scholarly journals Recurrent dermatofibrosarcoma protuberans of head and neck with fibrosarcomatous change: a challenge for the head and neck surgeon

Author(s):  
Balaji Ramamourthy ◽  
Kanika Arora ◽  
Balamurugan Thirunavukkarasu ◽  
Anurag S. Ramavat ◽  
Amanjit Bal

<p class="abstract">Dermatofibrosarcoma protuberans (DFSP) of head and neck is a rare, slow growing, intermediate to low grade malignant soft tissue neoplasm with high rates of local recurrence requiring multiple surgeries posing great distress for both the patient and treating physician alike. Fibrasarcomatous change is a very rare occurrence in such tumors increasing risk of distant metastasis. We report such a rare case of recurrent DFSP with fibrosarcomatous change of the head and neck region, the management protocol and the key points a surgeon should keep in mind while treating such patients.</p><p class="abstract"> </p>

Author(s):  
Chandra Veer Singh ◽  
Sheetal Radia ◽  
Saalim Sheikh ◽  
Vijay Haribhakti

<p class="abstract">Schwannoma are slow growing tumours, which can arise from any peripheral nerve. 10% of schwannomas that occur in the head and neck region mostly originate from the vagus or sympathetic nervous system. Extracranial schwannomas in the head and neck region are rare neoplasm. Intraoral schwannoma are only 1% of the all head and neck tumours. Diagnosis is established by imaging studies such as magnetic resonance imaging or computed tomography, while FNAC is used to rule out other conditions. We report a rare case of lingual schwannomas generally present as a painless lump schwannoma of the tongue in a 27-year-old male complaining of asymptomatic swelling over a posterolateral surface of the tongue, treated by complete surgical excision. The diagnosis was established on the basis of clinical, histopathological, and immunohistochemical examination. We report a rare case of schwannoma over the posterolateral surface of tongue. Prognosis is good for the patient when this condition is correctly diagnosed as the condition rarely recurs after complete resection.</p>


2010 ◽  
Vol 67 (7) ◽  
pp. 596-599
Author(s):  
Milan Jovanovic ◽  
Ljiljana Cvorovic ◽  
Rastislav Poljovka ◽  
Aleksandar Oroz ◽  
Ljubomir Pavicevic

Introduction. Schwannomas are tumors of neurogenic origin, that arise from Schwann cells which surround peripheral, cranial and autonomic nerves. Schwannomas account for only 5% of all benign soft tissue tumors, and 25-45% of extracranial schwannomas are present in the head and neck region. They are usually classified according to the nerve of origin and the site within the head and neck. Case report. We presented extremely rare extracranial localizations of schwannomas and discussed about diagnosis and management of these tumors. Conclusion. Schwannomas are slow-growing tumors and late symptoms appearance may cause a delay in diagnosis and treatment of patients with these tumors. An appropriate diagnostic protocol is indispensable tool in performing a differential diagnosis of malignant from benign lesions. Choice of surgical approach depends on schwannomas localization.


2020 ◽  
Vol 13 (4) ◽  
pp. e232485
Author(s):  
Beena R Varma ◽  
Krishna Santhosh Kumar ◽  
Rhea Susan Verghese ◽  
Mahija Janardhanan

Lipomas are benign soft tissue neoplasm which rarely occur in the oral cavity. Of the total reported cases of lipoma, only about 15% to 20% of cases have occurred in the head and neck region and the tongue is an even rarer site with only about 4% of the reported cases occurring in that region. They are slow growing and usually asymptomatic in nature. When it grows to a large size, it can hinder the physiological processes that are associated with the area. This case report describes the diagnostic features of tongue lipoma with a brief review of literature.


2020 ◽  
Vol 17 (1) ◽  
pp. 63-65
Author(s):  
Anisha Joshi ◽  
Deeptara Pathak Thapa

Schwannomas/ neurilemmomas are benign tumors of nerve sheath arising from Schwann cells that form myelin sheath around peripheral nerves. They are usually solitary, slow growing and encapsulated lesions. Head and neck are the common sites. We report a case of a 38 years old Nepalese female who had presented with a solitary asymptomatic, slow growing nodule on the left side of the chin for the last three years. Dermoscopy of the lesion revealed arborizing vessels with brownish pigmentation overlying a whitish to pinkish background. Complete excision of the lesion was performed. Histopathological evaluation of the lesion revealed schwannoma. Though schwannomas are a rare diagnosis, they should be considered as a differential diagnosis of any unilateral, asymptomatic, slow growing nodule in the head and neck region. Dermoscopy is a useful tool which helps to differentiate schwannoma from other lesions. Histopathology is the gold standard for diagnosis and the treatment of choice is surgical excision.  


2014 ◽  
Vol 57 (4) ◽  
pp. 162-164 ◽  
Author(s):  
Petr Kordač ◽  
Dimitar Hadži Nikolov ◽  
Katarína Smatanová ◽  
David Kalfeřt

Low-grade myofibroblastic sarcoma (LGMS) is a very rare, atypical myofibroblastic tumor with fibromatosis-like features with predilection mostly in head and neck region. LGMS occurs primarily in adult patients with a slight male predominance. Only few cases of LGMS affecting the larynx have been reported in literature to this date. We describe a case of low-grade myofibroblastic sarcoma of the larynx in a 40-year-old male patient. The clinicopathological characteristics, immunohistochemical findings and treatment are discussed.


2020 ◽  
Vol 13 (1) ◽  
pp. 78-82
Author(s):  
Brihaspati Sigdel ◽  
Rajesh Maharjhan ◽  
Tulika Dubey ◽  
Bhima Neupane

Hemangiomas of the head and neck region comprise about 60 to 70% of all benign tumors. Intramuscular hemangioma is a rare, slow-growing, angiomatous tumor. We report a rare case of an Intramuscular Hemangioma of Right sternocleidomastoid muscle in a six years old girl presenting for four years and with extensive involvement necessitating excision. Microscopic excision reduces the risk of recurrence.


2021 ◽  
Vol 14 (5) ◽  
pp. e237083
Author(s):  
Muhammad Hammad Deewani ◽  
Muhammad Hassan Danish ◽  
Muhammad Sohail Awan ◽  
Nasir Ud Din

Low-grade fibromyxoid sarcoma (LGFMS) is an uncommon soft-tissue malignancy. LGFMS preferentially affects trunks and extremities of young adults; however, occasional cases have been reported in different sites of head and neck region including oral cavity, larynx and oropharynx. LGFMS usually exhibit areas of collagenised and myxoid stroma with appearance of spindle cells in whorling pattern. It is a challenge to diagnose it accurately as most of the time it is misdiagnosed as benign neoplastic entity of spindle cells. There have been only few isolated cases of LGFMS reported in head and neck region and LGFMS originating from the parapharyngeal space has never been reported before. We recently experienced a case of low grade fibomyxoid sarcoma in parapharyngeal space of neck. LGFMS have the propensity to locally recur and to metastasise. Due to its rarity in head and neck region, there are no well-established treatment and follow-up guidelines.


2016 ◽  
Vol 2016 ◽  
pp. 1-4 ◽  
Author(s):  
Gimena Castro Pérez ◽  
Cintia Arias ◽  
Paula Luna ◽  
Irene Sorín ◽  
Luis Daniel Mazzuoccolo

Dermatofibrosarcoma protuberans (DFSP) is a malignant fibrohistiocytic tumor that appears exclusively on the skin. It is a low-grade malignant soft tissue tumor of subcutaneous tissues that has a propensity for local recurrence but seldom metastasizes. It may rarely occur on the head and neck accounting for less than one percent of total head and neck malignancies. We present a man with a giant DFSP on the face. Oncological, functional, and aesthetic aspects are set forth.


2021 ◽  
Vol 10 (22) ◽  
pp. 1735-1738
Author(s):  
Geetha Rajendran ◽  
Karthik Ragupathy ◽  
Sanjay Pasupathy ◽  
Ganesh Ramakrishnan ◽  
Kiruthika Shriranjani

Schwannomas are relatively rare benign neoplasms of neurogenic origin from the neural sheath of peripheral nerves occurring more commonly in the head and neck. Mandibular bone is the commonest site of occurrence of these nerve lesions. Radiographically, intraosseous schwannoma of mandible is very difficult to differentiate from other bony pathologies such as neurofibroma, ameloblastoma, fibrous dysplasia, myxoma, central giant cell lesion, or periapical lesion, so it should be included in the differential diagnosis of lower jaw swelling. Schwannoma as a pathologic entity was first reported in 1910 by Verocay. Schwannoma (also known as neurinoma, neurolemmoma, neurilemmoma, perineural fibroblastoma, and peripheral nerve sheath tumour) is a rare, slowgrowing, benign neurogenic neoplasm that originated from Schwann cells. Schwann cells cover myelinated sheath of nerve fibres.1 These intraosseous schwannomas account for not more than 1 % of the central neoplasms. More than one third of all schwannomas are found in the head and neck region. 2 Most of these originate from the lower cranial nerve and sympathetic nervous system. Schwannomas from the upper cranial nerves such as trigeminal nerve and its branches are less common. Other commonly reported sites include the vertebra, clavicle, ribs, sacrum, humerus, ulna radius, etc. This painless slow-growing neoplasm may develop at any age.


2004 ◽  
Vol 118 (2) ◽  
pp. 156-158 ◽  
Author(s):  
Robert Almeyda ◽  
Prasad Kothari ◽  
Ha Chau ◽  
Vincent Cumberworth

Neurilemmomas are slow growing, benign neoplasms of neural crest Schwann cell origin. They arise from any peripheral, spinal or cranial nerve except the olfactory and optic. Presentation is usually asymptomatic but focal neurological signs and symptoms may be associated with nerve compression. With approximately one third of all documented cases presenting in the head and neck region, we report a case of a submandibular neurilemmoma misdiagnosed pre-operatively. The diagnostic difficulties are discussed and the current literature reviewed. Thiscase highlights the importance of inclusion of nerve sheath tumours in differential diagnoses of soft tissue lesions in the head and neck.


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