scholarly journals Audiological Manifestations in Kabuki (Niikawa-Kuroki) Syndrome

2011 ◽  
Vol 26 (1) ◽  
pp. 21-26
Author(s):  
Celina Ann M. Tobias ◽  
Teresa Luisa Gloria-Cruz ◽  
Charlotte M. Chiong
Keyword(s):  
Hearing Loss ◽  
Hearing Aids ◽  
Binaural Hearing ◽  
University Hospital ◽  
Kabuki Syndrome ◽  
Ear Diseases ◽  
Rare Malformation ◽  
The Right ◽  
Speech And Language Development ◽  
Binaural Hearing Aids

Objective: To describe the audiological profile, clinical features and briefly summarize the speech and language development of a child with Kabuki syndrome (KS). KS is a rare malformation syndrome that usually presents with mental retardation and multiple congenital anomalies including ear diseases and hearing loss.   Methods: Design: Case report Setting: Tertiary Public University Hospital Subject: One patient   Results: A five-year-old female diagnosed with KS at age three presented with moderate to severe conductive hearing loss in the right ear with a drop at the high frequencies and moderate to severe conductive sloping hearing loss in the left ear. She also had fluctuating tympanometric findings. She was fit with binaural hearing aids.   Conclusion: Ear diseases and hearing loss should immediately be considered in patients diagnosed with KS. A comprehensive audiological and otolaryngological evaluation should also be performed when presented with a KS case.   Keywords: Kabuki syndrome, Niikawa-Kuroki syndrome, hearing loss, multiple anomalies

Some Implications of Binaural Signal Selection for Hearing Aid Evaluation

1964 ◽  
Vol 7 (3) ◽  
pp. 279-289
Author(s):  
Allan J. Heffler ◽  
Martin C. Schultz
Keyword(s):  
Hearing Loss ◽  
Hearing Aids ◽  
Binaural Hearing ◽  
Normal Hearing ◽  
The Other ◽  
Auditory Training ◽  
Signal Selection ◽  
Long Duration ◽  
Selection For ◽  
Binaural Hearing Aids

Clinical techniques for evaluating binaural hearing aids have been inconclusive. This paper offers some explanations of shortcomings in present approaches, concentrating upon several characteristics to be included in an adequate clinical procedure. These are the presence of competing sound; S/N ratios permitting measurable increases in discrimination from advantageous listening conditions; elimination of localization and sidedness effects; and the requirement of long duration signals with credit for partial responses. The study was an approach on normal-hearing individuals under several S/N ratios, with occlusion of one ear as an experimental variable. Listening was accomplished under homophasic and antiphasic conditions for each combination of the other conditions. Results demonstrated significant differences among the listening conditions and the results have been rationalized in schema for testing binaural hearing aids under various hearing-loss circumstances. Applications to auditory training are discussed.

The acceptance of hearing aids for children with otitis media with effusion

1999 ◽  
Vol 113 (4) ◽  
pp. 314-317 ◽  
Author(s):  
A. H. Jardine ◽  
M. V. Griffiths ◽  
E. Midgley
Keyword(s):  
Otitis Media ◽  
Hearing Aids ◽  
Otitis Media With Effusion ◽  
Binaural Hearing ◽  
Long Term Effects ◽  
Non Invasive ◽  
Parents And Children ◽  
Binaural Hearing Aids

AbstractConservative treatment for otitis media with effusion (OME) led us to consider the use of hearing aids as a way of managing the associated hearing loss. This study aimed to assess the compliance of patients and acceptance of hearing aids for the management of children with OME.Thirty-nine children who had been given binaural hearing aids to manage OME were assessed at routine follow-up after six months. A clinician who did not prescribe the aid administered a questionnaire to assess compliance, change in symptoms and acceptance of the aids.Thirty-eight parents thought the aids were easy to use and 25 (66 per cent) were completely satisfied with the management. Aided hearing improved by a mean of 17 dB (Range 10–30) over three frequencies, 0.5, 1.0, 2.0 Khz and all parents reported subjective hearing improvement in their children. The stigma of an aid was reported as minimal under the age of seven.Hearing aids provide a non-invasive way of managing the problems associated with OME which is acceptable to certain parents and children. Long-term effects of using aids need to be evaluated before they can be recommended.

scholarly journals Beamforming under Quantization Errors in Wireless Binaural Hearing Aids

2008 ◽  
Vol 2008 ◽  
pp. 1-8 ◽  
Author(s):  
Sriram Srinivasan ◽  
Ashish Pandharipande ◽  
Kees Janse
Keyword(s):  
Hearing Aids ◽  
Binaural Hearing ◽  
Binaural Hearing Aids

Prevalence and classification of asymmetric forms of sensorineural hearing loss in older age group

2021 ◽  
Vol 20 (5) ◽  
pp. 8-12
Author(s):  
T. Yu. Vladimirova ◽  
◽  
A. B. Martynova ◽  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Hearing Aids ◽  
Hearing Threshold ◽  
Older Age ◽  
Sensorineural Hearing ◽  
Age Group ◽  
The Difference ◽  
The Right

The significance of asymmetric sensorineural hearing loss (ASNHL) is due to a special approach to diagnosis, followed by the process of hearing aids and auditory rehabilitation. Currently, there is no standard audiometric criterion for determining the forms of asymmetry, which significantly affects the assessment of the prevalence of ASNHL. The study aimed to assess the prevalence and classification of ASNHL forms in the older age group using two methods of calculation: 1) the difference in the average hearing threshold at speech frequencies (in the range of 0,5–4 kHz) ≥15 dB was detected in 14,14% of cases; 2) the different degree of hearing loss, according to the International classification, in the right and left ear was 35,98%. In most cases, asymmetry was manifested by bilateral sensorineural hearing loss of varying severity, prevailing in the group of long-livers – 82,6%. Given the potentially high prevalence of asymmetry depending on the audiological criterion, the results of the work are a reason for further research in the development of a unified method for verifying a clinically significant form of ASNHL.

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