Möbius Syndrome with Dental Involvement: A Case Report and Literature Review

1998 ◽  
Vol 35 (3) ◽  
pp. 262-268 ◽  
Author(s):  
Maria Rizos ◽  
Reinaldo J. Negrón ◽  
Neill Serman

The clinicopathological findings on a 17-year-old female with the Möbius/Moebius syndrome are reported. The signs and symptoms of this neuromus-cular condition include congenital bilateral or unilateral palsies of the facial and abducens cranial nerves and a broad scope of multisystem abnormalities. A case of unilateral deficiencies of cranial nerves VI and VII, congenital ectro-dactyly of toes, and multiple congenitally missing primary and permanent teeth is reported. A review of the literature reveals various ideas regarding the diversity of symptoms and the etiology of the syndrome. The purpose of this article is to report oral manifestations, such as congenitally missing teeth, associated with Möbius syndrome.

1996 ◽  
Vol 33 (5) ◽  
pp. 436-439 ◽  
Author(s):  
Peter J. Anderson ◽  
Anthony L.H., Moss

The incidence of dental abnormalities in the cleft lip and palate population has been reported to be much higher than in the normal population. The role of genes in the production of a cleft lip and palate, and dental anomalies is thought to be complex, with autosomal dominant, recessive, and x-linked genes all playing a role. Noncleft parents can carry some of the cleft lip and palate genes, which produce clinically subtle manifestations in their facial skeleton. The purpose of this study was to look for evidence of increased dental anomalies in the non-cleft parents of cleft lip and palate children. The dentitions of the parents of 60 children with different types of cleft lip and palate were examined prospectively to see whether or not they exhibited features found more readily in the cleft lip and palate rather than did the normal population. Their dentitions were studied to record the following dental features: congenitally missing teeth, supernumerary teeth, or morphologic changes of the crowns of the permanent teeth. The number and position of any frenal attachments were also recorded. The results of this study did not show any differences in incidence of dental anomalies from the noncleft population. There was no evidence to support the hypothesis that congenital absence of lateral incisors is a microform of cleft lip and palate. Further, these results also failed to reveal any consistent pattern in the number and position of frenal attachments.


2017 ◽  
Vol 1 (2) ◽  

Background: Hypodontia or congenitally missing teeth is among dental anomalies with different prevalence in each region. The aim of this study was to evaluate the prevalence of congenitally missing permanent teeth in Aseer region population. Materials and Methods: A descriptive, retrospective and cross-sectional study was done. Panoramic radiographs of 1050 patients (370 girls and 680 boys), 12-40 years old, were collected. The radiographs were studied for evidence of congenitally missing teeth. Data were analyzed using Paired t-test, Mann-Whitney test, Fisher exact test and Chi-square test (0.05). Results: Prevalence of congenitally missing teeth was totally 7.42%. The most frequent congenitally missing teeth was mandibular second premolars (28.21%) followed by maxillary second premolars (25.64%). Upper jaw showed significantly higher number of congenitally missing teeth (P value 0.001). According to Chi-square test, congenital missing teeth were found approximately 7.42% in both females and males and there were no statistically significant difference between sexes (P 0.19). Conclusion: The prevalence of congenitally missing teeth (CMT) in Aseer region permanent dentition was 7.42%. The most common congenitally missing teeth were mandibular second premolar fallowed by maxillary second premolars.


2013 ◽  
Vol 07 (S 01) ◽  
pp. S009-S014 ◽  
Author(s):  
Deniz Uzuner ◽  
Meltem Melik Celik ◽  
Ebubekir Toy ◽  
Candan Okay Turkdonmez

ABSTRACT Objective: The aim of this retrospective study was to assess the prevalence and distribution of hypodontia in the permanent dentition in a sample of Turkish patients who referred to the Ankara Dental Hospital for orthodontic treatment. Materials and Methods: The pre-treatment orthodontic records of 2530 patients, 1382 girls (54.62%) and 1148 boys (45.38%) between the chronological ages of 7 and 16 years, were examined for evidence of hypodontia. The third molars were excluded in this study. Results: The prevalence of hypodontia in the inspected population was 5% (3.05% for girls, 1.95% for boys). The average number of the congenitally missing teeth per patient was 2.03 (1.08 for girls, 0.95 for boys). The prevalence of the congenitally missing permanent teeth was 34% for the upper laterals, 30% for the lower second premolars, 12.5% for the upper second premolars and 23.5% for the other teeth. Most patients with hypodontia (84.9%) (57.13% for girls, 27.77% for boys) had got missing either one tooth (45.23%) or two teeth (39.67%). Conclusions: The prevalence of hypodontia in girls was higher than in boys in this sample of the Turkish patients. The upper laterals and lower second premolars were consecutively the most symmetrically absent teeth. The prevalence of advanced hypodontia was lower than single and symmetrical hypodontia.


2017 ◽  
Vol 16 (3) ◽  
pp. 467-473
Author(s):  
Mohammad Khursheed Alam ◽  
Kathiravan Purmal ◽  
Amy Low ◽  
Abdullah Pohchi

Background: Patients presenting with congenitally missing teeth are relatively common and the aim of the dental team is to create a functional, healthy, and aesthetically acceptable dentition. The consequences of missing teeth include an abnormal occlusion or an altered facial appearance which may lead to psychological distress in some patients.Methods: The present case report describes a 23 year old patient with non-syndromic, congenitally missing permanent teeth (CMMPT). Clinical and radiographic examinations revealed agenesis of eight permanent teeth including the third molars. Following interdisciplinary treatment planning, the patient was treated with mechano therapy to correct a class III incisal relationship by space closure in the lower arch. In the upper arch, the right canine was substituted for a missing lateral incisor and space was opened for a prosthetic left lateral incisor (a mini implant).Results: Active orthodontic treatment was completed in 19 months. The management of CMMPT requires an interdisciplinary approach to achieve improved occlusal function and aesthetics.Conclusion: A combined orthodontic-implant-prosthodontic treatment approach can achieve an improved functioning occlusion, and favorable aesthetics.Bangladesh Journal of Medical Science Vol.16(3) 2017 p.467-473


2012 ◽  
Vol 36 (4) ◽  
pp. 329-334 ◽  
Author(s):  
SY Park ◽  
SC Choi ◽  
BJ Choi ◽  
SJ Kim ◽  
JH Park

Congenitally missing teeth are one of the most common dental anomalies. When permanent teeth are absent, various problems can occur. It is important to consider the facial profile, position of the incisor teeth, skeletal and dental development, and available dental space before planning treatment. Possible treatment methods include preserving and retaining the deciduous tooth, replacing the missing tooth with prosthesis, placing an implant, or performing a transplant after extracting the deciduous tooth. Among these possibilities, autotransplantation combined with orthodontic treatment corrects both function and esthetics. This report describes the case of a 7-year-old girl with multiple congenitally missing teeth and an impacted right mandibular second premolar. Timely autotransplantation of the impacted mandibular tooth to the region of the congenitally missing right maxillary second premolar produced favorable results.


2005 ◽  
Vol 42 (3) ◽  
pp. 314-317 ◽  
Author(s):  
Dror Aizenbud ◽  
Semin Camasuvi ◽  
Micha Peled ◽  
Ilana Brin

Objective The purpose of the study was to determine the prevalence of congenitally missing teeth in a group of Israeli children with various types of clefts. Design Prevalence of congenitally missing teeth was determined for 179 children with cleft lip, cleft lip and alveolar ridge, cleft lip and palate, and cleft palate. Subgroupings were assessed according to patient sex, origin, cleft type, tooth type, and the side of hypodontia. The diagnosis of congenitally missing teeth (CMT) was based on initial and follow-up panoramic roentgenograms. In case of doubt, occlusal or periapical roentgenograms as well as clinical dental photographs were also used. Setting Data collection was conducted at the Rambam Medical Center, Orthodontic and Craniofacial Unit, Haifa, Israel. Results In the total cleft group, 67.6% of the patients presented with hypodontia, totaling 246 missing teeth. A statistically significant difference was found in the distribution of patients with CMT of Jewish and minority origin according to sex. Cleft lip and palate was the most frequently affected group in which 195 teeth were missing. The most frequently missing tooth among the cleft population was the maxillary incisor. The order of frequency of the other missing teeth was the same as in the normal population. Hypodontia and malformations of permanent teeth were most common on the cleft side. Conclusion The frequency of CMT in the Israeli cleft population studied was higher than in the intact population. This confirms findings in other populations worldwide.


2018 ◽  
Vol 1 (2) ◽  
pp. 98
Author(s):  
Bunga Fatimah ◽  
I Gusti Aju Wahju Ardani

Background: Dental agenesis is a term that refers to the absence of one or more teeth, and hypodontia refers to a severe type of tooth agenesis involving less than six or more than one congenitally missing teeth, excluding the third molars. Purpose: This aimed to report the correction of overbite by using intrusion archwires. Case: A 20-year-old female patient had class I malocclusion and deep overbite, incisor retroclination, mild mandibular crowding and agenesis of 12, 13, 14, 15, and 24. Case management: The case was treated with non-extraction using 0.022 pre-adjusted technique to level and unravel using intrusion archwires to correct the deep overbite. Conclusion: The 17-month treatment resulted in a corrected overbite, good occlusion, and good facial aesthetics.


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