Audiological evaluation and self-assessed hearing problems in subjects with single-sided congenital external ear malformations and associated conductive hearing loss

Although the hearing loss of patients with Treacher Collins syndrome is well documented, few studies have reported jointly on their hearing loss and ear pathology. This paper reports on the hearing loss and computerized tomography (CT) assessments of ear malformations in a large pediatric series of patients with Treacher Collins. Of the 29 subjects assessed by the Craniofacial Program between 1986 and 1990, paired audiologic and complete CT assessments were available for 23 subjects. The external ear canal abnormalities were largely symmetric, either bilaterally stenotic or atretic. In most cases, the middle ear cavity was bilaterally hypoplastic and dysmorphic, and ossicles were symmetrically dysmorphic or missing. Inner ear structures were normal in all patients. The majority of patients had a unilateral or bilateral moderate or greater degree of hearing loss and almost half had an asymmetric hearing loss. The hearing loss of all subjects was conductive, except for three whose loss was bilateral mixed. Two types of bilaterally symmetric hearing loss configurations, flat and reverse sloping, were noted. Conductive hearing loss in patients with Treacher Collins is mainly attributable to their middle ear malformations, which are similar for those of patients with malformed or missing ossicles.

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Bilateral conductive deafness related to erosive lichen planus

The Journal of Laryngology & Otology ◽

10.1017/s0022215100140472 ◽

1998 ◽

Vol 112 (4) ◽

pp. 365-366 ◽

Cited By ~ 20

Author(s):

Ludovic Martin ◽

Sylvain Moriniere ◽

Marie-Christine Machet ◽

Alain Robier ◽

Loïc Vaillant

Keyword(s):

Hearing Loss ◽

Lichen Planus ◽

Conductive Hearing Loss ◽

External Ear ◽

Conductive Deafness ◽

Erosive Lichen Planus ◽

Conductive Hearing

AbstractA case of bilateral progressive stenosis of both external auditory canals with resultant conductive hearing loss is presented. The stenosis revealed multifocal erosive and synechiant lichen planus. To our knowledge, this is the first reported case of lichen planus involvement of the external ear.

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Neurofibroma in the external auditory canal

International Journal of Otorhinolaryngology and Head and Neck Surgery ◽

10.18203/issn.2454-5929.ijohns20192737 ◽

2019 ◽

Vol 5 (4) ◽

pp. 1095 ◽

Cited By ~ 1

Author(s):

Mona M. Saleh ◽

Pola E. George ◽

Mohammad M. Mohsen ◽

Amir M. Eldakiky ◽

Irinie G. Makarious

Keyword(s):

Nervous System ◽

Hearing Loss ◽

Head And Neck ◽

External Auditory Canal ◽

Conductive Hearing Loss ◽

Cosmetic Outcome ◽

External Ear ◽

Total Occlusion ◽

Conductive Hearing

<p class="abstract">Neurofibromas are relatively common tumours of the nervous system, but only few cases involving the external ear have been reported. We are reporting here a case of a 30-year-old male with neurofibroma of the external auditory canal. The primary complaint was cosmetic deformity and mild conductive hearing loss. There was total occlusion of the external auditory canal. The swelling was excised by postauricular approach. Surgery resulted in an superb purposeful and cosmetic outcome. Neurofibromas of the head and neck do not seem to be uncommon, however they seldom have an effect on the external ear and only a few such published reports are available.</p>

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Contralateral occlusion test: The effect of external ear canal occlusion on predicting conductive hearing loss

Acta Otorrinolaringologica (English Edition) ◽

10.1016/j.otoeng.2020.06.001 ◽

2020 ◽

Vol 71 (4) ◽

pp. 235-241

Author(s):

Luis Roque Reis ◽

Luís Castelhano ◽

Filipe Correia ◽

Pedro Escada

Keyword(s):

Hearing Loss ◽

Conductive Hearing Loss ◽

External Ear ◽

Ear Canal ◽

Occlusion Test ◽

External Ear Canal ◽

Conductive Hearing

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Lifetime prevalence of exostoses in New Zealand surfers

Journal of Primary Health Care ◽

10.1071/hc18097 ◽

2019 ◽

Vol 11 (1) ◽

pp. 47 ◽

Cited By ~ 3

Author(s):

Vini Simas ◽

Debbie Remnant ◽

James Furness ◽

Catherine J. Bacon ◽

Robert W. Moran ◽

...

Keyword(s):

Hearing Loss ◽

New Zealand ◽

Conductive Hearing Loss ◽

Fold Increase ◽

Lifetime Prevalence ◽

External Ear ◽

Prevention Strategies ◽

Progressive Hearing Loss ◽

Ear Infections ◽

Conductive Hearing

ABSTRACT INTRODUCTIONExternal auditory exostosis (EAE) is a benign, irreversible bony outgrowth that arises from the temporal bone. EAE projects into the external ear canal, potentially causing recurrent otitis externa and conductive hearing loss. AIMTo determine lifetime prevalence of EAE in New Zealand (NZ) surfers. METHODSThis study used an online national survey. RESULTSRespondents were 1376 NZ surfers (recreational = 868, competitive = 508). Mean surfing experience was 16.2 years. Most self-classified as advanced surfers (36.5%), followed by intermediate (30.2%), expert (20.1%) and beginner (13.2%). Surfers reported an average of 214.2 h surfing (28.6% during winter) for the previous year. Overall lifetime prevalence of EAE was 28.9% (32.1% male, 14.6% female; P < 0.001), with the highest proportion of EAE was observed bilaterally (21.3%). Competitive surfers reported a significantly (P < 0.001) higher lifetime prevalence of EAE than recreational surfers (45.3% vs. 19.2%). A significantly higher (P < 0.001) lifetime prevalence of EAE was identified as skill level increased (7.1% in beginners to 55.6% in experts) and a two-fold increase (P < 0.001) of EAE in the highest (vs. lowest) quartile of surfing exposure. Neither winter surfing exposure nor which Island surfed were associated with EAE prevalence. DISCUSSIONAlthough not as prevalent as in previous NZ research using otologic examinations, this study indicated that almost one-third of NZ surfers reported having had a diagnosis of EAE. Regular general practitioner otologic assessment and advice on appropriate prevention strategies for patients who surf may help prevent large lesions, recurrent ear infections and progressive hearing loss.

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Unusual case of unilateral conductive hearing loss: chronic lymphocytic leukaemia

BMJ Case Reports ◽

10.1136/bcr-2017-223444 ◽

2018 ◽

pp. bcr-2017-223444

Author(s):

Amelia Leigh Davis ◽

Shane Gangatharan ◽

Jafri Kuthubutheen

Keyword(s):

Hearing Loss ◽

Differential Diagnosis ◽

Chronic Lymphocytic Leukaemia ◽

Unusual Case ◽

Lymphocytic Leukaemia ◽

Conductive Hearing Loss ◽

Cutaneous Lesion ◽

External Ear ◽

Ear Canal ◽

Conductive Hearing

This presentation reports a novel case of chronic lymphocytic leukaemia (CLL), presenting with an early cutaneous lesion within the external auditory canal, in a patient being assessed for conductive hearing loss. It has previously been reported that infiltrative CLL can involve the head and neck; however, isolated external ear canal involvement is rare. Given that the incidence of CLL in Australia is rising, this case highlights the importance of considering CLL as a differential diagnosis for presentations of unilateral conductive hearing loss.

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