Congenital primary primitive neuroectodermal tumor of the orbit in a newborn

2021 ◽  
pp. 112067212199104
Author(s):  
Nirupama Kasturi ◽  
Sandip Sarkar ◽  
Tanmay Gokhale ◽  
Subashini Kaliaperumal ◽  
Pampa Ch Toi ◽  
...  

Introduction: Primitive neuroectodermal tumors arise from the progenitor cells of the neural crest, in the central nervous system or other peripheral locations. Case presentation: We report a rare case of a congenital malignant tumor, diagnosed as a primary orbital primitive neuroectodermal tumor on histopathological examination. Conclusion: Multidisciplinary management with adjuvant chemotherapy needed for the management of these cases.

2020 ◽  
Vol 1 (1) ◽  
pp. 01-03
Author(s):  
Yahyaoui Yosra

Primitive neuroectodermal tumors (PNETs) are extremely rare tumors. These neoplasms can occur at sites outside of the central nervous system. The head and neck location is unsual. We report a case with primitive neuroectodermal tumor (PNET) of the parotid. We analyze through this observation the clinical, histological and therapeutic characteristics of this entity.


2001 ◽  
Vol 125 (2) ◽  
pp. 264-266
Author(s):  
Satish Krishnamurthy ◽  
Stephen Kent Powers ◽  
Javad Towfighi

Abstract Primitive neuroectodermal tumors (PNETs) of the central nervous system are uncommon embryonal neoplasms, rarely occurring in adults. Differentiation into specific mesenchymal tissues, such as cartilage, bone, skeletal muscle, smooth muscle, or adipose tissue, is rare. We report a case of a 51-year-old woman with a PNET of cerebrum that showed extensive mature adipose tissue differentiation. This is the second case, to our knowledge, of PNET of cerebrum with adipose tissue elements that has been described.


Medicina ◽  
2011 ◽  
Vol 47 (8) ◽  
pp. 440 ◽  
Author(s):  
Virginija Ašmonienė ◽  
Daina Skiriutė ◽  
Inga Gudinavičienė ◽  
Šarūnas Tamašauskas ◽  
Kęstutis Skauminas ◽  
...  

Primitive neuroectodermal tumors are a group of rare, aggressive, and highly malignant embryonal tumors of unknown etiology of the central and peripheral nervous systems. It is a term for a group of small round cell tumors thought to be derived from fetal neuroectodermal precursor cells. Primitive neuroectodermal tumor is usually described as a tumor of children younger than 15 years and is very rare in adults. The article presents a short literature review and a rare case of a primary primitive neuroectodermal tumor of the central nervous system diagnosed in a 51-year-old woman.


2019 ◽  
Vol 07 (09) ◽  
pp. E1163-E1165
Author(s):  
Leonardo Blas Jhon ◽  
Paloma Sánchez-Fayos ◽  
Maria Jesus Martín Relloso ◽  
Daniel Calero Barón ◽  
Juan Carlos Porres Cubero

AbstractPrimitive neuroectodermal tumors (PNET) are very rare tumors that belong to a family of malignant neoplasms of tiny round cells which are derived from the neural crest. This report discusses a rare case of an adult woman with esophageal PNET, confirmed by immunohistochemistry, that presented with metastasis to the pineal gland. To our knowledge, this is the first case report of a PNET with these features. Despite surgery and chemotherapeutic treatment, our case has shown disease progression.


1997 ◽  
Vol 7 (2) ◽  
pp. 765-784 ◽  
Author(s):  
Lucy Balian Rorke ◽  
John Q. Trojanowski ◽  
Virginia MY Lee ◽  
Robert A. Zimmerman ◽  
Leslie N. Sutton ◽  
...  

2011 ◽  
Vol 35 (4) ◽  
pp. 573-582 ◽  
Author(s):  
Marco Gessi ◽  
Prashanth Setty ◽  
Michele Bisceglia ◽  
Anja zur Muehlen ◽  
Libero Lauriola ◽  
...  

Author(s):  
Xiaoyan Zheng ◽  
Fei Wang ◽  
Lei Wang ◽  
Xiaoli Li ◽  
Jingjing Li ◽  
...  

Abstract Background Cysticercosis is the commonest parasitic disease to affect the central nervous system (CNS). However, cysticercosis affecting the spine is extremely rare. We reported a rare case of cysticercosis involving the whole spinal canal in China. Case Presentation A rare case of cysticercosis involving the entire spinal cord, in a 52-year-old Chinese man, was detected in 2021. Epidemiological investigation, clinical and etiological examination was performed. Conclusion Since spinal cysticercosis is a rare but potentially life-threatening disease, clinicians should always consider the differential diagnosis of space-occupying lesions.


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