Surgical Treatment for Severe Decompensated Neuromuscular Scoliosis in Patient with Spinal Muscular Atrophy type II

Treatment results for 16 years old patient with grade 4 thoracolumbar scoliosis on the background of Type II spinal muscular atrophy are presented. One step surgical treatment via dorsal approach was performed: posterior corrective two-rodtranspedicular corporal screw C7 - S1 fusion with fixationof iliac bones by transpedicular system with bone autoplasty + osteomatrix. Surgical intervention resulted in the formation of satisfactory trunk balance, reduction of pelvic distortion and improvement of the patient’s quality of life.

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Surgical Treatment for Severe Decompensated Neuromuscular Scoliosis in Patient with Spinal Muscular Atrophy type II

N.N. Priorov Journal of Traumatology and Orthopedics ◽

10.17816/vto201724173-76 ◽

2017 ◽

Vol 24 (1) ◽

pp. 73-76

Author(s):

A. N Baklanov ◽

A. N Shaboldin ◽

B. Yu Barchenko

Keyword(s):

Surgical Treatment ◽

Spinal Muscular Atrophy ◽

Surgical Intervention ◽

Muscular Atrophy ◽

Type Ii ◽

Dorsal Approach ◽

Spinal Muscular Atrophy Type ◽

One Step ◽

Trunk Balance

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Surgical Treatment of Severe Spine Deformity in Patients with Spinal Muscular Atrophy

N.N. Priorov Journal of Traumatology and Orthopedics ◽

10.17816/vto20130464-67 ◽

2013 ◽

Vol 20 (4) ◽

pp. 64-67

Author(s):

S. V Kolesov ◽

S. A Kudryakov ◽

I. A Shavyrin ◽

A. N Shaboldin

Keyword(s):

Surgical Treatment ◽

Spinal Muscular Atrophy ◽

Surgical Intervention ◽

Muscular Atrophy ◽

Second Step ◽

Spine Deformity ◽

Sitting Position ◽

Hybrid Fixation ◽

Trunk Balance ◽

Fixation System

Two-step surgical treatment was conducted in a 17 year old woman with extremely severe kyphoscoliotic deformity on the background of spinal muscular atrophy. At first step a ring of haloapparatus was assembled and gradual halotraction was performed in an armchair within 21 days. Second step included dorsal correction and stabilization of scoliosis by hybrid fixation system at Th3-L4 level with pelvis fixation. As a result of surgical intervention a proper trunk balance was formed, pelvic deformity was diminished, selfservice and use of wheelchair in a sitting position was improved.

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Spinal muscular atrophy type II (intermediary) and III (Kugelberg-Welander): evolution of 50 patients with physiotherapy and hydrotherapy in a swimming pool

Arquivos de Neuro-Psiquiatria ◽

10.1590/s0004-282x1996000300007 ◽

1996 ◽

Vol 54 (3) ◽

pp. 402-406 ◽

Cited By ~ 16

Author(s):

Márcia C. B. Cunha ◽

Acary S. B. Oliveira ◽

Rita Helena D. D. Labronici ◽

Alberto Alain Gabbai

Keyword(s):

Muscle Strength ◽

Spinal Muscular Atrophy ◽

Daily Living ◽

Muscular Atrophy ◽

Swimming Pool ◽

Type Ii ◽

Spinal Muscular Atrophy Type ◽

Type Iii ◽

Conventional Physiotherapy

We added hydrotherapy to 50 patients with spinal muscular atrophy (SMA) who were being treated with individual conventional physiotherapy. Hydrotherapy was performed at an approximate temperature of 30 degrees Celsius, twice a week, for thirty minutes in children and for forty-five minutes in adults during a 2-year period. The outcome derived from this combined modality of treatment was rated according to physiotherapeutic evaluations, the MMT (Manual Muscular Test), and the Barthel Ladder. Patients were reevaluated at 2-month intervals. After two years of ongoing treatment, we were able to observe that the deformities in hip, knee and foot were progressive in all SMA Type II patients, and in some Type III. Muscle strength stabilized in most SMA Type III patients, and improved in some. MMT was not done in SMA Type II. In all patients we were able to detect an improvement in the Barthel Ladder scale. This study suggests that a measurable improvement in the quality of daily living may be obtained in patients with SMA Types II and III subjected to conventional physiotherapy when associated with hydrotherapy.

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