Unusual presentation during childhood of left ventricular myxoma

1998 ◽  
Vol 8 (1) ◽  
pp. 126-127 ◽  
Author(s):  
A. Kapoor ◽  
S. Radhakrishnan ◽  
N. Sinha
Keyword(s):  
Left Ventricle ◽  
Left Atrium ◽  
Febrile Illness ◽  
Left Ventricular ◽  
Unusual Presentation ◽  
Cardiac Tumors ◽  
History Of ◽  
Primary Cardiac Tumors

AbstractAmongst all primary cardiac tumors, myxomas are the commonest, and their commonest site of origin is the left atrium. Myxomas originating in the left ventricle are rare. When seen, they usually present with a history of systemic embolisation and/or syncopal episodes, with constitutional symptoms being absent. We report here a child with left ventricular myxoma who presented with a prolonged febrile illness.

scholarly journals HUGE SPORADIC AND COMPLEX CARDIAC RHABDOMYOMA WITH HYPOPLASTIC LEFT VENTRICLE AND LEFT LUNG

2021 ◽  
Author(s):  
Türkan Tansel ◽  
İbrahim Demir ◽  
Nilgün Yazıksız ◽  
Ümrah Aydoğan ◽  
İbrahim Kalelioğlu ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Left Atrium ◽  
Left Lung ◽  
Surgical Excision ◽  
Left Ventricular ◽  
Cardiac Tumors ◽  
Cardiac Rhabdomyoma ◽  
Hemodynamic Compromise ◽  
Urgent Surgery ◽  
Inferior Aspect

Cardiac rhabdomyomas are the most common fetal cardiac tumors and can be diagnosed antenatally and postnatally by echocardiography. They are usually asymptomatic and spontaneously regress within the first three years of life and often associated with tuberous sclerosis (TS). The prognosis of patients with rhabdomyomas is mostly determined by the size and location of the lesion. Rhabdomyomas may cause hemodynamic disturbances or arrhythmias due to obstructing the inflow or ventricular outflow tracts or alter valve function, leading to poor prognosis. Although it may regress spontaneously, surgical excision is usually curative, especially in sporadic and single tumors. We report an unique case of antenatally diagnosed as a huge cardiac rhabdomyoma accompanied by hypoplastic left lung and left ventricle, mimicking significant obstruction of the left ventricular and left atrial chamber. The patient underwent urgent surgery, because of severe hemodynamic compromise on the first day of life due to signs of severe obstruction of the left ventricle and left atrium. The large, lobulated epicardial cardiac rhabdomyoma located anterolateral and inferior aspect of the heart; involved the whole left ventricle through the left atrium excised.

scholarly journals Intracardiac EUS-B-Guided FNA for Diagnosing Cardiac Tumors

Respiration ◽  
2021 ◽  
pp. 1-5
Author(s):  
Haizea Alvarez Martinez ◽  
Jolanda C. Kuijvenhoven ◽  
Jouke T. Annema
Keyword(s):  
Left Atrium ◽  
Heart Surgery ◽  
Open Heart Surgery ◽  
Needle Aspiration ◽  
Invasive Technique ◽  
Cardiac Tumors ◽  
Surgical Interventions ◽  
Tumor Diagnostics ◽  
Specific Tumor ◽  
Primary Cardiac Tumors

Primary cardiac tumors are extremely rare. Obtaining a tissue diagnosis is difficult and commonly requires open-heart surgery with associated morbidity. Esophageal endoscopic ultrasound (EUS) and EUS with the EBUS scope (EUS-B) provide real-time sampling of centrally located lung tumors and mediastinal lymph nodes. They also provide an excellent view of the left atrium, since it is located adjacent to the esophagus. To date, left atrium tumor diagnostics by endosonography is poorly explored. We describe 2 exceptional diagnostic cases of left atrium tumors in which cardiac surgery was hazardous due to the clinical condition or previous surgical interventions. During EUS-B-guided fine-needle aspiration (FNA), the left atrial masses were successfully and safely sampled, revealing a Burkitt lymphoma and a synovial sarcoma. FNA including cell block analysis enabled specific tumor diagnosis and molecular subtyping. Our findings suggest that in selected cases, linear endosonography qualifies as a minimally invasive technique for intracardiac tumor diagnostics.

scholarly journals 1112 Discovering the origin of a mysterious heart cavity

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
V Vidal Urrutia ◽  
P Garcia Gonzalez ◽  
J L Perez Bosca ◽  
D Escribano Alarcon ◽  
J M Simon Machi ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Left Atrium ◽  
Left Atrial ◽  
Left Atrial Appendage ◽  
Contrast Echocardiography ◽  
Left Ventricular ◽  
Atrial Appendage ◽  
Invasive Approach ◽  
Cardiovascular Morbidity And Mortality ◽  
Doppler Color

Abstract Left atrial appendage aneurysm is an infrequent cardiac malformation, with less than 150 cases reported in the literature. It is a congenital anomaly in the majority of cases, related to a dysplasia of pectinate muscles and atrial muscle bands, which tends to grow with age. At the present time, and despite of being not considered in current guidelines, surgical resection is the standard of treatment in the current literature, even in asymptomatic cases, based on cardiovascular morbidity and mortality by predisposing to atrial tachyarrhythmia, thromboembolism, and other rare conditions as coronary or left ventricular compression and rupture of the aneurysm. We report the case of a 53-year-old male patient presenting an episode of supraventricular paroxysmal tachycardia with the casual finding of a mysterious cavity in the transthoracic echocardiography. We found out the presence of a 50 mm cavity adjacent to the left atrium and left ventricle, with a bidirectional blood flow between the left atrium and the cavity when applying Doppler color and with contrast echocardiography. Given this finding, several differential diagnosis had to be considered, including vascular and structural disorders. In order to clarify the diagnosis, a cardiac magnetic resonance was performed. It revealed the presence of a huge aneurysm of the left atrial appendage (50 x 53 mm) causing a mild compression of the left ventricle, with no thrombus and no other significant findings. Due to its size, the compression of the left ventricle and the history of atrial arrhythmia we decided to manage it with an invasive approach by performing a middle thoracotomy, in order to prevent potentially serious complications. Abstract 1112 Figure. CMR 3D reconstruction; echocardiography

Surgical Treatment of Primary Cardiac Tumors—Experience with 45 Patients

1995 ◽  
Vol 3 (2) ◽  
pp. 49-52
Author(s):  
Lin Jue Yi ◽  
Chu Shu Hsun ◽  
Lee Yuan Teh ◽  
Wang Shoei Shen ◽  
Lin Fang Yue ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Left Atrium ◽  
Malignant Tumors ◽  
Thyroid Tissue ◽  
University Hospital ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Incomplete Resection ◽  
Long Term Result ◽  
Primary Cardiac Tumors

Primary cardiac tumors are very rare and the majority of them are histologically benign and surgically curable. During a 30-year period from 1963 to January 1993, 45 cases of primary cardiac tumors were surgically excised at the National Taiwan University Hospital, representing 0.52% of 8,695 open heart surgical cases during the same period. In this series, 42 cases (94%) were benign tumors; 39 (88%) were myxoma (30 female, 9 male), and 32 (82%) originated in the left atrium. None were discovered in the left ventricle. In all but the first 6 cases, tumors in patients with myxoma in the left atrium were successfully excised by the transseptal approach. There were 3 patients with rare benign tumors: intracardiac goiter, rhabdomyoma, and hemangioma respectively. The intracardiac goiter was completely excised with no ectopic thyroid tissue after operation and the other 2 received palliative resection. The latter 2 patients suffered no recurrence. Rhabdomyosarcoma, leiomyosarcoma and malignant lymphoma were noted in one patient each, all of whom died of low cardiac output in the early postoperative course. In our experience, the majority of primary cardiac tumors were benign and located in the left atrium. The long-term result of surgical treatment of benign cardiac tumors is excellent, even incases of incomplete resection, while the results from surgical treatment of malignant tumors is poor.

scholarly journals Primary Cardiac Rhabdomyosarcoma in a child -- A case report

2020 ◽  
Author(s):  
KRISHNA PRASAD MARAM ◽  
Vikram Kudumula ◽  
Dilip Ratti
Keyword(s):  
Case Report ◽  
Left Ventricle ◽  
Right Ventricle ◽  
Malignant Tumor ◽  
Right Atrium ◽  
Malignant Tumors ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Cardiac Rhabdomyosarcoma ◽  
Primary Cardiac Tumors

Primary cardiac tumors are rare in children, usually consist of benign tumors like rhabdomyomas and fibromas that may spontaneously regress. Primary malignant tumors are extremely rare even in adults and very few paediatric cases were reported in literature. Rhabdomyosarcoma is a rare primary malignant tumor in children and most of the reported cases occur in right ventricle, left atrium and right atrium. We report a 15 month old child with primary rhabdomyosarcoma of left ventricle presenting in cardiac tamponade and circulatory failure.

scholarly journals Monophasic Synovial Sarcoma of the Left Ventricle of the Heart: An Extremely Rare Case and Literature Review

2021 ◽  
Vol 9 (C) ◽  
pp. 109-113
Author(s):  
Anindhita Muthmaina ◽  
Ery Kus Dwianingsih ◽  
Shinta Andi Sarasati ◽  
Hendry Purnasidha Bagaswoto ◽  
Hasanah Mumpuni
Keyword(s):  
Left Ventricle ◽  
Spindle Cell ◽  
Cardiac Tumors ◽  
Cell Component ◽  
Exertional Dyspnea ◽  
Mesenchymal Marker ◽  
Cell Components ◽  
History Of ◽  
Synovial Sarcomas ◽  
Bcl2 Protein

BACKGROUND: Cardiac sarcomas account for <25% of all cardiac tumors. Of these, angiosarcomas are the most frequent. Synovial sarcomas (SS) are exceedingly rare. We present a case of primary left ventricle (LV) SS, a form of sarcoma particularly rare in the heart. CASE DESCRIPTION: A 19-year-old male was referred for further investigation of a LV tumor, presented with a 3-month history of exertional dyspnea and palpitations. He also experienced several syncopal episodes. The radiologic examination confirmed a mass in the LV, suspected for myxoma of the LV. Histopathologic examination revealed a malignant tumor with spindle cell components, suggesting leiomyosarcoma with differential diagnosis of monophasic SS. Immunohistochemistry demonstrated reactivity of the spindle cell component with the mesenchymal marker vimentin and BCL2 protein, while the smooth muscle marker, desmin, was negative, confirming the diagnosis of monophasic SS. CONCLUSIONS: Monophasic SS in the heart is diagnostically challenging since it shares the broad list of differential diagnoses of spindle cell tumors. Immunostaining is helpful to differentiate those entities to obtain a definitive diagnosis and proper treatment.

Miscellaneous valvar pathology: Mitral stenosis, pulmonary stenosis, and tricuspid regurgitation

2018 ◽  
Author(s):  
Kazem Rahimi
Keyword(s):  
Mitral Valve ◽  
Left Ventricle ◽  
Left Atrium ◽  
Tricuspid Regurgitation ◽  
Mitral Stenosis ◽  
Left Atrial ◽  
Pulmonary Stenosis ◽  
Left Ventricular ◽  
Cor Triatriatum

Mitral stenosis is obstruction to inflow of blood from left atrium to left ventricle at the level of the mitral valve. Non-valvar causes of left ventricular inflow obstruction include left atrial tumours and cor triatriatum.

scholarly journals P777 Effects of chronic cigarette smoking on left ventricle, left atrium and right ventricle strain parameters with 2D speckle tracking echocardiography

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
B Yaman ◽  
L Cerit ◽  
H Kemal Gunsel ◽  
E Acikgoz ◽  
S Usalp ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Cigarette Smoking ◽  
Left Atrium ◽  
Speckle Tracking ◽  
Speckle Tracking Echocardiography ◽  
Left Ventricular ◽  
Smoking History ◽  
Healthy Participant ◽  
Diastolic Velocity ◽  
2D Speckle Tracking

Abstract Funding Acknowledgements None Background Cigarette smoking effects myocardium with several mechanisms such as sympathetic nervous system activation, oxidative stress and endothelial dysfunction. Chronic smokers have an increased risk of morbidity and mortality associated with adverse cardiac events. Echocardiography is the well-established non-invasive diagnostic tool for the assessment of cardiac systolic and diastolic functions. 2D speckle tracking echocardiography (STE) has been widely used for this purpose in recent years. Purpose The aim of this study is to compare the left ventricle, left atrium and right ventricle systolic functions with 2D speckle tracking echocardiography in chronic smokers and non-smoker healthy population. Method 40 healthy participant (mean age 33.4 ± 10.0) without smoking history, 42 healthy participant (mean age 33.9 ± 9.2) who had smoking history at least 3 years without history of cardiac disease or any other chronic diseases such as hypertension, diabetes mellitus, kidney failure were prospectively included. In addition to Standard 2D echocardiographic measurements, left ventricular global longitidunal strain (LvGLS), right ventricular global longitidunal strain (RvGLS), left atrial strain and strain rate were analyzed with Vivid E9, offline using a customized software package. Results Smokers had lower peak early diastolic velocity (E) and E/A (late diastolic velocity) ratio in mitral inflow (0.70 ± 0.13 vs 0.77 ± 0.13, p = 0.023; 1.47 ± 0.44 vs 1.73 ± 0.44, p = 0.011; respectively). Peak early diastolic velocity of mitral valve medial annulus and E’/A’ ratio (0.11 ± 0.02 vs 0.12 ± 0.02, p = 0.023; 1.20 ± 0.37 vs 1.40 ± 0.46, p = 0.039; respectively) was lower in smokers. LvGLS and RvGLS were significantly impaired in smokers (-17.65 ± 3.01 vs -19.21 ± 2.52, p = 0.013; -18.96 ± 4.47 vs -21.06 ± 4.58, p = 0.039; respectively). Although εs, reservoir phase strain of left atrium; εe, conduit phase strain of left atrium; εa, contractile phase strain of left atrium were similar between two groups, εe/εa was significantly lower in smokers than non-smokers (1.32 ± 0.59, 1.63 ± 0.63, p = 0.026). Conclusion Impaired RV deformation was found in chronic cigarette smokers. Besides standardized diastolic dysfunction parameters εe/εa might be used for the early indicator of diastolic dysfunction. Although there was no statistically significant difference with left ventricular ejection fraction between smokers and non-smokers, LvGLS which is the early indicator of LV systolic dysfunction in chronic smokers might be used for the early assesment of LV systolic impairment. Abstract P777 figure 1

scholarly journals Left Atrial Myxoma with Mild Left Ventricular Dysfunction— A Case Report

Pulse ◽  
2018 ◽  
Vol 10 (1) ◽  
pp. 29-33
Author(s):  
T Meher ◽  
SMAZN Palash ◽  
MK Hasan ◽  
TMNS Khan ◽  
NM Zahangir ◽  
...  
Keyword(s):  
Case Report ◽  
Left Atrial ◽  
Ventricular Dysfunction ◽  
Pulmonary Artery Hypertension ◽  
Left Ventricular ◽  
Atrial Myxoma ◽  
Cardiac Tumors ◽  
Ventricular Failure ◽  
Left Atrial Myxoma ◽  
Primary Cardiac Tumors

Atrial Myxoma is the most common primary cardiac tumors accounting for about 50% of benign primary cardiac tumors, with the majority located in the left atrium. This is a case of large left atrial (LA) myxoma presented with features of mitral stenosis associated with moderate left ventricular failure (LVF) and mild pulmonary artery hypertension (PAH) The patient improved markedly after tumor excision.Pulse Vol.10 January-December 2017 p.29-33

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