Resting energy expenditure in Gaucher's disease type 1: Effect of Gaucher's cell burden on energy requirements

Metabolism ◽  
1989 ◽  
Vol 38 (12) ◽  
pp. 1238-1243 ◽  
Author(s):  
Donald J. Barton ◽  
Mark D. Ludman ◽  
Keith Benkov ◽  
Gregory A. Grabowski ◽  
Neal S. LeLeiko
1986 ◽  
Vol 147 (5) ◽  
pp. 943-948 ◽  
Author(s):  
G Hermann ◽  
J Goldblatt ◽  
RN Levy ◽  
SJ Goldsmith ◽  
RJ Desnick ◽  
...  

2009 ◽  
Vol 24 (10) ◽  
pp. 1524-1530 ◽  
Author(s):  
Ichraf Kraoua ◽  
Jérôme Stirnemann ◽  
Maria João Ribeiro ◽  
Tiphaine Rouaud ◽  
Marc Verin ◽  
...  

2004 ◽  
Vol 65 (3) ◽  
pp. 124-130 ◽  
Author(s):  
S. Eileen Hogan

Energy requirements of children and adolescents with cerebral palsy appear to be disease-specific and different from the current recommendations for healthy children, varying depending upon functional capacity, degree of mobility, severity of disease, and level of altered metabolism. Feeding problems are prevalent in many of these children, and can result in inadequate energy intake. Wasting of voluntary muscles, a common symptom of cerebral palsy, contributes to reduced resting energy needs; nevertheless, the location of the central nervous system lesion may also influence energy requirements. To guarantee individualized, accurate, and optimal energy recommendations for this population, resting energy expenditure should preferentially be measured by indirect calorimetry. Equations and formulae to predict healthy people's resting energy expenditure are available, but tend to overestimate these children's energy needs. Future studies should address the role of the central nervous system in regulating energy metabolism in this population. When adequately nourished, children and adolescents with cerebral palsy appear more tranquil and require decreased feeding time, which gives caregivers time to develop the child's functional independence and character. Understanding energy requirements of this population will provide caregivers and health professionals with guidelines for providing optimal nutritional status.


The Lancet ◽  
2015 ◽  
Vol 385 (9985) ◽  
pp. 2355-2362 ◽  
Author(s):  
Timothy M Cox ◽  
Guillermo Drelichman ◽  
Renata Cravo ◽  
Manisha Balwani ◽  
Thomas Andrew Burrow ◽  
...  

2007 ◽  
Vol 103 (5) ◽  
pp. 1543-1550 ◽  
Author(s):  
Steven B. Heymsfield ◽  
Douglas Childers ◽  
Joel Beetsch ◽  
David B. Allison ◽  
Angelo Pietrobelli

Two observations favor the presence of a lower mass-specific resting energy expenditure (REE/weight) in taller adult humans: an earlier report of height (H)-related differences in relative body composition; and a combined model based on Quetelet and Kleiber's classic equations suggesting that REE/weight∝H−0.5. This study tested the hypothesis stating that mass-specific REE scales negatively to height with a secondary aim exploration of related associations between height, weight (W), surface area (SA), and REE. Two independent data sets ( n = 344 and 884) were evaluated, both with REE measured by indirect calorimetry and the smaller of the two including fat estimates by dual-energy X-ray absorptiometry. Results support Quetelet's equation (W∝H2), but Kleiber's equation approached the interspecific mammal form (REE∝W0.75) only after adding adiposity measures to weight and age as REE predictors. REE/weight scaled as H∼(−0.5) in support of the hypothesis with P values ranging from 0.17 to <0.001. REE and SA both scaled as H∼1.5, and REE/SA was nonsignificantly correlated with height in all groups. These observations suggest that adiposity needs to be considered when evaluating the intraspecific scaling of REE to weight; that relative to their weight, taller subjects require a lower energy intake for replacing resting heat losses than shorter subjects; that fasting endurance, approximated as fat mass/REE, increases as H0.5; and that thermal balance is maintained independent of stature by evident stable associations between resting heat production and capacity of external heat release. These observations have implications for the modeling of adult human energy requirements and associate with anthropological concepts founded on body size.


2018 ◽  
Vol 7 (4) ◽  
pp. 171 ◽  
Author(s):  
Majid Davari ◽  
Azita Nabizadeh ◽  
Bahman Amani ◽  
Maliheh Kadivar ◽  
Mahdi Toroski ◽  
...  

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