scholarly journals Inflammatory myofibroblastic tumour in the right ventricle of a 66-year-old man

2019 ◽  
Vol 29 (6) ◽  
pp. 967-968
Author(s):  
Diego Monzón Díaz ◽  
Gregorio Cuerpo Caballero ◽  
Angela Irabien Ortiz ◽  
Ángel Gonzalez Pinto
Keyword(s):  
Surgical Technique ◽  
Right Ventricle ◽  
Surgical Resection ◽  
Rare Entity ◽  
Inflammatory Myofibroblastic Tumour ◽  
Review Of The Literature ◽  
First Case ◽  
The Right

Abstract Herein, we present the case of a 66-year-old man with an inflammatory myofibroblastic tumour. An inflammatory myofibroblastic tumour is an extremely rare entity, with only 60 cases having been reported to date in the literature. The origin of this type of tumour is unknown and the treatment of choice is surgical resection. We present the surgical technique of our case and a review of the literature regarding this tumour. This is the first case described in a man above 60 years of age with a tumour located in the right ventricle.

Perinatal intracardiac teratoma: unusual presentation and review of the literature

2019 ◽  
Vol 29 (3) ◽  
pp. 439-441
Author(s):  
Anne Moreau de Bellaing ◽  
Lucile Houyel ◽  
Damien Bonnet
Keyword(s):  
Ventricular Arrhythmia ◽  
Right Ventricle ◽  
Surgical Resection ◽  
Cystic Mass ◽  
Unusual Presentation ◽  
Review Of The Literature ◽  
The Common ◽  
The Right ◽  
Almost All ◽  
Extracorporeal Support

AbstractIntracardiac teratomas are rare primary tumours. We report the case of an infant prenatally diagnosed with an isolated multi-cystic mass developed in the right ventricle causing neonatal refractory ventricular arrhythmia. Despite rescue extracorporeal support and partial surgical resection, he died as almost all the previous reported perinatal intracardiac teratomas whatever the prenatal tolerance and the size of the tumour. The common poor outcome of fetal intracardiac teratomas should be known when counselling parents during pregnancy.

scholarly journals Squamous Cell Carcinoma of Kidney and Its Prognosis: A Case Report and Review of the Literature

2015 ◽  
Vol 2015 ◽  
pp. 1-3 ◽  
Author(s):  
Tapan Kumar Sahoo ◽  
Saroj Kumar Das ◽  
Chandraprava Mishra ◽  
Ipsita Dhal ◽  
Rohani Nayak ◽  
...  
Keyword(s):  
Squamous Cell Carcinoma ◽  
Cell Carcinoma ◽  
Squamous Cell ◽  
Radical Nephrectomy ◽  
Advanced Stage ◽  
Rare Entity ◽  
Primary Squamous Cell Carcinoma ◽  
Review Of The Literature ◽  
Radiological Features ◽  
The Right

Primary squamous cell carcinoma of the renal parenchyma is an extremely rare entity. The diagnosis of squamous cell carcinoma of the renal pelvis is usually unsuspected due to the rarity and inconclusive clinical and radiological features. Most of the patients are diagnosed at an advanced stage and are with poor outcome. Radical nephrectomy is the mainstay of the treatment. We reported a case of squamous cell carcinoma of the kidney in a 50-year-old female who presented with the right sided abdomen pain. The patient was treated with radical nephrectomy.

scholarly journals Surgical approach and prognosis of primitive chest wall alveolar rhabdomyosarcoma in an adult: A case report and review of the literature

2020 ◽  
Vol 5 (2) ◽  
pp. 104-108
Author(s):  
Narindra Njarasoa Mihaja Razafimanjato ◽  
◽  
Tsiry Dama Ntsoa Ravelomihary ◽  
Mampionona Ranaivomanana ◽  
Guillaume Odilon Tsiambanizafy ◽  
...  
Keyword(s):  
Chest Wall ◽  
Surgical Approach ◽  
Complete Resection ◽  
Alveolar Rhabdomyosarcoma ◽  
Chest Wall Resection ◽  
Rare Entity ◽  
Review Of The Literature ◽  
Dorsi Muscle ◽  
First Case ◽  
Multimodal Management

Alveolar rhabdomyosarcomas (ARMS) are rare entities that occur predominantly on the extremities and represent 20% of rhabdomyosarcomas. Other common locations include the peri-rectal and perineal regions, head and neck, and genitourinary system. To our knowledge, this presentation is the first case of alveolar rhabdomyosarcoma of the chest wall reported in the literature. Here, we describe a case of a 64-year-old man with alveolar rhabdomyosarcomas who underwent a chest wall resection. The defect was reconstructed with polypropylene mesh and latissimus dorsi muscle. Our patient did not show recurrence ten months after complete resection. The present paper describes our surgical approach to a case of primary alveolar rhabdomyosarcoma of the chest wall in an adult. The authors discuss the principal judgment criteria for successful surgical resection and prognosis, highlighting the relevance of chest wall reconstruction and their complementary aspects in the multimodal management of this rare entity.

Monophasic Synovial Sarcoma Arising in the Vulva: A Case Report and Review of the Literature

2008 ◽  
Vol 132 (4) ◽  
pp. 698-702
Author(s):  
Beverly E. White ◽  
Alan Kaplan ◽  
Dolores H. Lopez-Terrada ◽  
Jae Y. Ro ◽  
Robert S. Benjamin ◽  
...  
Keyword(s):  
Synovial Sarcoma ◽  
Soft Tissues ◽  
English Literature ◽  
Review Of The Literature ◽  
First Case ◽  
Additional Surgery ◽  
Synovial Sarcomas ◽  
The Right ◽  
Disease Free ◽  
Vulvar Mass

Abstract Synovial sarcomas most commonly arise in the soft tissue of the extremities. Less commonly, these tumors present in the head and neck, abdominal wall, and other sites. However, synovial sarcoma occurring in the vulvar area is extremely rare. Only 2 previous cases of biphasic synovial sarcoma of the vulva have been reported, but no case of vulvar monophasic synovial sarcoma has been described in the English literature. We report the third case of synovial sarcoma and apparently the first case of monophasic synovial sarcoma arising in soft tissues of the vulva. The patient was a 33-year-old woman who presented for evaluation of a painless vulvar mass. The tumor was located in the deep fibroadipose tissue of the right vulva (6.5 × 4.2 × 3.5 cm). The histology of the lesion was that of a monophasic synovial sarcoma with a hemangiopericytic vascular pattern. A subsequent molecular analysis revealed SYT-SSX2 gene fusion, which confirmed the diagnosis of synovial sarcoma. After an initial wide local excision, the patient developed a recurrence in the right groin and received chemotherapy and additional surgery. The patient is currently disease free, on adjuvant chemotherapy, and being followed up closely.

scholarly journals 479 When 2 rights make a wrong

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
J Tong ◽  
P Joseph Francis ◽  
E Lee
Keyword(s):  
Right Ventricle ◽  
Tricuspid Valve ◽  
Cardiac Mri ◽  
Right Atrium ◽  
Cardiac Myxoma ◽  
Left Ventricular Ejection ◽  
Definitive Treatment ◽  
Transthoracic Echocardiogram ◽  
First Case ◽  
The Right

Abstract Background The presence of an intra-cardiac mass is always a cause for concern, with regards to not only aetiology, but also treatment of complications. We describe a case series of 2 right sided cardiac myxomas, where the first case described an unusual location for tumour occurrence, while the second case provided insights into complications of a cardiac myxoma. Methods The first case involved a 70 year old asymptomatic lady who was referred for an additional heart sound. A transthoracic echocardiogram (TTE) showed a large, mobile 1.5 X 1.2 cm mass, attached to the atrial surface of septal tricuspid valve leaflet, prolapsing in and out of the right sided chambers. This was confirmed on transoesophageal echocardiogram (TEE). Cardiac MRI (magnetic resonance imaging) showed a similar mass attached to the septal tricuspid leaflet with features consistent with a myxoma. She was referred to cardiothoracic surgery, and 2 lobulated tumours arising the septal tricuspid valve and adjacent posterior leaflet were seen. The tumours were resected and a bio-prosthetic tricuspid valve replacement implanted. Histology of the tumours showed myxomatous degeneration of tricuspid valve, consistent with cardiac myxoma. The second case was a 56 year old lady who had dyspnoea, pedal oedema and an elevated jugular venous pulse on examination. A TTE done showed a large 7 X 4 cm mass extending from the right atrium (RA) into the right ventricle (RV). The left ventricular ejection fraction was 35%. Cardiac MRI confirmed the presence of a large mass in the right ventricle that exerted pressure effects on the ventricular septum and RV anterior free wall. Intra-operatively, a large RA mass attached by a stalk to the fossa ovalis was seen. The mass was excised and histology was consistent with cardiac myxoma. A repeat transthoracic echocardiogram done 2 weeks later showed normalisation of the LVEF. See images below for more information. Conclusion While myxomas are the most common benign cardiac tumours, they occur less commonly in the right atrium, and much less so on the tricuspid valve. Clinical manifestations range from being completely asymptomatic, as in the 1st case, to non-specific constitutional symptoms such as fever or general malaise, and to life-threatening complications. These include embolism to the pulmonary circulation, causing sudden death, or to the systemic circulation through an intra-cardiac shunt, causing strokes. This risk is increased if the tumour is large, polypoidal and friable. Large tumours can also cause obstructive symptoms and heart failure. Thus timely diagnosis with multi-modality imaging tools, and definitive treatment with complete resection of the tumour are essential. Continued monitoring for recurrences of the tumour, which can occur in 1-5% of all cases, should be performed as well. Abstract 479 Figure. Right sided cardiac masses

Angioma Serpiginosum with Linear Distribution: Case Report and Review of the Literature

2008 ◽  
Vol 12 (4) ◽  
pp. 180-183 ◽  
Author(s):  
Mike S. Kalisiak ◽  
Richard M. Haber
Keyword(s):  
Case Report ◽  
Vascular Anomaly ◽  
Rare Entity ◽  
Review Of The Literature ◽  
Linear Distribution ◽  
Delayed Treatment ◽  
Skin Biopsies ◽  
The Common ◽  
The Right ◽  
Histopathologic Findings

Background: Angioma serpiginosum is a vascular anomaly that classically presents in childhood and predominantly affects females. Objective: To present a case of a young woman with linear distribution of angioma serpiginosum and review the common clinical characteristics and presentation of this condition. Methods: Case report with skin biopsies and dermoscopic findings. Results: A clinical examination revealed numerous irregular punctate red macules in a linear distribution over the right arm. On dermoscopy, the lesions appeared as multiple sharply demarcated red lagoons. The histopathologic findings of dilated blood vessels in the papillary dermis with absence of other changes confirmed the diagnosis of angioma serpiginosum. Conclusion: Angioma serpiginosum is a rare entity that can be distinguished by clinical and histopathologic examinations. Lack of recognition of this condition may lead to unnecessary investigations and delayed treatment.

scholarly journals Ganglioneuromatous Polyposis of the Colon: a Case Report and a Review of the Literature

2011 ◽  
Vol 02 (01) ◽  
pp. 018-021
Author(s):  
Cristina D'Ercole ◽  
Angelo Zullo ◽  
Maria Consiglia Bragazzi ◽  
Cesare Hassan ◽  
Roberto Lorenzetti ◽  
...  
Keyword(s):  
Nervous System ◽  
Abdominal Pain ◽  
Clinical Signs ◽  
Rare Entity ◽  
Ascending Colon ◽  
Review Of The Literature ◽  
Endoscopic Feature ◽  
Systemic Manifestations ◽  
The Right ◽  
Intestinal Ganglioneuromatosis

ABSTRACTThis report discusses a case of ganglioneuromatous polyposis of the colon in a woman without any other systemic manifestations. To our knowledge, this is the first report of the few cases of intestinal ganglioneuromatosis described in the literature presenting with abdominal pain and bloody diarrhea as unique clinical signs, with multiple polyps confined in the right side of the transverse colon and in the ascending colon. Of note, the endoscopic feature of such a rare entity - which involves the enteric nervous system - may mimic that of sessile adenomatous polyps which are diagnosed at routine colonoscopy. We emphasized that this condition may be misdiagnosed, and we reviewed the reported cases in the literature. (J Dig Endosc 2011;2(1):18-21)

Giant right ventricle infiltrative lipoma—a surgical success report

2020 ◽  
Vol 31 (2) ◽  
pp. 277-279
Author(s):  
Michelle Mizrahi ◽  
Silvia Jimenez-Becerra ◽  
Guillermo E Castro-Lozano ◽  
Mario Gómez-Sánchez
Keyword(s):  
Right Ventricle ◽  
Surgical Resection ◽  
Treatment Guidelines ◽  
Total Resection ◽  
Surgical Success ◽  
Cardiac Tumours ◽  
The Right ◽  
Heart Tumour ◽  
Great Portion

Abstract Benign primary cardiac tumours are rare, with lipomas accounting for <9% of them. Their presentation varies depending on the size and location of the tumour, with the majority of the cases being asymptomatic. We are presenting a case of an extremely rare primary heart-tumour infiltrating the right ventricle (RV) compromising its function. RV lipomas are so unusual that there are no clear treatment guidelines. In this case, we decided to treat the patient with surgical resection of the tumour. Although a total resection was not possible, due to the tumoural proximity to vital structures, a great portion of the tumour was removed, alleviating the patient’s symptoms.

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