scholarly journals Ebstein’s anomaly with constricitve pericarditis

2016 ◽  
Vol 31 (1) ◽  
pp. 46-49
Author(s):  
Apurba Thakur ◽  
Redoy Ranjan ◽  
Mohammad Samir Azam Sunny ◽  
Md Aftabuddin ◽  
Asit Baran Adhikary
Keyword(s):  
Tricuspid Valve ◽  
Life Science ◽  
Septal Defect ◽  
Symptomatic Improvement ◽  
Cardiac Malformation ◽  
Pericardial Disease ◽  
Direct Closure ◽  
Porcine Tissue ◽  
Congenital Cardiac Malformation

Ebstein’s anomaly is a rare congenital cardiac malformation that affects the tricuspid valve commonly, but its association with pericardial disease is even rarer. We report a case of 25 year old man presented with dyspnoea on exertion and fatigability. A diagnosis of Ebstein’s anomaly with atrial septal defect (ASD) with constrictive pericarditis was confirmed using transthoracic echocardiography. Peroperatively pericardiotomy was done after meticulous dissection of pericardium. Under cardiopulmonary bypass tricuspid valve was replaced with 29 mm Edward life science porcine tissue heart valve with direct closure of ASD. Patient showed excellent symptomatic improvement and was discharged on 7th POD with advice and after 3 months of follow up patient was doing well post operartive day.Bangladesh Heart Journal 2016; 31(1) : 46-49

scholarly journals Double-Outlet Right Ventricle in a Chianina Calf

Animals ◽  
2021 ◽  
Vol 11 (2) ◽  
pp. 318
Author(s):  
Domenico Caivano ◽  
Maria Chiara Marchesi ◽  
Piero Boni ◽  
Noemi Venanzi ◽  
Giovanni Angeli ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Septal Defect ◽  
Heart Defects ◽  
Double Outlet Right Ventricle ◽  
Cardiac Malformation ◽  
Septal Defects ◽  
Congenital Cardiac Malformation ◽  
The Right ◽  
Similar Complex ◽  
Echocardiographic Findings

Congenital heart defects have been occasionally reported in cattle and ventricular septal defect represents the most frequently encountered anomaly. The double-outlet right ventricle is a rare congenital ventriculoarterial malformation reported only in certain cattle breeds. We describe this rare and complex congenital cardiac malformation observed in a 10-day-old male Chianina calf. Clinical examination showed tachycardia, tachypnea, jugular pulses, cyanotic mucous membranes and a right apical systolic murmur. Transthoracic echocardiography revealed severe dilation of the right-sided cardiac chambers with a markedly hypoplastic left ventricle. Both aorta and pulmonary artery leaving the right ventricle in parallel alignment with the tricuspid valve were suggestive of a dual-outlet right ventricle. Interventricular and interatrial septal defects were also visualized. Post-mortem examination confirmed the echocardiographic findings. To the authors’ knowledge, a similar complex congenital cardiac malformation has not been reported in calves of the Chianina breed to date.

The current surgical perspective to repair of atrioventricular septal defect with common atrioventricular junction

2010 ◽  
Vol 20 (S3) ◽  
pp. 120-127 ◽  
Author(s):  
Tom R. Karl ◽  
Sylvio C. J. Provenzano ◽  
Graham R. Nunn ◽  
Robert H. Anderson
Keyword(s):  
Tetralogy Of Fallot ◽  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Indications For Surgery ◽  
Cardiac Malformation ◽  
Technical Aspects ◽  
Atrioventricular Junction ◽  
Congenital Cardiac Malformation ◽  
Surgery Timing

AbstractAtrioventricular septal defect with common atrioventricular junction is a relatively common congenital cardiac malformation. It sometimes presents challenging surgical problems, especially when seen in combination with tetralogy of Fallot. We describe herein our current concepts regarding surgical repair of atrioventricular septal defect with and without tetralogy, discussing indications for surgery, timing, technical aspects, and outcomes.

scholarly journals Tetralogy of Fallot with Scimitar syndrome in VACTERL: a very rare association

2017 ◽  
Vol 5 (1) ◽  
pp. 269
Author(s):  
Puneet Anand
Keyword(s):  
Congenital Anomaly ◽  
Tetralogy Of Fallot ◽  
Management Strategy ◽  
Septal Defect ◽  
Early Embryogenesis ◽  
Scimitar Syndrome ◽  
Cardiac Malformation ◽  
Rare Congenital Anomaly ◽  
Rare Association ◽  
Congenital Cardiac Malformation

The most common congenital cardiac malformation that occurs in VACTERL association is ventricular septal defect. Scimitar syndrome is a very rare congenital anomaly of the heart occurring due to maldevelopment of the lung bud or the pulmonary vascularization during early embryogenesis. The occurrence of Scimitar syndrome in VACTERL and its association with another cardiac congenital anomaly such as Tetralogy of Fallot (TOF) is extremely rare. The association of Tetralogy of Fallot with Scimitar syndrome alters the management strategy. Hereby, a very rare combination of Scimitar syndrome and tetralogy of Fallot in a four-year-old boy with VACTERL is presented, who underwent a successful single-stage surgical correction.

scholarly journals Surgical Management of a Case of Severe Coarctaton of Aorta with Biscuspic Aortic Valve

2018 ◽  
Vol 36 (1) ◽  
pp. 33-36
Author(s):  
Md Nazmul Hasan ◽  
Md Abu Siddique ◽  
Sajal Krishna Banerjee ◽  
Abu Sadique Abdullah
Keyword(s):  
Aortic Coarctation ◽  
Clinical Signs ◽  
Coarctation Of The Aorta ◽  
Cardiac Malformation ◽  
Exertional Dyspnea ◽  
Term Survival ◽  
Congenital Cardiac Malformation ◽  
Fourth Decade

Coarctation of the aorta is a congenital cardiac malformation that can go undiagnosed until old age with only hypertension as a marker of its presence because clinical signs can be subtle and overlooked if a complete physical exam is not performed. Long-term survival is exceptional in patients with untreated aortic coarctation. In this case report, we present a late diagnosis of aortic coarctation in a 45-year-old male. Our patient was relatively asymptomatic until he presented with exertional dyspnea and fatigue in his fourth decade of life. The patient was managed by surgery of aorta. After the 6 months follow-up visit, the patient was in good clinical condition.J Bangladesh Coll Phys Surg 2018; 36(1): 33-36

Aortopulmonary Window with Subaortic Fibrous Stenosis and Septal Defect: Surgery through a Minimal Right Vertical Infra-Axillary Thoracotomy

2011 ◽  
Vol 14 (4) ◽  
pp. 264 ◽  
Author(s):  
Jun Pan ◽  
Qing-Guo Li ◽  
Qing Zhou ◽  
Jie Zhang ◽  
Qiang Wang ◽  
...  
Keyword(s):  
Minimally Invasive Surgery ◽  
Cardiopulmonary Bypass ◽  
Ventricular Septal Defect ◽  
Minimally Invasive ◽  
Invasive Surgery ◽  
Septal Defect ◽  
Subaortic Stenosis ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window with subaortic stenosis and ventricular septal defect is an uncommon congenital cardiac malformation that is repaired using cardiopulmonary bypass. The authors describe a 3-year-old patient on whom we performed surgery through a minimal right vertical infra-axillary thoracotomy. This minimally invasive surgery is likely to be applicable in a few cases.

Temporary Tricuspid Valve Detachment for Ventricular Septal Defect Closure: Is It Worth Doing It?

2015 ◽  
Vol 16 (2) ◽  
pp. 99
Author(s):  
Alexander Weymann ◽  
Stanimir Georgiev ◽  
Carsten Vogelsang ◽  
Annette Ivad ◽  
Matthias Karck ◽  
...  
Keyword(s):  
Tricuspid Valve ◽  
Septal Defect ◽  
Control Group ◽  
Ventricular Septal Defects ◽  
Residual Shunt ◽  
Septal Defects ◽  
Ventricular Septal Defect Closure ◽  
Potential Risks ◽  
Valve Detachment

<p><b>Background:</b> Tricuspid valve detachment (TVD) may improve the access for closing certain ventricular septal defects (VSDs), but it has some potential risks. We aimed to study the benefits and drawbacks of this technique.</p><p><b>Methods:</b> The midterm outcomes of all 20 patients who underwent a TVD closure for VSD were reviewed and compared with a control group of 15 patients with VSD closure without TVD.</p><p><b>Results:</b> There was no significant residual shunt in either group at the last actuarial follow-up. Tricuspid regurgitation occurred in both groups (45% in the TVD group and 27% in the control group, <i>P</i> = .48). These lesions were considered insignificant in all patients. There were no atrioventricular blocks, and all patients were in sinus rhythm. The cardiopulmonary bypass times were significantly higher in the TVD group than in the control group (91.6 � 17.2 minutes versus 68.3 � 15.7 minutes, <i>P</i> ? .01), as were the aortic cross-clamping times (50.7 � 12.1 minutes versus 35.9 � 14.4 minutes, <i>P</i> ? .01).</p><p><b>Conclusion:</b> Our results, along with results from other series, suggest that TVD can be used effectively and safely for closure of certain VSDs.</p>

Prenatal diagnosis of isolated total anomalous systemic venous connection to the left atrium

2017 ◽  
Vol 27 (7) ◽  
pp. 1394-1397 ◽  
Author(s):  
Béatrice Miltner ◽  
Alain Jean Poncelet ◽  
Catherine Barrea
Keyword(s):  
Prenatal Diagnosis ◽  
Right Ventricular ◽  
Left Atrium ◽  
Venous Return ◽  
Cardiac Malformation ◽  
Caval Vein ◽  
Inferior Caval Vein ◽  
Congenital Cardiac Malformation

AbstractWe report the prenatal diagnosis and the neonatal follow-up of a patient with isolated total abnormal systemic venous connection to the left atrium. Right-sided and left-sided superior caval veins and the inferior caval vein were all connected to the left atrium. Pulmonary venous return was normal. This was associated with some right ventricular underdevelopment. To our knowledge, this is the first fetal description of this very rare congenital cardiac malformation.

scholarly journals Postpartum Deterioration of Hemodynamics in a Case of Uncorrected Ebstein's Anomaly

2012 ◽  
Vol 2012 ◽  
pp. 1-3
Author(s):  
Masato Kimura ◽  
Shuhei Kakizaki ◽  
Seiichi Tazawa ◽  
Osamu Adachi ◽  
Yoshikatsu Saiki ◽  
...  
Keyword(s):  
Cardiac Surgery ◽  
Right Ventricle ◽  
Tricuspid Valve ◽  
Postpartum Period ◽  
Ebstein’S Anomaly ◽  
Corrective Surgery ◽  
Cardiac Malformation ◽  
Successful Pregnancy ◽  
Ebstein's Anomaly ◽  
Congenital Cardiac Malformation

Ebstein's anomaly is a rare congenital cardiac malformation that is characterized by abnormalities of the tricuspid valve and right ventricle. Pregnancy is usually well tolerated unless cyanosis or arrhythmia develops. We report a case with Ebstein's anomaly, whose condition was asymptomatic before pregnancy but remarkably deteriorated down during the postpartum period, even though a successful pregnancy and cardiac surgery were achieved. Women with Ebstein's anomaly should be carefully assessed and may need to be advised to have corrective surgery prior to pregnancy even if they were asymptomatic.

Tricuspid valve detachment for ventricular septal defect closure in infants <5 kg: should we be hesitant?

2021 ◽  
Author(s):  
Jae Hong Lee ◽  
Sungkyu Cho ◽  
Jae Gun Kwak ◽  
Hye Won Kwon ◽  
Yujin Kwak ◽  
...  
Keyword(s):  
Ventricular Septal Defect ◽  
Clinical Outcomes ◽  
Tricuspid Valve ◽  
Septal Defect ◽  
Propensity Score Matching Analysis ◽  
All Cause Mortality ◽  
Ventricular Septal Defect Closure ◽  
Group D ◽  
Valve Detachment

Abstract OBJECTIVES We compared the clinical outcomes between tricuspid valve detachment (TVD) and non-TVD for ventricular septal defect (VSD) closure in infants &lt;5 kg. METHODS From January 2004 to April 2020, 462 infants &lt;5 kg with VSD without more complex intracardiac lesions and who had undergone VSD closure through the trans-atrial approach were enrolled. Propensity score-matching analysis was performed. Clinical outcomes were compared between the paired TVD group (group D) and paired non-TVD group (group N). RESULTS The median age and body weight at operation were 1.9 months [interquartile range(IQR), 1.4–2.5] and 4.2 kg (IQR, 3.7–4.6). The median follow-up duration was 83.4 months (IQR, 43.5–130.4). After matching, 44 pairs were extracted from each group. There were no significant differences in all-cause mortality (P = 0.176), reoperation (P = 0.172), postoperative morbidities, including residual VSD, aortic regurgitation, atrioventricular block and significant tricuspid regurgitation (TR) (P = 0.346) between group D and group N. However, group D showed significantly less TR progression during follow-up (P = 0.019). CONCLUSIONS In infants &lt;5 kg, TVD can be a reasonable and valid option for successful VSD closure without morbidities, including TR progression if the indication exists.

Surgical Strategy in Patients with Atrial Septal Defect and Severe Pulmonary Hypertension

2012 ◽  
Vol 15 (2) ◽  
pp. 111 ◽  
Author(s):  
Yang Hyun Cho ◽  
Tae-Gook Jun ◽  
Ji-Hyuk Yang ◽  
Pyo Won Park ◽  
June Huh ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Atrial Septal Defect ◽  
Tricuspid Regurgitation ◽  
Septal Defect ◽  
Maze Procedure ◽  
Severe Pulmonary Hypertension ◽  
Tricuspid Annuloplasty ◽  
Pulmonary Arterial ◽  
Asd Closure

The aim of the study was to review our experience with atrial septal defect (ASD) closure with a fenestrated patch in patients with severe pulmonary hypertension. Between July 2004 and February 2009, 16 patients with isolated ASD underwent closure with a fenestrated patch. All patients had a secundum type ASD and severe pulmonary hypertension. Patients ranged in age from 6 to 57 years (mean � SD, 34.9 � 13.5 years). The follow-up period was 9 to 59 months (mean, 34.5 � 13.1 months). The ranges of preoperative systolic and pulmonary arterial pressures were 63 to 119 mm Hg (mean, 83.8 � 13.9 mm Hg) and 37 to 77 mm Hg (mean, 51.1 � 10.1 mm Hg). The ranges of preoperative values for the ratio of the pulmonary flow to the systemic flow and for pulmonary arterial resistance were 1.1 to 2.7 (mean, 1.95 � 0.5) and 3.9 to 16.7 Wood units (mean, 9.8 � 2.9 Wood units), respectively. There was no early or late mortality. Tricuspid annuloplasty was performed in 14 patients (87.5%). The peak tricuspid regurgitation gradient and the ratio of the systolic pulmonary artery pressure to the systemic arterial pressure were decreased in all patients. The New York Heart Association class and the grade of tricuspid regurgitation were improved in 13 patients (81.2%) and 15 patients (93.7%), respectively. ASD closure in patients with severe pulmonary hypertension can be performed safely if we create fenestration. Tricuspid annuloplasty and a Cox maze procedure may improve the clinical result. Close observation and follow-up will be needed to validate the long-term benefits.

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