scholarly journals Bilateral Ectopic Hypoplastic Uteri Attached to Bilateral Pelvic Sidewalls in a 21-Year-Old Patient with Primary Amenorrhea: The First Published Report

2013 ◽  
Vol 2013 ◽  
pp. 1-4
Author(s):  
Ahmed Nazer ◽  
Ahmed Abu-Zaid ◽  
Osama AlOmar ◽  
Hany Salem ◽  
Ayman Azzam ◽  
...  
Keyword(s):  
Care Center ◽  
Tertiary Care ◽  
Primary Amenorrhea ◽  
Mullerian Duct ◽  
Tertiary Care Center ◽  
First Case ◽  
Published Report ◽  
Müllerian Duct Anomalies ◽  
Embryonic Life ◽  
Mullerian Duct Anomalies

Müllerian duct anomalies (MDAs) encompass a group of anatomical malformations resulting from defective development, fusion, migration, or resorption of Müllerian (paramesonephric) ducts during embryonic life. Herein, we report the first case of an exceedingly uncommon MDA (bilateral ectopic hypoplastic uteri attached to bilateral pelvic sidewalls) in a 21-year-old woman who was referred to our tertiary care center as a case of primary amenorrhea for workup and further management.

scholarly journals Mullerian ductal anomalies and its outcome

2019 ◽  
Vol 8 (2) ◽  
pp. 440
Author(s):  
Rupa C. Vyas ◽  
Ashleta M. Moghariya ◽  
Sapana R. Shah ◽  
Purvi M. Parikh ◽  
Prachi M. Shelat
Keyword(s):  
Congenital Anomalies ◽  
Developmental Disorders ◽  
Care Center ◽  
Tertiary Care ◽  
Management Strategies ◽  
Female Reproductive Tract ◽  
Primary Amenorrhea ◽  
Tertiary Care Center ◽  
Mullerian Anomalies ◽  
Müllerian Anomalies

Background: The aim is to study various investigative modalities to diagnose Mullerian anomalies and to evaluate the reproductive outcome that occurs as a result of malformation of genital tract.Methods: A prospective study of reproductive anomalies and its outcome was performed by using data from women with congenital anomalies attended in OPD either with complains or for operative treatment or incidental diagnosis during caesarean section, manual removal of placenta, during laparoscopy or laparotomy at tertiary care center. Total 70 women with different types of congenital anomalies were included in study. Out of them gynecological cases (27) were diagnosed on basis of clinical examination and other diagnostic aids while Mullerian anomalies in obstetric cases (43) were observed and their outcomes were studied.Results: Most common utero-vaginal anomaly seen in present study was septate uterus with 18 (25.7%) cases, followed by bicornuate uterus with 13 (18.6%) cases. Most common presenting symptom is primary amenorrhea 21 (30%) followed by cyclical abdominal pain 11 (15.7). HSG, USG are the primary tools to detect genital tract anomalies. Surgical correction was required in 47.1% patients.Conclusions: Present study shows prevalence of congenital malformation of female reproductive tract is 0.17% at our tertiary care center. Utero-vaginal anomalies are a morphologically diverse group of developmental disorders. Establishing an accurate diagnosis is essential for planning treatment and management strategies. The surgical approach for correction of utero-vaginal anomalies is specific to the type of malformation and may vary in a specific group.

Menstrual Problems

1983 ◽  
Vol 4 (10) ◽  
pp. 326-326
Keyword(s):  
Accurate Information ◽  
Primary Amenorrhea ◽  
Mullerian Duct ◽  
Polycystic Ovaries ◽  
Pelvic Ultrasound ◽  
Müllerian Duct ◽  
Müllerian Duct Anomalies ◽  
Ovarian Agenesis ◽  
Mullerian Duct Anomalies

A reader asked why Litt did not recommend the use of pelvic ultrasound as an aid in the diagnosis of amenorrhea (PIR 4:203, January 1983). Dr Litt responds: Pelvic ultrasound can certainly be helpful in ascertaining the presence or absence of ovaries and Mullerian duct structures and, thus, might have a place in the evaluation of a patient with primary amenorrhea. Similarly, it is often (but not always) possible to demonstrate polycystic ovaries by this method. We have not relied on it, however, because gonadotrophin analysis provides accurate information about the first (ovarian agenesis) and the last (polycystic ovaries) and Mullerian duct anomalies can best be explored by laparoscopy.

Study on Pattern of Primary Amenorrhea at Tertiary Care Center—A Retrospective Analysis

2019 ◽  
Vol 11 (1) ◽  
pp. 23-26
Author(s):  
Shreedhar Venkatesh ◽  
Lakshmidevi Muralidhar ◽  
Lopa M Pradhan
Keyword(s):  
Retrospective Analysis ◽  
Care Center ◽  
Tertiary Care ◽  
Primary Amenorrhea ◽  
Tertiary Care Center

scholarly journals Septate Uterus in a Girl with Rubinstein–Taybi Syndrome

2018 ◽  
Vol 2018 ◽  
pp. 1-4 ◽  
Author(s):  
Filipa de Castro Coelho ◽  
Sara Câmara ◽  
Inês Alves ◽  
Kathleen Brazão
Keyword(s):  
Reproductive Medicine ◽  
Clinical Phenotype ◽  
Mullerian Duct ◽  
Septate Uterus ◽  
First Case ◽  
Müllerian Duct Anomalies ◽  
Uterine Septum ◽  
Uterine Malformations ◽  
Mullerian Duct Anomalies ◽  
American Society

Rubinstein–Taybi syndrome is an extremely rare plurimalformative condition that can affect any organ. However, reports regarding gynecological problems are unusual. We report the first case of a septate uterus in an adolescent with this syndrome, in agreement with the American Society for Reproductive Medicine (ASRM) and the Congenital Uterine Malformations by Expert (CUME) criteria for uterine septum. Additional studies are required to determine whether there is an increased frequency of müllerian duct anomalies with the condition. Our report extends the data on the clinical phenotype associated with Rubinstein–Taybi syndrome.

scholarly journals Müllerian Duct Anomalies- Diagnostic Imaging in Pediatric and Adolescent Population

2019 ◽  
Vol 0 (0) ◽  
Author(s):  
Igor Ilic ◽  
Marija Bicanin Ilic ◽  
Aleksandra Dimitrijevic
Keyword(s):  
Tissue Characterization ◽  
Management Strategies ◽  
Young Female ◽  
Primary Amenorrhea ◽  
Mullerian Duct ◽  
Müllerian Duct ◽  
Adolescent Population ◽  
Müllerian Duct Anomalies ◽  
Reproductive Counseling ◽  
Mullerian Duct Anomalies

Abstract Müllerian duct anomalies (MDAs) are congenital entities that result from the non-development, defective vertical or lateral fusion, or the resorption failure of the Müllerian (paramesonephric) ducts. MDAs represent a more frequent entity than previously believed. Few recent meta-analyses reported a prevalence of 5.5 - 6.7%. MDAs are commonly associated with other anomalies, specially kidneys, so identification of both kidneys is important. In pediatric and adolescent population MDAs are discovered incidentally at patients observed for some other reason or because of the primary amenorrhea and low abdominal pain related to hematometra (colpos). Imaging is essential for a diagnosis, management, and reproductive counseling in patients with MDA. Patients suspected of having the MDA are often initially referred to pelvic ultrasonography (US). Field-of-view restrictions with US, patient body habitus and artifact from bowel gas may result in a request for the further MagneticRresonance Iimaging (MRI). Also US cannot help identify the type of the MDA. MRI is the imaging standard of reference because it is non-invasive, does not involve ionizing radiation, has a multiplanar capability, allows an excellent soft-tissue characterization, detailed delineation of the uterovaginal anatomy and accurate classification of the type of anomaly. This is especially true for young female patients, in whom the use of vaginal US probes is avoided. Establishing an accurate diagnosis is essential for planning treatment and management strategies. The surgical management of MDAs is specific to the type of malformation and may vary in a specific group.

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