Severe Valvular Pulmonary Stenosis and Bicuspid Pulmonary Valve

2015 ◽  
pp. 287-289
Author(s):  
Hakimeh Sadeghian ◽  
Zahra Savand-Roomi
Keyword(s):  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Valvular Pulmonary Stenosis

scholarly journals Case Presentation - Biventricular Hypertrophy and Valvular Pulmonary Stenosis in Adult Patient with Noonan Syndrome: A Rare Case

2021 ◽  
Vol 2 (2) ◽  
pp. 77
Author(s):  
Tinton Pristianto ◽  
Rosi Amrilla Fagi
Keyword(s):  
Noonan Syndrome ◽  
Pulmonary Valve ◽  
Genetic Disorder ◽  
Pulmonary Stenosis ◽  
Pulmonary Regurgitation ◽  
Nasolabial Fold ◽  
Pulmonary Valve Stenosis ◽  
Case Presentation ◽  
Valvular Pulmonary Stenosis ◽  
Chest Deformities

Introduction: Noonan syndrome (NS) is a genetic disorder often accompanied by multiple congenital abnormalities. The prevalence of NS at live birth has been reported as one in 1000-2500 individuals. About 80% of patients with Noonan syndrome have abnormalities in the cardiovascular system.Case presentation:41-year-old Javanese male presented with chief complaint shortness of breath.  His Body Mass Index (BMI) was 18,3. He had an oval-shaped face with a short neck, thin hair, and prominent nasolabial fold. Echocardiography showed biventricular hypertrophy alongside pulmonary valve stenosis, pulmonary regurgitation and minimal pericardial effusion. Discussion: In 1962, Jacqueline Noonan, a pediatric cardiologist, identified 9 patients whose faces were very similar, had short stature, significant chest deformities, and with pulmonary stenosis. Noonan syndrome is a relatively common non-chromosomal syndrome that is similar to the phenotype of Turner's syndrome and presents with cardiovascular malformations. Adult with NS has distinctive facial features such as ptosis, wide eyes, low posterior rotation of ears and helical thickening, and a wide neck.Pulmonary stenosis is the most common heartdefect found in NS, besides HCM isalsoquitecommon inabout20% of patients. We reported a case of a patient with typical characteristics of NS such as pulmonary valve stenosis accompanied by biventricular ventricular hypertrophyand its typical face who survived through adulthood.Conclusion: Syndrome Noonan in the adult is quite rare and difficult to diagnose. We reported a case of an adult man with facial appearance and echocardiographic findings identical with Noonan Syndrome.

Pulmonary Valve Cusp Augmentation for Pulmonary Regurgitation After Repair of Valvular Pulmonary Stenosis

2015 ◽  
Vol 99 (3) ◽  
pp. e57-e58 ◽  
Author(s):  
Yu Rim Shin ◽  
Han Ki Park ◽  
Young Hwan Park ◽  
Jo Won Jung ◽  
Young Jin Kim ◽  
...  
Keyword(s):  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Pulmonary Regurgitation ◽  
Valvular Pulmonary Stenosis

Experience with balloon pulmonary valvuloplasty and predictors of outcome: a ten-year study

2020 ◽  
Vol 30 (4) ◽  
pp. 482-488
Author(s):  
Sonia A. El-Saeidi ◽  
Hala S. Hamza ◽  
Hala M. Agha ◽  
Mohammed M. Soliman ◽  
Wael A. Attia ◽  
...  
Keyword(s):  
Pressure Gradient ◽  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Cross Sectional Study ◽  
P Value ◽  
Predictors Of Success ◽  
Post Intervention ◽  
Cross Sectional ◽  
Valvular Pulmonary Stenosis ◽  
A Minor

AbstractBackground:Balloon pulmonary valvuloplasty is the treatment of choice for patients with moderate to severe pulmonary valve stenosis.Methods:An observational retrospective cross-sectional study including neonates, small infants, and children who underwent balloon pulmonary valvuloplasty in the period from 2007 to 2016 in the cardiac catheterisation unit of the paediatric cardiology department in Cairo University. Multivariable models were built to report the predictors of the outcome of balloon pulmonary valvuloplasty and its complications.Results:A total of 1200 patients were included in the study and divided according to age into 3 groups: neonates and early infants (n = 282), infants (n = 362), and children (n = 556). Procedural success, defined as a drop pressure gradient across the pulmonary valve to less than or equal to 50% of the baseline measurements, was achieved in 82.7% of the patients. Multivariate analysis revealed that only infundibular pulmonary stenosis (p value 0.032), supravalvular in association with valvular pulmonary stenosis (p value <0.001), and pulmonary valve diameter by angiogram (p value <0.001) were significant predictors of success. The presence of supravalvular in association with valvular pulmonary stenosis (p value <0.001) was associated with a lower weight (p value 0.007) and higher right ventricular pressure before the intervention (p value <0.001), and a minor immediate drop in the pressure gradient post-intervention (p value <0.001) was found to be the most significant predictor of the occurrence of complications.Conclusion:The absence of infundibular and supravalvular stenosis and a large pulmonary valve diameter were the most significant predictors of success.

scholarly journals Balloon Pulmonary Valvuloplasty in patients with Congenital Valvular Pulmonary Stenosis

2013 ◽  
Vol 9 (1) ◽  
pp. 7-9 ◽  
Author(s):  
R Sharma ◽  
R Rajbhandari ◽  
Y Limbu ◽  
S Singh ◽  
YKD Bhatt ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Pressure Gradient ◽  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Systolic Pressure ◽  
Major Complication ◽  
Before And After ◽  
Single Balloon ◽  
Valvular Pulmonary Stenosis ◽  
Systolic Pressure Gradient

Background Congenital valvular pulmonary stenosis (PS) accounts for most of the etiology of PS, and constitutes about 5 to 10% of all congenital heart disease. Balloon Pulmonary Valvuloplasty has become the choice of treatment for valvular PS since the first series reported by Kan et al in 19824 and has almost replaced surgical valvotomy in pediatric patients. The purpose of this study was to investigate the immediate results of balloon valvuloplasty in patients with congenital valvular pulmonary stenosis. Method We analyzed hemodynamic data of 122 patients who underwent balloon pulmonary valvuloplasty (ages14days- 50 years mean 25 years). Single-balloon technique was used. Right ventricle systolic pressure and pulmonary valve Peak-to-peak systolic pressure gradient were recorded before and after balloon dilatation of pulmonary valve. Result Right ventricle systolic pressure decreased from 128±44.9 to 60±24.9 mmHg (p <0.001) and pulmonary valve peak-to-peak systolic pressure gradient decreased from 89±38.6 to 45 ± 22.4 mmHg (p <0.001). No major complication or mortality was noted. Conclusion Balloon pulmonary valvuloplasty is a safe and effective treatment for patients with congenital valvular PS. DOI: http://dx.doi.org/10.3126/njh.v9i1.8340 Nepalese Heart Journal Vol.9(1) 2012 pp.7-9ca

Pulmonary valve cusp augmentation for pulmonary regurgitation after percutaneous balloon pulmonary valvuloplasty of valvular pulmonary stenosis

2018 ◽  
Vol 28 (3) ◽  
pp. 507-510 ◽  
Author(s):  
Irfan Tasoglu ◽  
Atakan Atalay ◽  
Omer Nuri Aksoy ◽  
Vural Polat
Keyword(s):  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Pulmonary Regurgitation ◽  
Anterior Leaflet ◽  
Surgical Operation ◽  
Percutaneous Balloon ◽  
Expansion Technique ◽  
Valvular Stenosis ◽  
Valvular Pulmonary Stenosis ◽  
Polytetrafluoroethylene Patch

AbstractPulmonary valvular stenosis is a relatively common disorder, accounting for approximately 10% of all CHDs. Pulmonic valvular disease can get clinically detected at different ages of life. The more severe the obstruction, the earlier detected the valvular abnormality. Surgical pulmonary valvotomy has been available as a treatment since 1956. This article is about a case of pulmonary annular and valvular stenosis in a 1-year-old child, and it also explores surgical operation of this condition. Transannular patches are usually used within the 1st year of age in pulmonary annular and valvular stenosis. In recent years, anterior leaflet augmentation has been preferred for annulus enlargements. In our 1-year-old case, we expanded the annulus by the anterior leaflet expansion technique and we also augmented other leaflets by polytetrafluoroethylene patch.

scholarly journals Dysplastic pulmonary valve stenosis associated with unilateral absent first metacarpal: A rare association

2017 ◽  
Vol 5 ◽  
pp. 2050313X1772694 ◽  
Author(s):  
Ashwin Kodliwadmath
Keyword(s):  
Pulmonary Valve ◽  
Past History ◽  
Nyha Class ◽  
Pulmonary Stenosis ◽  
Pulmonary Valve Stenosis ◽  
Class 1 ◽  
Common Variety ◽  
Valvular Pulmonary Stenosis ◽  
Dysplastic Pulmonary Valve ◽  
Hand Anomalies

Context: Dysplastic pulmonary valve stenosis is a less common variety of valvular pulmonary stenosis. It is known to be part of Noonan syndrome. Bony hand anomalies in patients of pulmonary stenosis are very rare. Case report: A 50-year-old lady, with no significant past history, presented with slowly progressive breathlessness and fatigue, and had progressed from NYHA class 1 to 2 over 2 years. She had unilateral absent first metacarpal and diagnosed on workup to have dysplastic pulmonary valve stenosis and was treated with balloon valvuloplasty. Conclusion: Dysplastic pulmonary valve stenosis can rarely be associated with bony hand anomalies like absent first metacarpal.

Echocardiographic patterns of pulmonary valve motion in valvular pulmonary stenosis

1974 ◽  
Vol 34 (6) ◽  
pp. 644-651 ◽  
Author(s):  
Arthur E. Weyman ◽  
James C. Dillon ◽  
Harvey Feigenbaum ◽  
Sonia Chang
Keyword(s):  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Valve Motion ◽  
Valvular Pulmonary Stenosis

scholarly journals Mid- to long-term follow-up of pulmonary valve replacement with BioIntegral injectable valve

2020 ◽  
Author(s):  
Simone Ghiselli ◽  
Cristina Carro ◽  
Nicola Uricchio ◽  
Giuseppe Annoni ◽  
Stefano M Marianeschi
Keyword(s):  
Cardiopulmonary Bypass ◽  
Right Ventricular ◽  
Tetralogy Of Fallot ◽  
Valve Replacement ◽  
Pulmonary Valve ◽  
Pulmonary Stenosis ◽  
Pulmonary Regurgitation ◽  
Pulmonary Valve Replacement

Abstract OBJECTIVES Chronic pulmonary valve (PV) regurgitation is a common late sequela after repair of congenital heart diseases like tetralogy of Fallot or pulmonary stenosis, leading to right ventricular dilatation and failure and increased late morbidity and mortality. Timely reoperation may lead to a complete right ventricular recovery. An injectable PV allows pulmonary valve replacement, with or without cardiopulmonary bypass, under direct observation, thereby minimizing the impact of surgery on cardiac function. The aim of this study was to evaluate the feasibility and mid- to long-term clinical outcomes with this device. METHODS From April 2007 to October 2019, a total of 85 symptomatic patients with severe pulmonary regurgitation or pulmonary stenosis underwent pulmonary valve replacement with an injectable stented pulmonary prosthesis. Data were collected from the international proctoring registry. Mean patient age was 26.7 years. The underlying diagnosis was repaired tetralogy of Fallot in 69.4% patients; moderate or severe pulmonary regurgitation was present in 72.9%. All patients had echocardiographic scans before the operation and during the follow-up period. A total of 54.1% patients also had preoperative/postoperative cardiac magnetic resonance imaging (MRI) or catheterization; 25.9% had off-pump implants. In 53% patients, pulmonary valve replacement was associated with the repair of other cardiac defects. RESULTS Minor postoperative complications were observed in 10.8% patients. The overall mortality rate was 2.3%; mortality after valve replacement was linked to a severe cardiac insufficiency and it was not related to a prosthesis failure; 1 prosthesis was explanted from 1 patient because of endocarditis, and 6% of patients developed PV stenosis; minor complications occurred in 4.8%. The mean follow-up period was 4.8 years (2 months–12.7 years); 42% of the patients were followed for more than 5 years. Follow-up echocardiography and cardiac MRI showed a significant reduction in RV size and low gradients across the PV. CONCLUSIONS An injectable PV may be implanted without cardiopulmonary bypass and in a hybrid operating theatre with minimal surgical impact. The bioprosthesis, available up to large sizes, has a low profile, laminar flow and no risk of coronary artery compression. Incidence of endocarditis is rare. The lack of a suture ring permits the implant of a relatively larger prosthesis, thereby avoiding a right ventricular outflow tract obstruction. This device permits future percutaneous valve-in-valve procedures, if needed. Results concerning durability are encouraging, and mid- to long-term haemodynamic performance is excellent.

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