scholarly journals A Rare Case of Encephalotrigeminal Angiomatosis: A Case Report

2017 ◽  
Vol 7 (1) ◽  
pp. 13
Author(s):  
Lisa Elizabeth Jacob ◽  
Anuna Laila Mathew ◽  
Omal Pattali Mohanan ◽  
Thomas Abraham ◽  
Jerin Thomas ◽  
...  
Keyword(s):  
Case Report ◽  
Health Care Professionals ◽  
Rare Case ◽  
Dental Treatment ◽  
Disease Process ◽  
Adequate Knowledge ◽  
Weber Syndrome ◽  
Native Speakers Of English ◽  
Sturge Weber Syndrome ◽  
The Right

Aim: Sturge–Weber Syndrome, also known as encephalotrigeminal angiomatosis, is an uncommon, nonhereditary developmental anomaly. Methodology: A 48-year-old woman presented for routine dental treatment. She had a history of seizures and had a port wine stain on the right side of her face, which followed the distribution of the trigeminal nerve. Skull radiographs revealed “tram-track” calcifications. Conclusions: The early diagnosis of Sturge–Weber Syndrome requires a multidisciplinary approach. Oral health care professionals need adequate knowledge and understanding of the disease process to help diagnose and treat these patients.  How to cite this article: Jacob LE, Mathew AL, Omal PM, Abraham T, Thomas J, Varghese S. A Rare Case of Encephalotrigeminal Angiomatosis – A Case Report Int Dent Res 2017;7:13-6. Linguistic Revision: The English in this manuscript has been checked by at least two professional editors, both native speakers of English.

scholarly journals Bilateral Sturge Weber Syndrome- a rare case report

2013 ◽  
Vol 5 (1) ◽  
pp. 129-132 ◽  
Author(s):  
P Singh ◽  
S Singh
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Unusual Case ◽  
The Other ◽  
Advanced Stage ◽  
Weber Syndrome ◽  
Rare Case Report ◽  
The Face ◽  
Bilateral Condition ◽  
Sturge Weber Syndrome

Background: Sturge-Weber syndrome is a rare congenital neuro- oculo- cutaneous disorder. Objective: To report a very rare unusual case of bilateral manifestation of Sturge Weber syndrome. Case: We report an unusual case of a 17-year-old female with advanced stage of bilateral glaucoma associated with facial nevus extending to the other half of the face as well and bilateral intracranial calcification. Conclusion: Sturge -Weber syndrome can manifest as a bilateral condition. Nepal J Ophthalmol 2013; 5(9):129-132 DOI: http://dx.doi.org/10.3126/nepjoph.v5i1.7841

A Rare Case of Incidentally Detected Sturge-Weber Syndrome: a Case Report and Review of the Current Surgical Procedures

2019 ◽  
Vol 1 (9) ◽  
pp. 655-658
Author(s):  
Moawia Bushra Gameraddin ◽  
Kamal Dahan ◽  
Fathelrehman Alagab ◽  
Mariam Khojali
Keyword(s):  
Case Report ◽  
Surgical Procedures ◽  
Rare Case ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome

scholarly journals Sturge-Weber Syndrome– A Rare Case Report

2014 ◽  
Vol 13 (5) ◽  
pp. 39-41
Author(s):  
Divyank Pathak ◽  
◽  
Dhananjay.Y Shrikhande ◽  
Nilesh Maniya ◽  
Somdeepak Reddy ◽  
...  
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Weber Syndrome ◽  
Rare Case Report ◽  
Sturge Weber Syndrome

scholarly journals Management of Patient with Sturge-Weber Syndrome: a Case Report

2015 ◽  
Vol 9 (2) ◽  
pp. 102-104
Author(s):  
AKM Bazlul Karim ◽  
Mohammad Monirul Islam ◽  
Md Alamgir Hossain ◽  
Abu Md Shakurul Alam
Keyword(s):  
Case Report ◽  
Right Hemisphere ◽  
Resonance Imaging ◽  
Professional Counseling ◽  
Mentally Disabled ◽  
Weber Syndrome ◽  
The Face ◽  
Sturge Weber Syndrome ◽  
Slow Activity ◽  
The Right

Sturge-Weber syndrome sometimes referred to as encephalotrigeminal angiomatosis, is a rare congenital neurological and skin disorder. This is case report of 7 years old mentally disabled boy, with long-standing seizures, with a portwine nevi on the right side of the face along the distribution of trigeminal nerve. Interictal encephalogram showed bilateral slow activity, pronounced in the right hemisphere, with epileptogenic activity in the right fronto-parietal region. Computerized tomography and magnetic resonance imaging showed intracranial calcifications and atrophy of the right hemisphere of brain. Professional counseling and support in addition to drug treatment provide help to patients and their family to overcome their problems and improve the treatment outcome.Faridpur Med. Coll. J. 2014;9(2): 102-104

Popliteal nodal metastasis from squamous cell cancer of the foot. Case report and literature review

2019 ◽  
pp. 1-2
Keyword(s):  
Case Report ◽  
Lymph Node ◽  
Literature Review ◽  
Squamous Cell ◽  
Rare Case ◽  
Squamous Cell Cancer ◽  
Cell Cancer ◽  
Nodal Metastasis ◽  
Regional Disease ◽  
The Right

We report a very rare case of squamous cell cancer of the right foot which had metastasize to the ipsilateral popliteal lymph node after initial diagnosis and treatment for the loco-regional disease.

scholarly journals COVID-19-associated rhino-orbital mucormycosis (CAROM)—a case report

2021 ◽  
Vol 52 (1) ◽  
Author(s):  
Humsheer Singh Sethi ◽  
Kamal Kumar Sen ◽  
Sudhansu Sekhar Mohanty ◽  
Sangram Panda ◽  
Kolluru Radha Krishna ◽  
...  
Keyword(s):  
Case Report ◽  
Health Care Professionals ◽  
Opportunistic Infections ◽  
Fungal Spores ◽  
Nasal Discharge ◽  
Contributing Factors ◽  
Post Discharge ◽  
Pulmonary Mucormycosis ◽  
The Right

Abstract Background There has been a rapid rise in the number of COVID-19-associated rhino-orbital mucormycosis (CAROM) cases especially in South Asian countries, to an extent that it has been considered an epidemic among the COVID-19 patients in India. As of May 13, 2021, 101 CAROM cases have been reported, of which 82 cases were from India and 19 from the rest of the world. On the other hand, pulmonary mucormycosis associated with COVID-19 has a much lesser reported incidence of only 7% of the total COVID-19-associated mucormycosis cases (Singh AK, Singh R, Joshi SR, Misra A, Diab Metab Syndr: Clin Res Rev, 2021). This case report attempts to familiarize the health care professionals and radiologists with the imaging findings that should alarm for follow-up and treatment in the lines of CAROM. Case presentation Rhino-orbital mucormycosis (ROM) is a manifestation of mucormycosis that is thought to be acquired by inhalation of fungal spores into the paranasal sinuses. Here, we describe a 55-year-old male, post COVID-19 status with long standing diabetes who received steroids and ventilator therapy for the management of the viral infection. Post discharge from the COVID-19 isolation ICU, the patient complained of grayish discharge from the right nostril and was readmitted to the hospital for the nasal discharge. After thorough radiological and pathological investigation, the patient was diagnosed with CAROM and managed. Conclusion Uncontrolled diabetes and imprudent use of steroids are both contributing factors in the increased number of CAROM cases. Our report emphasizes on the radiological aspect of CAROM and reinforces the importance of follow-up imaging in post COVID-19 infection cases with a strong suspicion of opportunistic infections.

71. Sturge–Weber syndrome + cortical dysplasia. A dual pathology case report

2016 ◽  
Vol 127 (9) ◽  
pp. e319
Author(s):  
Areli Rosario Suarez-Roman ◽  
Enoe Cruz-Martinez ◽  
Yokary Amor Mellado-Ortiz ◽  
Ernesto Ramirez-Navarrete ◽  
Paul Shkurovich-Bialik
Keyword(s):  
Case Report ◽  
Cortical Dysplasia ◽  
Dual Pathology ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome

STURGE WEBER SYNDROME- A RARE CASE REPORT ORIGINAL

2021 ◽  
pp. 4-5
Author(s):  
Om Prakash Singh ◽  
Vikas Kumar ◽  
Pushp Kant Tiwari
Keyword(s):  
Rare Case ◽  
Signs And Symptoms ◽  
Port Wine ◽  
Occipital Area ◽  
Weber Syndrome ◽  
Rare Case Report ◽  
The Face ◽  
Sturge Weber Syndrome ◽  
The Brain ◽  
Embryonic Vessels

Sturge-Weber Syndrome (SWS) is one of the encephalotrigeminal angiomatosis and one of the important segmental vascular neurocutaneous disorders .The occurrence is not very uncommon and the prevalence is 1:20000 to 1:50000.(1) SWS occurs due to the presence of residual embryonic vessels . The various signs and symptoms include capillary malformation in the face a port wine birthmark and similar malformation in the brain involving leptomeniges as well as blood vessels of the eye causing glaucoma. The patient presents with seizures , hemiparesis and stroke like symptoms, headaches and developmental delay.(2) The imaging nding in SWS children is the calcication in the parietal and occipital area of the brain. The EEG ndings in SWS are the attenuation and the excess of slow activities.We are presenting here a rare case of , a fourteen year old male child who presented to our emergency department with status epilepticus. The aim of presenting this case is to share the classical presentation and the challenges involved in the management

Anesthesia for a Sturge-Weber Syndrome Patient with Severe Facial Hemangioma: A case report

2006 ◽  
Vol 51 (3) ◽  
pp. 371
Author(s):  
Kyu Don Chung ◽  
Youn Suk Son ◽  
Sang Hyun Hong ◽  
Hyun Sook Cho
Keyword(s):  
Case Report ◽  
Syndrome Patient ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome

scholarly journals Isolated leptomeningeal angiomatosis in the sixth decade of life, an adulthood variant of Sturge Weber Syndrome (Type III): role of advanced Magnetic Resonance Imaging and Digital Subtraction Angiography in diagnosis

BMC Neurology ◽  
2020 ◽  
Vol 20 (1) ◽  
Author(s):  
Vetrivel Muralidharan ◽  
Gaetano Failla ◽  
Mario Travali ◽  
Tiziana Liliana Cavallaro ◽  
Marco Angelo Politi
Keyword(s):  
Clinical Presentation ◽  
Subcortical White Matter ◽  
Digital Subtraction ◽  
Resonance Imaging ◽  
Radiological Findings ◽  
Hyperintense Signal ◽  
Right Cerebral Hemisphere ◽  
Weber Syndrome ◽  
Sturge Weber Syndrome ◽  
The Right

Abstract Background Sturge-Weber syndrome (SWS) is primarily diagnosed in pediatric population, but clinical presentation in late adulthood is rarely reported. Evolution of radiological findings in the adulthood variant of SWS with isolated leptomeningeal angiomatosis has never been reported to our knowledge. Case presentation We report here a case of an isolated temporo-parieto-occipital leptomeningeal angiomatosis on the right cerebral hemisphere in a sixty-two-year-old male who presented with generalized seizure, GCS score 14/15 (E4 V4 M6) with equal and reacting pupils, psychomotor slowing, left hemineglect and grade 4 power in the left upper and lower limbs. Over a period of 48 h his neurological status deteriorated, but recovered spontaneously over a week on titration with anticonvulsants. He had a prior history of treatment for focal leptomeningitis, three years ago. Cerebrospinal fluid (CSF) analysis showed glucose of 75 mg/dL, proteins of 65 mg/dL and culture grew no organisms. On follow-up, he had intermittent episodes of focal seizure for two years. Initial, computed tomography of brain showed hyperdense lesion in the parieto-occipital convexity subarachnoid space on the right cerebral hemisphere mimicking subarachnoid hemorrhage and computed tomography angiography showed no significant abnormality. Magnetic resonance imaging (MRI) of brain showed intense pial enhancement in the right temporo-parieto-occipital region with a subtle T2W hyperintense signal in the underlying subcortical white matter without edema or infarct or mass effect. Digital subtraction cerebral angiography (DSA) showed hypertrophy of the cerebral arteries, arteriolo-capillary bed and venules in the right temporo-parieto-occipital territory associated with early arterio-capillary and venous opacification. Serial MRI done after six months, one and two years showed increase in the T2W hyperintense signal in the subcortical white matter and cortical atrophy with no changes in the pial enhancement. MR perfusion imaging showed reduced cerebral blood flow (CBF) and cerebral blood volume (CBV) in the right parieto-temporo-occipital cortical and subcortical regions and increased perfusion in the leptomeninges with reduction of the NAA / Cr ratios in spectroscopy. Conclusion Conglomeration of various radiological findings in MRI, Perfusion, MRS and DSA with the clinical presentation can aid in establishing the diagnosis of this rare presentation of SWS-type 3 variant in late adulthood.

Sign in / Sign up

Export Citation Format

Share Document