scholarly journals Primitive neuroectodermal tumor of the esophagus with metastasis in the pineal gland

2019 ◽  
Vol 07 (09) ◽  
pp. E1163-E1165
Author(s):  
Leonardo Blas Jhon ◽  
Paloma Sánchez-Fayos ◽  
Maria Jesus Martín Relloso ◽  
Daniel Calero Barón ◽  
Juan Carlos Porres Cubero
Keyword(s):  
Case Report ◽  
Pineal Gland ◽  
Disease Progression ◽  
Rare Case ◽  
Primitive Neuroectodermal Tumor ◽  
Malignant Neoplasms ◽  
Primitive Neuroectodermal Tumors ◽  
First Case ◽  
Neuroectodermal Tumors ◽  
Chemotherapeutic Treatment

AbstractPrimitive neuroectodermal tumors (PNET) are very rare tumors that belong to a family of malignant neoplasms of tiny round cells which are derived from the neural crest. This report discusses a rare case of an adult woman with esophageal PNET, confirmed by immunohistochemistry, that presented with metastasis to the pineal gland. To our knowledge, this is the first case report of a PNET with these features. Despite surgery and chemotherapeutic treatment, our case has shown disease progression.

scholarly journals Primary intracranial peripheral primitive neuroectodermal tumor in an adult patient with aphasia: a rare case report

2021 ◽  
Author(s):  
kazem ghaemi ◽  
mahdieh rajabi-moghaddam ◽  
Hamid Abbaszadeh
Keyword(s):  
Case Report ◽  
Adult Patient ◽  
Rare Case ◽  
Primitive Neuroectodermal Tumor ◽  
Chief Complaint ◽  
Peripheral Primitive Neuroectodermal Tumor ◽  
Primitive Neuroectodermal Tumors ◽  
Neuroectodermal Tumors ◽  
Rare Case Report ◽  
First Time

Primary intracranial primitive neuroectodermal tumors (PNETs) are extremely rare malignancies, affects children and adolescents with only 10 cases has been reported over 33 years old. we present a case of PNET in a 36 years old female patient with the chief complaint of aphasia for the first time

scholarly journals Primitive Neuroectodermal Tumor of the Pancreas: A Case Report and Review of the Literature

2015 ◽  
Vol 2015 ◽  
pp. 1-4 ◽  
Author(s):  
Uirá Teixeira ◽  
Marcos Goldoni ◽  
Michelle Unterleider ◽  
João Diedrich ◽  
Diogo Balbinot ◽  
...  
Keyword(s):  
Case Report ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Neuroendocrine Cells ◽  
Malignant Neoplasms ◽  
Review Of The Literature ◽  
Primitive Neuroectodermal Tumors ◽  
Neuroectodermal Tumors

Primitive neuroectodermal tumors (PNETs) are presented as rare malignant neoplasms. In unusual cases, those neoplasms may arise in solid organs containing neuroendocrine cells, such as the pancreas. Herein the case of a 28-year-old patient that underwent gastroduodenopancreatectomy after the diagnosis of a huge mass (PNET) located in both head and body of the pancreas is reported. This is the 19th case of pancreatic PNET reported in literature.

scholarly journals Primary Pulmonary Primitive Neuroectodermal Tumor: A Case Report and Literature Review

2020 ◽  
pp. 1-3
Author(s):  
Guzmán-Casta Jordi
Keyword(s):  
Case Report ◽  
Soft Tissue ◽  
Chest Wall ◽  
Primitive Neuroectodermal Tumor ◽  
Lung Parenchyma ◽  
Round Cell ◽  
Primitive Neuroectodermal Tumors ◽  
Small Round Cell ◽  
Molecular Features ◽  
Neuroectodermal Tumors

Primitive Neuroectodermal Tumors (PNET) and Ewing Sarcoma (EWS) belong to the same family of malignant, small, round cell neoplasms of soft tissue or bone origin. Common locations for EWS-PNET include chest wall, pelvis, and extremities. EWSPNETs that arise in the lung parenchyma without chest wall involvement are extremely rare in adults. We report a case of EWS-PNET of the lung in an adult and review the distinct clinical, pathological, and molecular features of these tumors.

Congenital primary primitive neuroectodermal tumor of the orbit in a newborn

2021 ◽  
pp. 112067212199104
Author(s):  
Nirupama Kasturi ◽  
Sandip Sarkar ◽  
Tanmay Gokhale ◽  
Subashini Kaliaperumal ◽  
Pampa Ch Toi ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Rare Case ◽  
Primitive Neuroectodermal Tumor ◽  
Histopathological Examination ◽  
Neuroectodermal Tumor ◽  
Multidisciplinary Management ◽  
Case Presentation ◽  
Primitive Neuroectodermal Tumors ◽  
Neuroectodermal Tumors ◽  
The Central Nervous System

Introduction: Primitive neuroectodermal tumors arise from the progenitor cells of the neural crest, in the central nervous system or other peripheral locations. Case presentation: We report a rare case of a congenital malignant tumor, diagnosed as a primary orbital primitive neuroectodermal tumor on histopathological examination. Conclusion: Multidisciplinary management with adjuvant chemotherapy needed for the management of these cases.

scholarly journals Extraneural Supratentorial Primitive Neuroectodermal Tumor Metastasis: An Adult Case Report

2017 ◽  
Vol 06 (03) ◽  
pp. 210-212 ◽  
Author(s):  
Nidhal Matar ◽  
Kamel Bahri ◽  
Jallel Kallel ◽  
Adnene Boubaker ◽  
Hafedh Jemel
Keyword(s):  
Case Report ◽  
Tumor Metastasis ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Adult Case ◽  
Primitive Neuroectodermal Tumors ◽  
Extraneural Metastases ◽  
Supratentorial Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumors ◽  
Sporadic Cases

AbstractExtraneural metastases of supratentorial primitive neuroectodermal tumors (PNET) are very rare and have been reported in only sporadic cases. We present a patient with supratentorial PNET metastasizing to the lung, diagnosed 4 months after cerebral surgery.

A case report of neonatal orbital peripheral primitive neuroectodermal tumor and literature review

2020 ◽  
pp. 112067212092693
Author(s):  
Yian Li ◽  
Lian Chen ◽  
Xiaohong Zhou ◽  
Lu Gao ◽  
Xiaojing Cai ◽  
...  
Keyword(s):  
Primitive Neuroectodermal Tumor ◽  
Clinical Manifestations ◽  
Neuroectodermal Tumor ◽  
Malignant Neoplasms ◽  
Peripheral Primitive Neuroectodermal Tumor ◽  
Radiological Findings ◽  
Primitive Neuroectodermal Tumors ◽  
Sympathetic Nervous Systems ◽  
Neuroectodermal Tumors ◽  
Unilateral Proptosis

Primitive neuroectodermal tumors are rare malignant neoplasms from primitive neural crest cells. Most primitive neuroectodermal tumors occur in the central and sympathetic nervous systems. We report a Chinese newborn patient presenting a huge unilateral proptosis after birth, diagnosed as orbital peripheral primitive neuroectodermal tumor by histopathology and immunohistochemistry. Our case is the first reported case of orbital peripheral primitive neuroectodermal tumor diagnosed in the newborn period. The clinical manifestations, radiological findings, histopathologic, and immunohistochemistry results are described in detail. We also conducted a literature search focusing on primitive neuroectodermal tumor of the orbit. To the best of our knowledge, all articles with English abstracts were reviewed here.

scholarly journals A rare case of eight multiple primary malignant neoplasms in a female patient: A case report and review of the literature

2014 ◽  
Vol 9 (2) ◽  
pp. 587-590 ◽  
Author(s):  
JIEMIN ZHAO ◽  
YAN TAN ◽  
YUGANG WU ◽  
WEI ZHAO ◽  
JUN WU ◽  
...  
Keyword(s):  
Case Report ◽  
Female Patient ◽  
Rare Case ◽  
Malignant Neoplasms ◽  
Review Of The Literature ◽  
Multiple Primary

Primitive Neuroectodermal Tumor of the Lung

2001 ◽  
Vol 125 (3) ◽  
pp. 397-399
Author(s):  
Andrea G. Kahn ◽  
Alejandra Avagnina ◽  
Jorge Nazar ◽  
Boris Elsner
Keyword(s):  
Primitive Neuroectodermal Tumor ◽  
Neuron Specific Enolase ◽  
Middle Lobe ◽  
Neurosecretory Granules ◽  
Primitive Neuroectodermal Tumors ◽  
Ultrastructural Studies ◽  
Neuroectodermal Tumors ◽  
Right Middle Lobe ◽  
Cytoplasmic Processes

Abstract Primitive neuroectodermal tumors occur most frequently in bone and soft tissue but have been reported in other locations. Primary lung primitive neuroectodermal tumors without pleural or chest wall involvement are extremely rare. We present a case with immunohistochemical and ultrastructural studies and follow-up of the patient. An 18-year-old man presented with hemoptysis. Chest radiographs revealed a right middle lobe mass, and bronchoscopy showed an endobronchial tumor. The lesion was resected by middle lobectomy. After 2 years, a local recurrence was treated by pneumonectomy. The patient died after surgery. Histologically, the tumor was composed of uniform cells with round nuclei and scanty cytoplasm arranged in cohesive lobules with occasional rosette formation. Immunohistochemically, the tumor was positive for vimentin, CD99, neuron-specific enolase, and neurofilaments. Ultrastructural study revealed neurosecretory granules and cytoplasmic processes. Our case shows the value of immunohistochemistry and electron microscopy in the diagnosis of primitive neuroectodermal tumors in unusual locations.

scholarly journals Teratoma of larynx: case report

2021 ◽  
Vol 7 (10) ◽  
pp. 1700
Author(s):  
Rakesh Srivastava ◽  
Vini Tandon
Keyword(s):  
Carbon Dioxide ◽  
Case Report ◽  
Germ Cells ◽  
Carbon Dioxide Laser ◽  
Rare Case ◽  
Histopathological Examination ◽  
Flexible Laryngoscopy ◽  
First Case ◽  
Congenital Teratoma

<p class="abstract">Teratomas are embryonal neoplasm arises from totipotent germ cells. They are having tissues from all the three blastodermic layers. There are various locations of congenital teratoma. Naso-oropharyngeal site teratoma are either sessile or pedunculated. We describe a rare case of laryngeal teratoma in a five years old patient presented with change in voice and breathing difficulty. On flexible laryngoscopy, it appeared like supraglottic cyst but on CT scan it was confirmed as teratoma. Pre-operative tracheostomy and transoral carbon dioxide laser assisted excision done. Histopathological examination showed osteoid trabeculae, chondroid tissue with loose myxoid islands and adipose tissue. No recurrence of tumor on 18 months follow-up. This is the first case report of pediatric larynx teratoma reported in present century.</p>

Primitive Neuroectodermal Tumor of Cerebrum With Adipose Tissue

2001 ◽  
Vol 125 (2) ◽  
pp. 264-266
Author(s):  
Satish Krishnamurthy ◽  
Stephen Kent Powers ◽  
Javad Towfighi
Keyword(s):  
Skeletal Muscle ◽  
Central Nervous System ◽  
Nervous System ◽  
Adipose Tissue ◽  
Smooth Muscle ◽  
Primitive Neuroectodermal Tumor ◽  
Primitive Neuroectodermal Tumors ◽  
Mature Adipose Tissue ◽  
Neuroectodermal Tumors ◽  
The Central Nervous System

Abstract Primitive neuroectodermal tumors (PNETs) of the central nervous system are uncommon embryonal neoplasms, rarely occurring in adults. Differentiation into specific mesenchymal tissues, such as cartilage, bone, skeletal muscle, smooth muscle, or adipose tissue, is rare. We report a case of a 51-year-old woman with a PNET of cerebrum that showed extensive mature adipose tissue differentiation. This is the second case, to our knowledge, of PNET of cerebrum with adipose tissue elements that has been described.

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