Bilateral conductive deafness related to erosive lichen planus

1998 ◽  
Vol 112 (4) ◽  
pp. 365-366 ◽  
Author(s):  
Ludovic Martin ◽  
Sylvain Moriniere ◽  
Marie-Christine Machet ◽  
Alain Robier ◽  
Loïc Vaillant
Keyword(s):  
Hearing Loss ◽  
Lichen Planus ◽  
Conductive Hearing Loss ◽  
External Ear ◽  
Conductive Deafness ◽  
Erosive Lichen Planus ◽  
Conductive Hearing

AbstractA case of bilateral progressive stenosis of both external auditory canals with resultant conductive hearing loss is presented. The stenosis revealed multifocal erosive and synechiant lichen planus. To our knowledge, this is the first reported case of lichen planus involvement of the external ear.

scholarly journals Delayed-Onset NOG Gene-Related Syndromic Conductive Deafness: A Case Report

2020 ◽  
pp. 014556132094463
Author(s):  
Huiying Sun ◽  
Yufei Qiao ◽  
Na Chen ◽  
Hua Yang ◽  
Zhiqiang Gao ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Case Report ◽  
Otoacoustic Emissions ◽  
Normal Development ◽  
Conductive Hearing Loss ◽  
Newborn Hearing Screening ◽  
Delayed Onset ◽  
Conductive Deafness ◽  
Newborn Hearing ◽  
Conductive Hearing

We report a 6-year-old girl with progressive bilateral conductive hearing loss for 2 years. She passed the newborn hearing screening conducted with otoacoustic emissions testing and had a normal development of speech and language, which indicated that her deafness was delayed-onset. She also had congenital proximal interphalangeal joints. Proximal symphalangism was confirmed by genetic testing ( NOG gene: c.406C > T, p.R136C). Bilateral stapes ankyloses were proved by surgery and her hearing was improved after stapedotomy by over 30 dB. Besides, this case should remind clinicians to carefully distinguish NOG gene-related deafness from congenital ossicular malformation and pediatric otosclerosis.

Conductive hearing loss: investigation of possible inner ear origin in three cases studies

2002 ◽  
Vol 116 (11) ◽  
pp. 942-945 ◽  
Author(s):  
Hamad Al Muhaimeed ◽  
Yousry El Sayed ◽  
Abdulrahman Rabah ◽  
Abdulrahman Al-Essa
Keyword(s):  
Hearing Loss ◽  
Inner Ear ◽  
Conductive Hearing Loss ◽  
Round Window ◽  
The Third ◽  
Conductive Deafness ◽  
Mixed Hearing Loss ◽  
Stapedial Reflex ◽  
Conductive Hearing ◽  
Inner Ear Disorders

This is a report of three cases of mixed hearing loss that resulted from inner ear disorders. Two cases were unilateral and the third was bilateral. The diagnosis was based on the findings of normal middle and external ears in association with the absence of round window reflexes. The contralateral stapedial reflex was present in the two unilateral cases. This is the first documentation of conductive deafness due to inner ear abnormality. This diagnosis should be considered in cases of conductive hearing loss if the middle and external ears are normal. More studies are needed to establish the pathophysiology of this entity.

scholarly journals Neurofibroma in the external auditory canal

2019 ◽  
Vol 5 (4) ◽  
pp. 1095 ◽  
Author(s):  
Mona M. Saleh ◽  
Pola E. George ◽  
Mohammad M. Mohsen ◽  
Amir M. Eldakiky ◽  
Irinie G. Makarious
Keyword(s):  
Nervous System ◽  
Hearing Loss ◽  
Head And Neck ◽  
External Auditory Canal ◽  
Conductive Hearing Loss ◽  
Cosmetic Outcome ◽  
External Ear ◽  
Total Occlusion ◽  
Conductive Hearing

<p class="abstract">Neurofibromas are relatively common tumours of the nervous system, but only few cases involving the external ear have been reported. We are reporting here a case of a 30-year-old male with neurofibroma of the external auditory canal. The primary complaint was cosmetic deformity and mild conductive hearing loss. There was total occlusion of the external auditory canal. The swelling was excised by postauricular approach. Surgery resulted in an superb purposeful and cosmetic outcome. Neurofibromas of the head and neck do not seem to be uncommon, however they seldom have an effect on the external ear and only a few such published reports are available.</p>

Stapedius tendon ossification: A rare cause of congenital conductive hearing loss

1991 ◽  
Vol 105 (9) ◽  
pp. 763-764 ◽  
Author(s):  
William E. Grant ◽  
William J. Grant
Keyword(s):  
Hearing Loss ◽  
Conductive Hearing Loss ◽  
Presumptive Diagnosis ◽  
Bilateral Hearing Loss ◽  
Conductive Deafness ◽  
First Case ◽  
Conductive Hearing ◽  
Made In

AbstractTwo cases are presented of bilateral conductive deafness in siblings. An initial presumptive diagnosis of otosclerosis was made in the first case, that of a nine-year-old girl with a bilateral hearing loss of 45 dB. Exploratory tympanotomy revealed normal ossicles but the stapedius ‘tendon’ was found to be a solid bony bar fixing the stapes. Division of the ‘tendon’ resulted in normal ossicular mobility and return of hearing with closure of the air-bone gap. Identical ossification was found in her other ear, and some years later in both ears of one of her brothers. Similar surgery restored hearing successfully in each case. An acquired aetiology has been proposed in one of the three previously reported cases; this report, however, suggests the congenital nature of the anomaly. No previous cases have been described occurring in siblings.

Ear Malformation and Hearing Loss in Patients with Treacher Collins Syndrome

1993 ◽  
Vol 30 (1) ◽  
pp. 97-103 ◽  
Author(s):  
Gaylene Pron ◽  
Cheryl Galloway ◽  
Derek Armstrong ◽  
Jeffrey Posnick
Keyword(s):  
Hearing Loss ◽  
Inner Ear ◽  
Middle Ear ◽  
Conductive Hearing Loss ◽  
Treacher Collins Syndrome ◽  
External Ear ◽  
Ear Canal ◽  
Ear Malformations ◽  
Asymmetric Hearing Loss ◽  
Conductive Hearing

Although the hearing loss of patients with Treacher Collins syndrome is well documented, few studies have reported jointly on their hearing loss and ear pathology. This paper reports on the hearing loss and computerized tomography (CT) assessments of ear malformations in a large pediatric series of patients with Treacher Collins. Of the 29 subjects assessed by the Craniofacial Program between 1986 and 1990, paired audiologic and complete CT assessments were available for 23 subjects. The external ear canal abnormalities were largely symmetric, either bilaterally stenotic or atretic. In most cases, the middle ear cavity was bilaterally hypoplastic and dysmorphic, and ossicles were symmetrically dysmorphic or missing. Inner ear structures were normal in all patients. The majority of patients had a unilateral or bilateral moderate or greater degree of hearing loss and almost half had an asymmetric hearing loss. The hearing loss of all subjects was conductive, except for three whose loss was bilateral mixed. Two types of bilaterally symmetric hearing loss configurations, flat and reverse sloping, were noted. Conductive hearing loss in patients with Treacher Collins is mainly attributable to their middle ear malformations, which are similar for those of patients with malformed or missing ossicles.

scholarly journals Lifetime prevalence of exostoses in New Zealand surfers

2019 ◽  
Vol 11 (1) ◽  
pp. 47 ◽  
Author(s):  
Vini Simas ◽  
Debbie Remnant ◽  
James Furness ◽  
Catherine J. Bacon ◽  
Robert W. Moran ◽  
...  
Keyword(s):  
Hearing Loss ◽  
New Zealand ◽  
Conductive Hearing Loss ◽  
Fold Increase ◽  
Lifetime Prevalence ◽  
External Ear ◽  
Prevention Strategies ◽  
Progressive Hearing Loss ◽  
Ear Infections ◽  
Conductive Hearing

ABSTRACT INTRODUCTIONExternal auditory exostosis (EAE) is a benign, irreversible bony outgrowth that arises from the temporal bone. EAE projects into the external ear canal, potentially causing recurrent otitis externa and conductive hearing loss. AIMTo determine lifetime prevalence of EAE in New Zealand (NZ) surfers. METHODSThis study used an online national survey. RESULTSRespondents were 1376 NZ surfers (recreational = 868, competitive = 508). Mean surfing experience was 16.2 years. Most self-classified as advanced surfers (36.5%), followed by intermediate (30.2%), expert (20.1%) and beginner (13.2%). Surfers reported an average of 214.2 h surfing (28.6% during winter) for the previous year. Overall lifetime prevalence of EAE was 28.9% (32.1% male, 14.6% female; P &lt; 0.001), with the highest proportion of EAE was observed bilaterally (21.3%). Competitive surfers reported a significantly (P &lt; 0.001) higher lifetime prevalence of EAE than recreational surfers (45.3% vs. 19.2%). A significantly higher (P &lt; 0.001) lifetime prevalence of EAE was identified as skill level increased (7.1% in beginners to 55.6% in experts) and a two-fold increase (P &lt; 0.001) of EAE in the highest (vs. lowest) quartile of surfing exposure. Neither winter surfing exposure nor which Island surfed were associated with EAE prevalence. DISCUSSIONAlthough not as prevalent as in previous NZ research using otologic examinations, this study indicated that almost one-third of NZ surfers reported having had a diagnosis of EAE. Regular general practitioner otologic assessment and advice on appropriate prevention strategies for patients who surf may help prevent large lesions, recurrent ear infections and progressive hearing loss.

scholarly journals Unusual case of unilateral conductive hearing loss: chronic lymphocytic leukaemia

2018 ◽  
pp. bcr-2017-223444
Author(s):  
Amelia Leigh Davis ◽  
Shane Gangatharan ◽  
Jafri Kuthubutheen
Keyword(s):  
Hearing Loss ◽  
Differential Diagnosis ◽  
Chronic Lymphocytic Leukaemia ◽  
Unusual Case ◽  
Lymphocytic Leukaemia ◽  
Conductive Hearing Loss ◽  
Cutaneous Lesion ◽  
External Ear ◽  
Ear Canal ◽  
Conductive Hearing

This presentation reports a novel case of chronic lymphocytic leukaemia (CLL), presenting with an early cutaneous lesion within the external auditory canal, in a patient being assessed for conductive hearing loss. It has previously been reported that infiltrative CLL can involve the head and neck; however, isolated external ear canal involvement is rare. Given that the incidence of CLL in Australia is rising, this case highlights the importance of considering CLL as a differential diagnosis for presentations of unilateral conductive hearing loss.

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