scholarly journals Quasi Moyamoya Disease: Case report and literature review

2021 ◽  
Vol 3 (01) ◽  
pp. 39-41
Author(s):  
Srijana Neupane ◽  
Karuna Tamrakar Karki
Keyword(s):  
Moyamoya Disease ◽  
Internal Carotid ◽  
Inflammatory Diseases ◽  
Internal Capsule ◽  
Sudden Onset ◽  
Left Internal Carotid Artery ◽  
Digital Subtraction ◽  
Terminal Portion ◽  
Mr Image ◽  
Disease Case

Quasi moyamoya disease is the unilateral form of typical moyamoya disease which is associated with acute or chronic stages of inflammatory diseases. Here, I present 21-year-old boy presented with sudden onset of weakness of right sided limbs following physical workout, had acute ischemic infarction of left internal capsule in diffusion restriction MR image and unilateral steno- occlusive changes of terminal portion of left internal carotid artery was noted in digital subtraction angiography.

Unilateral sudden hearing loss as the first presenting symptom of moyamoya disease

2013 ◽  
Vol 127 (2) ◽  
pp. 196-199 ◽  
Author(s):  
L-S Tseng ◽  
S-D Luo
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Moyamoya Disease ◽  
Carotid Arteries ◽  
Internal Carotid ◽  
Cerebral Arteries ◽  
Sudden Onset ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Internal Carotid Arteries

AbstractObjective:We describe a rare case of sudden onset of unilateral sensorineural hearing loss occurring as the first symptom of moyamoya disease, which is characterised by progressive stenosis of the intracranial internal carotid arteries and their proximal anterior cerebral arteries and middle cerebral arteries.Method:Case report and review of the world literature regarding moyamoya disease with hearing loss.Results:The reported patient had moyamoya disease that initially presented as sudden, unilateral sensorineural hearing loss. Magnetic resonance imaging showed occlusion of the anterior cerebral, middle cerebral and distal internal carotid arteries bilaterally. The possible mechanism of this patient's sudden sensorineural hearing loss may have been vascular occlusion resulting from thrombotic narrowing or blockage by plaque.Conclusion:The described patient represents the first reported case of sudden onset, unilateral sensorineural hearing loss occurring as the first symptom of moyamoya disease. The possibility of a vascular lesion such as moyamoya disease should be considered in patients with sudden sensorineural hearing loss, especially children, young adults and Asian patients. Due to this disease's poor outcome, early diagnosis and treatment are important to prevent stroke.

scholarly journals Acute communicating hydrocephalus caused by extravasation of digital subtraction angiography contrast medium: a case report and literature review

2020 ◽  
Vol 48 (8) ◽  
pp. 030006052094550
Author(s):  
Jin-Xia Zhang ◽  
Xiao-Yong Shi ◽  
Zhu-Xiao Tang ◽  
Hu Sun ◽  
Zheng Shen ◽  
...  
Keyword(s):  
Contrast Medium ◽  
Internal Carotid ◽  
Mechanical Thrombectomy ◽  
External Ventricular Drainage ◽  
Left Internal Carotid Artery ◽  
Communicating Hydrocephalus ◽  
Digital Subtraction ◽  
Left Frontal Lobe ◽  
Drainage Fluid ◽  
Endovascular Technology

With the increasing use of endovascular technology in the treatment of various conditions, there has been an inevitable rise in cases with extravasation of contrast medium. We present a case in which extravasation of a large quantity of contrast medium resulted in acute communicating hydrocephalus. A 78-year-old woman came to the hospital because of abnormal right-sided limb movement, and was diagnosed with occlusion of the left internal carotid artery. The patient underwent timely intra-arterial mechanical thrombectomy. Postoperative computed tomography (CT) examination revealed a high-density shadow of the left basal ganglia and left frontal lobe. Twelve hours later, the patient fell into a coma. Repeat head CT indicated acute hydrocephalus with no evidence of obstruction. The patient underwent emergency external ventricular drainage, and the drainage fluid was observed to be clear. The patient regained consciousness after the procedure and the drainage tube was removed 4 days later. The patient had no recurrence of hydrocephalus. The mechanisms and treatment of this condition are discussed.

scholarly journals Vulnerability to shear stress caused by altered peri-endothelial matrix is a key feature of Moyamoya disease

2021 ◽  
Vol 11 (1) ◽  
Author(s):  
Muneaki Matsuo ◽  
Satomi Nadanaka ◽  
Minami Soga ◽  
Taku Sugiyama ◽  
Shota Serigano ◽  
...  
Keyword(s):  
Shear Stress ◽  
Wall Shear Stress ◽  
Progenitor Cells ◽  
Endothelial Progenitor Cells ◽  
Moyamoya Disease ◽  
Internal Carotid ◽  
Terminal Portion ◽  
Endothelial Progenitor ◽  
Wall Shear ◽  
Thickened Intima

AbstractMoyamoya disease (MMD) is characterized by progressive bilateral stenotic changes in the terminal portion of the internal carotid arteries. Although RNF213 was identified as a susceptibility gene for MMD, the exact pathogenesis remains unknown. Immunohistochemical analysis of autopsy specimens from a patient with MMD revealed marked accumulation of hyaluronan and chondroitin sulfate (CS) in the thickened intima of occlusive lesions of MMD. Hyaluronan synthase 2 was strongly expressed in endothelial progenitor cells in the thickened intima. Furthermore, MMD lesions showed minimal staining for CS and hyaluronan in the endothelium, in contrast to control endothelium showing positive staining for both. Glycosaminoglycans of endothelial cells derived from MMD and control induced pluripotent stem cells demonstrated a decreased amount of CS, especially sulfated CS, in MMD. A computational fluid dynamics model showed highest wall shear stress values in the terminal portion of the internal carotid artery, which is the predisposing region in MMD. Because the peri-endothelial extracellular matrix plays an important role in protection, cell adhesion and migration, an altered peri-endothelial matrix in MMD may contribute to endothelial vulnerability to wall shear stress. Invading endothelial progenitor cells repairing endothelial injury would produce excessive hyaluronan and CS in the intima, and cause vascular stenosis.

Etiology and pathogenesis of Moyamoya Disease: An update on disease prevalence

2017 ◽  
Vol 12 (3) ◽  
pp. 246-253 ◽  
Author(s):  
Shuo Huang ◽  
Zhen-Ni Guo ◽  
Mingchao Shi ◽  
Yi Yang ◽  
Mingli Rao
Keyword(s):  
Carotid Artery ◽  
Internal Carotid Artery ◽  
Moyamoya Disease ◽  
Internal Carotid ◽  
Disease Prevalence ◽  
Occlusive Disease ◽  
Terminal Portion ◽  
The Past ◽  
Cerebrovascular Occlusive Disease

Moyamoya disease is a chronic cerebrovascular occlusive disease that is characterized by progressive stenosis of the terminal portion of the internal carotid artery and its main branches. The occurrence of Moyamoya disease is related to immune, genetic, and other factors. Though the research of Moyamoya disease has made great strides in the past 60 years, the etiology and pathogenesis are largely unknown. This review will focus on the genetic pathogenic and inflammation factors of Moyamoya disease.

Idiopathic Moyamoya Disease Presenting as Isolated Hemichorea

2021 ◽  
Author(s):  
Omer Abdul Hamid ◽  
Paul Klimo ◽  
Asim F. Choudhri ◽  
Namrata Shah
Keyword(s):  
Carotid Artery ◽  
Internal Carotid Artery ◽  
Moyamoya Disease ◽  
Cerebral Artery ◽  
Internal Carotid ◽  
Lower Extremities ◽  
Medical Attention ◽  
Left Internal Carotid Artery ◽  
Caucasian Girl ◽  
Upper And Lower Extremities

AbstractThe study aimed to describe a case of a 7-year-old Caucasian girl who developed isolated chorea in her right upper and lower extremities progressively increasing over 2 years. This study is a case report and conducted at tertiary care center. A 7-year-old Caucasian girl who gradually developed worsening choreiform movements in her right upper and lower extremities over the course of 2 years until medical attention was sought. Literature review of children presenting with chorea as the only manifestation in moyamoya disease. A 7-year-old right-handed Caucasian girl presented with progressively worsening choreiform movements in her right upper and lower extremities affecting her fine motor skills and gait impairment There was no weakness, hyperreflexia, or spasticity on her neurological exam. Neuroimaging studies showed “ivy sign,” asymmetric prominence of vessels within the subarachnoid spaces overlying the left cerebral hemisphere with corresponding serpiginous T2 fluid-attenuated inversion recovery abnormality, but no parenchymal volume loss or diffusion restriction. Magnetic resonance angiography showed focal moderate-to-severe stenosis at the junction of the paraophthalmic and supraclinoid segments of the left internal carotid artery, with poststenotic dilatation. Angiography demonstrated focal stenosis involving the ophthalmic segment of the left internal carotid artery with 50% stenosis. There was compensation through a medium sized left posterior communicating artery as well as posterior cerebral artery to middle cerebral artery and anterior cerebral artery collateralization. Brain single-photon emission computerized tomography scan showed no evidence of perfusion defects in the cerebral hemispheres, basal ganglia, or thalami. She underwent successful revascularization procedure (left pial synangiosis) with resolution of her choreiform movements and normalization of her gait. Our case demonstrates that moyamoya disease should be suspected when evaluating a child with hemichorea and describes resolution of symptoms after revascularization surgery. Neuroimaging and vascular studies should be obtained in children with unilateral movement disorder.

scholarly journals Transvenous Embolization of Primitive Trigeminal Artery Variant-Cavernous Fistula with Guglielmi Detachable Coils

2008 ◽  
Vol 14 (2_suppl) ◽  
pp. 95-98 ◽  
Author(s):  
Yi-Ming Wu ◽  
Ho-Fai Wong
Keyword(s):  
Internal Carotid ◽  
Left Internal Carotid Artery ◽  
Inferior Petrosal Sinus ◽  
Digital Subtraction ◽  
Trigeminal Artery ◽  
Guglielmi Detachable Coils ◽  
Carotid Cavernous Fistula ◽  
Cavernous Fistula ◽  
Detachable Coils ◽  
Primitive Trigeminal Artery

Here, we present a 32-year-old male with proptosis and chemosis of the left eye following a close head injury. Digital subtraction angiography of the left internal carotid artery showed a left carotid-cavernous fistula (CCF) associated with a primitive trigeminal artery (PTA) variant. The patient was successfully treated with transvenous Guglielmi detachable coils embolization via the inferior petrosal sinus. The PTA variant was preserved without cerebellar or brainstem infarct.

scholarly journals Recurrent Intracranial Hemorrhage in an Adult with Moyamoya Disease: Case Report, Radiographic Studies and Pathology

1988 ◽  
Vol 15 (4) ◽  
pp. 430-434 ◽  
Author(s):  
Mark Kaufman ◽  
Brian W. Little ◽  
Bernard W. Berkowitz
Keyword(s):  
Moyamoya Disease ◽  
Internal Carotid ◽  
Artery Occlusion ◽  
Carotid Artery Occlusion ◽  
Vascular Lesions ◽  
Vascular Disorder ◽  
Intracranial Hemorrhages ◽  
Disease Case ◽  
Cerebral Ischemic ◽  
Ischemic Events

ABSTRACT:Moyamoya disease is an unusual vascular disorder highlighted by progressive bilateral internal carotid artery occlusion and collateralization of intracranial blood flow. Recurrent multifocal cerebral ischemic events and isolated intracerebral hemorrhage are known to occur in this disorder. We report a 52 year old man who over a nine year period had four apparent intracranial hemorrhages. Serial angiograms demonstrated the evolution of moyamoya disease. Pathologic examination confirmed multiple vascular lesions, including two that were clinically silent.

scholarly journals Carotid Dissection and Isolated Paralysis of Ipsilateral Half Tongue: Clinical Cases

2020 ◽  
Vol 2020 ◽  
pp. 1-6
Author(s):  
Komi Igneza Agbotsou ◽  
Damelan Kombate ◽  
Christopher Mehri ◽  
Kossivi Apetse ◽  
Kpalma Duga Bakpatina-Batako ◽  
...  
Keyword(s):  
Internal Carotid ◽  
Brain Mri ◽  
Good Prognosis ◽  
Sudden Onset ◽  
Moderate Intensity ◽  
Left Internal Carotid Artery ◽  
Carotid Dissection ◽  
Left Half ◽  
Surgical History ◽  
The Subject

Objective. We report two cases of carotid dissection revealed by isolated paralysis of the ipsilateral half tongue. Observations. First patient, 52 years old, with no particular medical or surgical history, presented with isolated paralysis of the left half tongue preceded by two weeks of moderate-intensity cervicalgia and having been the subject to cervical manipulation. MRI revealed dissection of the left internal carotid artery in its prepetrous portion. The evolution after 6 weeks of platelet aggregating inhibitors treatment was favorable. The second patient, 74 years old, with no particular medical or chirurgical history, presented with a sudden onset of paralysis of the left half tongue preceded by unusual headaches associated with neck pain. Brain MRI showed aneurysmal ectasia of the left internal carotid with parietal irregularity suggestive of carotid dissection. The evolution after four weeks of treatment with anticoagulant was favorable. Conclusion. Carotid dissection revealed by isolated paralysis of the half tongue is rare. It is generally of good prognosis. However, in paralysis of half tongue, it must be urgently sought and treated to reduce the risk of a transient or constituted ischemic accident.

REPAIR OF AN ALARMING INTRAOPERATIVE INTRACAVERNOUS CAROTID ARTERY TEAR WITH ANASTOCLIPS: TECHNICAL CASE REPORT

Neurosurgery ◽  
2009 ◽  
Vol 65 (5) ◽  
pp. E998-E999 ◽  
Author(s):  
Rossana Romani ◽  
Riku Kivisaari ◽  
Özgür Çelik ◽  
Mika Niemelä ◽  
Giancarlo Perra ◽  
...  
Keyword(s):  
Carotid Artery ◽  
Internal Carotid Artery ◽  
Digital Subtraction Angiography ◽  
Internal Carotid ◽  
Lateral Wall ◽  
Anterior Wall ◽  
Left Internal Carotid Artery ◽  
Digital Subtraction ◽  
Bifurcation Aneurysm ◽  
Intraoperative Rupture

Abstract OBJECTIVE Surgical treatment of an intracavernous carotid aneurysm (ICCA) is difficult because of the close relationship to bone, dura, and neurovascular structures. Intraoperative rupture of an ICCA is challenging, especially if the site of rupture is at the base of the aneurysm. We present a case of intraoperative rupture of an ICCA caused by clinoidectomy. We repaired it by using a single-clamp applicator (AnastoClip Vessel Closure System, 1.4 mm; LeMaitre Vascular, Burlington, MA). CLINICAL PRESENTATION In April 2007, a 40-year-old woman underwent neurosurgical treatment at another institution for a ruptured basilar bifurcation aneurysm, with good recovery. Digital subtraction angiography performed at this time showed the presence of left internal carotid artery aneurysms, 1 at the anterior wall of the paraclinoidal segment and 1 at the lateral wall of the intracavernous segment. In February 2008, the patient was referred from outside Finland to our department for microsurgical treatment of both aneurysms. TECHNIQUE A lateral supraorbital approach was used, and during extradural removal of the anterior clinoid with a rongeur, the ICCA ruptured. The base of the intracavernous aneurysm was involved in the rupture, and we used a single-clamp applicator to repair the internal carotid artery. Intraoperative digital subtraction angiography, indocyanine green video angiography, and Doppler ultrasonography showed a good flow in the artery. The paraclinoid aneurysm was uneventfully clipped during the same intervention. CONCLUSION Intraoperative rupture of ICCA was repaired quickly and effectively by using a single-clamp applicator. Our case and experimental data from other microsurgical vascular experiences suggest that the future of intracranial vessel repair/anastomoses will be using microclips and other simpler devices more, allowing the neurosurgeon to perform fast and effective vessel repair.

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