scholarly journals Aorto-pulmonary Window, a Rare Congenital Heart Disease: Case Report

2021 ◽  
pp. 17-21
Author(s):  
M. Lakhrissi ◽  
A. Ayad ◽  
M. Kmari ◽  
A. Ourrai ◽  
A. Hassani ◽  
...  
Keyword(s):  
Respiratory Symptoms ◽  
Congenital Heart ◽  
Ascending Aorta ◽  
Pulmonary Vascular Disease ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Heart Murmurs ◽  
Associated Lesions ◽  
Congenital Cardiac Malformation ◽  
Disease Case

Aortopulmonary window (APW) is an uncommon congenital cardiac malformation, accounting for 0.1% of all congenital cardiac diseases. It is a defect between the ascending aorta and the trunk of the pulmonary artery. Such abnormality may occur as an isolated lesion or it can be associated with other cardiac abnormalities in one third to one half of cases. Clinical and hemodynamic presentation of this condition depends on the size of the defect and on the associated lesions. It is usually fatal in infancy or childhood if untreated with the development of irreversible pulmonary hypertension. Once the diagnosis is made, surgery must be performed quickly to avoid irreversible pulmonary vascular disease. We report the case of a 5-month-old infant with APW who was referred to our center by respiratory symptoms and heart murmurs.

Brain Abscess in an Infant With Cyanotic Congenital Heart Disease

PEDIATRICS ◽  
1974 ◽  
Vol 54 (1) ◽  
pp. 113-115
Author(s):  
J. B. Tingelstad ◽  
H. F. Young ◽  
R. B. David
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Brain Abscess ◽  
Congenital Heart ◽  
Cyanotic Congenital Heart Disease ◽  
Intensive Treatment ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

An infant with a cyanotic congenital cardiac malformation and brain abscess is described. The rarity of this combination before age 2 years and the need for intensive treatment once it is recognized are stressed.

Introduction

ESC CardioMed ◽  
2018 ◽  
pp. 737-739
Author(s):  
John Deanfield
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Surgical Care ◽  
Cardiac Malformation ◽  
Surgical Experience ◽  
Live Births ◽  
Cardiac Malformations ◽  
Congenital Cardiac Malformation

A congenital cardiac malformation complicates approximately 8 per 1000 live births. The treatment of such patients in childhood is now a mature speciality, with over 70 years of surgical experience. This has transformed the outlook for even the most complex of congenital cardiac malformations and more than 90% of all children born with congenital heart disease will reach adulthood. As a result, there are now more adults than children with congenital heart disease and their number will increase greatly over the coming years, with further improvements in medical and surgical care.

scholarly journals Employment and advice regarding careers for adults with congenital heart disease

2005 ◽  
Vol 15 (4) ◽  
pp. 391-395 ◽  
Author(s):  
David S. Crossland ◽  
Susan P. Jackson ◽  
Rosalind Lyall ◽  
John Burn ◽  
John J. O'Sullivan
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation ◽  
Congenital Cardiac Disease ◽  
Career Advice ◽  
The Impact ◽  
To Receive ◽  
Trained Nurse

Aims: To compare the rates of employment, and advice offered concerning careers, in adults with congenital heart disease and controls. To assess the impact of the severity of the congenital cardiac malformation on the chances for employment. Methods: We solicited responses from 299 adults with congenitally malformed hearts, asking them to answer questions from a questionnaire posed at interview by a trained nurse. The adults were asked to give an identical questionnaire to a friend to act as a control. We received responses from 177 of the controls. Results: The responses showed that 51 of 156 (33 per cent) adults with congenital heart disease were unemployed, and 37 of 151 (25 per cent) had been unemployed for more than a year. This is significantly more than 25 of 156 (16 per cent) matched controls unemployed, and 5 of 151 (3 per cent) controls unemployed for more than a year. Almost one-fifth of the adults with congenital heart disease (19 per cent) had received advice regarding their career which they found helpful, which is significantly fewer than the 31 per cent of controls. More (42 per cent) had been given advice against certain occupations than controls (11 per cent). Receiving career advice was significantly associated with employment in the population with congenitally malformed hearts, with almost three-quarters (73 per cent) of those given advice being employed compared to 46 per cent of those not given advice. This pattern was not seen in controls. The severity of the congenital cardiac malformation did not significantly affect the rates of unemployment. Conclusions: Whatever the severity of their disease, adults with congenitally malformed hearts are more likely to be unemployed than matched controls. They are less likely to receive useful advice regarding potential careers, and find the advice given less helpful, than controls, although receiving suitable advice is associated with being employed in the population with congenital cardiac disease.

scholarly journals Late Presentation of Aortopulmonary Window with Tetralogy of Fallot: Report of a Very Rare Case

2021 ◽  
pp. 1-3
Author(s):  
Muhammad Ishtiaque Sayeed Al-Manzo ◽  
Prodip Kumar Biswas ◽  
M.A.K. Azad ◽  
Eliyas Patwary ◽  
Jesmin Hossain ◽  
...  
Keyword(s):  
Tetralogy Of Fallot ◽  
Rare Case ◽  
Surgical Repair ◽  
Preoperative Evaluation ◽  
Late Presentation ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window (APW) itself is a rare congenital cardiac malformation and its association with Tetralogy of Fallot (TOF) makes it more uncommon. We report a case of APW with TOF who presented at 4-year 10 months of age. As the boy was still in operable state, after thorough preoperative evaluation successful surgical repair was done.

scholarly journals It Is Not Always Sepsis: Fatal Tachypnea in a Newborn

2018 ◽  
Vol 2018 ◽  
pp. 1-3 ◽  
Author(s):  
Rachel Levene ◽  
Elza Pollak-Christian ◽  
Ashish Garg ◽  
Michael Keenaghan
Keyword(s):  
Congenital Heart ◽  
Coarctation Of The Aorta ◽  
Pediatric Emergency ◽  
Pediatric Emergency Department ◽  
Cardiac Malformation ◽  
Significant Delay ◽  
Newborn Period ◽  
Suspected Sepsis ◽  
Timely Initiation ◽  
Congenital Cardiac Malformation

Coarctation of the aorta (CoA) is a congenital cardiac malformation that is well understood. Despite being well characterized, CoA is a commonly missed congenital heart disease (CHD) during the newborn period. We report a full-term nine-day-old male who presented to the pediatric emergency department (ED) with isolated tachypnea. After an initial sepsis workup, subsequent investigations revealed critical CoA. Because the primary workup focused on sepsis, there was a significant delay in prostaglandin E1 (PGE1) initiation. This case illustrates the importance of early CoA recognition and timely initiation of PGE1 in newborns who present with suspected sepsis along with tachypnea.

Aortopulmonary Window with Subaortic Fibrous Stenosis and Septal Defect: Surgery through a Minimal Right Vertical Infra-Axillary Thoracotomy

2011 ◽  
Vol 14 (4) ◽  
pp. 264 ◽  
Author(s):  
Jun Pan ◽  
Qing-Guo Li ◽  
Qing Zhou ◽  
Jie Zhang ◽  
Qiang Wang ◽  
...  
Keyword(s):  
Minimally Invasive Surgery ◽  
Cardiopulmonary Bypass ◽  
Ventricular Septal Defect ◽  
Minimally Invasive ◽  
Invasive Surgery ◽  
Septal Defect ◽  
Subaortic Stenosis ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window with subaortic stenosis and ventricular septal defect is an uncommon congenital cardiac malformation that is repaired using cardiopulmonary bypass. The authors describe a 3-year-old patient on whom we performed surgery through a minimal right vertical infra-axillary thoracotomy. This minimally invasive surgery is likely to be applicable in a few cases.

Triple Outlet Right Ventricle, With Duplication of the Aortic Root and Intrapericardial Ascending Aorta

2017 ◽  
Vol 11 (4) ◽  
pp. NP94-NP98 ◽  
Author(s):  
Ashish Katewa ◽  
Balswaroop Sahu ◽  
Vishal Jain ◽  
Robert H. Anderson
Keyword(s):  
Computed Tomography ◽  
Right Ventricle ◽  
Aortic Root ◽  
Double Outlet Right Ventricle ◽  
Ascending Aorta ◽  
Cardiac Malformation ◽  
Aortic Valves ◽  
Congenital Cardiac Malformation ◽  
Infundibular Stenosis ◽  
The Right

We present a case of a highly unusual congenital cardiac malformation, namely, triple outlet right ventricle with duplication of the aortic root and the intrapericardial component of the ascending aorta. A girl, aged five, presented with complaints of cyanosis and effort intolerance and was diagnosed with double-outlet right ventricle and subpulmonary infundibular stenosis. Intraoperatively, we noted that the aortic root was guarded by two separate aortic valves, oriented anteroposteriorly relative to each other, and separated within the right ventricle by a muscle bar. Postoperative interrogation by both echocardiography and computed tomography confirmed the surgical findings. To the best of our knowledge, our case is the first example of duplication of the aortic root to produce triple outlet right ventricle.

scholarly journals Cardiac disease and pregnancy: hyper vigilance and extreme caution for optimal outcome

2020 ◽  
Vol 9 (2) ◽  
pp. 825
Author(s):  
Naresh Dhawan ◽  
Rohin Kumar ◽  
Reema Kumar Bhatt
Keyword(s):  
Aortic Valve ◽  
Bicuspid Aortic Valve ◽  
Cardiac Disease ◽  
Congenital Heart ◽  
Single Ventricle ◽  
Heart Diseases ◽  
Fetal Outcome ◽  
Coordinated Care ◽  
Extreme Caution ◽  
Congenital Cardiac Malformation

Cardiac disease in pregnancy is a leading cause of maternal death in more so high-income countries. The armamentarium for winning this difficult battle involves shared decision-making with communication across the clinical team and the patient. There is limited clinical evidence concerning effective approaches to managing such complex care and moreover involvement of different specialists makes coordinated care challenging. Bicuspid aortic valve (BAV) is the most common congenital cardiac malformation, occurring in 1-2% of the population whereas a single ventricle is a rare congenital heart disease that accounts for less than 1% of all congenital heart diseases. We had two cases of pregnancy with bicuspid aortic valve in one case and the other with single ventricle. The involvement of multidisciplinary team involving cardiologist, cardiothoracic anaesthetist and fetal maternal medicine specialist resulted in good maternal and fetal outcome in both the cases.

scholarly journals A Rare Case of Adult Aortopulmonary Window Combined with Anomalous Origin of the Right Pulmonary Artery from the Aorta Leading to Eisenmenger Syndrome

2021 ◽  
Vol 49 (1) ◽  
pp. 030006052098465
Author(s):  
Mingyue Cui ◽  
Binfeng Xia ◽  
Heru Wang ◽  
Haihui Liu ◽  
Xia Yin
Keyword(s):  
Pulmonary Artery ◽  
Rare Case ◽  
Congenital Heart ◽  
Respiratory Tract Infections ◽  
Anomalous Origin ◽  
Aortopulmonary Window ◽  
Eisenmenger Syndrome ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Tract Infections

Aortopulmonary window is a rare congenital heart disease that can increase pulmonary vascular resistance, exacerbate left-to-right shunt and lead to heart failure and respiratory tract infections. Most patients die during childhood. We report a 53-year-old male patient with a large aortopulmonary window combined with anomalous origin of the right pulmonary artery from the aorta, with Eisenmenger syndrome and without surgery.

scholarly journals Double-Outlet Right Ventricle in a Chianina Calf

Animals ◽  
2021 ◽  
Vol 11 (2) ◽  
pp. 318
Author(s):  
Domenico Caivano ◽  
Maria Chiara Marchesi ◽  
Piero Boni ◽  
Noemi Venanzi ◽  
Giovanni Angeli ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Septal Defect ◽  
Heart Defects ◽  
Double Outlet Right Ventricle ◽  
Cardiac Malformation ◽  
Septal Defects ◽  
Congenital Cardiac Malformation ◽  
The Right ◽  
Similar Complex ◽  
Echocardiographic Findings

Congenital heart defects have been occasionally reported in cattle and ventricular septal defect represents the most frequently encountered anomaly. The double-outlet right ventricle is a rare congenital ventriculoarterial malformation reported only in certain cattle breeds. We describe this rare and complex congenital cardiac malformation observed in a 10-day-old male Chianina calf. Clinical examination showed tachycardia, tachypnea, jugular pulses, cyanotic mucous membranes and a right apical systolic murmur. Transthoracic echocardiography revealed severe dilation of the right-sided cardiac chambers with a markedly hypoplastic left ventricle. Both aorta and pulmonary artery leaving the right ventricle in parallel alignment with the tricuspid valve were suggestive of a dual-outlet right ventricle. Interventricular and interatrial septal defects were also visualized. Post-mortem examination confirmed the echocardiographic findings. To the authors’ knowledge, a similar complex congenital cardiac malformation has not been reported in calves of the Chianina breed to date.

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