scholarly journals Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity

2018 ◽  
Vol 2018 ◽  
pp. 1-3
Author(s):  
Hilal Erinanc ◽  
Mehmet Ozulku ◽  
Aysen Terzi
Keyword(s):  
World Literature ◽  
Inferior Vena ◽  
Vena Cava ◽  
Initial Diagnosis ◽  
Management Options ◽  
Complete Surgical Resection ◽  
Vascular Origin ◽  
Short Saphenous Vein ◽  
Aggressive Tumor ◽  
Vascular Leiomyosarcoma

Primary leiomyosarcomas of vascular origin are rare tumors. They frequently arise within the inferior vena cava; however, the peripheral vein was also affected. To date, only a few hundred cases have been reported in the world literature. Although it is an extremely aggressive tumor, the symptoms may be unspecific, especially in the lower extremities. In this report, we present a case of primary vascular leiomyosarcoma, arising from the short saphenous vein, with symptoms mimicking thrombus in the initial diagnosis. The diagnosis of leiomyosarcomas was confirmed by standard H&E staining and immunohistochemical staining. Recurrence of the tumor has been observed five years after surgical treatment. Due to its rarity, experience in the management of this type of tumor is limited. The mainstay of treatment for these tumors is complete surgical resection. The purpose of the presented case is to discuss the clinicopathological features and management options of this tumor, under the light of the most recent literatures.

scholarly journals Leiomyosarcoma of the inferior vena cava: Analysis and search of world literature on 141 patients and report of three new cases

1991 ◽  
Vol 14 (5) ◽  
pp. 688-699 ◽  
Author(s):  
Andrea Mingoli ◽  
Richard J. Feldhaus ◽  
Antonino Cavallaro ◽  
Sergio Stipa
Keyword(s):  
Inferior Vena Cava ◽  
World Literature ◽  
Inferior Vena ◽  
Vena Cava

Inferior Vena Cava Aneurysm

Vascular ◽  
2009 ◽  
Vol 17 (5) ◽  
pp. 284-289 ◽  
Author(s):  
Karen Woo ◽  
Patrick Cook ◽  
Mohsin Saeed ◽  
Ralph Dilley
Keyword(s):  
Case Report ◽  
Natural History ◽  
Inferior Vena Cava ◽  
World Literature ◽  
Inferior Vena ◽  
Surgical Intervention ◽  
Vena Cava ◽  
The World ◽  
History Of ◽  
Embryologic Development

Aneurysms of the inferior vena cava (IVC) are exceedingly rare; less than 50 cases have been reported in the world literature. Owing to the paucity of data regarding the natural history of IVC aneurysms, there is no consensus on their treatment. This case report describes the evaluation of an IVC aneurysm in a 56-year-old male, briefly discusses the embryologic development of the IVC, and revisits the question of whether surgical intervention is indicated in these patients.

scholarly journals Complete Surgical Resection of a Leiomyosarcoma Arising from the Inferior Vena Cava

2015 ◽  
Vol 2015 ◽  
pp. 1-4 ◽  
Author(s):  
Hirofumi Sonoda ◽  
Keisuke Minamimura ◽  
Yuhei Endo ◽  
Shoichi Irie ◽  
Toru Hirata ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Surgical Resection ◽  
Inferior Vena ◽  
Vena Cava ◽  
Abdominal Ultrasound ◽  
Complete Surgical Resection ◽  
Old Japanese ◽  
Multinuclear Cells ◽  
The Right ◽  
Posterosuperior Segment

A 76-year-old Japanese man was referred to our hospital with chief complaint of right hypochondoralgia. Abdominal ultrasound showed a retroperitoneal tumor in the suprarenal region of the right kidney. Computed tomography revealed an enhanced lobular tumor with irregular, circumscribed, and indistinct border. Ultrasound-guided biopsy was performed. The tumor consisted of spindle-shaped cells with a giant nucleus and multinuclear cells. The diagnosis was leiomyosarcoma by immunohistochemical staining. The patient underwent surgery accessed by a right eighth intercostal thoracoabdominal incision. The tumor was completely resected, accompanied by removal of the posterosuperior segment of the right hepatic lobe, right adrenal gland, and a portion of the inferior vena cava (IVC). The histopathologic diagnosis was leiomyosarcoma arising from the IVC. We present a rare case of a successfully managed leiomyosarcoma of the IVC. This case suggests the importance of curative surgical resection of the tumor due to low efficacy of adjuvant chemotherapy for leiomyosarcoma.

scholarly journals Hepatocellular Carcinoma with Atrial Extension: A Case Report

2020 ◽  
pp. 1-4
Author(s):  
Eduardo Dantas ◽  
Daniel Matos ◽  
Mariana Coelho ◽  
Cristiana Sequeira ◽  
Cláudia Cardoso ◽  
...  
Keyword(s):  
Hepatocellular Carcinoma ◽  
Right Atrium ◽  
Inferior Vena ◽  
Vena Cava ◽  
Rare Condition ◽  
Right Heart Failure ◽  
Large Mass ◽  
Aggressive Tumor ◽  
The Right ◽  
Common Malignancy

Hepatocellular carcinoma is a common malignancy usually associated with cirrhosis. Despite being a highly aggressive tumor with several cases of vascular invasion, metastatic disease to the heart is a rare condition. A 65-year-old male cirrhotic patient was admitted with dyspnea, ascites, and lower extremity edema. A transthoracic echocardiogram showed a large mass in the right atrium. Further imaging studies revealed the presence of hepatocellular carcinoma extending from the liver to the right atrium through the inferior vena cava. The cardiac mass was surgically removed to treat the symptoms of right heart failure, but unfortunately the patient died on the 30th day after surgery due to septic shock.

scholarly journals Leiomyosarcoma of the Inferior Vena Cava: A Case Report of Complete and Sustained Response with Trabectedin

2016 ◽  
Vol 29 (4) ◽  
pp. 284 ◽  
Author(s):  
André Cruz ◽  
Luís Bretes ◽  
Carlos Reis ◽  
Irene Furtado
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Soft Tissue Sarcomas ◽  
Progression Free Survival ◽  
Radical Resection ◽  
Sustained Response ◽  
Free Survival ◽  
Vascular Origin ◽  
Third Line

<p>Inferior vena cava leiomyosarcoma is a very rare tumor, accounting for only 0.5% of all soft tissue sarcomas. As the other leyomiosarcomas of vascular origin, they have a poor prognosis, and radical resection with surgical margins free of tumor is the only potentially curative treatment. We present a case of a 46 year-old woman with metastatic inferior vena cava leiomyosarcoma who progressed after anthracyclines and ifosfamide and achieved a complete and sustained response with trabectedin. Beyond progression, the patient started third line treatment with pazopanib. A brief review of literature is also given. This case supports the efectiveness of a recent therapeutic agent, with an impressive progression-free survival in a recurrent metastatic inferior vena cava leiomyosarcoma.</p>

scholarly journals Primary leiomyosarcoma in the inferior vena cava- a case report

2017 ◽  
Vol 5 (4) ◽  
pp. 1702
Author(s):  
Ravindra Kumar ◽  
Suman Chaudhary ◽  
Hemant Kumar Mishra ◽  
Divesh Goyal
Keyword(s):  
Right Atrium ◽  
Inferior Vena ◽  
Vena Cava ◽  
Poor Response ◽  
Complete Resection ◽  
Middle Segment ◽  
History Of ◽  
Inferior Border ◽  
Vascular Leiomyosarcoma ◽  
Extensive Involvement

Vascular leiomyosarcoma of IVC is a rare tumor. Only about 200 cases have been reported worldwide. There is a strong predilection for females and middle segment of IVC is most commonly affected. The diagnosis is often challenging as patients present with non-specific complaints such as dyspnoea, abdominal discomfort, or back pain. A 43-year-old male presented with history of vague abdominal distention, discomfort, and dyspnoea in our hospital. Ultrasound of abdomen detected a mass in retro peritoneum with mixed echogenicity inseparable from IVC. CT Imaging examination of abdomen revealed a large elongated, heterogenous mass extending from right atrium to the confluence of common iliac veins. in IVC reaching up to inferior border of right atrium. Then USG guided biopsy done and Leiomyosarcoma of IVC was diagnosed by immunohistochemistry. Due to extensive involvement of intrahepatic segment and right atrium complete resection of mass was not possible, so radiotherapy followed by chemotherapy was started. Patient started deteriorating due to intolerability with poor response to radiotherapy and chemotherapy so he was put on supportive treatment.

scholarly journals Primary Leiomyosarcoma Of Inferior Vena Cava : An Uncommon Entity

2020 ◽  
Vol 2 (3) ◽  
Author(s):  
Kruti Dave ◽  
Shwetang Solanki ◽  
Ritesh Prajapati
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Growth Patterns ◽  
Rare Tumor ◽  
Vascular Leiomyosarcoma ◽  
Slow Growing ◽  
Primary Leiomyosarcoma

Primary vascular leiomyosarcoma is a rare tumor that arises mainly from the inferior vena cava (IVC). It is usually a slow-growing progressive tumor. It shows mainly three type of growth patterns; 62% of cases demonstrate extraluminal pattern, 5% cases show intraluminal pattern, and 33% extra- and intraluminal growth patterns.

Leiomyosarcoma of the inferior vena cava: Analysis and search of world literature on 141 patients and report of three new cases

1991 ◽  
Vol 14 (5) ◽  
pp. 688-699 ◽  
Author(s):  
Ashok V. Mehta ◽  
Andrea V. Mingoli ◽  
Richard J. Feldhaus ◽  
Antonio J. Cavallaro
Keyword(s):  
Inferior Vena Cava ◽  
World Literature ◽  
Inferior Vena ◽  
Vena Cava

Vascular leiomyosarcoma arising from the inferior vena cava diagnosed by intraluminal biopsy

1998 ◽  
Vol 433 (1) ◽  
pp. 97-100 ◽  
Author(s):  
Haruka Shimoda ◽  
K. Oka ◽  
Shinichi Otani ◽  
Hando Hakozaki ◽  
Takao Yoshimura ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Vascular Leiomyosarcoma
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