Anterior mediastinal solitary fibrous tumor resection by da Vinci ® Surgical System in obese patient

Solitary fibrous tumor of pleura (SFTP) is a rare tumor. Complete tumor resection is the curative treatment and the key to preventing recurrence. We present here the case of a 65-year-old female diagnosed with a Doege-Potter syndrome who underwent resection of pleural solitary fibrous tumor.

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Pediatric sellar solitary fibrous tumor/ hemangiopericytoma: A rare case report and review of the literature

Surgical Neurology International ◽

10.25259/sni_234_2020 ◽

2020 ◽

Vol 11 ◽

pp. 238

Author(s):

Hammad Ghanchi ◽

Tye Patchana ◽

Eisha Christian ◽

Chao Li ◽

Mark Calayag

Keyword(s):

Solitary Fibrous Tumor ◽

Vision Loss ◽

Adult Population ◽

Tumor Resection ◽

The Body ◽

Subtotal Resection ◽

Adjuvant Radiation ◽

Sellar Region ◽

First Case ◽

Fibrous Tumor

Background: Solitary fibrous tumor (SFT)/hemangiopericytoma (HPC) is a rare tumor which originates from the walls of capillaries and has historically been thought to be able to occur anywhere in the body that blood vessels are found. It is rarely found in the sellar region. Case Description: InS this report, we present the first case of this tumor occurring in the sellar region of a pediatric patient. This 12-year-old male presented with progressive vision loss which prompted surgical resection after a sellar lesion was discovered on imaging. The initial transsphenoidal approach resulted in subtotal resection and the patient experienced reoccurrence within 3 months. He underwent an orbitozygomatic craniotomy to achieve gross total tumor resection. Conclusion: We conducted a literature review of intracranial SFT/HPC in the pediatric population and found it to be an extremely rare occurrence, with <30 cases reported. The incidence of SFT/HPC occurring in the sellar region for any age group was also found to be a rare entity. Treatment recommendations for this tumor are also scarce, based on retrospective chart reviews from the adult population. The role for adjuvant radiation has mixed results.

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Transtemporal Suprajugular Approach with Neck Dissection for Jugular Foramen Tumor Resection: Operative Video

Journal of Neurological Surgery Part B Skull Base ◽

10.1055/s-0040-1701680 ◽

2020 ◽

Author(s):

Christina E. Sarris ◽

Shawn M. Stevens ◽

Kaith K. Almefty

Keyword(s):

Neck Dissection ◽

Solitary Fibrous Tumor ◽

Initial Period ◽

Tumor Resection ◽

Jugular Foramen ◽

World Health ◽

Cervical Region ◽

Retropharyngeal Space ◽

Radiographic Findings ◽

Fibrous Tumor

AbstractThis video demonstrates the transmastoid suprajugular approach with neck dissection to a solitary fibrous tumor involving the jugular foramen and upper cervical region. This patient was a 39-year-old man who presented with dysphagia and cranial nerve (CN) XI and CN XII palsies. Imaging revealed a large homogenously enhancing lesion involving the jugular foramen and extending into the retropharyngeal space (Fig. 1). Radiographic findings supported a diagnosis of jugular foramen schwannoma. After an initial period of observation, the tumor demonstrated significant growth, and the patient agreed to proceed with surgery. The suprajugular approach allowed for exposure and resection of the tumor without mobilization of the facial nerve. The patient had an excellent clinical outcome with House–Brackmann grade-1 facial function, safely tolerated a regular diet, had intact CN XI function, and had a stable CN XII palsy (Fig. 2). Pathology findings identified the tumor as a hemangiopericytoma World Health Organization grade 1 (solitary fibrous tumor).The link to the video can be found at: https://youtu.be/C4sPyHcLMA0.

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Solitary fibrous tumor of the pleura as a rare cause of severe hypoglycemia: Doege-Potter syndrome

Perspectives in Surgery ◽

10.33699/pis.2020.99.2.95-98 ◽

2020 ◽

Vol 99 (2) ◽

pp. 95-98

Keyword(s):

Case Report ◽

Growth Factor ◽

Solitary Fibrous Tumor ◽

Tumor Resection ◽

Insulin Like Growth Factor ◽

En Bloc ◽

Solitary Fibrous Tumors ◽

Factor Ii ◽

Fibrous Tumor ◽

Recurrent Hypoglycemia

Introduction: Doege-Potter syndrome is a rare syndrome characterized by hypo-insulinemic hypoglycemia. It is caused by excessive ectopic secretion of insulin-like growth factor II from a solitary fibrous tumors of intrapleural or extrapleural origin. Laboratory tests reveal low levels of C-peptide and insulin, on the contrary insulin-like growth factor II level is elevated, which is characteristic for Doege-Potter syndrome. Majority of solitary fibrous tumors present no symptomatology, recurrent hypoglycemia is relatively rare, but it may be the only clinical manifestation. The therapy is surgical, consisting of radical en-bloc tumor resection. Case report: Authors present a case report of a patient with recurrent hypoglycemia caused solely by solitary fibrous tumor. Hypoglycemia resolved immediately after surgical resection and there were no recurrences. Conclusion: Doege-Potter syndrome should be considered as the differential diagnosis in a patient with suspicion on thoracic malignancy if accompanied by features suggestive of hypoglycemia. Prolonged follow up is strongly advised because of the risk of disease recurrence, even in patients with benign solitary fibrous tumors of the pleura (SFTP).

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Intracranial solitary fibrous tumor/hemangiopericytoma – A case series

Surgical Neurology International ◽

10.25259/sni_490_2020 ◽

2020 ◽

Vol 11 ◽

pp. 414

Author(s):

Chi-Man Yip ◽

Shu-Shong Hsu ◽

Wei-Chuan Liao ◽

Szu-Hao Liu ◽

Yung-Shang Lin ◽

...

Keyword(s):

Solitary Fibrous Tumor ◽

Adjuvant Radiotherapy ◽

Tumor Resection ◽

Case Series ◽

Extent Of Resection ◽

Treatment Modalities ◽

Total Resection ◽

Initial Surgery ◽

Fibrous Tumor

Background: Intracranial solitary fibrous tumor/hemangiopericytoma (HPC) is a rare and aggressive tumor. We conducted this retrospective study to investigate the outcome of patients after treatment, the efficacy of postoperative adjuvant radiotherapy, and the factors not conducive to total resection. Methods: We conducted a retrospective review of the medical records of patients harboring fresh intracranial solitary fibrous tumor/HPC treated from January 2009 to December 2019 in our hospital. We reviewed their clinical presentations, radiologic appearances, tumor size and location, extent of resection, estimate intraoperative blood loss, treatment modalities and results, and duration of follow-up. Results: There were seven consecutive patients (three males and four females). The ages of the patients at the time of diagnosis ranged from 35 to 77 years (mean: 52.86 years). Five patients (71.43%) got tumor bigger than 5 cm in dimension and only 1 patient (14.29%) underwent gross total tumor resection in the first operation without complication. Five patients (71.43%) underwent postoperative adjuvant radiotherapy. Follow-up period ranged from 4.24 to 123.55 months and the median follow-up period was 91.36 months. Three patients had favorable outcome with Glasgow Outcome Scale (GOS) equal to 4; four patients had unfavorable outcome with GOS equal to 2 or 3. No mortality was happened. Conclusion: Gross total tumor resection in the initial surgery is very important to achieve a better outcome. Massive intraoperative bleeding and venous sinus or major vessels adjoining are factors not conducive to total resection. Radiotherapy can be administered as adjuvant therapy for cases showing an aggressive phenotype or not treated with gross total resection.

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Transsphincteric tumor resection in case of a pararectal solitary fibrous tumor

International Journal of Surgery Case Reports ◽

10.1016/j.ijscr.2015.12.027 ◽

2016 ◽

Vol 19 ◽

pp. 159-162

Author(s):

Achim Troja ◽

Nader El-Sourani ◽

Dalibor Antolovic ◽

Hans Rudolf Raab

Keyword(s):

Solitary Fibrous Tumor ◽

Tumor Resection ◽

Fibrous Tumor

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Recurrence of a malignant solitary fibrous tumor of the pleura 17 years after primary tumor resection – A case report

Respiratory Medicine Case Reports ◽

10.1016/j.rmcr.2019.100895 ◽

2019 ◽

Vol 28 ◽

pp. 100895

Author(s):

Tamas Kovacs ◽

Jonathan Waxman

Keyword(s):

Case Report ◽

Solitary Fibrous Tumor ◽

Primary Tumor ◽

Tumor Resection ◽

Primary Tumor Resection ◽

Fibrous Tumor

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Solitary fibrous tumor of the pleura with Doege–Potter syndrome: Second recurrence in a 93-year-old female

SAGE Open Medical Case Reports ◽

10.1177/2050313x18823468 ◽

2019 ◽

Vol 7 ◽

pp. 2050313X1882346 ◽

Cited By ~ 2

Author(s):

Céline Forster ◽

Aurélien Roumy ◽

Michel Gonzalez

Keyword(s):

Solitary Fibrous Tumor ◽

Tumor Resection ◽

Mesenchymal Tumors ◽

Complete Tumor Resection ◽

High Molecular Weight Form ◽

Solitary Fibrous Tumors ◽

Factor Ii ◽

Fibrous Tumor ◽

Molecular Weight Form ◽

Complete Tumor

Solitary fibrous tumors are rare mesenchymal tumors most commonly arising from the pleura. When associated with paraneoplastic syndrome of hypoglycemia caused by the secretion of a high-molecular-weight form of insulin-like growth factor II, it is referred to as the Doege–Potter syndrome. Surgery with complete tumor resection is the only curative treatment. We present here the case of a 93-year-old female diagnosed with a Doege–Potter syndrome who underwent three repetitive surgical resections of recurrent solitary fibrous tumor.

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Doege–Potter Syndrome and Hypoglycemia associated with Solitary Fibrous Tumor of the Pleura: Two Case Reports

Clinical Medicine Insights Circulatory Respiratory and Pulmonary Medicine ◽

10.1177/1179548420964759 ◽

2020 ◽

Vol 14 ◽

pp. 117954842096475

Author(s):

Liliana Fernández-Trujillo ◽

Jhon E Bolaños ◽

Carolina Álvarez ◽

Julián Giraldo ◽

Mauricio Velásquez ◽

...

Keyword(s):

Growth Factor ◽

Solitary Fibrous Tumor ◽

Incidental Finding ◽

Case Reports ◽

Tumor Resection ◽

Insulin Like Growth Factor ◽

Solitary Fibrous Tumors ◽

Mesenchymal Neoplasms ◽

Single Mass ◽

Fibrous Tumor

Solitary fibrous tumors of the pleura (SFTP) are rare mesenchymal neoplasms that originate from mesenchymal growth in the pleura, tend to be single tumors, usually have an indolent course and show nonspecific symptoms. SFTP can be often diagnosed from an incidental finding of a single mass in the thorax and should be confirmed by biopsy and immunohistochemistry. A minority of cases may present Doege–Potter syndrome (DPS, episodes of refractory hypoglycemia) associated with production of insulin-like growth factor 2 (IGF-2). Both SFTP and DPS are rare occurrences with less than 2000 cases reported worldwide. The curative treatment is tumor resection. Two cases of patients with DPS caused by SFTP are presented below.

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