Cementum and other root abnormalities of permanent teeth in cleidocranial dysostosis

BDJ ◽  
1975 ◽  
Vol 139 (8) ◽  
pp. 313-318 ◽  
Author(s):  
A D Hitchin
Keyword(s):  
Permanent Teeth ◽  
Cleidocranial Dysostosis

MONGOLISM (MONGOLOID DEFICIENCY) DURING EARLY INFANCY—SOME NEWLY RECOGNIZED DIAGNOSTIC CHANGES IN THE PELVIC BONES

PEDIATRICS ◽  
1956 ◽  
Vol 17 (5) ◽  
pp. 642-651
Author(s):  
John Caffey ◽  
Steven Ross
Keyword(s):  
General Population ◽  
Permanent Teeth ◽  
Dental Anomalies ◽  
Pelvic Bones ◽  
Cleidocranial Dysostosis ◽  
Vertebral Bodies ◽  
The Mean ◽  
Frontal Sinuses ◽  
Base Of The Skull ◽  
Diagnostic Changes

IN MONGOLOID defectives, stigmas in the skeleton have been reported at several sites: hypoplasia of the base of the skull; hypoplasia of the nasal and other facial bones, and dysplasia and hypoplasia of metacarpals and phalanges. Undergrowth of the vertebral bodies and the tubular bones in the extremities is responsible for the dwarfism which is one of the most consistent components of this syndrome. Maturation of the skeleton varies greatly in different mongoloid infants; it may be advancecd, normal, or retarded. At birth practically all infants with mongolism show normal or advanced maturation, in our experience. Spitzer and Robinson found the frontal sinuses to be absent in 26 out of 28 individuals with mongolism in contrast to an absence in 4 to 5 per 100 of the remainder of the general population. Only 2 of the 28 individuals with mongolism showed no dental aplasia. The erupted teeth were commonly stunted, eruption of the permanent teeth was often delayed, and there was a higher incidence of the dental anomalies found than in the general population. No pathognomonic lesions in the teeth were found. The partial anodontia, deformed teeth and delayed eruption resemble the changes found in ectodermal dysplasia and in cleidocranial dysostosis. Smith and McKeown found the mean weights of newly born infants with mongolism to be 2860 gm. in contrast to 3220 gm. for normal newborns. the mean duration of gestation to he shorter for infants with mongolism than for normal newborns, 269 days and 278 days respectively. So far as we have been able to ascertain, stigmas in the pelvic bones of infants with mongolism have not been reported in either anatomical or roentgenographic studies.

scholarly journals Orthodontic Treatment in a Patient with Cleidocranial Dysostosis

2009 ◽  
Vol 79 (1) ◽  
pp. 178-185 ◽  
Author(s):  
Giampietro Farronato ◽  
Cinzia Maspero ◽  
Davide Farronato ◽  
Silvia Gioventù
Keyword(s):  
Ethnic Group ◽  
Orthodontic Treatment ◽  
Primary Dentition ◽  
Permanent Teeth ◽  
Supernumerary Teeth ◽  
Impacted Teeth ◽  
Cleidocranial Dysostosis ◽  
Skeletal Disorder ◽  
Maxilla And Mandible ◽  
Delayed Closure

Abstract Cleidocranial dysostosis is a rare congenital skeletal disorder, associated with clavicular hypoplasia or aplasia, delayed closure of cranial fontanels, brachycephalic skull, delayed exfoliation of primary dentition, eruption of permanent teeth, and multiple supernumerary and morphologic abnormalities of the maxilla and mandible. The disorder is caused by mutation in the CBFA1 gene, on the short arm of chromosome 6p21. The prevalence of cleidocranial dysostosis is estimated one per million, without sex or ethnic group predilection. The purpose of this paper is to describe the orthodontic treatment in a patient with cleidocranial dysostosis. Therapy may include removal of supernumerary teeth, surgical exposure of impacted teeth, and orthodontic treatment.

The Surgical and Orthodontic Management of Unerupted Teeth in Cleidocranial Dysostosis

1987 ◽  
Vol 14 (1) ◽  
pp. 43-47 ◽  
Author(s):  
T. M. Davies ◽  
D. H. Lewis ◽  
G. V. Gillbe
Keyword(s):  
Permanent Dentition ◽  
Permanent Teeth ◽  
Deciduous Teeth ◽  
The Past ◽  
Cleidocranial Dysostosis ◽  
Unerupted Teeth ◽  
Orthodontic Forces

A common feature of patients with cleidocranial dysostosis is delayed shedding of deciduous teeth and failure of eruption of the permanent dentition. This article describes a method whereby orthodontic forces may be applied to these unerupted permanent teeth to move them into a satisfactory functional and aesthetic position with good periodontal support whilst maintaining their vitality. This method of treatment avoids the need for overdentures or other prosthetic aids which have often been used in the past.

Signs and symptoms of craniomandibular dysfunction in a population of Spanish children

2018 ◽  
Vol 16 (1) ◽  
pp. 24
Author(s):  
Maria Esperanza Sánchez-Sánchez
Keyword(s):  
Signs And Symptoms ◽  
Permanent Teeth ◽  
Tooth Sensitivity ◽  
Craniomandibular Dysfunction ◽  
Teeth Grinding ◽  
Specific Questionnaire ◽  
Other Hand ◽  
Opening And Closing

The craniomandibular dysfunction (CMD) is a pathology that can appear at early ages. In a sample of 36 childrenresiding in Madrid (Spain), of both sexes, with ages between 7 and 13 years, the prevalence of signs and symptomsof CMD was analyzed. For that purpose, we did a dental and muscular examination, together with temporomandibularjoints, functional and occlusal examination, and completed with a specific questionnaire. The results revealedthat 100% showed some sign or sympthom of CMD. 77,8% of the pacients presented 3 or more CMD signs.The most prevalent were painful muscle palpation (94,4%), together with sliding anteriorly (91,7%), painful jointpalpation (69,4%), wear facets in permanent teeth (41,7%) and altered opening and closing trayectory (38,9%). Onthe other hand, only 38,9% showed any CMD symptom. The most prevalent symptoms were night teeth grinding(27,8%), followed by tooth sensitivity (19,4%) and fullness in the ears (16,7%). We conclude that in our sample,25% presented mild CMD (less that 3 signs or symptoms), 58,3% presented moderate CMD (from 3 to 6 signs orsymptoms) and 16,7% showed severe CMD (more than 6 symptoms). Nevertheless, it’s important to remark thatnone of these pacients came seeking treatment for his CMD and these symptoms were refered only when beingasked. Hence the importance of a comprehensive clinic history to precociously diagnose this pathology and havethe ability to prevent its progression.

A Case of Immature Permanent Teeth with Traumas

1992 ◽  
Vol 46 (6) ◽  
pp. 848-854
Author(s):  
Akiko Morimoto ◽  
Tosiko Sakamoto ◽  
Syoji Kodama ◽  
Kyoko Nagoshi ◽  
Ryuiti Nakashima ◽  
...  
Keyword(s):  
Permanent Teeth

Resorption of multirooted temporary teeth in children with dentofacial anomalies in accordance with the orthopantomography data

2020 ◽  
Vol 20 (3) ◽  
pp. 235-241
Author(s):  
F. S. Ayupova ◽  
S. N. Alekseenko ◽  
V. Ya. Zobenko ◽  
T. V. Gayvoronskaya
Keyword(s):  
Primary Teeth ◽  
Root Resorption ◽  
Type A ◽  
Mixed Dentition ◽  
Permanent Teeth ◽  
Primary Molars ◽  
Second Primary ◽  
X Rays ◽  
Primary Molar ◽  
Posterior Teeth

Relevance. To study the incidence of different types of resorption of multirooted primary teeth, to specify indications for deciduous molar extraction to prevent eruption abnormalities of permanent posterior teeth in mixed dentition.Materials and methods. Root resorption of 375 multirooted primary teeth (166 first primary molars and 209 second primary molars) was studied on panoramic X-rays of 60 children (30 girls and 30 boys) aged between 7 and 15. Illustrated classification by T.F. Vinogradova (1967) improved by authors was used to determine type and degree of root resorption of multi-rooted primary teeth. Received data were described with absolute values of number of cases and percentage. Chi-square was used to detect differences in sign incidence rate between groups, p<0.05 was considered statistically significant.Results. There were no statistically significant gender differences (p>0,05) in type and degree of root resorption of multirooted primary teeth. Type A resorption prevailed and constituted 53.3% of all primary molars. Disturbances in root resorption of multirooted primary teeth in mixed dentition were related to health condition of primary teeth. Transition of even resorption to unven was considered a risk factor of delayed eruption and aberrant position of permanent teeth, and indication for extraction of a primary molar in question. Conclusions. 1) Even root resorption (type A) was detected in 53.3% of primary molars in mixed dentition by orthopantomography. 2) Transition from even resorption of primary molar roots to uneven resorption was associated with eruption deviations and delayed premolar eruption. 3) Timely extraction of primary molars with uneven root resorption facilitated correct eruption of premolars and increased effectiveness of secondary prevention of malocclusion in children.

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