scholarly journals Congenital prepubic sinus: a series of six cases of extremely rare congenital anomaly

2017 ◽  
Vol 4 (2) ◽  
pp. 803
Author(s):  
Sudhir Singh ◽  
Digamber Chaubey ◽  
J. D. Rawat ◽  
Gurmeet Singh
Keyword(s):  
Congenital Anomaly ◽  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Female Child ◽  
Urethral Duplication ◽  
Abdominal Wall Closure ◽  
Rare Congenital Anomaly

Congenital prepubic sinus (CPS) is a very rare congenital anomaly. The baby generally present with discharge from an opening situated in midline below umbilicus to root of penis in male or clitoris in female child. The etiology of this congenital anomaly is not exactly known. There is debate in etiology as one theory support anomalous anterior abdominal wall closure and another support variant of dorsal urethral duplication. Here we are presenting the six cases of CPS with their management and brief discussion on theories that have been proposed for their etiology.

scholarly journals Rare presentation of incomplete male urethral duplication: A case report and review of literature

2021 ◽  
Vol 9 (1) ◽  
pp. 292-296
Author(s):  
Orgeness J Mbwambo ◽  
Alex Mremi ◽  
Mohamed Mbarouk ◽  
Jasper Mbwambo ◽  
Frank Bright ◽  
...  
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Postoperative Period ◽  
Surgical Removal ◽  
Urethral Duplication ◽  
Review Of Literature ◽  
Rare Presentation ◽  
Rare Congenital Anomaly ◽  
Accessory Urethra

Urethral duplication is a rare congenital anomaly affecting mainly males. Here, we report a case of urethral duplication in a 19 years old male presented as a scrotal sinus discharging pus for 1 year. Surgical removal of accessory urethra was done and postoperative period was uneventful.

scholarly journals Prune Belly Syndrome with Overlapping Presentation of Partial Urorectal Septum Malformation Sequence in a Female Newborn with Absent Perineal Openings

2014 ◽  
Vol 2014 ◽  
pp. 1-4 ◽  
Author(s):  
Azhar Farooqui ◽  
Alaa AlAqeel ◽  
Zakaria Habib
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Abdominal Wall ◽  
Ambiguous Genitalia ◽  
Prune Belly Syndrome ◽  
Rare Congenital Anomaly ◽  
Prune Belly ◽  
Bilateral Cryptorchidism ◽  
Original Case ◽  
Classical Triad

Prune belly syndrome (PBS) is a rare congenital anomaly characterized in males by a triad of anomalous genitourinary tract, deficient development of abdominal wall muscles, and bilateral cryptorchidism. Although similar anomalies have been reported in females, by definition they do not full fill the classical triad. Urorectal septum malformation sequence (URSM) is a lethal condition characterized by presence of ambiguous genitalia, absent perineal openings (urogenital and anal), and lumbosacral abnormalities. In this original case report, the authors discuss the presentation and management of what would be analogous to a Woodhouse category 1 PBS in a female newborn associated with an overlapping presentation of URSM.

scholarly journals Progressive Dilatation as a Successful Treatment for Y duplication of Urethra

2021 ◽  
Author(s):  
Akash Pati ◽  
Subrat K Sahoo ◽  
Bikasha B Tripathy
Keyword(s):  
Congenital Anomaly ◽  
Case Reports ◽  
Case Series ◽  
Urethral Duplication ◽  
Rare Congenital Anomaly ◽  
Standardized Treatment ◽  
Rectourinary Fistula ◽  
Lost To Follow Up ◽  
Multiple Stages

Duplication of urethra is a rare congenital anomaly that has been reported in case reports and case series. A Y-shaped urethral duplication is the rarest variant as per the classification suggested and hence lacks a standardized treatment option. We report a case of Y-duplication of urethra diagnosed during neonatal age and presented to us at nine years of age. The patient had undegone a vesicostomy at seventh day of life for passing urine per anus and was lost to follow up thereafter. An attempt at disconnection of the duplicated urethral tract to anus after colostomy, at eight years of age had failed. The patient was managed successfully by progressive dilatation of the orthotopic urethra, which required multiple stages, followed by separation of the urethra from the rectum. At three years follow up the patient is continent and asymptomatic. Keywords: Y duplication of the urethra; PADUA technique; Rectourinary fistula; Urethral duplication.

scholarly journals Congenital duplication of the urethra with urethral diverticulum: a case report

F1000Research ◽  
2014 ◽  
Vol 3 ◽  
pp. 99 ◽  
Author(s):  
Darshan H Shah ◽  
Arvind P Ganpule ◽  
Ravindra B Sabnis ◽  
Mahesh R Desai
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Treatment Modality ◽  
List Item ◽  
Urethral Diverticulum ◽  
Endoscopic Management ◽  
List Type ◽  
Urethral Duplication ◽  
Small Opening ◽  
Rare Congenital Anomaly

Duplication of the urethra is a rare congenital anomaly. Urethral duplication with the presence of diverticulum is a rare combination and to the best of our knowledge has  not been previously reported. We report a case of a 16 month old male child with duplication of the urethra and diverticulum arising from the ventral urethra. We also cover the intricacies and challenges in the management of such a case.The opening of the narrowed accessory dorsal urethra at the verumontanum was cauterized and gradually the dorsal urethra became atrophied. The ventral urethral diverticulum was excised. This case is unique due to:The unusual presentation of swelling over the dorsum of the penis, together with duplication of the urethra with diverticulum.The use of cauterization as a treatment modality. Cauterization of the ventral urethra with a Bugbee electrode and diverticulectomy was performed. A glidewire helped in identifying the small opening of the dorsal urethra at the level of the verumontanum. The case also highlights the importance of endoscopic management of this clinical entity.

scholarly journals Congenital prepubic sinus with dorsal penile curvature: a case report and literature review

2019 ◽  
Vol 19 (1) ◽  
Author(s):  
Chuan Wang ◽  
Xue Ma
Keyword(s):  
Congenital Anomaly ◽  
Histological Examination ◽  
Symphysis Pubis ◽  
Early Age ◽  
Penile Curvature ◽  
Urethral Duplication ◽  
Case Presentation ◽  
Rare Congenital Anomaly ◽  
Further Development ◽  
Histological Result

Abstract Background Congenital prepubic sinus (CPS) is a rare congenital anomaly and widely thought to be a variant of urethral duplication. Histological examination of this case gives a clue to this theory. CPS with dorsal penile curvature has been reported in previous publications, but their procedures to correct the curvature are different from this case. Case presentation A 10-year-old boy complained of the pain in the dorsal base of the penis. Physical examination revealed an accessory meatus located in the midline of the dorsal proximal penis and moderate dorsal penile curvature with deficient dorsal foreskin. Imaging examination showed that the meatus did not communicate with either normal urethra or urinary bladder, and ended blindly at the level of the symphysis pubis. The intact 4-cm-long sinus was completely separated and excised. Penile curvature was corrected after the dorsal proximal fibrous cord was detached. Histological examination confirmed the diagnosis of urethral duplication. Conclusions The histological result of this case supports the theory that CPS is a variant of the dorsal urethra. Moreover, this case indicates that the curvature in patients with CPS may be caused by the dorsal fibrous cord at the beginning and the operation should be conducted at an early age to avoid further development of the curvature during puberty.

scholarly journals Urethral Duplication with Two Hypospadic Meati—An Unusual Variant

2016 ◽  
Vol 04 (01) ◽  
pp. 037-040 ◽  
Author(s):  
Joseph Davidson ◽  
Naomi Wright ◽  
Massimo Garriboli
Keyword(s):  
Congenital Anomaly ◽  
Male Infant ◽  
Single Stage ◽  
Type Ii ◽  
Urethral Duplication ◽  
Unique Case ◽  
Rare Congenital Anomaly ◽  
Unusual Variant ◽  
Proximal Urethra

AbstractDuplication of the urethra is a rare congenital anomaly, with approximately 300 cases reported in the literature. We report a unique case of this condition in a male infant. This case differs from the classical Effman type II-A2 duplication because of the presence of two hypospadic urethral meati, as opposed to a ventral or dorsal accessory meatus with a normally positioned distal urethra. The patient underwent a single-stage repair consisting of a proximal urethra-urethral anastomosis and distal urethral tubularization at 21 months of age with excellent results in terms of both function and cosmesis.

scholarly journals Technique of Midline Abdominal Incision Closure Among Surgical Trainees

2020 ◽  
Vol 17 (2) ◽  
pp. 72-75
Author(s):  
Alex Muturi ◽  
Kotecha Vihar ◽  
Pulei Ann ◽  
Maseghe Philip
Keyword(s):  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Tertiary Hospital ◽  
Fascial Closure ◽  
Wound Complications ◽  
Absorbable Suture ◽  
Abdominal Wall Closure ◽  
Abdominal Incision ◽  
Abdominal Closure ◽  
Surgical Trainees

Background: Technique of anterior abdominal wall closure (AAWC) determines wound-related surgical complications. Residents in obstetrics and gynecology and surgery departments perform most midline abdominal wall closure; data is lacking on how it is being done. This study identifies abdominal wall closure techniques used. Methods: A descriptive study was carried out from October 2015 to May 2016. Results: 71 (35 surgical, 36 ObGyn) residents completed a self-administered questionnaire. Knowledge of midline abdominal closure was acquired from medical officers (58.6%) or consultants before residency (28.6%). Absorbable suture was preferred for clean wounds by 75% of residents; 70% used size 1 suture for fascial closure. Most residents (95.7%) closed fascia in clean wound by continuous suturing. Interrupted suturing was preferred in contaminated and dirty wounds. Half of the residents in both groups would close skin in contaminated wounds, while 16% of surgery and 9.4% ObGyn will close skin in dirty wounds. Conclusion: Inconsistencies exist in anterior abdominal wall closure between groups of residents despite presence of clear guidelines. It is important to harmonize training on AAWC at the tertiary hospital. Keywords: Abdominal closure, Midline incision, Wound complications

scholarly journals Two Cases of Dorsal Urethral Duplication

2013 ◽  
Vol 59 (1) ◽  
pp. 52-54 ◽  
Author(s):  
H Gozar ◽  
Ra Prișcă ◽  
Zoltán Derzsi
Keyword(s):  
Congenital Anomaly ◽  
Urethral Duplication ◽  
Rare Congenital Anomaly ◽  
Proximal Urethra ◽  
Accessory Urethra

Abstract Urethral duplication is a rare congenital anomaly. In addition to a normally urethra, there is an accessory urethra arising from the bladder or the proximal urethra which may open anywhere on the penis or even on the perineum. Many patients with this malformation are asymptomatic. Some patients may complain of intermittent discharge from the accessory urethra, incontinence, infection, double streams or stricture. The duplicated urethra may be complete or incomplete, may be located dorsal, ventral or in Y-type. The treatment of urethral duplication is individualized, depending on the type of malformation. We report two cases of dorsal urethral duplication discovered in two boys.

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