A assistência de enfermagem em crianças e adolescentes portadores de anemia falciforme

Anemia Falciforme é uma doença autossômica recessiva com elevada prevalência e morbimortalidade no Brasil. Apresenta uma variedade de complicações que se manifestam de forma peculiar em cada paciente, principalmente na infância e na adolescência. Levantar os diagnósticos e intervenções de enfermagem mais relevantes às crianças e aos adolescentes portadores da doença para proporcionar uma melhor qualidade de vida. Realizou-se o levantamento bibliográfico sobre o tema nas bases de dados SciELO, LILACS e AAFESP, além de dados sobre mortalidade da doença no portal DATASUS. Em 2008, 38,6% das mortes por Anemia Falciforme no Brasil compreendeu a faixa etária entre 0 e 19 anos, evidenciando a necessidade de uma assistência de enfermagem específica, baseada na prevenção e no tratamento das principais complicações da doença. O preparo do enfermeiro é fundamental para individualizar essa assistência junto às crianças e adolescentes portadores da doença para que se obtenha sucesso na prevenção das crises e no tratamento para amenizar os sintomas.Descritores: Enfermagem, Anemia Falciforme, Crianças e Adolescentes. Nursing care in children and adolescents with sickle cell anemiaAbstract: Sickle cell anemia is an autosomal recessive disease with a high prevalence, morbidity and mortality in Brazil. Features a variety of complications that manifest in a peculiar way in each patient, especially in childhood and adolescence. Raise the diagnoses and nursing interventions most relevant to children and adolescents with the disease to provide a better quality of life. We carried out the literature on the subject in the databases SciELO, LILACS and AAFESP, plus data on mortality rates in DATASUS portal. In 2008, 38.6% of deaths from sickle cell disease in Brazil comprised the age group between 0 and 19 years, highlighting the need for specific nursing care based on prevention and treatment of major complications of the disease. The preparation of nurses is critical to individualize this intervention with children and adolescents with the disease in order to achieve success in crisis prevention and treatment to alleviate the symptoms.Descriptors: Nursing, Sickle Cell Anemia, Children and Adolescents. Enfermería de atención a la infancia y la adolescencia con anemia de células falciformesResumen: La anemia falciforme es una enfermedad autosómica recesiva, con una alta prevalencia, morbilidad y mortalidad en Brasil. Cuenta con una variedad de complicaciones que se manifiestan de una manera peculiar en cada paciente, especialmente en la infancia y la adolescencia. Elevar los diagnósticos e intervenciones de enfermería más relacionados con los niños y adolescentes con la enfermedad de proporcionar una mejor calidad de vida. Hemos llevado a cabo la literatura sobre el tema en la bases de datos SciELO, LILACS y AAFESP, además de datos sobre las tasas de mortalidad en DATASUS portal. En 2008, el 38,6% de las muertes por la enfermedad de células falciformes en Brasil comprende el grupo de edad entre 0 y 19 años, destacando la necesidad de cuidados de enfermería específicos basados en la prevención y tratamiento de las principales complicaciones de la enfermedad. La preparación de las enfermeras es fundamental para individualizar la intervención con niños y adolescentes que padecen la enfermedad con el fin de lograr el éxito en la prevención de crisis y el tratamiento para aliviar los síntomas.Descriptores: Enfermería, Anemia de Células Falciformes, la Niñez y la Adolescencia.

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Comprehensive neuropsychological evaluation of children and adolescents with sickle cell anemia: a hospital-based sample

Revista Brasileira de Hematologia e Hemoterapia ◽

10.1016/j.bjhh.2016.09.004 ◽

2017 ◽

Vol 39 (1) ◽

pp. 32-39 ◽

Cited By ~ 5

Author(s):

Samantha Nunes ◽

Nayara Argollo ◽

Marivania Mota ◽

Camilo Vieira ◽

Eduardo Pondé de Sena

Keyword(s):

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Neuropsychological Evaluation

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Cognitive Functioning And Academic Achievement In Children And Adolescents With Sickle Cell Anemia:, A Meta-Analysis

10.35395/1728-007-003-104 ◽

2020 ◽

pp. 1663

Author(s):

Faiza Semai

Keyword(s):

Academic Achievement ◽

Cognitive Functioning ◽

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Meta Analysis

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Hypnotically Induced Pain Control in Sickle Cell Anemia

PEDIATRICS ◽

10.1542/peds.64.4.533 ◽

1979 ◽

Vol 64 (4) ◽

pp. 533-536

Author(s):

Lonnie Zeltzer ◽

Jerry Dash ◽

J. Paul Holland

Keyword(s):

Sickle Cell Disease ◽

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Pain Control ◽

Gain Control ◽

Disease Status ◽

Similar Technique ◽

Cell Disease

Recurrent painful vaso-occlusive crises often represent sources of frustration and debilitation to those afflicted with sickle cell disease. We present two adolescents with sickle cell disease who have been able to gain control over the frequency and intensity of these crises by utilizing self-hypnosis. We feel that the utilization of similar technique(s) may allow many ill children and adolescents to obtain mastery over abnormal physiologic processes concomitant with their particular disease status.

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Growth and nutritional status of children and adolescents with sickle cell anemia

The Egyptian Journal of Haematology ◽

10.4103/ejh.ejh_15_20 ◽

2020 ◽

Vol 45 (4) ◽

pp. 188

Author(s):

MeaadK Hassan ◽

RaadS Fadhil ◽

LamiaM Al-Naama

Keyword(s):

Nutritional Status ◽

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Nutritional Status Of Children

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Complicações de estomia intestinal e pele periestoma: evidências para o cuidado de enfermagem [Complications of ostomy bowel and peristomal skin: evidence for nursing care] [Complicaciones de la ostomía intestinal y de la piel peristoma: evidencia para el cuidado de enfermeira]

Revista Enfermagem UERJ ◽

10.12957/reuerj.2019.45758 ◽

2019 ◽

Vol 27 ◽

pp. e45758

Author(s):

Marina Bavaresco ◽

Geruza Maria Da Silva Gonçalves Manfredini ◽

Camila Mendonça de Moraes ◽

Rogério Silva Lima ◽

Silvana Maria Coelho Leite Fava ◽

...

Keyword(s):

Nursing Care ◽

Surgical Techniques ◽

Educational Programs ◽

Intestinal Loop ◽

Calidad De Vida ◽

Prevention And Treatment ◽

Peristomal Skin ◽

Innovative Techniques

Objetivo: identificar e analisar as evidências disponíveis na literatura sobre as complicações de estomia intestinal e pele periestoma. Método: revisão integrativa, em bases virtuais de dados, com inclusão de estudos do tipo ensaio clínico randomizado, publicados nos idiomas inglês, espanhol e português, no período de maio 2013 a maio de 2019. Resultados: foram selecionados 19 estudos e agrupados em três categorias: técnicas cirúrgicas apontando técnicas inovadoras acerca do tipo de suturas, ressecção e exteriorização de alça intestinal, além de reforços para prevenção de hérnias; barreiras de pele e equipamentos coletores, abordando principalmente as barreiras de pele para prevenção e tratamento da dermatite; cuidados de enfermagem mostrando cuidados e programas de acompanhamento, como visitas domiciliares, consultas e programas educativos. Conclusões: As estratégias descritas nos estudos revisados são importantes na medida em que poderão enriquecer o conhecimento do enfermeiro e dessa forma reduzir complicações de estomia e pele periestoma e melhorar a qualidade de vida dessas pessoas.ABSTRACTObjective: to identify and analyze the evidence available in the literature on the complications of intestinal ostomy and peristomal skin. Method: integrative review in virtual databases, including randomized clinical trial studies published in English, Spanish and Portuguese, from May 2013 to May 2019. Results: 19 studies were selected and grouped into three categories: surgical techniques pointing innovative techniques about the type of sutures, resection and externalization of the intestinal loop, in addition to reinforcements to prevent hernias; skin barriers and collecting equipment, mainly addressing skin barriers for the prevention and treatment of dermatitis; nursing care showing care and follow-up programs such as home visits, consultations, and educational programs. Conclusion: the strategies described in the reviewed studies are important as they may enrich the knowledge of nurses and thus reduce complications of ostomy and peristome skin and improve the quality of life of these people.RESUMENObjetivo: identificar y analizar la evidencia disponible en la literatura sobre las complicaciones de la ostomía intestinal y la piel peristomal. Método: revisión integradora en bases de datos virtuales, incluidos estudios de ensayos clínicos aleatorizados publicados en inglés, español y portugués, de mayo de 2013 a mayo de 2019. Resultados: se seleccionaron 19 estudios y se agruparon en tres categorías: técnicas quirúrgicas que apuntan técnicas innovadoras sobre el tipo de suturas, resección y externalización del asa intestinal, además de refuerzos para prevenir hernias; barreras cutáneas y equipos de recolección, principalmente para abordar las barreras cutáneas para la prevención y el tratamiento de la dermatitis; atención de enfermería que muestra programas de atención y seguimiento, como visitas domiciliarias, consultas y programas educativos. Conclusiones: Las estrategias descritas en los estudios revisados on importantes ya que pueden enriquecer el conocimiento de las enfermeras y, por lo tanto, reducir las complicaciones de la ostomía y la piel peristómica y mejorar la calidad de vida de estas personas.

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Bioelectric Impedance Analysis of Body Composition of Children and Adolescents with Sickle Cell Anemia in Enugu, Nigeria

Pediatric Hematology and Oncology ◽

10.3109/08880018.2015.1010111 ◽

2015 ◽

Vol 32 (4) ◽

pp. 258-268 ◽

Cited By ~ 3

Author(s):

Christopher Bismarck Eke ◽

Bartholomew Friday Chukwu ◽

Anthony Nnaemeka Ikefuna ◽

Osita Uchenna Ezenwosu ◽

Ifeoma Josephine Emodi

Keyword(s):

Body Composition ◽

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Impedance Analysis ◽

Bioelectric Impedance Analysis ◽

Bioelectric Impedance

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Abnormal Pulmonary Function and Associated Risk Factors in Children and Adolescents With Sickle Cell Anemia

Journal of Pediatric Hematology/Oncology ◽

10.1097/mph.0000000000000011 ◽

2014 ◽

Vol 36 (3) ◽

pp. 185-189 ◽

Cited By ~ 30

Author(s):

Manuel Arteta ◽

Andrew Campbell ◽

Mehdi Nouraie ◽

Sohail Rana ◽

Onyinye C. Onyekwere ◽

...

Keyword(s):

Risk Factors ◽

Pulmonary Function ◽

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Associated Risk Factors ◽

Abnormal Pulmonary Function

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Epidemiology and Risk Factors for Pain In Children and Adolescent with Sickle Cell Anemia.

Blood ◽

10.1182/blood.v116.21.1651.1651 ◽

2010 ◽

Vol 116 (21) ◽

pp. 1651-1651 ◽

Cited By ~ 1

Author(s):

Deepika Darbari ◽

Onyinye Onyekwere ◽

Mehdi Nouraie ◽

Gregory J. Kato ◽

Caterina Minniti ◽

...

Keyword(s):

Risk Factors ◽

Confidence Interval ◽

Children And Adolescents ◽

Sickle Cell ◽

Sickle Cell Anemia ◽

Odds Ratio ◽

Severe Pain ◽

History Of ◽

Pain Crisis ◽

Thalassemia Trait

Abstract Abstract 1651 Background: Pain crises are the most common symptom experienced by individuals with sickle cell anemia (SCA). Frequency of pain crises varies significantly and high rate is a risk factor for higher mortality in adults with SCA. The risk factors for pain crises in children and adolescents with SCA are not completely understood. To determine factors associated with frequent severe pain crises, we analyzed the cohort of children and adolescents with SCA who were enrolled in the prospective study “The Pulmonary Hypertension and the Hypoxic Response in SCD (PUSH)”. All children were evaluated in their steady, non-crisis state. Methods: Family-reported history of number of severe pain crises in the preceding 12 months was recorded prospectively in 365 children and adolescents with SCA. Severe pain crises were defined as painful vaso-occlusive episodes requiring evaluation in Emergency Department (ED) or in-patient hospitalization. Lifetime history of red cell transfusions, echocardiography, and laboratory studies were obtained. Clinical and laboratory characteristics of study subjects who had ≥3 severe pain crises in the preceding year were compared to subjects with < 3 severe pain crises. Results: Study subject ranged in age from 3–20 years and 175 (48%) were female. Seventy two children (20 %) had ≥3 severe pain crises in the preceding year (frequent pain crisis group); 293 (80%) children had < 3 severe pain crises (infrequent pain crisis group), including 224 (61%) subjects who had no admissions/ ED visits for pain. Associated factors for frequent pain crisis included older age (odds ratio 1.2; 95% confidence interval 1.12–1.35; P <0.001) and α-thalassemia trait (odds ratio 3.22; 95% confidence interval 1.55–6.69; P =0.002) while higher steady state serum lactate dehydrogenase (LDH) was associated with infrequent pain crisis (odds ratio 0.35; 95% confidence interval 0.13–0.98; P =0.045). In a group of patients without α-thalassemia trait, older age and low LDH were linked to frequent pain crisis. Subjects in the frequent pain crisis group had higher median hemoglobin (9.0 vs. 8.5 gm/dL; p=0.003) and higher ferritin (median 455 vs. 191 ng/mL; p=0.008). Higher ferritin in the frequent pain crisis group was mirrored by the higher percentage who reported >10 lifetime transfusions (42% vs. 22%; p=0.001). Median tricuspid regurgitation jet velocity (TRV) was higher in the frequent pain crisis group (2.41 vs. 2.31; p= 0.001) but the proportion of children with TRV>2.5 was not different (19.4% vs.11.5% in infrequent crises group; p=0.09). Hydroxyurea use was not different between the groups (51% vs. 40%; p=0.08) nor was fetal hemoglobin (10% vs. 12%; p=0.2). Conclusions: The occurrence of severe pain crisis varies among children and adolescents with SCA with a large number of children experiencing no severe painful episodes. Consistent with the Cooperative Study of Sickle Cell Disease report, the risk of severe pain crisis increases with age. Individuals with α-thalassemia trait are likely to experience more frequent pain crises possibly related to higher hemoglobin concentration and viscosity. However, even after controlling for α-thalassemia trait, children and adolescents who reported more frequent severe pain crises showed evidence of less hemolysis, consistent with a hypothetical model associating the hemolytic subphenotype of SCA with less frequent vasoocclusive pain crises. Further studies are indicated to identify the molecular mechanisms of pain in sickle cell anemia. Disclosures: No relevant conflicts of interest to declare.

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