Urinary Tract Anomalies in Neonates With Spontaneous Pneumothorax and/or Pneumomediastinum

Spontaneous pneumothorax is reportedly occurring in 0.05% to 1% of all live births.1,2 Pediatricians have long been aware of the apparent association between spontaneous pneumothorax, with or without pneumomediastinum, and congenital anomalies of the urinary tract. However, reports of the incidence of this relationship have been inconclusive, based on small numbers of infants.3-5 We therefore sought to determine this incidence in a large clinical population. METHODS We reviewed the records of all 6,236 infants admitted to the neonatology unit during 1961-1967 and selected all cases of spontaneous pneumothorax or pneumomediastinum or both (lung rupture) and of congenital urinary tract anomalies.

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Screening for Renal and Urinary Tract Anomalies in Asymptomatic First Degree Relatives of Children with Congenital Anomalies of the Kidney and Urinary Tract (CAKUT)

The Indian Journal of Pediatrics ◽

10.1007/s12098-020-03262-7 ◽

2020 ◽

Vol 87 (9) ◽

pp. 686-691 ◽

Cited By ~ 2

Author(s):

Aravindhan Manoharan ◽

Sriram Krishnamurthy ◽

Palanisamy Sivamurukan ◽

Ramesh Ananthakrishnan ◽

Bibekanand Jindal

Keyword(s):

Urinary Tract ◽

Congenital Anomalies ◽

First Degree Relatives ◽

Urinary Tract Anomalies

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Prune-belly syndrome

Paediatrica Indonesiana ◽

10.14238/pi49.5.2009.304-8 ◽

2009 ◽

Vol 49 (5) ◽

pp. 304

Author(s):

Yenny Yenny ◽

Kusuma P. A ◽

Damanik M. P.

Keyword(s):

Congenital Anomaly ◽

Prognostic Factors ◽

Urinary Tract ◽

Pulmonary Hypoplasia ◽

Clinical Findings ◽

Prune Belly Syndrome ◽

Live Births ◽

Prune Belly ◽

Clinical Variants ◽

Urinary Tract Anomalies

Prune-belly syndrome, also known as Eagle-Barretsyndrome, is a congenital anomaly comprisingthree clinical findings: deficient abdominalmusculature, urinary tract anomalies, andbilateral cryptorchidism. Other clinical findings involvingrespiratory, skeletal, digestion and cardiovascular systemmay also accompany the syndrome. The incidence isapproximately 1 : 30,000 to 40,000 live births and 95%of cases occur in boys. Pulmonary hypoplasia and kidneyfailure are important prognostic factors that contributeto 60% of mortality rate. Treatment includes surgicalcorrection of the abdominal wall and urinary tract,orchidopexy and other supportive managements.l-4 Wereport 4 cases on typical Prune-belly syndrome, togetherwith other clinical variants.

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Congenital Anomalies of the Kidney and Urinary Tract in Children Born Small for Gestational Age

PRILOZI ◽

10.1515/prilozi-2017-0007 ◽

2017 ◽

Vol 38 (1) ◽

pp. 53-57 ◽

Cited By ~ 2

Author(s):

Aleksandra Janchevska ◽

Zoran Gucev ◽

L. Tasevska-Rmus ◽

Velibor Tasic

Keyword(s):

Urinary Tract ◽

Congenital Anomalies ◽

Early Recognition ◽

Growth Failure ◽

Live Births ◽

Gestation Age ◽

Assessment And Treatment ◽

Birth Data ◽

Normal Glomerular Filtration Rate

Abstract Introduction: Congenital anomalies of the kidney and urinary tract (CAKUT) represent several types of malformations with occurrence of 1 in about 500 live births. Objective: Small for gestation age (SGA) may influence in prevalence of CAKUT and progression of chronic kidney disease (CKD) in children. The aim of this study was to elaborate our experiences with detected CAKUT in a cohort of SGA born children in Macedonia. Methods: Our cohort consisted of 100 SGA born children investigated for associated congenital anomalies of urinary tract. We analyzed anthropometric and clinical birth data in children with diagnosed CAKUT and estimated the stage and time of onset of CKD by biochemical and imaging technics. Results: We revealed 7 (7.0%) SGA born children with congenital anomalies of the urinary tract. Their mean birth weight was very low 1855 gr (-3.93 SDS) and the birth length 45.57cm (-2.17 SDS), as well. A significant growth failure with reduced weight and BMI were noticed at the time of diagnosis. A diagnosis of CAKUT in 4/7 was established in the first few months of life, but in others 3 later in early childhood. Three children revealed with unilateral kidney agenesis, 2 had hypo-dysplastic kidneys and in 2 children was found vesicoureteral reflux. Normal glomerular filtration rate was estimated in 2 children with CAKUT. Stage 2 CKD with GFR 60-90 ml/minx1.73m2 had 3 children, 1 patient was graded in stage 3 and one child needed kidney transplantation, stage 5 CKD. Conclusions: We presented 7 SGA born children with CAKUT. An early recognition, assessment and treatment of these anomalies might improve their quality of life.

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LACK OF MAJOR URINARY TRACT ANOMALIES IN ASSOCIATION WITH NON-FATAL SPONTANEOUS PNEUMOTHORAX IN NEAR-TERM AND TERM NEONATES. 1174

Pediatric Research ◽

10.1203/00006450-199604001-01196 ◽

1996 ◽

Vol 39 ◽

pp. 198-198

Author(s):

Joel S Brenner ◽

M. Gary Karlowicz

Keyword(s):

Urinary Tract ◽

Spontaneous Pneumothorax ◽

Term Neonates ◽

Near Term ◽

Urinary Tract Anomalies

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Urinary System Birth Defects in Surgically Treated Infants in Sarajevo Region of Bosnia and Herzegovina

Bosnian Journal of Basic Medical Sciences ◽

10.17305/bjbms.2008.2965 ◽

2008 ◽

Vol 8 (2) ◽

pp. 126-130

Author(s):

Selma Aličelebić ◽

Dina Kapić ◽

Zakira Mornjaković

Keyword(s):

Urinary Tract ◽

Vesicoureteral Reflux ◽

Bosnia And Herzegovina ◽

Congenital Anomalies ◽

Prune Belly Syndrome ◽

Urinary System ◽

Renal Hypoplasia ◽

Female Patients ◽

Clinical Records ◽

Urinary Tract Anomalies

Congenital anomalies of the urinary system are relatively common anomalies. In Bosnia and Herzegovina there is no existent unique evidence of congenital anomalies and registries. The aim of this study was to obtain the frequency of different urinary tract anomalies types and their sex distribution among cases hospitalized in the Department of Pediatric Surgery of the University of Sarajevo Clinics Centre, Bosnia and Herzegovina, during the period from January 2002 to December 2006. Retrospective study was carried out on the basis of clinical records. Standard methods of descriptive statistics were performed for the data analysis. Among 289 patients that were surgically treated 62,37% of the patients were male patients, while 37,63% were female patients. Twenty nine different urinary system anomalies types were found in this study. These were: vesicoureteral reflux (99 cases or 30,75%), hypospadias (62 cases or 19,26%), pelviureteric junction obstruction (42 cases or 13,04%), megaureter (35 cases or 10,87%), duplex pelvis and ureter (16 cases or 4,97%), bladder diverticulum (8 cases or 2,48%), ureterocoele (7 cases or 2,17%), stenosis of the external urethral opening (6 cases or 1,86%), ectopic kidney, duplex kidney and pelvis (each 5 cases or 1,55%), polycystic kidneys and urethral stricture (each 4 cases or 1,24%), multicystic kidney (3 cases or 0,93%), kidney agenesis, ureter agenesis, urethral diverticulum, ectopic ureter, horseshoe kidney and fetal kidney (each 2 cases or 0,62%), renal aplasia, urethral atresia, renal cyst, urachal cyst, epispadias, bladder exstrophy, renal hypoplasia, renal malrotation and Prune-Belly syndrome (each 1 case or 0,31%). According to this study, urinary tract anomalies were more common in male than in female patients (62,37%), Generally, the most frequent anomaly type was vesicoureteral reflux in total number of 99 cases, and in females (66 cases), but hypospadias was the most common anomaly in males (62 cases). The anomalies of other systems associated with urinary system anomalies were found in ten cases. These were: cryptorchidism, congenital inguinal hernia, open inner inguinal ring, uterus bicornis unicollis and one case of multiple anomalies.

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Obstructing calculus in a single limb of a duplicated ureter: A Recall of the surgical anatomy and the Variable Ureter Anomalies

Asploro Journal of Biomedical and Clinical Case Reports ◽

10.36502/2019/asjbccr.6156 ◽

2019 ◽

Vol 2 (2) ◽

pp. 30-33

Author(s):

Shawish FA ◽

Shawish WA

Keyword(s):

Urinary Tract ◽

Young Patient ◽

Congenital Anomalies ◽

Correct Diagnosis ◽

Surgical Anatomy ◽

Common Site ◽

Considerable Morbidity ◽

Complete Duplication ◽

Urinary Tract Anomalies ◽

Duplicated Ureter

The ureter is a common site of congenital anomalies which may be associated with a considerable morbidity particularly among young patient. The congenital anomalies of the ureter coexist with multitude of other urinary tract anomalies but it may occur independently. It is more common in females. The complete duplication of the ureter may not produce symptoms which would suggest the presence of malformation. Therefore, such anomaly may not become apparent until later in life. Further, this anomaly might not be recognized prior to the surgery and hence, missing of the stone is highly possible. Herein we present a case of complete ureter duplicate with an obstructive stone located close to VUJ of one limb of the duplicate. A sound knowledge of the surgical anatomy and of the congenital ureter anomalies is essential for correct diagnosis and appropriate management.

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