scholarly journals A Rare Presentation of Cecal Diverticulitis in a Patient With Cystic Fibrosis

2019 ◽  
Vol 9 (1) ◽  
pp. 13-16
Author(s):  
Manrique Guerrero ◽  
Mariam Selevany ◽  
Monica Sridhar ◽  
Paul Hanna ◽  
Jamshed Zuberi
Keyword(s):  
Cystic Fibrosis ◽  
Rare Presentation ◽  
Cecal Diverticulitis

scholarly journals HAIR DEPIGMENTATION AND DERMATITIS – AN UNEXPECTED PRESENTATION OF CYSTIC FIBROSIS

2013 ◽  
Vol 16 (2) ◽  
pp. 81-83
Author(s):  
O. Milankov ◽  
R. Savic ◽  
J. Tosic
Keyword(s):  
Cystic Fibrosis ◽  
Female Patient ◽  
Pancreatic Enzyme ◽  
Vitamin Supplementation ◽  
Rare Presentation ◽  
Skin Changes ◽  
Presenting Symptoms ◽  
Brown Colour ◽  
Hair Depigmentation

ABSTRACT Hair depigmentation is very rare presentation of cystic fibrosis (CF). We present 3.5-month-old female patient who had dermatitis and depigmentation of hair and eye lashes, malnutrition, edema and anemia as presenting symptoms of CF. After pancreatic enzyme and vitamin supplementation therapy, skin changes gradually disappeared, and her hair regained its normal brown colour

Bilateral Antrochoanal Polyp with Diabetes: A Rare Presentation of Cystic Fibrosis

2010 ◽  
Vol 3 (3) ◽  
pp. 173-176
Author(s):  
Monica Gupta ◽  
Manish Gupta
Keyword(s):  
Cystic Fibrosis ◽  
Endoscopic Sinus Surgery ◽  
English Literature ◽  
Functional Endoscopic Sinus Surgery ◽  
Sinus Surgery ◽  
Adolescent Male ◽  
Antrochoanal Polyp ◽  
Rare Presentation ◽  
First Case

Abstract Bilateral antrochoanal (AC) polyps have been rarely reported in english literature. Here we report the first case of an adolescent male with bilateral AC polyps, cystic fibrosis and diabetes. The case was managed successfully by functional endoscopic sinus surgery (FESS). The patient has been under follow-up for the last six months with no signs of recurrence.

Kwashiorkor‐like dermatosis: a rare presentation of cystic fibrosis

2020 ◽  
Vol 46 (1) ◽  
pp. 213-215
Author(s):  
C. Shajil ◽  
D. Sathishkumar ◽  
M. J. Chiramel ◽  
M. Kumar ◽  
S. Varkki ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Rare Presentation

scholarly journals Acute Pancreatitis with Normal Amylase/Lipase Levels? A Rare Case Study in Pakistan, an unusual manifestation of cystic fibrosis

2021 ◽  
Vol 5 (2) ◽  
pp. 47-51
Author(s):  
Huzaifa Azam ◽  
Muhammad Haziq Khan ◽  
Asjad Salman Zahid ◽  
Hassan Waqar ◽  
Ameen Mehmood Abdo Rageh ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Acute Pancreatitis ◽  
Serum Amylase ◽  
Critical Role ◽  
Pancreatic Enzyme ◽  
Uneventful Recovery ◽  
Rare Presentation ◽  
Diagnostic Dilemma ◽  
Chief Complaints ◽  
Enzyme Elevation

Acute Pancreatitis (AP) is the inflammation and auto-digestion of the pancreas and is usually associated with the elevation of serum amylase and lipase levels. Here, we report a rare presentation of AP with normal pancreatic enzymes and lupus vulgaris (LV) in a patient with cystic fibrosis (CF). The chief complaints included severe abdominal pain in association with fever and vomiting. On examination, the abdomen was tense and tender. There were bilateral coarse crepitations with expiratory wheeze more pronounced on the left lower chest. After detailed clinical evaluation, a provisional diagnosis of acute pancreatitis, with pneumonitis and oral thrush was established. Routine laboratory investigations were performed to confirm the diagnosis. However, the serum amylase and lipase came out within the normal reference range. So, computerized tomography (CT) scan of the abdomen was performed which showed a diffusely swollen and edematous pancreas along with peri-pancreatic stranding, and hence confirmed the diagnosis. Afterward, the patient was managed conservatively and he had an uneventful recovery. The purpose of reporting this case is to promote awareness among fellow healthcare professionals about this rare manifestation of AP and to prevent any missed diagnosis and serious complications. To conclude, cystic fibrosis may have an unusual presentation like AP without pancreatic enzyme elevation which may create a diagnostic dilemma. Hence, in such cases, a strong clinical suspicion and supportive radiological findings play a critical role in the establishment of the diagnosis.

Rare Presentation of an H-Type Tracehoesophageal Fistula in an Adolescent Male with Cystic Fibrosis

2019 ◽  
Author(s):  
T. Klouda ◽  
E. Lindholm ◽  
E. Poletto ◽  
S. Rani ◽  
L. Varlotta ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Adolescent Male ◽  
Rare Presentation

Pregnancy in cystic fibrosis of the pancreas

JAMA ◽  
1966 ◽  
Vol 195 (12) ◽  
pp. 993-1000 ◽  
Author(s):  
R. J. Grand
Keyword(s):  
Cystic Fibrosis

Freeze-Fracture Examination of Tight Junctions of Human Eccrine Sweat Glands

1980 ◽  
Vol 38 ◽  
pp. 634-635
Author(s):  
J. V. Briggman ◽  
J. Bigelow ◽  
H. Bank ◽  
S. S. Spicer
Keyword(s):  
Cystic Fibrosis ◽  
Freeze Fracture ◽  
Sweat Glands ◽  
Hypertonic Solution ◽  
Dark Cells ◽  
Clear Cells ◽  
Junctional Complexes ◽  
Secretory Coil ◽  
Eccrine Sweat Glands ◽  
Eccrine Sweat

The prevalence of strands shown by freeze-fracture in the zonula occludens of junctional complexes is thought to correspond closely with the transepi-thelial electrical resistance and with the tightness of the junction and its obstruction to paracellular flow.1 The complexity of the network of junc¬tional complex strands does not appear invariably related to the degree of tightness of the junction, however, as rabbit ileal junctions have a complex network of strands and are permeable to lanthanum. In human eccrine sweat glands the extent of paracellular relative to transcellular flow remains unknown, both for secretion of the isotonic precursor fluid by the coil and for resorption of a hypertonic solution by the duct. The studies reported here undertook, therefore, to determine with the freeze-fracture technique the complexity of the network of ridges in the junctional complexes between cells in the secretory coil and the sweat ducts. Glands from a patient with cystic fibrosis were also examined because an alteration in junctional strands could underlie the decreased Na+ resorption by sweat ducts in this disease. Freeze-fracture replicas were prepared by standard procedures on isolated coil and duct segments of human sweat glands. Junctional complexes between clear cells, between dark cells and between clear and dark cells on the main lumen, and between clear cells on intercellular canaliculi of the coil con¬tained abundant anastomosing closely spaced strands averaging 6.4 + 0.7 (mean + SE) and 9.0 +0.5 (Fig. 1) per complex, respectively. Thus, the junctions in the intercellular canaliculi of the coil appeared comparable in complexity to those of tight epithlia. Occasional junctions exhibited, in addition, 2 to 5 widely spaced anastomosing strands in a very close network basal to the compact network. The fewer junctional complexes observed thus far between the superficial duct cells consisted on the average of 6 strands arranged in a close network and 1 to 4 underlying strands that lay widely separated from one another (Fig. 2). The duct epitelium would, thus, be judged slightly more "leaky" than the coil. Infrequent junctional complexes observed to date in the secretory coil segment of a cystic fibrosis specimen disclosed rela¬tively few closely crowded strands.

Chronic airway colonization by Penicillium emersonii in a patient with cystic fibrosis

1999 ◽  
Vol 37 (4) ◽  
pp. 291-293 ◽  
Author(s):  
B. Cimon ◽  
J. Carrere ◽  
J. P. Chazalette ◽  
J. F. Vinatier ◽  
D. Chabasse ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Airway Colonization ◽  
Chronic Airway

Heat stable toxin of E. coli (STa) stimulates duodenal mucosal bicarbonate secretion in cystic fibrosis knockout mice

2001 ◽  
Vol 120 (5) ◽  
pp. A137-A137
Author(s):  
D CHILDS ◽  
D CROMBIE ◽  
V PRATHA ◽  
Z SELLERS ◽  
D HOGAN ◽  
...  
Keyword(s):  
Cystic Fibrosis ◽  
Knockout Mice ◽  
Bicarbonate Secretion ◽  
E Coli ◽  
Heat Stable
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