scholarly journals Rare Tumors of the Thyroid

2021 ◽  
pp. 149-154
Author(s):  
Murat Ozdemir ◽  
Özer Makay
Keyword(s):  
Rare Tumors

Proteomics of Pancreatic Neuroendocrine Tumors: A Systematic Review

2020 ◽  
Vol 27 (12) ◽  
pp. 1276-1287
Author(s):  
Brigida Anna Maiorano ◽  
Giovanni Schinzari ◽  
Sabrina Chiloiro ◽  
Felicia Visconti ◽  
Domenico Milardi ◽  
...  
Keyword(s):  
Systematic Review ◽  
Neuroendocrine Tumors ◽  
Prognostic Markers ◽  
State Of The Art ◽  
Therapeutic Targets ◽  
The State ◽  
Pancreatic Neuroendocrine Tumors ◽  
Rare Tumors ◽  
Personalized Approach ◽  
Future Management

Pancreatic neuroendocrine tumors (PanNETs) are rare tumors having usually an indolent behavior, but sometimes with unpredictable aggressiveness. PanNETs are more often non-functioning (NF), unable to produce functioning hormones, while 10-30% present as functioning (F) - PanNETs, such as insulinomas , gastrinomas , and other rare tumors. Diagnostic and prognostic markers, but also new therapeutic targets, are still lacking. Proteomics techniques represent therefore promising approaches for the future management of PanNETs. We conducted a systematic review to summarize the state of the art of proteomics in PanNETs. A total of 9 studies were included, focusing both on NF- and F-PanNETs. Indeed, proteomics is useful for the diagnosis, the prognosis and the detection of therapeutic targets. However, further studies are required. It is also warranted to standardize the analysis methods and the collection techniques, in order to validate proteins with a relevance in the personalized approach to PanNETs management.

scholarly journals Successful implementation of an international desmoid tumor virtual tumor board: A novel platform for the management of rare tumors

Rare Tumors ◽  
2020 ◽  
Vol 12 ◽  
pp. 203636132098453
Author(s):  
Aaron R Weiss ◽  
Marlene Portnoy ◽  
Jeanne Whiting ◽  
Palma Dileo
Keyword(s):  
Desmoid Tumor ◽  
Tumor Board ◽  
Successful Implementation ◽  
Rare Tumors

Randomized trials in rare tumors.

1985 ◽  
Vol 3 (9) ◽  
pp. 1163-1165
Author(s):  
J F Holland
Keyword(s):  
Randomized Trials ◽  
Rare Tumors

scholarly journals Intralabyrinthine Schwannomas: Disease Presentation, Tumor Management, and Hearing Rehabilitation

2019 ◽  
Vol 80 (02) ◽  
pp. 196-202 ◽  
Author(s):  
Baishakhi Choudhury ◽  
Matthew Carlson ◽  
Daniel Jethanamest
Keyword(s):  
Magnetic Resonance Imaging ◽  
Hearing Loss ◽  
Magnetic Resonance ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Resonance Imaging ◽  
Hearing Rehabilitation ◽  
Rare Tumors ◽  
Auditory Rehabilitation ◽  
Tumor Management

AbstractIntralabyrinthine schwannomas (ILS) are rare tumors that frequently cause sensorineural hearing loss. The development and increased use of magnetic resonance imaging in recent years have facilitated the diagnosis of these tumors that present with otherwise nondiscriminant symptoms such as tinnitus, vertigo, and hearing loss. The following is a review of the presentation, pathophysiology, imaging, and treatment with a focused discussion on auditory rehabilitation options of ILS.

Malignant transformation of spinal meningeal melanocytoma

2007 ◽  
Vol 6 (5) ◽  
pp. 451-454 ◽  
Author(s):  
Fulin Wang ◽  
Xianghong Li ◽  
Linghong Chen ◽  
Xiaolu Pu
Keyword(s):  
Radiation Therapy ◽  
Malignant Melanoma ◽  
Malignant Transformation ◽  
Gross Total Resection ◽  
Pertinent Literature ◽  
Total Resection ◽  
Meningeal Melanocytoma ◽  
Rare Tumors ◽  
Subcutaneous Metastases

✓Meningeal melanocytomas are rare tumors and malignant transformation of these lesions is even rarer. The authors report on a case of a 57-year-old man who presented with a melanocytoma located at the L5–S1 level. After gross-total resection of the tumor, it recurred 1 year later as a malignant melanoma. In addition, multiple subcutaneous metastases were found at that time. The patient was treated with radiation therapy (5000 cGy). Five months later metastases in the liver and the left ninth rib were discovered. The pertinent literature is reviewed and disease criteria are presented to distinguish meningeal melanocytoma from malignant melanoma and from meningiomas or schwannomas containing melanotic pigment. Patients and investigators should be cautioned that a meningeal melanocytoma may recur and transform into a malignant melanoma.

scholarly journals The European Paediatric Rare Tumours Network ‐ European Registry (PARTNER) project for very rare tumors in children

2021 ◽  
Author(s):  
Daniel Orbach ◽  
Andrea Ferrari ◽  
Dominik T. Schneider ◽  
Yves Reguerre ◽  
Jan Godzinski ◽  
...  
Keyword(s):  
Rare Tumors ◽  
European Paediatric ◽  
Rare Tumours ◽  
European Registry

scholarly journals Rare Tumors Through the Looking Glass

2011 ◽  
Vol 147 (9) ◽  
pp. 1058 ◽  
Author(s):  
Steve R. Martinez
Keyword(s):  
Rare Tumors ◽  
Looking Glass

Current Management of Lesions of the Pediatric Larynx

1987 ◽  
Vol 96 (1) ◽  
pp. 122-123 ◽  
Author(s):  
Gerald B. Healy
Keyword(s):  
Carbon Dioxide ◽  
Treatment Regimen ◽  
Carbon Dioxide Laser ◽  
Pediatric Anesthesia ◽  
Subglottic Stenosis ◽  
Current Management ◽  
Current Technology ◽  
Rare Tumors

A variety of congenital and acquired lesions of the larynx are now managed effectively with the use of the carbon dioxide laser. This instrument seems to be the most effective of all available lasers for this type of therapy. Argon and neodymium:yttrium aluminum garnet lasers do not appear appropriate for such lesions for several reasons. On occasion, patients with congenital and acquired subglottic stenosis, as well as those afflicted with rare tumors of the larynx, require open procedures as part of their treatment regimen. The need for appropriate equipment and competent pediatric anesthesia is paramount when undertaking cases of this type. These patients offer unique challenges to a laryngologist, but correction of their problems is effectively managed by appropriate application of current technology.

Pathologic Evaluation of Soft Tissue Sarcoma

2017 ◽  
Author(s):  
Narasimhan P. Agaram
Keyword(s):  
Soft Tissue ◽  
Tertiary Care ◽  
Soft Tissue Sarcomas ◽  
Molecular Diagnostic ◽  
Nerve Sheath Tumor ◽  
Rare Tumors ◽  
Pathologic Evaluation ◽  
Nerve Sheath ◽  
Different Types ◽  
Tertiary Care Centers

Soft tissue sarcomas are rare tumors and are mostly managed in tertiary care centers. They are broadly classified based on their differentiation into multiple different types. They affect patients of all ages and mostly occur in the extremities. Pathologic examination of the biopsy or resection of the tumor is an extremely important aspect in the diagnosis of these tumors and appropriately guiding the clinical team in the management of these rare tumors. This review focuses on the aspects of pathologic evaluation of these tumors and discusses the morphologic aspects of the predominant soft tissue sarcomas based on differentiation. The review also highlights the latest molecular diagnostic studies that are used in the accurate subtyping of these tumors.  This review contains 12 figures, 2 tables, and 28 references. Key words: angiosarcoma, fibromatosis, fibrous, liposarcoma, myxoid, nerve sheath tumor, sarcoma, synovial sarcoma

Sign in / Sign up

Export Citation Format

Share Document