Dermatofibrosarcoma protuberans. A rare case involving the pediatric foot

1999 ◽  
Vol 89 (8) ◽  
pp. 419-423 ◽  
Author(s):  
JA Cione ◽  
B Lynn ◽  
J Boylan
Keyword(s):  
Rare Case ◽  
Malignant Neoplasm ◽  
Neck Region ◽  
Dermatofibrosarcoma Protuberans ◽  
Surgical Excision ◽  
Head And Neck Region ◽  
Pathologic Features ◽  
Pediatric Foot ◽  
Grade Malignancy ◽  
Slow Growing

Dermatofibrosarcoma protuberans is a rare, slow-growing, locally destructive, intermediate-grade malignancy that originates in the dermal layer of the skin. Dermatofibrosarcoma protuberans rarely metastasizes and has a marked tendency to recur following local surgical excision. The lesion is found most commonly on the trunk, on the proximal aspect of both the lower and upper extremities, and in the head and neck region. Dermatofibrosarcoma protuberans occurs most commonly in people between the ages of 20 and 50. This article describes the clinical and pathologic features of this rare, malignant neoplasm and describes a rare case of dermatofibrosarcoma protuberans involving the pediatric foot.

scholarly journals A rare clinical case: schwannoma of tongue

2019 ◽  
Vol 5 (3) ◽  
pp. 789
Author(s):  
Chandra Veer Singh ◽  
Sheetal Radia ◽  
Saalim Sheikh ◽  
Vijay Haribhakti
Keyword(s):  
Head And Neck ◽  
Rare Case ◽  
Neck Region ◽  
Surgical Excision ◽  
Imaging Studies ◽  
Head And Neck Tumours ◽  
Head And Neck Region ◽  
Complete Surgical Excision ◽  
Slow Growing ◽  
Rule Out

<p class="abstract">Schwannoma are slow growing tumours, which can arise from any peripheral nerve. 10% of schwannomas that occur in the head and neck region mostly originate from the vagus or sympathetic nervous system. Extracranial schwannomas in the head and neck region are rare neoplasm. Intraoral schwannoma are only 1% of the all head and neck tumours. Diagnosis is established by imaging studies such as magnetic resonance imaging or computed tomography, while FNAC is used to rule out other conditions. We report a rare case of lingual schwannomas generally present as a painless lump schwannoma of the tongue in a 27-year-old male complaining of asymptomatic swelling over a posterolateral surface of the tongue, treated by complete surgical excision. The diagnosis was established on the basis of clinical, histopathological, and immunohistochemical examination. We report a rare case of schwannoma over the posterolateral surface of tongue. Prognosis is good for the patient when this condition is correctly diagnosed as the condition rarely recurs after complete resection.</p>

A RARE CASE OF RECURRENT ADENOID CYSTIC CARCINOMA OF THE BUCCAL MUCOSA

2021 ◽  
pp. 1-2
Author(s):  
Surya Rao Rao Venkata Mahipathy ◽  
Alagar Raja Durairaj ◽  
Narayanamurthy Sundaramurthy ◽  
Anand Prasath Jayachandiran ◽  
Suresh Rajendran
Keyword(s):  
Adenoid Cystic Carcinoma ◽  
Buccal Mucosa ◽  
Malignant Neoplasm ◽  
Neck Region ◽  
Surgical Excision ◽  
Minor Salivary Glands ◽  
Head And Neck Region ◽  
Adenoid Cystic ◽  
The Right ◽  
Carcinoma Buccal Mucosa

Adenoid cystic carcinoma is a malignant neoplasm most commonly originating in the minor salivary glands of head and neck region. Among intra oral adenoid cystic carcinoma, buccal mucosa is one of the rarer sites. Here, we report a case of recurrent adenoid cystic carcinoma of the right buccal mucosa in a 33 year old female. As this is an uncommon site for adenoid cystic carcinoma, it should be considered as a differential diagnosis of mass of buccal mucosa. It is imperative that we identify such cases and plan for early surgical excision with adequate margins.

scholarly journals Large-extension osteosarcoma with involvement of multiple maxillofacial structures: a rare case report

2020 ◽  
Vol 9 (10) ◽  
pp. e1519108461
Author(s):  
Rani Iani Costa Gonçalo ◽  
Cristiane Kalinne Santos Medeiros ◽  
Humberto Pereira Chaves Neto ◽  
Janaina Lessa de Moraes dos Santos ◽  
Adriano Rocha Germano ◽  
...  
Keyword(s):  
Rare Case ◽  
Correct Diagnosis ◽  
Malignant Neoplasm ◽  
Neck Region ◽  
Primary Treatment ◽  
Histopathological Diagnosis ◽  
Anatomical Structures ◽  
Case Presentation ◽  
Head And Neck Region ◽  
Rare Case Report

Background: Osteosarcoma is a malignant neoplasm that occurs most often in long bones, with the head and neck region being rarely affected, accounting for less than 1% of all cancers in this region. Objective: To report a rare case of a large-extension osteosarcoma with emphasis on its clinical and diagnostic aspects. Case presentation: A 43-year-old woman presenting an intraoral exophytic lesion with involvement of other maxillofacial structures, such as nostril, zygoma and orbit. Despite the initial clinical diagnosis of actinomycosis, an incisional biopsy confirmed the histopathological diagnosis of osteosarcoma, showing a wide morphological variety. Conclusion: This case highlights the importance of clinical and histopathological findings for the correct diagnosis of osteosarcoma. Moreover, it shows that, although surgical resection is the primary treatment for this neoplasia, depending on the extent of the tumor and its proximity to vital anatomical structures, the most appropriate conduct is not always feasible.

scholarly journals Extremely rare case of retropharyngeal space benign plexiform schwannoma - Excised through Smith- Robinson Approach

2020 ◽  
Vol 11 ◽  
pp. 182
Author(s):  
Rajendra Sakhrekar ◽  
Vishal Peshattiwar ◽  
Ravikant Jadhav ◽  
Bijal Kulkarni ◽  
Sanjiv Badhwar ◽  
...  
Keyword(s):  
Cervical Spine ◽  
Rare Case ◽  
Neck Region ◽  
Retropharyngeal Space ◽  
Case Description ◽  
Head And Neck Region ◽  
Plexiform Schwannoma ◽  
Spine Mr ◽  
The Right ◽  
Slow Growing

Background: Approximately 25–45% of schwannomas are typically slow-growing, encapsulated, and noninvasive tumors that occur in the head-and-neck region where they rarely involve the retropharyngeal space. Here, we report deep-seated benign plexiform schwannoma located in the retropharyngeal C2-C5 region excised utilizing the Smith-Robinson approach. Case Description: A 30-year-old male presented with dysphagia and impaired phonation attributed to an MR documented C2-C5 retropharyngeal schwannomas. On examination, the lesion was soft, deep seated, and extended more toward the right side of the neck. Utilizing a right-sided Smith-Robinson’s approach, it was successfully removed. The histopathology confirmed the diagnosis of a plexiform schwannoma. Conclusion: Retropharyngeal benign plexiform schwannomas are rare causes of dysphagia/impaired phonation in the cervical spine. MR studies best document the size and extent of these tumors which may be readily resected utilizing a Smith-Robinson approach.

scholarly journals Asymptomatic nodule on face: Dermoscopic and histopathological clue for diagnosis

2020 ◽  
Vol 17 (1) ◽  
pp. 63-65
Author(s):  
Anisha Joshi ◽  
Deeptara Pathak Thapa
Keyword(s):  
Head And Neck ◽  
Peripheral Nerves ◽  
Neck Region ◽  
Surgical Excision ◽  
Benign Tumors ◽  
Complete Excision ◽  
Head And Neck Region ◽  
The Common ◽  
Slow Growing ◽  
Rare Diagnosis

Schwannomas/ neurilemmomas are benign tumors of nerve sheath arising from Schwann cells that form myelin sheath around peripheral nerves. They are usually solitary, slow growing and encapsulated lesions. Head and neck are the common sites. We report a case of a 38 years old Nepalese female who had presented with a solitary asymptomatic, slow growing nodule on the left side of the chin for the last three years. Dermoscopy of the lesion revealed arborizing vessels with brownish pigmentation overlying a whitish to pinkish background. Complete excision of the lesion was performed. Histopathological evaluation of the lesion revealed schwannoma. Though schwannomas are a rare diagnosis, they should be considered as a differential diagnosis of any unilateral, asymptomatic, slow growing nodule in the head and neck region. Dermoscopy is a useful tool which helps to differentiate schwannoma from other lesions. Histopathology is the gold standard for diagnosis and the treatment of choice is surgical excision.  

Intramuscular Hemangioma of the sternocleidomastoid muscle: A Rare Unusual Neck Mass

2020 ◽  
Vol 13 (1) ◽  
pp. 78-82
Author(s):  
Brihaspati Sigdel ◽  
Rajesh Maharjhan ◽  
Tulika Dubey ◽  
Bhima Neupane
Keyword(s):  
Head And Neck ◽  
Rare Case ◽  
Neck Region ◽  
Neck Mass ◽  
Sternocleidomastoid Muscle ◽  
Benign Tumors ◽  
Head And Neck Region ◽  
Intramuscular Hemangioma ◽  
Slow Growing ◽  
Extensive Involvement

Hemangiomas of the head and neck region comprise about 60 to 70% of all benign tumors. Intramuscular hemangioma is a rare, slow-growing, angiomatous tumor. We report a rare case of an Intramuscular Hemangioma of Right sternocleidomastoid muscle in a six years old girl presenting for four years and with extensive involvement necessitating excision. Microscopic excision reduces the risk of recurrence.

scholarly journals Malignant Chondroid Syringoma With Nose and Paranasal Sinus Extension: A Case Report

2019 ◽  
Vol 10 ◽  
pp. 215265671989336
Author(s):  
Raghul Sekar ◽  
Raja Kalaiarasi ◽  
Sivaraman Ganesan ◽  
Arun Alexander ◽  
Sunil K. Saxena
Keyword(s):  
Benign Tumor ◽  
Bone Destruction ◽  
Neck Region ◽  
Surgical Excision ◽  
Mixed Tumor ◽  
Head And Neck Region ◽  
Chondroid Syringoma ◽  
Slow Growing ◽  
Nose And Sinuses

Chondroid syringoma is a rare, skin appendageal tumor. It is also known as mixed tumor of skin, as it histologically resembles mixed tumor of salivary gland (pleomorphic adenoma). It is most commonly a benign tumor, but a few malignant counterparts have been described in history. It usually presents as a solid, slow-growing, solitary, and painless nodule in the head and neck region. Malignant counterpart is rare and commonly affects trunk and extremities. Early diagnosis and surgery by wide local excision are the most reliable treatments to date. Recurrences are common and hence close follow-up is advised. In this study, we present a case of malignant chondroid syringoma of face with extensive extension into nose and paranasal sinuses, which was recurrent and managed by surgical excision and radiotherapy. To the best of our knowledge, this is the first reported case with extension and bone destruction into nose and sinuses.

Palatal Schwannoma: A Rare Case Report

2016 ◽  
Vol 8 (1) ◽  
pp. 29-31
Author(s):  
Nikhil Arora ◽  
PS Shahul Hameed
Keyword(s):  
Case Report ◽  
Oral Cavity ◽  
Schwann Cells ◽  
Rare Case ◽  
Benign Tumor ◽  
Neck Region ◽  
Head And Neck Region ◽  
Nerve Sheath ◽  
Rare Case Report ◽  
Slow Growing

ABSTRACT Schwannoma is a benign tumor that originates from perineural Schwann cells of nerve sheath. They are solitary, wellencapsulated, slow-growing adjacent to the parental nerve but extrinsic to the nerve fascicles. Approximately 25 to 45% of all schwannomas are seen in the head and neck region and are found rarely in the oral cavity. Most of the intraoral schwannomas are located in the tongue. Palatal schwannoma is very rare as till date and only 16 cases have been reported; one such rare case we came across is reported here. How to cite this article Hameed PSS, Arora N, Malhotra V. Palatal Schwannoma: A Rare Case Report. Int J Otorhinolaryngol Clin 2016;8(1):29-31.

scholarly journals Giant Lipoma of Posterior Cervical Region

2014 ◽  
Vol 2014 ◽  
pp. 1-2
Author(s):  
Mahendra Singh ◽  
Ashish Saxena ◽  
Lovekesh Kumar ◽  
Snehal K. Karande ◽  
Yuvraj Kolhe
Keyword(s):  
Soft Tissue ◽  
Rare Case ◽  
Neck Region ◽  
Soft Tissue Tumors ◽  
Malignant Potential ◽  
Cervical Region ◽  
Head And Neck Region ◽  
Giant Lipoma ◽  
Benign Nature ◽  
Slow Growing

Lipomas are the slow growing soft tissue tumors of benign nature. They commonly grow on torso and extremities but may also develop in head and neck region. Rarely lipomas can grow to acquire gigantic proportions, turning into an entity termed as giant lipoma. Such lipomas are entitled to immediate attention as they have a relatively high malignant potential. We report a rare case of giant cervical lipoma in an elderly gentleman, followed by a brief discussion on diagnosis and management of the disorder.

scholarly journals Schwannoma Base of Tongue: Report of a Rare Case and Review of Literature

2013 ◽  
Vol 4 (3) ◽  
pp. 133-135 ◽  
Author(s):  
Hitendra Prakash Singh ◽  
SP Agarwal ◽  
Nidhi Verma ◽  
Madhukar Vashistha ◽  
Amit Chaddha ◽  
...  
Keyword(s):  
Rare Case ◽  
Neck Region ◽  
Surgical Excision ◽  
Needle Aspiration ◽  
Review Of Literature ◽  
Complete Excision ◽  
Base Of Tongue ◽  
Magnetic Resonance Imaging Mri ◽  
Needle Aspiration Cytology ◽  
Slow Growing

ABSTRACT Schwannomas or neurilemmomas are benign, slow growing, usually solitary and encapsulated tumor, originating from Schwann cells of the nerve sheath. Extracranially, 25% of all schwannomas are located in the head and neck region. The intraoral lesions show a predilection for the tongue, followed by the palate, buccal mucosa, lips and gingiva respectively. Among these, base of tongue schwannoma are extremely rare. Schwannomas involving the tongue base remain asymptomatic unless they attain appreciable size. Diagnostic investigations include ultrasound scanning, computed tomography, magnetic resonance imaging (MRI), and fine-needle aspiration cytology. MRI is superior to other imaging modalities for the examination of the base of the tongue. The definitive diagnosis is based on histopathology. Surgical excision or enucleation with preserve nerve function is the treatment of choice for this rare tumor. The most common approach for complete excision is transoral route for base of tongue schwannoma. Authors report a case of base of tongue schwannoma which was treated with surgery by transoral route. How to cite this article Singh HP, Kumar S, Verma N, Vashistha M, Chaddha A, Agarwal SP, Babu S. Schwannoma Base of Tongue: Report of a Rare Case and Review of Literature. Int J Head Neck Surg 2013;4(3):133-135.

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