scholarly journals Bladder exstrophy

2016 ◽  
Vol 62 (3) ◽  
pp. 197-198 ◽  
Author(s):  
Gustavo Gomes Mendes ◽  
Joel Rodrigo Beal Lusa
Keyword(s):  
Congenital Anomaly ◽  
Abdominal Wall ◽  
Musculoskeletal System ◽  
Bladder Exstrophy ◽  
Genitourinary Tract ◽  
Rare Congenital Anomaly ◽  
Live Births ◽  
Lower Abdominal Wall

SUMMARY Bladder exstrophy is a rare congenital anomaly resulting from failure of fusion of the middle of the pelvis line tissues during embryogenesis. It is characterized by malformation of the lower abdominal wall involving the genitourinary tract and the musculoskeletal system. Its incidence is estimated at 1:30,000 to 1:50,000 live births, and it is 2 or 3 times more frequent in males. The child’s age is important and the best results are obtained when treatment is performed shortly after birth.

scholarly journals Scar Endometriosis in a Patient With Bladder Exstrophy

2013 ◽  
Vol 98 (2) ◽  
pp. 145-148 ◽  
Author(s):  
Takahito Kitajima ◽  
Mikihiro Inoue ◽  
Keiichi Uchida ◽  
Kohei Otake ◽  
Masato Kusunoki
Keyword(s):  
Abdominal Wall ◽  
Bladder Exstrophy ◽  
Uterine Cavity ◽  
Excisional Biopsy ◽  
High Signal ◽  
Resonance Imaging ◽  
Scar Endometriosis ◽  
Abdominal Magnetic Resonance Imaging ◽  
History Of ◽  
Lower Abdominal Wall

Abstract Endometriosis is an ectopic occurrence of tissue morphologically and functionally resembling endometrial tissue in regions outside the uterine cavity. Although scar endometriosis after surgery has been shown to be most common among all the extrapelvic forms of endometriosis, endometriosis after bladder exstrophy surgery has not been reported, and here we present the first known case. A 26-year-old woman with a history of bladder exstrophy was aware of a painful induration at the operative scar located in the left lower abdominal wall, and presented at our hospital. Although the symptoms resolved, recurring exacerbation was observed after 9 months. Abdominal magnetic resonance imaging showed a heterogeneous mass 16 mm in diameter in the left abdominal wall with high signal intensity on T1W1 and T2W1 images. She underwent excisional biopsy of the lesion under general anesthesia. Histopathology confirmed the diagnosis of endometriosis. Eighteen months after surgery, she was well and free from recurrence.

scholarly journals Prune Belly Syndrome with Overlapping Presentation of Partial Urorectal Septum Malformation Sequence in a Female Newborn with Absent Perineal Openings

2014 ◽  
Vol 2014 ◽  
pp. 1-4 ◽  
Author(s):  
Azhar Farooqui ◽  
Alaa AlAqeel ◽  
Zakaria Habib
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Abdominal Wall ◽  
Ambiguous Genitalia ◽  
Prune Belly Syndrome ◽  
Rare Congenital Anomaly ◽  
Prune Belly ◽  
Bilateral Cryptorchidism ◽  
Original Case ◽  
Classical Triad

Prune belly syndrome (PBS) is a rare congenital anomaly characterized in males by a triad of anomalous genitourinary tract, deficient development of abdominal wall muscles, and bilateral cryptorchidism. Although similar anomalies have been reported in females, by definition they do not full fill the classical triad. Urorectal septum malformation sequence (URSM) is a lethal condition characterized by presence of ambiguous genitalia, absent perineal openings (urogenital and anal), and lumbosacral abnormalities. In this original case report, the authors discuss the presentation and management of what would be analogous to a Woodhouse category 1 PBS in a female newborn associated with an overlapping presentation of URSM.

Pregnancy in case of exstrophy of bladder

2017 ◽  
Vol 6 (4) ◽  
pp. 1676
Author(s):  
Kinnari Vilaschandra Amin ◽  
Namrata Tiwari ◽  
Anchal Goel ◽  
Anahita R. Chauhan
Keyword(s):  
Congenital Anomaly ◽  
Urinary Bladder ◽  
Cesarean Section ◽  
Pelvic Floor ◽  
Surgical Repair ◽  
Mode Of Delivery ◽  
Bladder Exstrophy ◽  
Bony Pelvis ◽  
Variable Presentation ◽  
Lower Abdominal Wall

Bladder exstrophy or ectopia vesica is an unusual congenital anomaly which exists in the spectrum of the exstrophy- epispadias complex. It most commonly involves protrusion of the urinary bladder due to defect in the lower abdominal wall. It has variable presentation and often includes abnormalities of the pelvic floor, bony pelvis and genitalia. Patients undertaking pregnancy after surgical repair of such an anomaly are rare. Planned Cesarean section at term is considered the appropriate mode of delivery. We present a case of 21-year-old patient who had uneventful preterm vaginal delivery following surgical repair of bladder exstrophy in childhood.

scholarly journals Laparoscopic management of rare “ H type” duplication of gall bladder

2020 ◽  
Vol 6 (6) ◽  
pp. 354-357
Author(s):  
Dr. Anurag Mishra ◽  
◽  
Dr. Md Abu Masud Ansari ◽  
Dr. Shivanshu Misra ◽  
◽  
...  
Keyword(s):  
Congenital Anomaly ◽  
Laparoscopic Cholecystectomy ◽  
Gall Bladder ◽  
Gallstone Disease ◽  
Current Case ◽  
Rare Congenital Anomaly ◽  
Live Births ◽  
Cholecystoenteric Fistula ◽  
Double Gallbladder ◽  
Symptomatic Gallstone Disease

A duplicated gallbladder is a rare congenital anomaly with an incidence of 1:4000 live births. Theycan remain asymptomatic and identified incidentally or present as acute cholecystitis, empyema,torsion, cholecystoenteric fistula, Gall bladder lump, or carcinoma. Here the current case is aboutdiscussing a case of a 25-year-old female who presented with symptomatic gallstone disease with aduplicated gallbladder having multiple stones in both the gallbladders. MRCP performedpreoperatively revealed Y type duplication (double Gall bladder with common cystic duct).Laparoscopic cholecystectomy was performed and it finally revealed H type duplication (double Gallbladder with separate cystic ducts for each Gall Bladder).

scholarly journals Congenital prepubic sinus: a series of six cases of extremely rare congenital anomaly

2017 ◽  
Vol 4 (2) ◽  
pp. 803
Author(s):  
Sudhir Singh ◽  
Digamber Chaubey ◽  
J. D. Rawat ◽  
Gurmeet Singh
Keyword(s):  
Congenital Anomaly ◽  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Female Child ◽  
Urethral Duplication ◽  
Abdominal Wall Closure ◽  
Rare Congenital Anomaly

Congenital prepubic sinus (CPS) is a very rare congenital anomaly. The baby generally present with discharge from an opening situated in midline below umbilicus to root of penis in male or clitoris in female child. The etiology of this congenital anomaly is not exactly known. There is debate in etiology as one theory support anomalous anterior abdominal wall closure and another support variant of dorsal urethral duplication. Here we are presenting the six cases of CPS with their management and brief discussion on theories that have been proposed for their etiology.

scholarly journals Female Epispadias Presenting as Urinary Incontinence

2017 ◽  
Vol 8 (2) ◽  
pp. 10
Author(s):  
Asmir Jonuzi ◽  
Nusret Popović ◽  
Zlatan Zvizdić ◽  
Emir Milišić ◽  
Kenan Karavdić ◽  
...  
Keyword(s):  
Congenital Anomaly ◽  
Urinary Incontinence ◽  
Bladder Neck ◽  
Bladder Exstrophy ◽  
Voiding Cystourethrogram ◽  
Rare Congenital Anomaly ◽  
Anatomical Features ◽  
Labia Minora ◽  
One Stage Reconstruction ◽  
Proximal Urethra

Isolated female epispadias without bladder exstrophy is a rare congenital anomaly affecting 1 in 484,000 females. The presenting features of female epispadias are urinary incontinence and abnormal anatomical features. A 6-year-old girl presented with primary urinary incontinence who on physical examination had a bifid clitoris and labia minora. The vagina and hymen were normal. Voiding cystourethrogram showed no reflux and a funnel shaped proximal urethra. With the diagnosis of isolated female epispadias, one-stage reconstruction of the urethra, bladder neck, labia minora and clitoris was performed.

scholarly journals Retrocaval ureter - a case report

2013 ◽  
Vol 02 (01) ◽  
pp. 044-047
Author(s):  
Margaret Chinnappan ◽  
M. Elangovan
Keyword(s):  
Congenital Anomaly ◽  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Proximal Part ◽  
Urinary System ◽  
Rare Congenital Anomaly ◽  
Live Births ◽  
Retrocaval Ureter ◽  
The Right

AbstractRetrocaval ureter is a rare congenital anomaly which has a incidence of occurence of one in 1500 live births. It is known to occur 2.8 times more commonly in males than females. While carrying out a study on congenital anomalies in urinary system in a collection of still born fetuses, a case of retrocaval ureter was noticed in a still born male foetus. In Retrocaval ureter, ureter is S shaped on the right side and a part of inferior vena cava is anterior to the proximal part of the ureter. Here the development of ureter is normal. Whereas the development of inferior vena cava is abnormal.

scholarly journals OEIS complex – a rare developmental anomaly

2017 ◽  
Vol 06 (04) ◽  
pp. 291-296
Author(s):  
Gaddam Vijaya Lakshmi ◽  
Jacob Abraham ◽  
Deena Sara Mathew
Keyword(s):  
Congenital Anomaly ◽  
Health Care ◽  
Imperforate Anus ◽  
External Genitalia ◽  
Developmental Anomaly ◽  
Congenital Defects ◽  
Surgical Interventions ◽  
Rare Congenital Anomaly ◽  
Live Births ◽  
Health Care Centers

AbstractOEIS complex is a rare congenital anomaly comprising of the following four components: Omphalocoele, Exstrophy of cloaca, Imperforate anus and Spinal defects. It fonns the extreme end of exstrophy-epispadias complex [BEC] of congenital defects. It is associated with anomalies of gastro-intestioaI, urinary and genital systems. External genitalia are bifid, if present. Etiology is not clear. It can be diagnosed by prenatal ultrasound on visualization of 'diaper type' of distribution of anomalies, along with malformations of the limbs. The condition causes severe psychosocial trauma to the parents and family members. In live births, surgical interventions in several stages, are perfonned by skilled expertise only at selected tertiary health care centers. Outcome is highly variable. Prenatal identification of the condition is necessary to give adequate counselling, and have proper planning of the delivery and postnatal management of the baby.

scholarly journals Diphallia with Associated Anomalies: A Case Report and Literature Review

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Pande Made Wisnu Tirtayasa ◽  
Robertus Bebet Prasetyo ◽  
Arry Rodjani
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Literature Review ◽  
Pubic Symphysis ◽  
Associated Anomalies ◽  
Rare Congenital Anomaly ◽  
Live Births ◽  
Pubic Symphysis Diastasis ◽  
Symphysis Diastasis

Diphallia or penile duplication is an extremely rare congenital anomaly. It occurs once in every 5.5 million live births. The extent of penile duplication and the number of associated anomalies vary greatly, ranging from a double glans from a penis with no associated anomaly up to complete penile duplication associated with multiple anomalies. Here, we report a 12-year-old boy with complete bifid diphallia associated with bifid scrotum, epispadia, and pubic symphysis diastasis along with a review of the articles pertaining to this anomaly.

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