scholarly journals Fibrous Dysplasia of the Temporal Bone

2010 ◽  
Vol 1 (2) ◽  
pp. 121-124
Author(s):  
Baldev Singh ◽  
Prahlad Duggal ◽  
Ruchika Grover

Abstract We report a case of monostotic fibrous dysplasia of temporal bone in a 15-year-old male which presented with mass in the temporomastoid region. There was no associated complaint and patient came only for cosmetic correction of the asymmetry of skull. Conductive hearing loss was an incidental finding on audiogram. Computed tomography showed increased bone thickness with ground glass appearance. Shaded surface display of the skull was used in assessing the external bony deformity. Patient was operated for contouring of the bone and canalplasty which improved the cosmetic appearance as well as corrected the hearing loss thereby avoiding an extensive surgery. Patient is under regular follow-up with good cosmetic and functional results. This case highlights the importance of conservative surgery and regular follow-up in selective cases of temporal bone fibrous dysplasia along with use of shaded surface display for planning the correction of external deformity.

2020 ◽  
pp. 014556132092792
Author(s):  
Kun Zhang ◽  
Peng Qu ◽  
Bing Wang ◽  
Endong Zhang ◽  
Bing Chen

Objective: This article summarizes the experience of diagnosis and treatment of temporal bone fibrous dysplasia (FD) with external auditory canal (EAC) stenosis and secondary cholesteatoma in the Chinese population, in order to improve the quality of life of patients in the future. Methods: Eleven patients with FD of the temporal bone who underwent surgery were retrospectively reviewed. Results: All lesions originated from the temporal bone, and all involved of the EAC. There were 11 cases of cholesteatoma in the EAC, 4 cases of cholesteatoma in the middle ear. The most common symptoms were hearing loss (100%), tinnitus (36.4%), and otorrhea (36.4%). Two patients were severe-profound sensorineural hearing loss, and one patient was complicated with subperiosteal abscesses. All 11 patients underwent surgery. There were no perioperative complications in this series and median follow-up time was 4.2 years. Conclusion: Temporal bone FD remains a rare diagnosis, especially in the Asian population. The lesions mainly lead to stenosis of the EAC, especially at the osteochondral junction. Cholesteatoma is the main complication of this disease, which is secondary to occlusion of the EAC with the growth of the lesion. Canaloplasty of EAC combined with wide meatoplasty can provide excellent prognosis in most cases.


2019 ◽  
Vol 8 (2) ◽  
pp. 1-5
Author(s):  
Adam Roszkowski Roszkowski ◽  
Alicja Witkowska ◽  
Piotr Baranek ◽  
Anna Rzepakowska ◽  
Emilia Wnuk ◽  
...  

Proliferative-inflammatory pathologies may occupy the temporal bone, resulting in: hearing loss, vestibular dysfunction, and neuropathies from cranial nerve compression. Although their occurrence is episodic, the appropriate diagnostic procedure is extremely important to achieve expected therapeutic effect. The aim of study was characterization of selected proliferative-inflammatory pathologies that may occupy the temporal bone: fibrous dysplasia, inflammatory pseudotumor, osteoradionecrosis, and presentation of diagnostic methods for the differentiation of these diseases as well as discussion on appropriate therapeutic options. Fibrous dysplasia (fibrous dysplasia) is a slowly progressive, benign bone disorder of unknown etiology characterized by abnormal proliferation of fibrous tissue. IPT (inflammatory pseudotumor) is a rare, non-malignant inflammatory process of unknown etiology, characterized by connective tissue proliferation and infiltration of inflammatory cells. Osteoradionecrosis of the temporal bone (TB-ORN) is a rare but potentially fatal complication of radiotherapy for head and neck cancer. Due to the similarity of symptoms with typical inflammatory conditions of middle ear (pain, otorrhea, hearing loss), selected disorders may be a dilemma regarding the diagnosis and proper further treatment. The clinical examination is mandatory, however radiological imaging may demonstrate the existence of specific changes and direct the diagnosis. The computed tomography of fibrous dysplasia shows the abnormal organization of the bone structure. Magnetic resonance, as the most sensitive for inflammatory pseudotumors, visualizes inflammatory infiltrates in soft tissues. The spiral tomography of temporal identifies the erosion in the course of osteoradionecrosis. However the final diagnosis may be establish post the histopathological examination and exclusion of the neoplastic process.


1999 ◽  
Vol 113 (8) ◽  
pp. 772-774 ◽  
Author(s):  
J. Xenellis ◽  
A. Bibas ◽  
L. Savy ◽  
P. Maragoudakis ◽  
P. Nomicos

AbstractFibrous dysplasia is a slowly progressive bony disorder where normal bone is replaced by abnormal fibroosseous tissue. Its monostotic variety in the temporal bone is very rare and such a case is presented here. Computed tomography (CT) may be adequate for the diagnosis and follow-up of these patients. Limited surgery should only be considered in cases of symptomatic disease.


1994 ◽  
Vol 73 (5) ◽  
pp. 328-330 ◽  
Author(s):  
Martin J. Donnelly ◽  
Donald P. McShane ◽  
Hugh Burns

Fibrous dysplasia of bone is a benign idiopathic disorder where abnormal fibro-osseous tissue replaces normal bone. The bony abnormalities may be associated with endocrine disorders and abnormal pigmentation of the skin and mucous membranes. Involvement of the temporal bone is a very rare occurrence. We report a case of monostotic fibrous dysplasia of the temporal bone with associated lymphadenopathy. To our knowledge this association has not been previously described in the literature. We also emphasise the need for long term follow up of patients with this condition as cholesteatoma may develop insidiously.


2021 ◽  
Vol 17 (1) ◽  
Author(s):  
Obay Abdul Aziz Edan

Abstract Background A prospective study was conducted on 65 cases with distal hypospadias operated using the urethral mobilization technique between July 2017 and December 2019. Patients with proximal hypospadias and those with distal hypospadias, but with a hypoplastic urethra, were excluded from the study. In this technique, the urethral tube was mobilized proximally in a ratio of 3–4:1 (the ratio of mobilized urethral length to the initial distance between the native meatus and the tip of the glans) then positioned distally after creating wide glans wings. The aim of this study was to assess the outcome of the urethral mobilization technique in distal hypospadias in our center. Results The age of patients was ranged 9 months to 7 years old (mean 37.5 months); 17 (26%) cases were already circumcised. During the postoperative follow-up, 62 (95.4%) patients had a good caliber neomeatus with a good and straight urinary stream; the remaining 3 (4.6%) cases developed meatal stenosis which responded well to urethral dilatation. One (1.5%) patient had a minor retraction of neomeatus but remained within the glans and not requiring further intervention. Four (6%) cases developed minor hematoma which was resolved on conservative measures. Six (9.2%) patients developed minor wound infection which was treated with daily dressing and antibiotic coverage. Conclusion The urethral mobilization technique is a good choice for repairing distal hypospadias especially for boys who are previously circumcised as the preputial flap is not required in this technique. It provides good cosmetic and functional results, with a fewer complication rate.


Author(s):  
C. Bianchi ◽  
N. Auzzi ◽  
I. Turrini ◽  
A. De Magnis ◽  
M. G. Fallani ◽  
...  

Abstract The purpose of this study is to evaluate the efficiency of CO2 laser colposcopic guided surgery performed in an outpatient see and treat setting in the management of VHSIL. Women with a suspected diagnosis of VHSIL and no vulvoscopic suspicion of vSCC were enrolled. An electronic register of CO2 laser treatment was created where description of performing parameters (excision or ablation) was specified and personal history was recorded. Statistical analysis was performed by Fisher’s exact test. Relative risks (RR) of risk factor were calculated and expressed in odds. From September 2014 to September 2018, we enrolled a total of 63 patients who underwent CO2 laser procedure and had a minimum follow-up time of 2 years at Careggi University Hospital in Florence. Forty-eight (76.2%) patients underwent laser excision and 15 (23.8%) patients underwent ablative treatment without histological results. Undertreatment was performed in 3 cases (6.3%) with definitive histology of vSCC. Therapeutical appropriateness of CO2 laser excision was reached in 85.4% of the cases (41/48). No volunteer loss to follow-up was registered; thus, fidelity to treatment was assess at 100%. Recurrence rate within 2 years attested in 8/60 followed patients (13.3%). No personal factor was found to influence the VHSIL course. CO2 laser excision may represent an excellent therapeutic option to VHSIL because it provides adequate oncological purpose with good cosmetic and functional results and high patients’ loyalty to treatment. An expert team could allow to undergo patients with VHSIL suspicion to unique diagnostic and therapeutic procedure with significant benefits.


Author(s):  
Abdul Rehman Khan ◽  
Farzana Siddiqui

<p class="abstract"><strong>Background:</strong> The aim of the study was to determine the effect of interlay tympanoplasty on anterior tympanomeatal angle and on puretone average at 1 month, 6 month and 1 year follow up.</p><p class="abstract"><strong>Methods:</strong> This study was done at department of Otorhinolaryngology, RMRI, Bareilly, India, a tertiary-care Teaching hospital. A total number of 187 patients (86 females, 101 males) were included in this study from April 2014 to March 2018. Age range of selected patients was 15 years to 62 years, 133 patients were having subtotal perforation and remaining having perforation in the anterior half extending upto the annulus.  </p><p class="abstract"><strong>Results:</strong> The anterior tympanomeatal angle blunting and pure tone audiometry (PTA) at the due follow up time was assessed and results were analyzed in terms of angle of blunting and hearing loss detected by PTA. Anterior tympanomeatal angle (ATA) blunting was categorized in three groups as follows &lt;90<sup>o</sup>,90-120<sup>o </sup>and &gt;120<sup>o</sup>. Only 3 patients were having &gt;120<sup>o </sup>ATA after one year and mean hearing loss (air bone gap) was significantly less after 1 year follow up. There were only 3 patients with remnant perforation, after 1 year of surgery out of 187 cases, with 98.4% success rate.</p><p class="p1"><strong>Conclusions:</strong> Interlay tympanoplasty was significantly effective in repairing anterior and subtotal tympanic membrane perforations with avoidance of blunting at the anterior tympanomeatal angle and achieved good functional results. </p>


2021 ◽  
Vol 7 ◽  
Author(s):  
Yibo Zhang ◽  
Feitian Li ◽  
Chunfu Dai ◽  
Wuqing Wang

Purpose: The presence of endolymphatic hydrops (EH) in patients with intralabyrinthine schwannomas (ILSs) is poorly understood. This study aims to determine whether there is a correlation between endolymphatic hydrops and clinical presentations of ILS.Methods: Data from nine patients with ILSs were retrospectively reviewed between 2007 and 2020. Temporal bone MRI with intratympanic or intravenous injection of gadolinium was applied to detect ILSs and EH.Results: 3D real inversion recovery (IR) sequence MRI of the temporal bone confirmed ipsilateral EH in four patients (4/6). All four patients with EH on MRI presented with vertigo similar to Meniere's disease. Among these patients with EH, one patient with EH in the cochlea showed moderate sensorineural hearing loss, while three patients with EH in both the vestibule and cochlea showed profound hearing loss. MRI demonstrated a transmacular tumor (TMA) in one patient, intravestibular (IV) in four patients, and vestibulocochlear (VC) in four patients. Two IV cases showed moderated hearing loss, while the TMA and VC cases showed profound hearing loss. Transotic resection of the tumor was applied in five patients; translabyrinthine resection was applied in one patient; two patients were under observation; and one patient was given intratympanic injection of gentamicin (ITG). During follow-up, all of the treated patients reported relief of vertigo, and postoperative MRI was performed in two patients, which showed no tumor recurrence. The two patients under observation showed no deterioration of hearing loss or vertigo. One patient was lost to follow-up.Conclusion: EH concurrent with ILSs has been underestimated previously. With the extensive application of temporal bone MRI paradigms, such as 3D-real IR sequence MRI, more cases of potential EH in patients with ILS will be identified. The severity of hearing loss may be associated with the location of the tumor and the degree of EH.


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