Evidence of unilateral diaphragmatic paralysis on lung scintigraphy after double lung transplantation: impact on lung function and survival

2020 ◽  
Vol 80 (6) ◽  
pp. 454-455
Author(s):  
Anna Warncke Kristensen ◽  
Anders Møller Greve ◽  
Rasmus H. Dahl ◽  
Michael Perch ◽  
Jann Mortensen ◽  
...  
Keyword(s):  
Lung Function ◽  
Lung Transplantation ◽  
Diaphragmatic Paralysis ◽  
Lung Scintigraphy

Lymphangioleiomyomatosis

2020 ◽  
pp. 4257-4259
Author(s):  
S. J. Bourke
Keyword(s):  
Smooth Muscle ◽  
Lung Function ◽  
Lung Transplantation ◽  
Hormonal Therapy ◽  
Muscle Cells ◽  
Gas Diffusion ◽  
Hormonal Replacement ◽  
Increased Risk ◽  
Genes Encoding ◽  
Thin Walled

Lymphangioleiomyomatosis is characterized by cystic destruction of the lungs due to abnormal proliferation of smooth muscle cells. It is caused by mutations of the genes encoding hamartin and tuberin, sometimes in association with tuberous sclerosis. CT imaging shows characteristic multiple thin-walled cysts. There is usually progressive airways obstruction and impaired gas diffusion, and two-thirds of patients suffer pneumothoraces. Sirolimus can stabilize lung function and improve symptoms. Patients should avoid exogenous oestrogens, including oestrogen contraceptives or hormonal replacement therapy. Pregnancy may be associated with an increased risk of pneumothorax and loss of lung function. Hormonal therapy with progesterone or tamoxifen appears to be ineffective: other antioestrogen therapies, such as letrozole, are being studied. Lung transplantation is the main option for advanced disease.

N-octanoyl dopamine ameliorates lung function in the acute phase after lung transplantation

2014 ◽  
Vol 31 (4) ◽  
pp. 257-258
Author(s):  
C.M.V. Hottenrott ◽  
C. Tsagogiorgas ◽  
H.G.D. Leuvenink ◽  
M.E. Erasmus
Keyword(s):  
Lung Function ◽  
Lung Transplantation ◽  
Acute Phase

Lung Function Decline in Cystic Fibrosis Patients and Timing for Lung Transplantation Referral

CHEST Journal ◽  
2004 ◽  
Vol 126 (2) ◽  
pp. 412-419 ◽  
Author(s):  
Daniel B. Rosenbluth ◽  
Kevin Wilson ◽  
Thomas Ferkol ◽  
Daniel P. Schuster
Keyword(s):  
Cystic Fibrosis ◽  
Lung Function ◽  
Lung Transplantation ◽  
Lung Function Decline

Testing Lung Function Decline to Time Lung Transplantation

CHEST Journal ◽  
2005 ◽  
Vol 128 (1) ◽  
pp. 472-473 ◽  
Author(s):  
Theodore G. Liou ◽  
Frederick R. Adler ◽  
Barbara C. Cahill
Keyword(s):  
Lung Function ◽  
Lung Transplantation ◽  
Lung Function Decline

Predictive value of donor age for recipient lung function and CLAD-free survival after lung transplantation

2015 ◽  
Author(s):  
Henrik Auråen ◽  
Arnt Fiane ◽  
Odd Geiran ◽  
Øystein Bjørtuft ◽  
Inga Leuckfeld ◽  
...  
Keyword(s):  
Lung Function ◽  
Lung Transplantation ◽  
Predictive Value ◽  
Donor Age ◽  
Free Survival
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