Primary Renal BCOR-CCNB3 Fusion Sarcoma: A Case Report and Review of the Literature
Keyword(s):
<i>BCOR-CCNB3</i> fusion sarcoma is a recently described undifferentiated sarcoma with a novel recurrent inversion of 2 nearby genes <i>BCOR</i> and <i>CCNB3</i>. It typically affects bone and soft tissues of the pelvis, extremity, and paraspinal region and pursues variable clinical course. Primary renal <i>BCOR-CCNB3</i> fusion sarcoma is very rare, and only a small number of cases have been documented. Accurate diagnosis is often challenging, and there is not any agreement for the treatment of this entity due to its rarity. We report findings of primary renal <i>BCOR-CCNB3</i> fusion sarcoma in a 16-year-old boy with a brief review of the literature.
2015 ◽
Vol 24
(2)
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pp. 235-239
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2004 ◽
Vol 128
(2)
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pp. 210-213
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2005 ◽
Vol 129
(10)
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pp. 1322-1325
1998 ◽
Vol 77
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pp. 51-55
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2012 ◽
Vol 16
(6)
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pp. 438-441
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2018 ◽
Vol 30
(6)
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pp. 951-954
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