scholarly journals Protruded duodenal tumor arising from Santorini’s duct of the pancreas: a rare case of intraductal papillary mucinous neoplasm mimicking a duodenal polypoid tumor

2020 ◽  
Vol 20 (1) ◽  
Author(s):  
Haruna Komatsubara ◽  
Hiroyuki Kato ◽  
Daisuke Noguchi ◽  
Kazuyuki Gyoten ◽  
Aoi Hayasaki ◽  
...  
Keyword(s):  
Intraductal Papillary Mucinous Neoplasm ◽  
Rare Case ◽  
Resected Specimen ◽  
Case Presentation ◽  
Duodenal Tumor ◽  
Mucinous Neoplasm ◽  
First Case ◽  
Enhanced Ct ◽  
Duodenal Lumen ◽  
Polypoid Tumor

Abstract Background We experienced a rare case of intraductal papillary mucinous neoplasm arising from Santorini’s duct (SD) forming a tumor protruding into the duodenum . Case presentation A 71-year-old woman was incidentally diagnosed with a 3 cm type Isp polypoid tumor in the second portion of the duodenum at another hospital. Enhanced CT and endoscopic ultrasound revealed that the origin of this protruding tumor was arising from SD and that the tumor mimicked a pedunculated duodenal tumor. Our preoperative diagnosis was a malignant pancreatic tumor arising from SD with invasion into the duodenum. She underwent a subtotal stomach-preserving pancreaticoduodenectomy, and the resected specimen showed a 25 mm tumor protruding into the duodenum with a villous surface. The pathological findings revealed that the tumor was intraductal papillary mucinous adenoma (IPMA) arising from SD. Conclusions To the best of our knowledge, this is the first case of IPMA protruding into the duodenal lumen from SD, although most of the tumors arising from SD have been reported to be malignant.

scholarly journals Intraductal papillary mucinous neoplasm of the oesophagus: an unusual case of dysphagia

2012 ◽  
Vol 94 (2) ◽  
pp. e92-e94 ◽  
Author(s):  
E Crighton ◽  
A Botha
Keyword(s):  
Surgical Resection ◽  
Intraductal Papillary Mucinous Neoplasm ◽  
Unusual Case ◽  
Heterotopic Pancreas ◽  
Common Symptom ◽  
Ivor Lewis ◽  
Mucinous Neoplasm ◽  
Extensive Search ◽  
First Case ◽  
Oesophageal Wall

We report the case of a 58-year-old woman presenting with dysphagia secondary to an intraductal papillary mucinous neoplasm arising from a heterotopic pancreas in the oesophageal wall. This was successfully treated with a laparoscopic/thoracoscopic ivor Lewis oesophagectomy. Dysphagia is the most common symptom of oesophageal tumours regardless of aetiology of the tumour and can be treated successfully with surgical resection. Through an extensive search of the literature, we found that a heterotopic pancreas in the oesophagus is extremely rare with only ten cases being reported. We describe what we believe to be the first case of a heterotopic pancreas in the oesophagus transforming into an intraductal papillary mucinous neoplasm.

scholarly journals Favorable Response After Gemcitabine-Radiotherapy for Invasive Pancreatic Intraductal Papillary Mucinous Neoplasm: A Case Report

2013 ◽  
Vol 98 (4) ◽  
pp. 340-345 ◽  
Author(s):  
Takanori Ochiai ◽  
Kimihiro Igari ◽  
Takaki Furuyama ◽  
Hiromitsu Ito ◽  
Yusuke Mitsunori ◽  
...  
Keyword(s):  
Pancreatic Duct ◽  
Intraductal Papillary Mucinous Neoplasm ◽  
Ductal Carcinoma ◽  
Total Pancreatectomy ◽  
Surgical Margin ◽  
Resected Specimen ◽  
Pancreatic Ductal Carcinoma ◽  
Positive Surgical Margin ◽  
Mucinous Neoplasm ◽  
Remnant Pancreas

Abstract The efficacy of chemoradiotherapy for invasive pancreatic ductal carcinoma derived from an intraductal papillary mucinous neoplasm (IPMN) has not been established. The subject of the present report was a 53-year-old man admitted for the treatment of IPMN. The tumor, located in the pancreatic body, was of the mixed type of IPMN, and it involved the branch duct, where it was 38 mm in diameter, and the main duct, where it was 6 mm in diameter. Distal pancreatectomy was performed and the postoperative course was uneventful; however, histopathologic diagnosis revealed invasive ductal carcinoma with a positive surgical margin in the pancreatic duct. Although total pancreatectomy was recommended, chemoradiotherapy (50.4-Gy irradiation and gemcitabine) was preferred by the patient. At 9-month follow up, computed tomography and magnetic resonance imaging showed a cystic mass at the surgical margin of the pancreas. Endoscopic ultrasonography showed a 44-mm cystic lesion with nodules in the remnant pancreas, on the basis of which he underwent total pancreatectomy. Pathologic examination of the resected specimen revealed absence of the epithelium at the surgical margin of the main pancreatic duct, and malignant cells were not detected.

Fatal Case of Vulvar Pyoderma Gangrenosum with Pulmonary Involvement: Case Presentation and Literature Review

2014 ◽  
Vol 18 (6) ◽  
pp. 424-429 ◽  
Author(s):  
Joshua M. Mercer ◽  
Paul Kuzel ◽  
Muhammad N. Mahmood ◽  
Alain Brassard
Keyword(s):  
Literature Review ◽  
Pyoderma Gangrenosum ◽  
Rare Case ◽  
Fatal Case ◽  
Pulmonary Involvement ◽  
Review Of The Literature ◽  
Treatment Resistant ◽  
Case Presentation ◽  
First Case ◽  
Systemic Therapies

Introduction: We report a case of a 61-year-old woman with locally destructive vulvar pyoderma gangrenosum (PG) with pulmonary involvement who was refractory to numerous systemic therapies and developed complications resulting in her demise. Objective: To report a rare case of treatment-resistant vulvar PG with pulmonary involvement that proved to be fatal. Methods: PubMed was used to search for other reports that discuss PG, or more specifically perigenital PG, with pulmonary involvement. Results and Conclusion: A thorough review of the literature revealed 33 cases of PG with pulmonary involvement, with only 4 involving the perigenital region. We report the second case of a female with vulvar PG and pulmonary involvement. In contrast to the first case described, our patient did not respond to systemic therapy, and, ultimately, her disease was fatal. It is hoped that with continued documentation of this rare and potentially lethal presentation of PG, physicians will determine more effective treatments.

scholarly journals Intraductal Papillary Mucinous Neoplasm Presenting as Bleeding Duodenal Mass: A Surgical Rarity

2020 ◽  
Vol 18 (1) ◽  
Author(s):  
Nornazirah Azizan ◽  
Firdaus Hayati ◽  
Andee Dzulkarnaen Zakaria ◽  
Nordashima Abd Shukor
Keyword(s):  
Intraductal Papillary Mucinous Neoplasm ◽  
Surgical Intervention ◽  
Pancreatic Neoplasm ◽  
Massive Bleeding ◽  
Intestinal Bleeding ◽  
Recurrent Pancreatitis ◽  
Imaging Studies ◽  
Mucinous Neoplasm ◽  
First Case ◽  
Final Histological Diagnosis

Intraductal papillary mucinous neoplasm (IPMN) is a rare pancreatic neoplasm. The presentation varies from recurrent pancreatitis, steatorrhea and weight loss to incidental findings during imaging studies. The recognition of IPMN is crucial in deciding for prompt surgical intervention, which is the best treatment modality for this precancerous condition. Here, we report a case of 55-year-old man with massive upper gastro intestinal bleeding arising from a huge fungating duodenal mass. In view of massive bleeding, a decision for emergency Whipple's pancreaticoduodenectomy was made. Final histological diagnosis confirmed as IPMN. To the best of our knowledge, this is the first case of IPMN presented with a huge fungating duodenal mass causing massive UGIB requiring surgical intervention.

scholarly journals Incidental para-ureteral aggressive angiomyxoma: a rare case report and literature review

BMC Urology ◽  
2020 ◽  
Vol 20 (1) ◽  
Author(s):  
Ming Liu ◽  
Ting-Shuai Zhai ◽  
Xiao-Feng Zhao ◽  
Li-Jin Feng ◽  
Xin-Sheng Lyu ◽  
...  
Keyword(s):  
Literature Review ◽  
Rare Case ◽  
Reproductive Age ◽  
Aggressive Angiomyxoma ◽  
Case Presentation ◽  
Left Ureter ◽  
First Case ◽  
Rare Case Report

Abstract Background Aggressive angiomyxoma (AA) is a rare tumor that typically occurs in the pelvis and perineum, most commonly in women of reproductive age. However, no para-ureteral AA has been reported according to the literature. Case presentation We herein describe the first case of para-ureteral AA. A 62-year-old male presented to our institute in March 2017 with a para-ureteral mass that was 15 mm in diameter incidentally. No symptom was observed and laboratory analysis was unremarkable. Magnetic resonance and computed tomography imaging showed a non-enhancing mass abutting the left ureter without causing obstruction. Laparoscopic resection of the mass was performed without injury to the ureter. Pathologic and immunohistochemical results were consistent with AA. Till now, no recurrence was noticed. Conclusions We reported a rare case of para-ureteral AA, along with a literature review. Early diagnosis, proper surgical plan and long-term close follow-up is recommended for its high risk of recurrence and malignant potential.

scholarly journals An extremely rare case of Rosai-Dorfman disease in the spleen

BMC Surgery ◽  
2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Xuewu Yang ◽  
Chuang Fang ◽  
Yuanpu Sha ◽  
Qi Li ◽  
Xing Zhang ◽  
...  
Keyword(s):  
Rare Case ◽  
Young Male ◽  
Abdominal Ultrasonography ◽  
Case Presentation ◽  
Rosai Dorfman Disease ◽  
Enhanced Ct ◽  
Splenic Involvement ◽  
Next Generation Sequencing Ngs ◽  
Generation Sequencing ◽  
Ct And Mri

Abstract Background Rosai-Dorfman disease (RDD) is a rare, multisystemic histiocytic disorder, and commonly manifesting as lymphadenopathy in the young male. Abdominal manifestations of RDD are extremely rare. Case presentation In August 2018, a 42-year-old man underwent an abdominal ultrasonography examination due to his weight loss of 10 kg in only three months and found a giant solid tumor was found in his spleen. Then, he was admitted to our hospital and diagnosed as a splenic mass via abdominal enhanced CT and MRI. Laparoscopic splenectomy was administrated within six days of admission due to the clear surgical indications. The pathogenesis of RDD remained poorly understood and the disease should be diagnosed based on histopathology and immunohistochemistry (IHC). The mutations in ATM and NFKBIA were observed using next generation sequencing (NGS). Conclusion We reported a case of splenic involvement of RDD with NGS genetic testing, indicating the difficulty of making a diagnosis before surgery. This extremely rare case offers new references for the understanding of abdominal viscera RDD.

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