Extraosseous Ewing Sarcoma Arising at the Papilla of Vater

2018 ◽  
Vol 27 (1) ◽  
pp. 8-8 ◽  
Author(s):  
Ilan Kent ◽  
Evgeny Edelstein ◽  
Olga Levin ◽  
Yaron Wiener
Keyword(s):  
Ewing Sarcoma ◽  
Papilla Of Vater ◽  
Extraosseous Ewing Sarcoma

.

Multi-modality management of extraosseous Ewing sarcoma: 10-year experience from a tertiary care centre

2020 ◽  
pp. 1-7
Author(s):  
Arvind Sathyamurthy ◽  
Ashish Singh ◽  
Tarun Jose ◽  
Patricia Sebastian ◽  
Rajesh Balakrishnan ◽  
...  
Keyword(s):  
Ewing Sarcoma ◽  
Univariate Analysis ◽  
Tertiary Care ◽  
Disease Free Survival ◽  
Molecular Techniques ◽  
Adjuvant Radiation ◽  
Free Survival ◽  
The Impact ◽  
Extraosseous Ewing Sarcoma ◽  
Disease Free

Abstract Aim: To analyse the presentation, diagnosis and patterns of care of extraosseous Ewing sarcoma treated at our institution between 2008 and 2018. Methods: Electronic medical records of extraosseous Ewing sarcoma patients treated at our institution between January 2008 and April 2018 were reviewed. Kaplan–Meier curves were plotted to assess the overall and disease-free survival with 95% confidence intervals. A univariate analysis was carried out to assess the impact of variables such as surgical excision, completeness of surgery, completeness of chemotherapy and addition of radiation therapy on the survivorship. Results: The records of 65 patients treated at our institution were available for review. The mean age was 26·4 years. The most frequent sites of extraosseous Ewing tumour were kidney—9/65 (13·8%) and brain—10/65 (15·4%). Sixteen (24·6%) patients presented with inoperable/metastatic disease at diagnosis. The other 49 (75·4%) had localised disease at presentation. The median overall survival of the 49 non-metastatic patients was 46 months, and the disease-free survival was 45 months. Conclusion: Extraosseous Ewing sarcoma is a rare and aggressive tumour diagnosed by molecular techniques. Multi-modality treatment including surgical resection with wide margins, adjuvant radiation when indicated and completion of systemic chemotherapy results in optimum outcomes.

Primary Intradural Extraosseous Ewing Sarcoma of the Spine: Case Report and Literature Review

Neurosurgery ◽  
2011 ◽  
Vol 69 (4) ◽  
pp. E995-E999 ◽  
Author(s):  
Isaac O Karikari ◽  
Ankit I Mehta ◽  
Shahid Nimjee ◽  
Tiffany R Hodges ◽  
June Tibaleka ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Ewing Sarcoma ◽  
Correct Diagnosis ◽  
Immunohistochemical Analysis ◽  
Leg Pain ◽  
Treatment Modalities ◽  
Magnetic Resonance Imaging Mri ◽  
The Right ◽  
Extraosseous Ewing Sarcoma

Abstract BACKGROUND AND IMPORTANCE: To report a rare case of spinal intradural extraosseous Ewing sarcoma in an adult and review current literature. Although Ewing sarcoma belongs to the family, the treatment modalities are different, and thus the correct diagnosis is very important despite its rare occurrence. CLINICAL PRESENTATION: A 56-year-old woman presented with nocturnal bilateral buttock and leg pain. Magnetic resonance imaging (MRI) showed an enhancing intradural extramedullary extraosseous tumor at L1. INTERVENTION: A T12-L2 laminectomy was performed to resect the tumor. Immunohistochemical analysis confirmed the diagnosis of Ewing sarcoma. A thorough diagnostic workup did not reveal any bony origin of the tumor. Primary intradural central nervous system Ewing sarcoma is infrequently encountered and shares imaging and histopathological features with central primitive neuroectodermal tumors. Establishment of the right diagnosis is crucial because it mandates a distinct workup and treatment modality different from that for central primitive neuroectodermal tumor. Although osseous Ewing sarcoma predominantly occurs in children and young adults, extraosseous central nervous system Ewing sarcoma is not uncommon in adults and should therefore be considered in the differential diagnosis of extraosseous small blue cell tumors in adult patients.

Extraosseous Ewing sarcoma in the mesentery: the first report of cases in children

2015 ◽  
Vol 31 (10) ◽  
pp. 995-999 ◽  
Author(s):  
Soichi Shibuya ◽  
Shigeru Takamizawa ◽  
Tomoko Hatata ◽  
Kazutoshi Komori ◽  
Yoshifumi Ogiso ◽  
...  
Keyword(s):  
Ewing Sarcoma ◽  
First Report ◽  
Extraosseous Ewing Sarcoma

Primary pediatric intraspinal sarcomas

2009 ◽  
Vol 4 (3) ◽  
pp. 222-229 ◽  
Author(s):  
Paul Klimo ◽  
Patrick J. Codd ◽  
Holcombe Grier ◽  
Liliana C. Goumnerova
Keyword(s):  
Peripheral Nerve ◽  
Ewing Sarcoma ◽  
Pediatric Population ◽  
Spinal Nerve ◽  
Neurological Deficits ◽  
Nerve Sheath Tumors ◽  
Peripheral Nerve Sheath Tumors ◽  
Nerve Sheath ◽  
Lumbar Spinal ◽  
Extraosseous Ewing Sarcoma

Sarcomas that arise from within the spinal canal are rare, particularly within the pediatric population. In general, these primary intraspinal sarcomas are highly aggressive, posing unique treatment challenges with respect to surgery and choice of adjuvant therapy. The goal must be to obtain the most complete resection possible to minimize the risk of recurrence and metastasis, while preventing potential neurological deficits that may result from aggressive surgery. Among these primary intraspinal sarcomas are malignant peripheral nerve sheath tumors and members of the Ewing sarcoma family of tumors. The authors present 3 cases of unique spinal sarcomas in children—2 malignant peripheral nerve sheath tumors in patients without neurofibromatosis and an intradural extraosseous Ewing sarcoma arising from the sensory component of a lumbar spinal nerve—and discuss their management and outcome with a review of the current literature.

Intradural extramedullary extraosseous Ewing sarcoma/PNET of foramen magnum

2014 ◽  
Vol 115 (3) ◽  
pp. 423-424 ◽  
Author(s):  
Miloš A. Lučić ◽  
Duško Kozić ◽  
Mladen Bjelan ◽  
Snežana Marić
Keyword(s):  
Ewing Sarcoma ◽  
Foramen Magnum ◽  
Intradural Extramedullary ◽  
Extraosseous Ewing Sarcoma

Evaluation of outcome and prognostic factors in extraosseous Ewing sarcoma

2014 ◽  
Vol 61 (11) ◽  
pp. 1925-1931 ◽  
Author(s):  
Bivas Biswas ◽  
N.K. Shukla ◽  
S.V.S. Deo ◽  
Sandeep Agarwala ◽  
D.N. Sharma ◽  
...  
Keyword(s):  
Prognostic Factors ◽  
Ewing Sarcoma ◽  
Extraosseous Ewing Sarcoma

scholarly journals Primary extraosseous Ewing sarcoma of the lung: Case report and literature review

2013 ◽  
Vol 8 (2) ◽  
pp. 832 ◽  
Author(s):  
Narendra Shet ◽  
Luana Stanescu ◽  
Gail Deutsch
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Ewing Sarcoma ◽  
Extraosseous Ewing Sarcoma

scholarly journals Extraosseous Ewing sarcoma of the vagina: a rare entity

2013 ◽  
Vol 33 (2) ◽  
pp. 182-186 ◽  
Author(s):  
Lovina Machado ◽  
Aisha Al-Hamdani ◽  
Dilip K. Sankhla ◽  
Mansour S. Al-Moundhri
Keyword(s):  
Ewing Sarcoma ◽  
Rare Entity ◽  
Extraosseous Ewing Sarcoma

scholarly journals Extraosseous Ewing sarcoma

2010 ◽  
Author(s):  
Henry Knipe ◽  
Hani Salam
Keyword(s):  
Ewing Sarcoma ◽  
Extraosseous Ewing Sarcoma

Primary Extraosseous Ewing Sarcoma of the Thoracic Spine Presenting as Chest Pain Mimicking Spinal Schwannoma

2020 ◽  
Vol 141 ◽  
pp. 507-510
Author(s):  
Moon-Soo Han ◽  
Seul-Kee Lee ◽  
Bong Ju Moon ◽  
Jung-Kil Lee ◽  
Yoo-Duk Choi
Keyword(s):  
Chest Pain ◽  
Thoracic Spine ◽  
Ewing Sarcoma ◽  
Spinal Schwannoma ◽  
Extraosseous Ewing Sarcoma
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