cytoplasmic antibody (ANCA) associated glomerulonephritis (ANCA-GN) and connective tissue diseases (CTD) has been reported mainly as case series in the literature. Frequency of this association, as well as presentation and outcomes are unknown. Materials and Methods: Patients from the Maine-Anjou ANCA-associated vasculitides (AAV) registry with ANCA-GN diagnosed between 01/01/2000 and 01/01/2018, ANCA positivity, and at least six months of follow-up, were included. Results: 106 out of 142 patients fulfilled the inclusion criteria and were analyzed. CTD was present at ANCA-GN diagnosis in 16 (15.1%) patients. The most common CTD were rheumatoid arthritis, Sjogren syndrome and systemic sclerosis. Compared to the control group, females were more represented in the CTD group (75%, p = 0.001). Renal presentation was comparable between groups, including the pathological analysis of renal biopsies. Patients of CTD group presented a higher rate of non-renal relapse (25% versus 7.7%, p = 0.037), and experienced more frequently a venous thrombotic event (31.2% versus 10%, p = 0.021). No difference between groups was observed according to major outcomes. Conclusion: Association between CTD and ANCA-GN is not a rare condition and predominantly affects females. While AAV presentation is not significantly different, CTD patients experience more frequently non-renal relapse and venous thrombotic events.

scholarly journals HIV and Autoimmune Hepatitis: A Case Series and Literature Review

2017 ◽  
Vol 06 (02) ◽  
Author(s):  
Samir Parekh ◽  
Zachary Spiritos ◽  
Paul Reynolds ◽  
Samir Parekh ◽  
Adam Perricone ◽  
...  
Keyword(s):  
Literature Review ◽  
Autoimmune Hepatitis ◽  
Hepatitis A ◽  
Case Series

scholarly journals Myelodysplastic Syndrome and Autoimmunity: A Case Report of an Unusual Presentation of Myelodysplastic Syndrome

2011 ◽  
Vol 2011 ◽  
pp. 1-4 ◽  
Author(s):  
Andrea L. Merrill ◽  
Hedy Smith
Keyword(s):  
Case Report ◽  
Connective Tissue ◽  
Myelodysplastic Syndrome ◽  
Lacrimal Gland ◽  
Case Reports ◽  
Connective Tissue Diseases ◽  
Case Series ◽  
Organizing Pneumonia ◽  
Trisomy 8 ◽  
Autoimmune Phenomena

Myelodysplastic syndrome (MDS) commonly presents asymptomatically or with symptomatic cytopenias. However, autoimmune phenomena in association with MDS have been well described in several case reports and case series. Typically, these autoimmune phenomena take the form of vasculitides, arthritis, connective tissue diseases, pulmonary infiltrates, or polymyalgia rheumatica. We present the case of a woman with MDS (karyotype 46,XX,+1,der(1;7)(q10;p10)[20], that evolved with an additional trisomy 8 clone) and a novel spectrum of autoimmune diseases including acute fibrinous and organizing pneumonia (AFOP) and lacrimal gland pseudotumor.

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