Fanconi-Bickel syndrome - the original patient and his natural history, historical steps leading to the primary defect, and a review of the literature

1998 ◽  
Vol 157 (10) ◽  
pp. 783-797 ◽  
Author(s):  
R. Santer ◽  
R. Schneppenheim ◽  
D. Suter ◽  
J. Schaub ◽  
B. Steinmann
Keyword(s):  
Natural History ◽  
Review Of The Literature ◽  
Primary Defect

Clinical Features, Natural History and Outcomes of Intraneural Perineuriomas: A Systematic Review of the Literature

2021 ◽  
Author(s):  
Karina A. Lenartowicz ◽  
Anshit Goyal ◽  
Michelle L. Mauermann ◽  
Thomas J. Wilson ◽  
Robert J. Spinner
Keyword(s):  
Systematic Review ◽  
Natural History ◽  
Clinical Features ◽  
Review Of The Literature

scholarly journals P.014 The natural history of third ventricle colloid cysts includes asymptomatic regression: a report of two cases and review of the literature

2017 ◽  
Vol 44 (S2) ◽  
pp. S17-S17
Author(s):  
R Bokhari ◽  
J Chankowsky ◽  
J Marcoux
Keyword(s):  
Natural History ◽  
Third Ventricle ◽  
Symptomatic Patient ◽  
Review Of The Literature ◽  
Indication For Surgery ◽  
Asymptomatic Patients ◽  
Signal Characteristics ◽  
History Of ◽  
Colloid Cysts

Background: Colloid cysts of the third ventricle are a rare entity with an unclear natural history. Although intervening in the setting of a symptomatic patient is fairly straightforward, decision-making for asymptomatic patients is not. Few studies address this question and proposed risk factors for cyst progression vary.A cyst diameter exceeding 1 cm is a common indication for surgery. This is rooted in the belief that the natural history is continued growth. A few cases have recently surfaced that suggests some cysts may spontaneously regress without complication. We describe our experience with two such cases and contrast it with those of others. Methods: We collected all cases of “colloid cysts” identified as incidental findings on Brain CT scans in a large urban center with available follow-up. We then conducted a comprehensive review of the literature. Results: Among all incidental cases from our database, none required surgery and two were found to decrease in size on neuroimaging surveillance with interesting evolution in MRI signal characteristics. These cysts remain asymptomatic at last follow up. Conclusions: The natural history of colloid cysts includes spontaneous regression. This should be mentioned in counseling asymptomatic patients.

Pleomorphic adenoma of the external auditory canal: a case report and review of the literature

1996 ◽  
Vol 110 (1) ◽  
pp. 52-56 ◽  
Author(s):  
Hidetoshi Haraguchi ◽  
Hitoshi Hentona ◽  
Hidekazu Tanaka ◽  
Atsushi Komatuzaki
Keyword(s):  
Case Report ◽  
Natural History ◽  
Pleomorphic Adenoma ◽  
Clinical Features ◽  
External Auditory Canal ◽  
World Wide ◽  
Review Of The Literature ◽  
The World ◽  
History Of ◽  
Uncommon Tumour

AbstractPleomorphic adenoma arising in the external auditory canal is rare. We report the case of a 38-year-old man. To better grasp the clinical features and natural history of this uncommon tumour, we also reviewed the world wide literature and found 24 similar cases, which we analysed together with our own.

Malignant melanoma arising in the frontal sinuses

1997 ◽  
Vol 111 (4) ◽  
pp. 376-378 ◽  
Author(s):  
Samuel M. Jayaraj ◽  
Jonathan D. Hern ◽  
George Mochloulis ◽  
Graham C. Porter
Keyword(s):  
Malignant Melanoma ◽  
Natural History ◽  
Nasal Cavity ◽  
Paranasal Sinuses ◽  
Frontal Sinus ◽  
Poor Prognosis ◽  
Review Of The Literature ◽  
History Of ◽  
Frontal Sinuses ◽  
Sinonasal Malignant Melanoma

AbstractSinonasal malignant melanoma is rare and usually occurs in the nasal cavity. Presentation is often varied and occurs late in the natural history of the disease, resulting in a poor prognosis. A case is reported of a patient with malignant melanoma arising from the frontal sinus who presented with a forehead swelling and progressive confusion. A review of the literature on malignant melanoma in the nasal cavity and paranasal sinuses regarding its presentation, site of origin and principles of management is discussed.

Idiopathic Avascular Necrosis of the Scaphoid

1994 ◽  
Vol 19 (2) ◽  
pp. 174-182 ◽  
Author(s):  
T. J. HERBERT ◽  
M. LANZETTA
Keyword(s):  
Natural History ◽  
Avascular Necrosis ◽  
Rare Condition ◽  
Staging System ◽  
Ulnar Variance ◽  
Review Of The Literature ◽  
Proximal Pole ◽  
Preiser’S Disease

Idiopathic avascular necrosis of the scaphoid is a rare condition. A review of the literature shows a variety of conditions labelled as spontaneous avascular necrosis or Preiser’s disease. In this paper we report on a study of eight patients with idiopathic avascular necrosis affecting only the proximal pole of the scaphoid. Seven of these patients had positive ulnar variance. The possible aetiology is discussed and the natural history has been studied. A staging system is proposed, as this helps to determine the prognosis and appropriate management. Two of our patients were managed conservatively; the others were treated successfully by partial silastic replacement of the scaphoid

Beetles feeding on bugs (Coleoptera, Hemiptera): repeated shifts from mycophagous ancestors

2000 ◽  
Vol 14 (6) ◽  
pp. 917 ◽  
Author(s):  
Richard A. B. Leschen
Keyword(s):  
Natural History ◽  
Prey Type ◽  
Host Shift ◽  
Review Of The Literature ◽  
Phylogenetic Information ◽  
History Data ◽  
Number Of Species ◽  
Annotated List ◽  
Sooty Moulds

A review of the literature shows that predation on Hemiptera (mainly Sternorrhyncha) by Coleoptera is widespread in the order, but little understood, even from a biocontrol perspective. Phylogenetic information indicates that feeding on hemipterans evolved predominantly in lineages containing fungus feeders (Derodontidae, Silvanidae, Laemophloeidae, Nitidulidae, Endomychidae, Anthribidae) and whose ancestors were fungus feeders (Coccinellidae) or were sap feeders (cetoniine Scarabaeidae). Other predators on Hemiptera whose ancestry could not be determined unequivocally (predatory/phytophagy or phytophagy/mycophagy) are included in families that contain a large number of species that are mycophagous (Trogossitidae, Mycetophagidae, and Salpingidae). Because changes in diet to feeding on hemipterans have repeatedly occurred in mycophagous taxa, and this shift is not present in other largely predatory groups of beetles, it is presumed that certain preconditions, which have promoted this specialised behaviour, only exist in these lineages. Ancestral associations with sooty moulds that grow on honeydew may have mediated shifts from mycophagy to predation, rather than having ancestors that were predatory and attracted to a novel prey type. Natural history data show that species that prey on Hemiptera also feed on honeydew and sooty moulds and a model is presented for the host shift from mycophagy to feeding on Hemiptera. An annotated list of Hemiptera prey for beetles (exclusive of Coccinellidae) includes records for species in the families Adelgidae, Aleyrodidae, Aphididae, Coccidae, Diaspididae, Kermesidae, Kerriidae, Margarodidae, Membracidae, Phoenicococcidae, and Pseudococcidae.

scholarly journals Eccrine Porocarcinoma: A Case Report and Review of the Literature

2003 ◽  
Vol 11 (3) ◽  
pp. 153-156 ◽  
Author(s):  
Mark Sheldon Lloyd ◽  
Naguib El-Muttardi ◽  
A Robson
Keyword(s):  
Case Report ◽  
Skin Cancer ◽  
Natural History ◽  
Current Literature ◽  
Typical Case ◽  
Pathological Findings ◽  
Review Of The Literature ◽  
Rare Form ◽  
Skin Malignancy ◽  
Eccrine Porocarcinoma

Eccrine porocarcinoma is a rare form of skin cancer that is often con-fused with other types of skin malignancy The present paper high-lights a typical case to remind plastic surgeons of the natural history, pathological findings and current literature on the management of this cancer.

scholarly journals Intracerebral schwannomas: a rare disease with varying natural history

2013 ◽  
Vol 12 (1) ◽  
pp. 6-12 ◽  
Author(s):  
William W. Scott ◽  
Korgun Koral ◽  
Linda R. Margraf ◽  
Laura Klesse ◽  
David J. Sacco ◽  
...  
Keyword(s):  
Natural History ◽  
Aggressive Behavior ◽  
Rare Disease ◽  
Case Reports ◽  
Intracranial Tumors ◽  
Review Of The Literature ◽  
Rare Tumors ◽  
Small Series ◽  
The Difference

Although intracerebral schwannomas are typically regarded as benign intracranial tumors, malignancy and recurrence have been reported among patients harboring such neoplasms. The available literature consists of case reports and small series that present variable characteristics distinguishing these unusual lesions. Little advancement has been made to further the understanding and management of these tumors. The authors present 3 cases from their institution that highlight the difference between typical benign intracerebral schwannomas and histopathological variants that may portend more aggressive behavior. Also provided is a review of the literature in the hope of gaining a better understanding of these rare tumors.

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