scholarly journals Cor Triatriatum Sinistrum

2021 ◽  
Vol 21 (2) ◽  
pp. e324-326
Author(s):  
Al Rumitha Al Sabri ◽  
Niranjan Joshi ◽  
Hamood Al Kindi ◽  
Khalfan S Al Senaidi
Keyword(s):  
Heart Failure ◽  
Pulmonary Hypertension ◽  
Male Infant ◽  
Surgical Excision ◽  
University Hospital ◽  
Cor Triatriatum ◽  
Uneventful Recovery ◽  
Cardiac Anomaly ◽  
Sultan Qaboos University ◽  
Congenital Cardiac Anomaly

Cor triatriatum sinistrum (CTS) is a rare congenital cardiac anomaly characterised by an abnormal septum within the left atrium impairing blood flow to the left ventricle. We report the case of a two-month-old male infant who presented with symptoms of heart failure since the age of two weeks. He was admitted to a local hospital and was managed with antibiotics because of the impression of pneumonia. Due to persistent unresolved tachypnoea and tachycardia, he was referred to Sultan Qaboos University Hospital, Muscat, Oman, in 2019 for cardiac evaluation which confirmed a diagnosis of isolated CTS with severe stenosis and pulmonary hypertension. He underwent an urgent surgical excision of the membrane with uneventful recovery. Keywords: Cor Triatriatum Sinistrum; Congenital Heart Disease; Pulmonary Hypertension; Heart Failure; Case Report; Oman.

scholarly journals Isolated Cor Triatriatum Sinister: A Case Report

2020 ◽  
Vol 18 (1) ◽  
pp. 28-30
Author(s):  
Zanda Grīnberga ◽  
Pauls Sīlis ◽  
Elīna Ligere ◽  
Ingūna Lubaua ◽  
Inta Bergmane ◽  
...  
Keyword(s):  
Left Atrium ◽  
Pulmonary Veins ◽  
Surgical Excision ◽  
Venous Drainage ◽  
Treatment Method ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
The Right

SummaryCor triatriatum sinister is a rare congenital cardiac anomaly that has been identified in 0.1% of children with congenital heart disease. It is defined as a fibromuscular membrane that divides the left atrium into two chambers: a superior (proximal) that in most cases receives drainage from the pulmonary veins and an inferior (distal) chamber that communicates with the mitral valve and the left atrium. Cor triatriatum sinister can be an isolated lesion (approximately 25% of cases), but in many cases it is associated with other congenital cardiovascular anomalies, the most common one being – atrial septal defect(3). Symptoms in patients with cor triatriatum sinister are related to obstruction of pulmonary venous drainage, pressure loading of the right side of the heart and congestive cardiac failure. Depending on the severity of the obstruction and presence of associated cardiac anomalies it can be diagnosed at any age. Diagnosis is usually achieved by echocardiography in early infancy. Elective treatment method is surgical excision of the membrane. Here we present a pediatric patient (4 months old) presenting in cardiogenic shock with a successful correction of isolated cor triatriatum sinister. To confirm diagnosis and success of surgical repair, transthoracic and transesophageal echocardiography were used.

Cor Triatriatum Dexter: A Rare Cause of Aneurysmal Right Atrium

2021 ◽  
pp. 215013512110366
Author(s):  
Mrinal Patel ◽  
Nikunj Vaidhya ◽  
Kartik Patel ◽  
Megha Sheth ◽  
Amit Mishra
Keyword(s):  
Right Atrium ◽  
Surgical Excision ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Age Group ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Dexter

Cor triatriatum dexter (CTD) is a rare congenital cardiac anomaly with a diverse presentation in every age group. We report a case of CTD in a 36-year-old female who presented with palpitations due to giant right atrium (RA), which we managed successfully with surgical excision of the membrane and RA reduction.

scholarly journals A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

2020 ◽  
Vol 2020 ◽  
pp. 1-3
Author(s):  
Can Yilmaz Yozgat ◽  
Erkan Cakir ◽  
Hakan Yazan ◽  
Hafize Otcu Temur ◽  
Kahraman Yakut ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Arteriovenous Malformation ◽  
Pulmonary Arteries ◽  
Venous Hypertension ◽  
Pulmonary Arteriovenous Malformation ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Arteries And Veins

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.

Cor Triatriatum: A Review

2017 ◽  
Vol 21 (2) ◽  
pp. 178-185 ◽  
Author(s):  
Ajay Kumar Jha ◽  
Neeti Makhija
Keyword(s):  
Heart Failure ◽  
Sudden Cardiac Arrest ◽  
Cor Triatriatum ◽  
Definitive Treatment ◽  
Cardiac Anomaly ◽  
Classical Form ◽  
Congenital Cardiac Anomaly ◽  
Systemic Embolization ◽  
Congenital Cardiac Anomalies ◽  
Cardiac Asthma

Cor triatriatum is a rare congenital cardiac anomaly defined by an abnormal septation within the atrium (left or right) leading to inflow obstruction to the respective ventricles. It exists either in isolated classical form or may be associated with simple to complex congenital cardiac anomalies. Several anatomical variants exist even in the classical form, and therefore, it may require multimodal diagnostic modalities to characterize and differentiate for better percutaneous interventional or surgical planning. It commonly presents in infancy but may remain undetected till death. Symptomatology typically mimics mitral and tricuspid stenosis in sinister and dexter varieties, respectively. However, features of systemic embolization, heart failure, atrial fibrillation, cyanosis, cardiac asthma, syncope, and sudden cardiac arrest have also been reported in the literature. Surgical correction under cardiopulmonary bypass is the preferred treatment. Nevertheless, balloon dilatation may be considered in anatomically compatible variants and in special circumstances, such as heart failure, pregnancy, or as a bridge to definitive treatment.

Cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein

2013 ◽  
Vol 24 (3) ◽  
pp. 546-548 ◽  
Author(s):  
Claire Galoin-Bertail ◽  
Marielle Gouton
Keyword(s):  
Pulmonary Hypertension ◽  
Atrial Septal Defect ◽  
Septal Defect ◽  
Venous Return ◽  
Innominate Vein ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Anomalous Pulmonary Venous Return

AbstractCor triatriatum sinister is an uncommon congenital cardiac anomaly accounting for 0.1% of all congenital cardiac malformations, with an anomalous venous return being a frequently associated condition. We present the case of a 14-year-old girl misdiagnosed as having an atrial septal defect with pulmonary hypertension who actually had a cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein.

scholarly journals Cor Triatriatum Sinister in a 25 Year Old Patient - A Case Report

2020 ◽  
Vol 2020 ◽  
Author(s):  
Ketak Nagare
Keyword(s):  
Balloon Dilatation ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Early Age ◽  
Corrective Surgery ◽  
Emergency Case ◽  
Adult Age ◽  
Congenital Cardiac Anomaly ◽  
Choice Of Treatment ◽  
Cor Triatriatum Sinister

Cor triatriatum sinister is a rare congenital cardiac anomaly in which a fibromuscular membrane divides the left atria into 2 chambers. It is even rarer when present at an adult age. Symptoms and presentation of the patient depend on the size of the opening into the membrane through which 2 chambers of left atrium communicate with each other. Cor triatriatum sinister rarely remains asymptomatic till adulthood. In adults symptoms of Cor triatriatum sinister mimic the symptoms of mitral stenosis. Corrective surgery is the choice of treatment, but when it present as an emergency case especially at an early age, balloon dilatation of the membrane opening is done. Elective balloon dilatation of membrane opening at an early age diagnosed with Cor triatriatum sinister followed by corrective surgery at an adult age can be a safer option compared to direct corrective surgery at an early age.  We present a case of a 25-year-old female who was diagnosed first time at this age as cor triatriatum sinister and treated successfully with corrective surgery.

Severe right heart failure and pulmonary hypertension because of cor triatriatum sinister in a 54year-old patient

2011 ◽  
Vol 151 (1) ◽  
pp. e29-e31 ◽  
Author(s):  
Erkan İlhan ◽  
Mehmet Ergelen ◽  
Özer Soylu ◽  
Rodi Tosu ◽  
Tolga Sinan Güvenç ◽  
...  
Keyword(s):  
Heart Failure ◽  
Pulmonary Hypertension ◽  
Right Heart Failure ◽  
Cor Triatriatum ◽  
Right Heart ◽  
Cor Triatriatum Sinister

scholarly journals Unexpected Echocardiographic Findings: Accessory Mitral Valve Tissue in Adults

2020 ◽  
Author(s):  
Ying Rao ◽  
Wei Chen ◽  
Yu Wang ◽  
wenjuan Song
Keyword(s):  
Mitral Valve ◽  
Heart Diseases ◽  
Incidental Finding ◽  
Surgical Excision ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Valve Tissue ◽  
Accessory Mitral Valve Tissue

Abstract Background: Accessory mitral valve tissue (AMVT) is a rare congenital cardiac anomaly, which is associated with other congenital heart diseases. It is diagnosed in neonates or childhood and rarely in adulthood. Nevertheless, AMVT is an incidental finding or described as isolated. Echocardiography, especially three-dimensional(3D) echocardiography is considered as an optimal imaging technique for AMVT diagnosis.Case presentation: We herein presented the two asymptomatic adult cases with AMVT, who presented with varying degrees of symptomatic left ventricular outflow tract (LVOT) obstruction. One presented with mild LVOT obstruction and no surgery was required, and another one with significant LVOT obstruction was recommended for surgical excision.Conclusions: We emphasized the usefulness of echocardiography in the morphology detection of AMVT, and the importance of operation guidance and follow-up.

Cardiac examination in children with Laron syndrome undergoing mecasermin therapy

2018 ◽  
Vol 31 (6) ◽  
pp. 675-679 ◽  
Author(s):  
Nurdan Erol ◽  
Metin Yıldız ◽  
Ayla Güven ◽  
Ayse Yıldırım
Keyword(s):  
Growth Hormone ◽  
Pulmonary Hypertension ◽  
Demographic Data ◽  
Hormone Deficiency ◽  
Cardiac Anomaly ◽  
Recessive Trait ◽  
Laron Syndrome ◽  
Congenital Cardiac Anomaly ◽  
Normal Ranges ◽  
Receive Treatment

Abstract Background: Laron syndrome (LS), which can be defined as primary growth hormone resistance or insensitivity, is a rare genetic disease inherited by an autosomal recessive trait. Although it is undistinguishable from growth hormone deficiency, LS has high levels of growth hormone, but insulin-like growth factor (IGF-1) cannot be synthesized. Mecasermin treatment is the only option for the patients who suffer from LS. This study aims to research cardiac findings of children with LS, who receive treatment with mecasermin. Methods: The study enrolled five children four males and one female, 4 M/1 F with LS, two of whom were siblings with a mean age of 6.3±2.1 years, a body weight of 13.36±4.74 kg, a height of 88±8.7 cm, and a body mass index (BMI) of 16.47±3.35. Their demographic data were obtained from their family and files. The children received mecasermin via subcutaneous injection at 0.04–0.12 μg/kg doses twice per day. The duration of mecasermin treatment was 8–53 months. All of them were examined clinically by electrocardiogram and echocardiogram. Results: Their cardiac examinations were normal, except for one case, who had systolic murmur at cardiac auscultation. Arrhythmia was not observed on their electrocardiograms. The echocardiograms did not show a significant congenital cardiac anomaly. Their cardiac measure and functions were within normal ranges. The echocardiogram of the child with the murmur showed mitral and tricuspid insufficiency. The Doppler images showed pulmonary hypertension findings. These findings were proven by angiography. The vasoreactivity test results of that patient were negative. No reason could be found for the observed pulmonary hypertension. We diagnosed this finding as a primary pulmonary hypertension and Bosentan therapy was started. Conclusions: In this study, we showed that cardiac findings were consistent with previous studies. To the best of our knowledge, the observed pulmonary hypertension in children with LS, who received treatment with or without mecasermin, is reported for first time in the literature.

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