Proteomic assessment of a cell model of spinal muscular atrophy

BMC Neuroscience ◽

10.1186/1471-2202-12-25 ◽

2011 ◽

Vol 12 (1) ◽

pp. 25 ◽

Author(s):

Chia-Yen Wu ◽

Dosh Whye ◽

Lisa Glazewski ◽

Leila Choe ◽

Douglas Kerr ◽

...

Keyword(s):

Spinal Muscular Atrophy ◽

Muscular Atrophy ◽

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Established Stem Cell Model of Spinal Muscular Atrophy Is Applicable in the Evaluation of the Efficacy of Thyrotropin-Releasing Hormone Analog

Stem Cells Translational Medicine ◽

10.5966/sctm.2015-0059 ◽

2015 ◽

Vol 5 (2) ◽

pp. 152-163 ◽

Author(s):

Kazuki Ohuchi ◽

Michinori Funato ◽

Zenichiro Kato ◽

Junko Seki ◽

Chizuru Kawase ◽

...

Keyword(s):

Stem Cell ◽

Spinal Muscular Atrophy ◽

Muscular Atrophy ◽

Thyrotropin Releasing Hormone ◽

Releasing Hormone ◽

Hormone Analog ◽

Stem Cell Model

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Stem Cell Model of Spinal Muscular Atrophy

Archives of Neurology ◽

10.1001/archneurol.2010.89 ◽

2010 ◽

Vol 67 (6) ◽

Author(s):

Allison D. Ebert ◽

Clive N. Svendsen

Keyword(s):

Stem Cell ◽

Spinal Muscular Atrophy ◽

Muscular Atrophy ◽

Stem Cell Model

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Sensory Neurons Do Not Induce Motor Neuron Loss in a Human Stem Cell Model of Spinal Muscular Atrophy

PLoS ONE ◽

10.1371/journal.pone.0103112 ◽

2014 ◽

Vol 9 (7) ◽

pp. e103112 ◽

Author(s):

Andrew J. Schwab ◽

Allison D. Ebert

Keyword(s):

Stem Cell ◽

Spinal Muscular Atrophy ◽

Motor Neuron ◽

Sensory Neurons ◽

Muscular Atrophy ◽

Human Stem Cell ◽

Neuron Loss ◽

Stem Cell Model ◽

Motor Neuron Loss

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Recapitulation of spinal motor neuron-specific disease phenotypes in a human cell model of spinal muscular atrophy

Cell Research ◽

10.1038/cr.2012.166 ◽

2012 ◽

Vol 23 (3) ◽

pp. 378-393 ◽

Author(s):

Zhi-Bo Wang ◽

Xiaoqing Zhang ◽

Xue-Jun Li

Keyword(s):

Spinal Muscular Atrophy ◽

Motor Neuron ◽

Muscular Atrophy ◽

Spinal Motor Neuron ◽

Disease Phenotypes ◽

Specific Disease ◽

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Characteristic of the spinal muscular atrophy cell model

THE ELEVENTH INTERNATIONAL YOUNG SCIENTISTS SCHOOL ◽

10.18699/sbb-2019-32 ◽

2019 ◽

Keyword(s):

Spinal Muscular Atrophy ◽

Muscular Atrophy ◽

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Survival of motor neuron gene downregulation by RNAi: towards a cell culture model of spinal muscular atrophy

Molecular Brain Research ◽

10.1016/j.molbrainres.2003.10.015 ◽

2004 ◽

Vol 120 (2) ◽

pp. 145-150 ◽

Author(s):

Barbara Trülzsch ◽

Kay Davies ◽

Matthew Wood

Keyword(s):

Cell Culture ◽

Spinal Muscular Atrophy ◽

Motor Neuron ◽

Muscular Atrophy ◽

Cell Culture Model ◽

Culture Model ◽

A Cell ◽

Survival Of Motor Neuron

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Clenbuterol-sensitive delayed outward potassium currents in a cell model of spinal and bulbar muscular atrophy

Pflügers Archiv - European Journal of Physiology ◽

10.1007/s00424-021-02559-6 ◽

2021 ◽

Author(s):

Vladimir A. Martínez-Rojas ◽

Daniele Arosio ◽

Maria Pennuto ◽

Carlo Musio

Keyword(s):

Muscular Atrophy ◽

Potassium Currents ◽

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ClC-2-like Chloride Current Alterations in a Cell Model of Spinal and Bulbar Muscular Atrophy, a Polyglutamine Disease

Journal of Molecular Neuroscience ◽

10.1007/s12031-020-01687-5 ◽

2020 ◽

Author(s):

Vladimir A. Martínez-Rojas ◽

Aura M. Jiménez-Garduño ◽

Daniela Michelatti ◽

Laura Tosatto ◽

Marta Marchioretto ◽

...

Keyword(s):

Muscular Atrophy ◽

Chloride Current ◽

Polyglutamine Disease ◽

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Mitochondrial dysfunction in a neural cell model of spinal muscular atrophy

Journal of Neuroscience Research ◽

10.1002/jnr.22106 ◽

2009 ◽

Vol 87 (12) ◽

pp. 2748-2756 ◽

Author(s):

Gyula Acsadi ◽

Icksoo Lee ◽

Xingli Li ◽

Magomed Khaidakov ◽

Alena Pecinova ◽

...

Keyword(s):

Spinal Muscular Atrophy ◽

Mitochondrial Dysfunction ◽

Muscular Atrophy ◽

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Dilysine motifs in exon 2b of SMN protein mediate binding to the COPI vesicle protein α-COP and neurite outgrowth in a cell culture model of spinal muscular atrophy

Human Molecular Genetics ◽

10.1093/hmg/ddt254 ◽

2013 ◽

Vol 22 (20) ◽

pp. 4043-4052 ◽

Author(s):

Sara K. Custer ◽

Adrian G. Todd ◽

Natalia N. Singh ◽

Elliot J. Androphy

Keyword(s):

Cell Culture ◽

Spinal Muscular Atrophy ◽

Neurite Outgrowth ◽

Muscular Atrophy ◽

Cell Culture Model ◽

Culture Model ◽

A Cell ◽

Copi Vesicle ◽

Vesicle Protein ◽

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