TMJ Total Joint Prosthesis in Treacher Collins Syndrome and Hemifacial Microsomia

2022 ◽  
pp. 393-412
Author(s):  
Adam Wandell ◽  
Daniel Perez ◽  
Aaron Liddell
Keyword(s):  
Treacher Collins Syndrome ◽  
Joint Prosthesis ◽  
Hemifacial Microsomia

Difficult Laryngoscopy/Intubation: The Child with Mandibular Hypoplasia

1983 ◽  
Vol 92 (4) ◽  
pp. 401-404 ◽  
Author(s):  
Steven D. Handler ◽  
Thomas P. Keon
Keyword(s):  
Temporomandibular Joint ◽  
Direct Laryngoscopy ◽  
Anterior Commissure ◽  
Difficult Laryngoscopy ◽  
Treacher Collins Syndrome ◽  
Pierre Robin Sequence ◽  
Hemifacial Microsomia ◽  
Mandibular Hypoplasia ◽  
Pierre Robin ◽  
Infants And Young Children

The child with mandibular hypoplasia (Treacher Collins syndrome, Pierre Robin sequence, hemifacial microsomia, etc) presents the otolaryngologist and anesthesiologist with considerable problems when direct laryngoscopy and/or endotracheal intubation is attempted. In addition to the small mandible, several other features of these patients contribute to the difficult laryngoscopy: macroglossia, glossoptosis, trismus related to temporomandibular joint abnormalities, and prominent maxilla or maxillary incisors. Most of the techniques that have been described for laryngoscopy/intubation in problem cases are difficult or impossible to use in infants and young children with mandibular hypoplasia. We present a modification of the standard direct laryngoscopic procedure, utilizing the 9-cm anterior commissure laryngoscope and an optical stylet in the task of exposing and intubating the larynx of a child with mandibular hypoplasia.

scholarly journals Reconstruction of the Adult Hemifacial Microsomia Patient with Temporomandibular Joint Total Joint Prosthesis and Orthognathic Surgery

2018 ◽  
Vol 2018 ◽  
pp. 1-6 ◽  
Author(s):  
Piero Cascone ◽  
Valentino Vellone ◽  
Valerio Ramieri ◽  
Emanuela Basile ◽  
Achille Tarsitano ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Temporomandibular Joint ◽  
Distraction Osteogenesis ◽  
Orthognathic Surgery ◽  
Joint Prosthesis ◽  
Hemifacial Microsomia ◽  
Primary Methods ◽  
Jaw Reconstruction ◽  
The Right ◽  
Reconstructive Techniques

Background. HFM patients’ reconstruction has always been a challenge for maxillofacial surgeons, and numerous reconstructive techniques have been described. Surgical treatment depends on the patient’s age and contemplates Temporomandibular Joint (TMJ) reconstruction in conjunction with orthognathic surgery, usually necessary following completion of growth to maximize the functional and esthetic results. Distraction osteogenesis had gained popularity as valid alternative in growing patients, but the two primary methods to reconstruct the TMJs involve the use of autogenous, using free or microvascular bone grafts, or alloplastic graft, but there is no widely accepted method. Methods. The increasing use of temporomandibular prosthesis for temporomandibular problems has led us to use them even in HFM. A case of female nongrowing patients with HFM type IIb treated with temporomandibular prosthesis in an all-in-one protocol is presented. Results. Incisal opening, measured with BioPAK system (Bioresearch Inc., Milwaukee, USA), was 21.4 mm in the presurgical period and 32.2 mm after all-in-one procedure, for an increase of 50.5%. Excursive movement to the right side was 2.2 mm in the presurgical period and was 1.5 mm after surgery, for a decrease of 31.8%. Left excursion movement changed from 5 mm to 6.1 mm, for an increase of 22.0%. Conclusions. The TMJ Concepts patient-fitted TJP in conjunction with orthognathic surgery for TMJ and jaw reconstruction is a valid option for patients with HFM.

scholarly journals Hemifacial Microsomia (HFM) and Treacher Collins Syndrome

2021 ◽  
pp. 1769-1812
Author(s):  
Manikandhan Ramanathan
Keyword(s):  
The Body ◽  
Treacher Collins Syndrome ◽  
Abnormal Development ◽  
Hemifacial Microsomia ◽  
Dentofacial Deformities ◽  
Dentofacial Deformity ◽  
Branchial Arches ◽  
Assessment And Treatment ◽  
Maxilla And Mandible ◽  
Parental Counselling

AbstractHemifacial microsomia and Treacher Collins syndrome are two entities which arise as a consequence of abnormal development of first and second branchial arches in utero. As a result, these dentofacial deformities present with abnormal facies especially the maxilla and mandible. They may also occur as part of other syndromes and may involve other structures of the body. In this chapter, we have discussed the etiology, clinical features, radiological assessment and treatment planning of such cases. Special emphasis should be made on early diagnosis, challenges of airway management and feeding and parental counselling. Since the two deformities are largely considered to be non-progressive, early distraction plays an important role in correction of the dentofacial deformity in these patients.

Ear Anomalies

2019 ◽  
pp. 63-68
Author(s):  
Robin D. Clark ◽  
Cynthia J. Curry
Keyword(s):  
Maternal Diabetes ◽  
Recurrence Risk ◽  
Treacher Collins Syndrome ◽  
Background Information ◽  
Hemifacial Microsomia ◽  
Mendelian Disorders ◽  
Organ Systems ◽  
Common Causes ◽  
Incidence Risk ◽  
Ear Anomalies

This chapter reviews background information about the incidence, risk factors, genetics, recurrence risk, family history and epidemiology of isolated and syndromic ear anomalies. The discussion on the differential diagnosis of ear anomalies summarizes its common causes, including teratogenic agents (isotretinoin, maternal diabetes, mycophenylate), chromosome anomalies (aneuploidy, 22q11 deletion), common sporadic multiple congenital anomaly syndromes (Hemifacial microsomia/Goldenhar), and Mendelian disorders that are primarily craniofacial (Treacher-Collins and other mandibulofacial dysostoses) and others that include malformations in other organ systems (CHARGE). The chapter gives recommendations for evaluation and management. A clinical case presentation features a child with mycophenylate embryopathy, who had been incorrectly diagnosed with Treacher Collins syndrome.

Craniofacial surgery

2020 ◽  
pp. 289-314
Keyword(s):  
Vascular Malformations ◽  
Common Factor ◽  
Craniofacial Surgery ◽  
Treacher Collins Syndrome ◽  
Hemifacial Microsomia ◽  
The Face ◽  
The Common ◽  
Skull Deformity ◽  
The Uk ◽  
Single Suture

Craniofacial surgery is the subspecialist area of surgery that diagnoses and manages a large heterogeneous group of both congenital and acquired conditions. The common factor is the involvement of the cranium (and its contents) and the face. This chapter first introduces craniofacial surgery and goes on to cover craniosynostosis, single-suture synostosis, syndromic synostosis, torticollis and positional skull deformity, craniofacial procedures, craniofacial clefting disorders, tumours, vascular malformations of the head and neck, hemifacial microsomia, and Treacher Collins syndrome. Finally it outlines the members of the craniofacial team, and the organization of craniofacial services in the UK.

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