Lymphangioleiomyomatosis Unusual Cause of Spontaneous Pneumothorax
2021 ◽
Vol 11
(6)
◽
pp. 226-230
Keyword(s):
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease, predominately affect premenopausal female. LAM could be an inherited disease associated with Tuberous Sclerosis Complex syndrome or sporadic. Most common pulmonary symptoms are dyspnea and pneumothorax. We report 31- year female, presented with right-side pneumothorax chest drainage was inserted. Further investigation revealed multiple cystic lesions in chest computed tomography images suggestive of LAM disease. She underwent video-assisted thoracoscopic surgery (VATs) to obtain a lung biopsy. Histopathology lung tissue confirms pulmonary Lymphangioleiomyomatosis. Key words: Lymphangioleiomyomatosis; Tuberous Sclerosis Complex syndrome; video-assisted thoracoscopic surgery.
2008 ◽
Vol 56
(2)
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pp. 81-84
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2003 ◽
Vol 17
(1)
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pp. 44-47
1999 ◽
Vol 13
(1)
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pp. 48-52
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2019 ◽
2015 ◽
Vol 68
(6)
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pp. 219-224
2019 ◽
Vol 68
(05)
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pp. 450-456
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2006 ◽
Vol 40
(Supplement 4)
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pp. S190