scholarly journals Mucinous Carcinomatosis: A Rare Association between an Ovarian Tumor and an E-GIST

2018 ◽  
Vol 2018 ◽  
pp. 1-4 ◽  
Author(s):  
Hugo Palma Rios ◽  
André Goulart ◽  
Pedro Leão
Keyword(s):  
Pseudomyxoma Peritonei ◽  
Ovarian Tumor ◽  
Incidental Finding ◽  
Intestinal Type ◽  
Mesenchymal Tumor ◽  
Emergency Laparotomy ◽  
Mucinous Tumor ◽  
Appendiceal Tumor ◽  
Stromal Tumors ◽  
Rare Association

Pseudomyxoma peritonei (PMP) and extragastrointestinal stromal tumors (E-GISTs) are both rare entities. Most of the time, PMP is associated with an appendiceal tumor. An ovarian mucinous tumor can mimic appendiceal metastases. E-GIST is a mesenchymal tumor that can arise from the omentum, retroperitoneum, mesentery, or pleura. We present a case of an 87-year-old woman with mucinous carcinomatosis and acute intestinal occlusion submitted to an emergency laparotomy. She has found to have a borderline mucinous tumor of the ovary from the intestinal type with several lesions of pseudomyxoma peritonei and an E-GIST from the epiploons retrocavity (intermediated risk). In the literature, no relation was found between these two rare tumors. E-GIST was an incidental finding in the context of a mucinous carcinomatosis.

scholarly journals A case of Pseudomyxoma Peritonei of an unexpected origin

2021 ◽  
Vol 16 (1) ◽  
Author(s):  
Marie Csanyi-Bastien ◽  
France Blanchard ◽  
Aude Lamy ◽  
Jean-Christophe Sabourin
Keyword(s):  
Pseudomyxoma Peritonei ◽  
Ovarian Tumor ◽  
Histological Analysis ◽  
Mucinous Cystadenoma ◽  
Ovarian Teratoma ◽  
Mucinous Tumor ◽  
Case Presentation ◽  
Mucinous Neoplasm ◽  
Ovarian Lesion

Abstract Background Pseudomyxoma peritonei (PMP) is a complex and partially understood disease defined by mucin deposits in the peritoneal cavity, mostly of appendiceal origin caused by the rupture of a mucocele often containing Low or High grade Appendiceal Mucinous Neoplasm (LAMN/HAMN). Other origins include primitive ovarian mucinous cystadenoma or cystadenocarcinoma almost always with an associated teratoma, but to our knowledge no case of ovarian teratomatous appendiceal-like mucocele with LAMN has been reported as a cause of PMP. Case presentation A 25-year old female with infertility was diagnosed with an isolated left ovarian tumor in a context of PMP. Histological examination revealed an ovarian teratoma containing an appendiceal-like structure with mucocele and LAMN, without any associated lesion of the appendix on full histological analysis. Molecular characterization of the ovarian lesion showed co-KRAS and GNAS mutations, as described in PMP of appendiceal origin, while only KRAS mutations are reported in primitive ovarian mucinous tumor. Conclusions Detection of co-KRAS and GNAS mutations in our case of ovarian teratomatous appendiceal-like mucocele with LAMN shows that when PMP derives from a mucinous ovarian lesion (with histological proof of none-appendiceal involvement), it is probably of a digestive teratomatous origin, emphasizing the need to actively search for tetatomatous signs in a context of ovarian PMP.

scholarly journals Management of Pseudomyxoma Peritonei Syndrome during Pregnancy

2016 ◽  
pp. 161-165
Author(s):  
Hanny Aditanzil ◽  
Bayu Mahendra ◽  
Ketut Suwiyoga
Keyword(s):  
Case Report ◽  
Gestational Age ◽  
Pseudomyxoma Peritonei ◽  
Ovarian Tumor ◽  
Obstet Gynecol ◽  
Mucinous Tumor ◽  
Diagnosis And Management ◽  
Grade Of Malignancy ◽  
Surgery Management

Objectives: To improve skill in making a diagnosis and management of pseudomyxoma peritoneum originating borderline mucinous ovarian tumor during pregnancy. Methods: Case report. Conclusion: Diagnosis of pseudomyxoma peritoneum during pregnancy is difficult before surgery. Management is based on grade of malignancy and gestational age of pregnancy. [Indones J Obstet Gynecol 2013; 1-3: 161-5] Keywords: mucinous tumor, pregnancy, pseudomyxoma peritoneum

scholarly journals A case of Pseudomyxoma Peritonei of an unexpected origin.

2021 ◽  
Author(s):  
Marie Csanyi-Bastien ◽  
France Blanchard ◽  
Aude Lamy ◽  
Jean-Christophe Sabourin
Keyword(s):  
Pseudomyxoma Peritonei ◽  
Ovarian Tumor ◽  
Histological Analysis ◽  
Mucinous Cystadenoma ◽  
Ovarian Teratoma ◽  
Mucinous Tumor ◽  
Case Presentation ◽  
Mucinous Neoplasm ◽  
Ovarian Lesion

Abstract Background:Pseudomyxoma peritonei (PMP) is a complex and partially understood disease defined by mucin deposits in the peritoneal cavity, mostly of appendiceal origin caused by the rupture of a mucocele often containing Low or High grade Appendiceal Mucinous Neoplasm (LAMN/HAMN). Other origins include primary ovarian mucinous cystadenoma or cystadenocarcinoma almost always with an associated teratoma, but to our knowledge no case of ovarian teratomatous appendiceal-like mucocele with LAMN has been reported as a cause of PMP.Case presentation:A 25-year old female with infertility was diagnosed with an isolated left ovarian tumor in a context of PMP. Histological examination revealed an ovarian teratoma containing an appendiceal-like structure with mucocele and LAMN, without any associated lesion of the appendix on full histological analysis. Molecular characterization of the ovarian lesion showed co-KRAS and GNAS mutations, as described in PMP of appendiceal origin, while only KRAS mutations are reported in primary ovarian mucinous tumor.Conclusions:Detection of co-KRAS and GNAS mutations in our case of ovarian teratomatous appendiceal-like mucocele with LAMN shows that when PMP derives from a mucinous ovarian lesion (with histological proof of none-appendiceal involvement), it is probably of a digestive teratomatous origin, emphasizing the need to actively search for tetatomatous signs in a context of ovarian PMP.

Ovarian Strumal Carcinoid Containing Appendiceal-Type Mucinous Tumor Patterns Presenting as Pseudomyxoma Peritonei

2015 ◽  
Vol 34 (3) ◽  
pp. 293-297 ◽  
Author(s):  
Enoe Quiñonez ◽  
Maolly Schuldt ◽  
Juan A. Retamero ◽  
Francisco F. Nogales
Keyword(s):  
Pseudomyxoma Peritonei ◽  
Mucinous Tumor ◽  
Strumal Carcinoid

scholarly journals An unusual presentation of pancreatic serous cystadenoma

2020 ◽  
Vol 7 (4) ◽  
pp. 1280
Author(s):  
Alexandra O. Stathis ◽  
Samuel C. Kuo
Keyword(s):  
Incidental Finding ◽  
Mass Effect ◽  
Serous Cystadenoma ◽  
Sudden Onset ◽  
Unusual Presentation ◽  
Emergency Laparotomy ◽  
Cystic Neoplasms ◽  
Show Evidence ◽  
Pancreatic Cystic Neoplasms ◽  
Spontaneous Haemorrhage

Pancreatic cystic neoplasms (PCNs) are predominantly benign entities which represent almost 50 percent of all cystic lesions of the pancreas. PCNs are often an incidental finding on abdominal imaging and are not indicated for surgical resection unless they show evidence of malignant transformation or become symptomatic due to mass effect. This report examines an unusual presentation of a PCN, in a 70 years old female with sudden onset abdominal pain, who was found to have spontaneous intraabdominal haemorrhage secondary to a benign PCN. Emergency laparotomy was performed and a distal pancreatectomy or splenectomy were required to achieve haemostasis. Incidence of spontaneous haemorrhage in a benign PCN is a rare but serious complication.

scholarly journals Pseudomyxoma peritonei presenting with port site hernia

2021 ◽  
pp. 89-92
Keyword(s):  
Pseudomyxoma Peritonei ◽  
Case Reports ◽  
Abdominal Distension ◽  
Right Hemicolectomy ◽  
Port Site ◽  
Mucinous Tumor ◽  
Ovarian Mass ◽  
First Case ◽  
Port Site Hernia ◽  
History Of

Pseudomyxoma peritonei (PMP) is a rare disease with an incidence of two per million. Acute appendicitis, ovarian mass, and abdominal distension are the most common presentations. A 72-year-old male patient with a history of laparoscopic cholecystectomy was admitted to the hospital with abdominal pain and increased supraumbilical port site swelling. Radiological examination revealed a mass in the terminal ileum and severe intraabdominal mucinous fluid. Intraabdominal gelatinous fluid protruding from the port site defect and a mass in the distal ap-pendix were observed during operation. He underwent a right hemicolectomy, ileocolic anasto-mosis and peritoneal debridement; cytoreductive surgery was administered two months later due to mucinous tumor of the appendix. There are only a few case reports describing PMP presen-ting with an incisional hernia after open surgical procedures. To the best of our knowledge, this report describes the first case of PMP presenting with a port site hernia after a laparoscopic in-tervention.

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