Congenital bifid origin of right coronary artery co-existing with congenital right coronary to right ventricular fistula

1997 ◽  
Vol 7 (3) ◽  
pp. 325-327
Author(s):  
Samuel Ramirez-Marroquin ◽  
Alfredo Santibañez-Salgado ◽  
Juan Calderon-Colmenero

AbstractAnomalous origin of the coronary arteries is a well-known phenomenon, but is less well reported in world literature. We present our findings in a one year old boy in whom there was bifid, or “y”, origin of the right coronary artery, co-existing with a fistula from the right coronary artery which opened into the right ventricle.

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
S Padmanabhan

Abstract OnBehalf Cornwall A term neonate with poor condition at birth was noted to be markedly bradycardic when crying. ECG showed first degree heart block. Echocardiogram demonstrated poor bi-ventricular function. He was treated for Hypoxic ischemic encephalopathy (HIE). In the next few hours he developed short episodes of ventricular tachycardia with left bundle branch block and non-conducted P waves suggesting an origin of tachycardia from the right ventricle. His repeat ECHO suggested that he had right ventricular infarction due to a very rare finding of intermittent occlusion of the origin of the right coronary artery by an echogenic mass. He was transferred for emergency cardiac surgery to remove a clot of 1.6cm, occluding the right coronary artery. Histology findings were in keeping with a thrombus. Thrombophilia screen for both parents and infant were negative. MRI Brain did not show evidence of HIE suggesting his poor condition at birth was secondary to intermittent coronary ischemia. Discussion: Myocardial infarction (MI) in neonates is a rarely encountered and potentially life-threatening condition, with mortality rate as high as 90%. We present one of the first reported cases of successful surgical management of an acute right coronary artery thrombosis after an early diagnosis. The cause of thrombosis remains unclear in our patient. They were born in poor condition with initial pH 6.9 and lactate of 10, but with a structurally normal heart and negative thrombophilia screen. Perinatal asphyxia is a potential cause; however there is doubt that this may be a symptom rather than cause of the right coronary artery occlusion. Early diagnosis was key in management after a high level of clinical suspicion. He made significant recovery with near normal RV function, and is currently on captopril and carvedilol post-surgery. This is one of the first cases to document near full return of cardiac function following ischaemia to the right ventricle Abstract 478 Figure. 5


2019 ◽  
Vol 22 (4) ◽  
pp. E308-E309
Author(s):  
He Fan ◽  
Weng Jiakan ◽  
He Qicai ◽  
Qian Ximing ◽  
Chen Huaidong

Anomalies of the coronary arteries -- especially their abnormal origin from the pulmonary artery (ARCAPA) trunk -- are among the least common. They’re also the most dangerous of congenital heart defects with an incidence of 0.002% in the general population [Williams 2006]. The diagnosis exceedingly is difficult because anatomical abnormalities of the coronary arteries are subtle. We present a case of an anomalous origin of the right coronary artery.


2019 ◽  
Vol 30 (1) ◽  
pp. 47-49
Author(s):  
Ali A. Alakhfash ◽  
Mohamad Tagelden ◽  
Abdulrahman Almesned ◽  
Abdullah Alqwaiee

AbstractAortopulmonary window is a rare congenital heart lesion. It might be associated with other CHDs, as well as with anomalous origin of the coronary arteries. Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is the most commonly described coronary artery anomaly in association with aortopulmonary window. We are describing a premature neonate who was diagnosed to have aortopulmonary window and ARCAPA immediately after birth, and had a successful operation at the age of 4 months. This report highlights the importance of very careful assessment of the coronary arteries in patients with aortopulmonary window.


2013 ◽  
Vol 19 (3) ◽  
pp. 130-135
Author(s):  
V. Ispas ◽  
P. Bordei ◽  
D. M. Iliescu ◽  
R. Baz

Abstract Our study was performed on a total of 24 angioCT’s by each coronary artery executed on a GE LightSpeed VCT64 Slice CT Scanner. To assess the type of vascularization (coronary dominance) we used also dissection on fresh and formalin preserved hearts, injection of contrast substance followed by radiography and plastic mass injection followed by corrosion. Left coronary artery from origin I found a diameter of between 4.1 to 5.8 mm, the length of the left main coronary artery until its branching (bi or trifurcation) ranging from 3 to 11.8 mm. The diameter of the anterior interventricular artery, was between 1.8 to 3.4 mm, and when the anterior interventricular artery branched off a left marginal artery, it was less voluminous than the case when the marginal artery origin by trifurcation of coronary artery, with 1.8-2.5 mm. Anterior interventricular artery detach left anterior ventricular branches with a diameter of 1.2-2.2 mm. Circumflex artery present a diameter of 2.1 to 4.2 mm at the left aspect of the heart circumflex artery has a diameter of 2.1 to 3.4 mm. On the posterior surface of left ventricle from circumflex artery branches come off with 1.2 to 2.4 mm in diameter. Left marginal artery, when originate from the left coronary artery had a diameter of 2.1 to 2.8 mm. The right coronary artery presents at origin a diameter of 3.1 to 5.4 mm, from the coronary right for the anterior aspect of the right ventricle unhooking the branches with a diameter of 2.2 to 4.2 mm. To the posterior of the right ventricle right coronary artery gave branches with a diameter of 1.6 to 2.6 mm. Right marginal artery had a diameter of 1.6-2.2 mm, and in one case (4.17% from cases) had a diameter of 3.4 mm (when the right coronary origin was 5.4 mm ). From right the coronary atrial branches detaches with a caliber of 0.6-2 mm. Regarding the coronary dominance, we found on a number of 88 hearts that in 29.54% of cases there is predominance of right coronary artery in 25% of cases there is a predominance of the left coronary artery, and in 45.46% of cases there is a balance between the territories of the vascularity of the two coronary arteries.


2007 ◽  
Vol 17 (4) ◽  
pp. 387-396 ◽  
Author(s):  
A. Louise Calder ◽  
Charles R. Peebles ◽  
Christopher J. Occleshaw

AbstractBackgroundThe relatively high mortality in patients with pulmonary atresia and intact ventricular septum may be related to the presence of significant coronary arterial anomalies. This retrospective review of cineangiocardiograms was undertaken to further elucidate the types and variety of such coronary arterial abnormalities, and to assess their effect on postoperative survival.Material and resultsDetails regarding coronary arterial anatomy and abnormalities were assessed in 116 patients. We noted the site and severity of lesions, and the presence of fistulous communications from the right ventricle to the coronary arteries, assessing the proportion of left ventricular myocardium affected by coronary arterial interruptions or significant stenoses, in other words, the amount dependent on coronary circulation from the right ventricle. We also measured diameters of the tricuspid and mitral valves. Fistulas were found in 87 patients (75%), interruptions of major coronary arteries in 40 patients (34%), lack of connections between the coronary arteries and the aorta in 18 patients (16%), and single origin of a coronary artery, with the right coronary artery arising from the left, in 6 patients (5%). We found increased mortality in 47 patients (40%) who had a right ventricular-dependent coronary arterial circulation. The presence of fistulas in itself was not associated with higher mortality, but the presence of coronary arterial interruptions (p = 0.05), and a higher myocardial score (p = 0.0009), were.ConclusionWe encountered a higher prevalence of both coronary arterial abnormalities and right ventricular-dependent circulation than previously reported. Awareness of the severity of the coronary arterial abnormalities should assist in planning treatment.


2007 ◽  
Vol 17 (S4) ◽  
pp. 56-67 ◽  
Author(s):  
Alan H. Friedman ◽  
Mark A. Fogel ◽  
Paul Stephens ◽  
Jeffrey C. Hellinger ◽  
David G. Nykanen ◽  
...  

AbstractThe coronary arteries, the vessels through which both substrate and oxygen are provided to the cardiac muscle, normally arise from paired stems, right and left, each arising from a separate and distinct sinus of the aortic valve. The right coronary artery runs through the right atrioventricular groove, terminating in the majority of instances in the inferior interventricular groove. The main stem of the left coronary artery bifurcates into the anterior descending, or interventricular, and the circumflex branches. Origin of the anterior descending and circumflex arteries from separate orifices from the left sinus of Valsalva occurs in about 1% of the population, while it is also frequent to find the infundibular artery arising as a separate branch from the right sinus of Valsalva.Anomalies of the coronary arteries can result from rudimentary persistence of an embryologic coronary arterial structure, failure of normal development or normal atrophy as part of development, or misplacement of connection of a an otherwise normal coronary artery. Anomalies, therefore, can be summarized in terms of abnormal origin or course, abnormal number of coronary arteries, lack of patency of the orifice of coronary artery, or abnormal connections of the arteries.Anomalous origin of the left coronary artery from the pulmonary trunk occurs with an incidence of approximately 1 in 300,000 children. The degree of left ventricular dysfunction produced likely relates to the development of collateral vessels that arise from the right coronary artery, and provide flow into the left system. Anomalous origin of either the right or the left coronary artery from the opposite sinus of Valsalva can be relatively innocuous, but if the anomalous artery takes an interarterial course between the pulmonary trunk and the aorta, this can underlie sudden death, almost invariably during or immediately following strenuous exercise or competitive sporting events. Distal anomalies of the coronary arteries most commonly involve abnormal connections, or fistulas, between the right or left coronary arterial systems and a chamber or vessel.We discuss the current techniques available for imaging these various lesions, along with their functional assessment, concluding with a summary of current strategies for management.


Author(s):  
Daniel Martinez Lopez ◽  
Javier Goicolea Ruigomez ◽  
Carlos Esteban Martín López ◽  
Alberto Forteza Gil

Abstract Cardiac paragangliomas are extremely rare. Sometimes surgical resection is a challenge owing to the proximity of vital structures and coronary arteries involvement. We report a case of a 34-year-old man with cardiac paragangliomas located between right atrium and right ventricle with a feeding blood supply from collaterals of the right coronary artery. In this case, we implanted a covered single stent (PK Papyrus®) in the right coronary artery with the objective of embolizing collateral branches and to reinforce the coronary artery wall. Although tumour mass was not reduced, vascularization was minimized, and this hybrid strategy made the surgery easier and safer.


2010 ◽  
Vol 20 (S3) ◽  
pp. 20-25 ◽  
Author(s):  
Anthony Hlavacek ◽  
Marios Loukas ◽  
Diane Spicer ◽  
Robert H. Anderson

AbstractIn the normal heart, the right and left coronary arteries arise from the aortic valvar sinuses adjacent to the pulmonary trunk. The right coronary artery then directly enters the right atrioventricular groove, whereas the main stem of the left coronary artery runs a short course before dividing to become the anterior interventricular and circumflex arteries. These arteries can have an anomalous origin from either the aorta or pulmonary trunk; their branches can have various anomalous origins relative to arterial pedicles. Other abnormal situations include myocardial bridging, abnormal communications, solitary coronary arteries, and duplicated arteries. Understanding of these variations is key to determining those anomalous patterns associated with sudden cardiac death. In the most common variant of an anomalous origin from the pulmonary trunk, the main stem of the left coronary artery arises from the sinus of the pulmonary trunk adjacent to the anticipated left coronary arterial aortic sinus. The artery can, however, arise from a pulmonary artery, or the right coronary artery can have an anomalous pulmonary origin. The key feature in the anomalous aortic origin is the potential for squeezing of the artery, produced by either the so-called intramural origin from the aorta, or the passage of the abnormal artery between the aortic root and the subpulmonary infundibulum.


1997 ◽  
Vol 7 (4) ◽  
pp. 434-437
Author(s):  
G. Michielon ◽  
G. Stellin ◽  
O. Milanesi

AbstractWe report on a case of a newborn with echocardiographic diagnosis of anomalous origin of the right coronary artery from the main pulmonary artery. Intraoperative inspection demonstrated a proximal anomalous course of the right coronary artery but a normal origin from the right sinus of Vansalva of the Aorta. We suggest a complete investigation, including coronary angiography, when isolated and rare congenitaj malformations of the coronary arteries are suspected.


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