Sodium citrate supplementation in inborn argininosuccinate lyase deficiency: A study in a 5-year-old patient under total parenteral nutrition

1995 ◽  
Vol 154 (11) ◽  
pp. 909-914 ◽  
Author(s):  
C. Renner ◽  
A. C. Sewell ◽  
K. Bervoets ◽  
H. Förster ◽  
H. Böhles
Keyword(s):  
Parenteral Nutrition ◽  
Total Parenteral Nutrition ◽  
Sodium Citrate ◽  
Argininosuccinate Lyase ◽  
Lyase Deficiency

Total parenteral nutrition changes intestinal ion transport and increases epithelial permeability in a mouse model

2001 ◽  
Vol 120 (5) ◽  
pp. A675-A675
Author(s):  
H YANG ◽  
F ROBERT ◽  
Y FAN ◽  
D TEITELBAUM
Keyword(s):  
Mouse Model ◽  
Parenteral Nutrition ◽  
Ion Transport ◽  
Total Parenteral Nutrition ◽  
Epithelial Permeability ◽  
Intestinal Ion Transport

Abstract #916 Total Parenteral Nutrition (TPN) Interferences with Testosterone Assay

2018 ◽  
Vol 24 ◽  
pp. 215-216
Author(s):  
Tariq Alrasheed ◽  
Gaurav Bhalla ◽  
Naveen Kakumanu ◽  
George Hebdon ◽  
Saleh Aldasouqi
Keyword(s):  
Parenteral Nutrition ◽  
Total Parenteral Nutrition

Planning Total Parenteral Nutrition

1983 ◽  
Vol 1 (3) ◽  
pp. 633-646
Author(s):  
Wiley W. Souba ◽  
Douglas W. Wilmore
Keyword(s):  
Parenteral Nutrition ◽  
Total Parenteral Nutrition

scholarly journals Clinical improvement of encapsulating peritoneal sclerosis after challenging course and 6 months of total parenteral nutrition in child with nephronophthisis: a case report

2021 ◽  
Vol 15 (1) ◽  
Author(s):  
Saeed Mohammed AlZabali ◽  
Abdulkarim AlAnazi ◽  
Khawla A. Rahim ◽  
Hassan Y. Faqeehi
Keyword(s):  
Peritoneal Dialysis ◽  
Parenteral Nutrition ◽  
Total Parenteral Nutrition ◽  
Bowel Perforation ◽  
Clinical Signs ◽  
Oral Intake ◽  
Pediatric Intensive Care ◽  
Abdominal Ultrasound ◽  
Peritoneal Dialysis Catheter ◽  
Refractory Peritonitis

Abstract Background Encapsulating peritoneal sclerosis is a rare but potentially lethal complication of long-term peritoneal dialysis that is associated with significant morbidity and mortality. The occurrence of encapsulating peritoneal sclerosis varies worldwide, but is increased in patients maintained on peritoneal dialysis for 5–8 years. The etiology of encapsulating peritoneal sclerosis remains unidentified, and a high index of clinical suspicion is required for diagnosis. Case presentation We report a 5-year-old Saudi female with end-stage renal disease secondary to nephronophthisis type 2. She underwent peritoneal dialysis for 30 months, with four episodes of peritonitis. She presented with clinical signs of peritonitis. Three days later, she developed septic shock, which required pediatric intensive care unit admission. The peritoneal dialysis catheter was removed because of refractory peritonitis. Her course was complicated by small bowel perforation, and severe adhesions were revealed on abdominal ultrasound and computed tomography, consistent with a diagnosis of EPS. This finding was later confirmed by diagnostic laparotomy performed twice and complicated by recurrent abdominal wall fistula. She received total parenteral nutrition for 6 months and several courses of antibiotics. The patient received supportive treatment including nutritional optimization and treatment for infection. No other treatments, such as immunosuppression, were administered to avoid risk of infection. Following a complicated hospital course, the patient restarted oral intake after 6 months of total parenteral nutrition dependency. Her abdominal fistula resolved completely, and she was maintained on hemodialysis for few years before she received a kidney transplant. Conclusion When treating patients using peritoneal dialysis, it is important to consider encapsulating peritoneal sclerosis with refractory peritonitis, which is not always easy to identify, particularly if the patient has been maintained on peritoneal dialysis for less than 3 years. Early identification of encapsulating peritoneal sclerosis and appropriate conservative treatment, including nutritional optimization and treatment of infections, are essential to achieve a better prognosis.

Sign in / Sign up

Export Citation Format

Share Document